Ngati muli ndi vuto la nthawi yayitali, kapena losatha, monga matenda obadwa nawo a ATTR amyloidosis, muyenera gulu lalikulu la madokotala ndi akatswiri azaumoyo kuti akuthandizeni kuthana nalo. Izi ndi zoona makamaka kwa anthu omwe ali ndi hATTR amyloidosis. Imeneyi ndi vuto la majini. Chomwe chimachitika ndichakuti puloteni yosadziwika bwino yotchedwa amyloid imasonkhana m'ziwalo zofunika monga mtima wanu, impso, mitsempha, ndi matumbo. Chifukwa chake, chifukwa vutoli limakhudza ziwalo zambiri za thupi lanu, gulu lanu lazaumoyo la hATTR lidzaphatikizapo akatswiri angapo.
Ndani ali m'gulu lanu lachipatala la hATTR amyloidosis?
Tiyeni tsopano tiwone akatswiri azachipatala ofunikira omwe angakuthandizeni pa chisamaliro chanu chaumoyo. Pamodzi, adzakuthandizani kusamalira bwino vuto lanu.
Katswiri wa za ubongo
Mu hATTR, vuto lotchedwa peripheral neuropathy ndi lofala kwambiri. Mwachidule, izi ndi kuwonongeka kwa mitsempha m'manja, m'mapazi, ndi m'miyendo. Mutha kukumana ndi zizindikiro monga izi:
Pamene matendawa akupitirira, minofu yanu ikhoza kuuma ndi kufooka, zomwe zimapangitsa kuti zikhale zovuta kuyenda ndikuchita chilichonse chomwe chimafuna luso loyendetsa bwino thupi.
Katswiri wa mitsempha adzachita mayeso, monga mayeso oyendetsera mitsempha, kuti ayang'anire bwino momwe mitsempha yanu imagwirira ntchito. Izi zidzakuthandizani kudziwa ngati muli ndi vuto la mitsempha komanso momwe lilili loopsa.
Mankhwala ambiri ovomerezeka a hATTR angathandizenso kuchiza matenda anu amitsempha. Dokotala wanu angakupatseninso mankhwala ena othandizira kupweteka kwa mitsempha.
| Gulu la mankhwala | Zitsanzo za mankhwala osokoneza bongo |
|---|---|
| Mankhwala ovomerezeka a hATTR | Eplontersen (Wainua), Inotersen (Tegsedi), Patsiran (Onpattro), Vutrisiran (Amvuttra) |
| Mankhwala ochizira ululu wa mitsempha | Amitriptyline, Duloxetine (Cymbalta), Gabapentin (Neurontin), Pregabalin (Lyrica) |
Katswiri wa mtima
Dokotala uyu amachiritsa matenda a mtima ndi mitsempha yamagazi. Anthu omwe ali ndi hATTR ali pachiwopsezo chachikulu cha matenda a mtima. Izi zili choncho chifukwa chakuti amyloid deposits imatha kudziunjikira mumtima. Izi zingayambitse matenda awa:
Chofunika kwambiri ndikudziwa zizindikiro izi ndikupempha upangiri wa dokotala mwamsanga ngati pakufunika kutero.
| Zotsatira zomwe zingachitike pamtima | Kufotokozera kosavuta |
|---|---|
| Kulephera kwa Mtima Wodzaza ndi Mitsempha | Mtima umafooka ndipo madzi amasonkhana m'mapapo ndi minofu ina. |
| Hypertrophic Cardiomyopathy | Kukhuthala kwa minofu ya mtima. |
| Matenda a Mtima wa Mitsempha | Kutsekeka kwa mitsempha yamagazi yomwe imapereka magazi ku mtima. |
| Kusakhazikika kwa mtima (arrhythmia) | Kugunda kwa mtima kosakhazikika. |
| Kusinthasintha kwa chibadwa | Chizungulire kapena kukomoka. |
Ngati mwapezeka ndi hATTR, dokotala wanu wa mtima adzakuyesani mayeso angapo kuti aone momwe mtima wanu ukugwira ntchito. Izi zingaphatikizepo echocardiogram , MRI scan, mayeso oyenda kwa mphindi 6, ndi mayeso a magazi. Ngati mtima wanu uli wofooka, mudzapatsidwa mankhwala ochiritsira vutoli, monga diuretics, mchere ndi madzi oletsa, komanso mwina pacemaker .
Dokotala wa maso
Ngati muli ndi hATTR, ndikofunikira kukaonana ndi dokotala wa maso nthawi zonse. Pafupifupi 20% ya kusintha kwa majini komwe kumayambitsa hATTR kumakhudza maso. Izi zingayambitse zizindikiro monga:
- Ma dark floating (kuona madontho akuda akuyandama patsogolo pa maso)
- Maso ouma
- Glaucoma kapena kuthamanga kwa magazi m'maso
- Kusawoneka bwino kwa ma vitreous (kupindika kwa gel yoyera yomwe imadzaza diso)
- Kusintha kwina kwa masomphenya
Ngati pakufunika kutero, dokotala wanu wa maso angachite opaleshoni yotchedwa trabeculectomy kuti athetse glaucoma. Angachitenso opaleshoni yotchedwa vitrectomy kuti achotse gel m'diso.
Mlangizi wa Majini
Ngati dokotala wanu akukayikira kuti muli ndi hATTR, adzakutumizani kwa katswiri wa majini . Akhoza kuyesa kusintha kwa majini komwe kungayambitse matendawa. Komanso, ngati wina m'banja mwanu (kholo, m'bale, kapena mwana) wapezeka ndi hATTR, muyenera kuyezetsa. Izi zili choncho chifukwa achibale anu ali ndi mwayi wa 50% wolandira kusintha kwa majini kumeneku. Mlangizi wa majini adzakufotokozerani mayesowa ndikukambirana nanu zotsatira zake zikangopezeka.
Anthu ena ofunikira mu gulu lanu lachipatala
Kuwonjezera pa akatswiri omwe atchulidwa pamwambapa, ena ambiri amachita mbali yofunika kwambiri pa thanzi lanu.
| Katswiri | Kodi angakuthandizeni bwanji? |
|---|---|
| Dokotala wa matenda a minyewa | Pafupifupi gawo limodzi mwa magawo atatu a anthu omwe ali ndi hATTR akhoza kukhala ndi amyloid deposits mu impso zawo. Simungafunike kuonana ndi katswiriyu mpaka mutapeza zizindikiro za matenda a impso. Dokotala wanu wamkulu adzayang'ana momwe impso zanu zimagwirira ntchito poyesa magazi chaka chilichonse (monga serum creatinine ). Ngati mayesowa ndi osazolowereka, mudzatumizidwa kwa katswiri wa matenda a impso. |
| Katswiri wa Mafupa | Odwala omwe ali ndi hATTR ali pachiwopsezo chachikulu chotenga matenda a carpal tunnel syndrome . Izi zitha kuchitika chifukwa cha kuyika kwa amyloid m'manja. Ma splints a dzanja ndi masewera olimbitsa thupi angalimbikitsidwe akagona. Pa milandu yovuta kwambiri, opaleshoni ingafunike. |
| Katswiri Wothandizira Pantchito/Kulimbitsa Thupi | hATTR ingapangitse kuti kuyenda ndi kuchita zinthu za tsiku ndi tsiku zikhale zovuta. Akatswiri a zamaganizo ndi akatswiri a zamaganizo angakuthandizeni kuti ntchitozi zikhale zosavuta. Kafukufuku wasonyeza kuti kuphatikiza njirazi ndi njira zina zochiritsira, monga mankhwala, kungapangitse zotsatira zabwino. |
| Wopereka Chisamaliro Choyamba | Ngakhale mutakumana ndi akatswiri ambiri, dokotala wa banja lanu kapena dokotala wothandiza kwambiri ndi gawo lofunika kwambiri la gulu lanu. Iye akhoza kukuyezani thanzi lanu pachaka, kukuthandizani mukadwala, komanso kukhala "mtsogoleri" wa gulu lanu lazachipatala, kulankhulana ndi madokotala ena onse. |
Kawirikawiri, mudzatha kupeza chithandizo chonse chomwe mukufuna kuchipatala kapena kuchipatala chachikulu chomwe chimagwira ntchito yochiza matenda a hATTR amyloidosis. Izi zimapangitsa kuti madokotala anu onse azigwira ntchito limodzi ngati gulu. Lankhulani ndi dokotala wanu wamkulu za kugwirizanitsa chithandizo chanu.
Uthenga Wopita Nawo Kunyumba
- Matenda a hATTR amyloidosis ndi matenda ovuta omwe amakhudza ziwalo zingapo m'thupi, kotero amafunika gulu la madokotala omwe ali ndi luso losiyanasiyana kuti awachiritse.
- Gulu lanu lachipatala likhoza kuphatikizapo akatswiri m'magawo monga matenda a mitsempha, matenda a mtima, matenda a maso, ndi matenda a nephrology.
- Dokotala wanu wamkulu (dokotala wa banja) ndiye chigwirizano chofunikira chomwe chimagwirizanitsa gulu lonseli.
- Kambiranani momasuka ndi gulu lanu la zachipatala za matenda anu, chithandizo chanu, ndi nkhawa zilizonse zomwe mungakhale nazo. Musaope kufunsa mafunso. Ndinu membala wokangalika wa gulu lanu lazaumoyo.
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