Mwana wako mudiki anogara achineta here? Anoita seane dambudziko rekufema here? Dzimwe nguva ganda rake rinotaridzika sebhuruu here? Kunyange zvazvo izvi zvichiwanzova zvakajairika, dzimwe nguva zvinogona kunge zvichikonzerwa nedambudziko remwoyo raakaberekwa naro. Nhasi tichataura nezvechimwe chirwere chemwoyo chisingawanzoitiki asi chakakosha. Chinonzi Ebstein's Anomaly.
Chii chaizvo chinonzi Ebstein's Anomaly?
Zvichitaurwa zviri nyore, ichi chirwere chemwoyo chekuzvarwa nacho. Kureva kuti, chikanganiso mumoyo chinokura mwana achiri mudumbu. Mwoyo wedu une makamuri mana, makamuri maviri epamusoro nemakamuri maviri epasi. Pakati pemakamuri aya pane mavharuvhu anoshanda semasuo. Aya anodzora kuyerera kweropa munzira imwe chete.
Dambudziko reEbstein's Anomaly rinonyanya kukanganisa vharuvhu yetricuspid, iri pakati pekamuri repamusoro (right atrium) nekamuri rezasi (right ventricle) kurudyi kwemoyo. Zvinhu zviviri zvikuru zvinoitika kana munhu arwara neizvi:
1. Vharuvhu iri rakaiswa zvisirizvo: Vharuvhu iyi ine tricuspid iri pasi zvakanyanya kupfuura zvayaifanira kuva, mukamuri rezasi rekurudyi.
2. Mapepa evharuvhu haana kuumbwa zvakanaka: Mapepa evharuvhu haana chimiro chakajairwa. Dzimwe nguva anogona kutonamatira pamadziro emwoyo.
Funga nezvezvinoitika kana gonhi rikasavharwa zvakanaka. Saizvozvowo, nekuti vharuvhu iyi haivharwe zvakanaka, ropa rinoda kupombwa kubva mukamuri repasi rinodzokera mukamuri repamusoro.
Izvi zvinoita kuti imba yepamusoro iri kurudyi rwemoyo ikure. Uyewo, imba yepasi, ine vharuvhu iri pasi, haina nzvimbo yakawanda yekushanda zvakanaka. Nekufamba kwenguva, iyi nzvimbo yekurudyi yakakura yemoyo inogona kupera simba uye kutokonzera kutadza kushanda kwemoyo .
Dambudziko iri haribate vana vese nenzira imwe chete. Vamwe vanogona kunge vaine zviratidzo zvisina kunyanya kuipa, nepo vamwe vangave nezviratidzo zvakakomba.
Kazhinji, vana vane `Ebstein's Anomaly` vane mamwe matambudziko emwoyo. Anonyanya kuitika iburi riri pakati pemakamuri maviri epamusoro emwoyo. Izvi zvinonzi `(Atrial Septal Defect - ASD )`.
Ndezvipi zviratidzo zvechirwere ichi?
Zviratidzo zvakasiyana-siyana. Dzimwe nguva, kana chirwere chacho chakanyanya kuipa, zviratidzo zvinogona kuonekwa mukati memazuva mashoma ekuzvarwa. Zvisinei, kana chirwere chacho chisina kunyanya kuipa, panogona kunge pasina zviratidzo zvachose kusvika pakukura.
| Mukana | Zviratidzo zvakajairika |
|---|---|
| Vacheche (zviitiko zvakakomba) |
|
| Vana vakuru nevadiki |
|
Sei izvi zvichiitika? Chikonzero chacho ndechei?
Kutaura zvazviri, zvinowanzova zvakaoma kuwana chikonzero chaicho cheizvi. Asi vanachiremba vanotenda kuti shanduko dzemajini dzinogona kuita basa. Kunewo fungidziro yekuti kusangana nemishonga yakadai se lithium kana benzodiazepines panguva yekuzvitakura kunogonawo kukonzera njodzi diki. Asi izvi zvichiri muchikamu chekutsvagisa.
Chiremba anowana sei izvi? (Kuongororwa)
Kana mwana wako aine zviratidzo izvi, chiremba achatanga amuongorora nokungwarira. Zvadaro, vanogona kuraira bvunzo dzinoverengeka kuti vaone kuti mwoyo uri kushanda sei chaizvo.
- Echocardiogram: Iyi ndiyo bvunzo inonyanya kukosha. Kufanana nekuongororwa kwemwana ari mudumbu neultrasound, inotora mufananidzo wakadzama wemoyo. Inogona kuratidza kuti mavharuvhu ari kupi, chimiro chawo, kana ropa riri kudonha richidzokera kumashure, kuti makamuri emwoyo akakura sei, uye kuti akakura sei.
- Electrocardiogram (EKG): Iyi inoyera mashandiro emagetsi emwoyo. Izvi zvinobatsira kuona kurova kwemoyo kusina kurongeka (arrhythmias).
- MRI yemwoyo: Izvi zvinogona kuburitsa mifananidzo yakajeka yemoyo nemavharuvhu. Izvi zvakakosha zvikuru mumamiriro ezvinhu akadai seasati avhiyiwa.
- Kuedzwa Kwekushushikana Kwekurovedza Muviri: Kune vana vakuru, EKG inoitwa pavanenge vachifamba patreadmill. Izvi zvinobatsira kuona kuti mwoyo unoita sei kana munhu achiedza.
- Holter Monitor: Ichi chishandiso chidiki chinopfekwa mumuviri kwemaawa makumi maviri nemana kusvika makumi mana nemasere. Chinonyora kurova kwemoyo mukati mezuva uye chinoshandiswa kuona chero kurova kwemoyo kusina kurongeka kunoitika masikati.
Ndezvipi zvinorapwa izvi?
Kurapwa kunoenderana nekuoma kwechirwere uye zviratidzo zvemwana.
Kurapa nemishonga
Kana zviratidzo zvacho zvisiri zvakanyanya, chiremba anogona kusarudza kutarisa mamiriro emwana. Kana paine zviratidzo zvekukundikana kwemoyo, vanogona kupa mishonga inobatsira moyo kuti ushande zvakanaka kana kubvisa mvura yakawandisa mumuviri. Kana kurova kwemoyo kusina kurongeka, kunewo mishonga yekudzora.
Kuvhiya
Kana zviratidzo zvacho zvakanyanya kana kuti mwoyo uchidzikira zvishoma nezvishoma, kuvhiyiwa kungave kwakakosha.
- Kugadzirisa Mavharuvhu: Sarudzo yekutanga yavanachiremba ndeyekuedza kugadzirisa vharuvhu yemwana. Vachishandisa tishu yemwana, mavharuvhu anogadziriswa kuti ashande nemazvo.
- Kutsiva Vharuvhu: Kana vharuvhu ikakuvara zvekusagona kugadziriswa, vharuvhu yekugadzira inoiswa panzvimbo payo. Izvi zvinogona kugadzirwa nesimbi (Mechanical valve) kana kugadzirwa nenyama yemhuka (Biological valve). Kana vharuvhu yesimbi ikaiswa, uchafanirwa kutora mishonga inobvisa ropa kweupenyu hwako hwese.
- Mamwe maitiro: Panguva yekuvhiyiwa, buri riri mumoyo (ASD) rinogona kuvharwa uye chikamu chemoyo chiri kukonzera kurova kwemoyo kusina kurongeka (catheter ablation) chinogona kurapwa.
Mune zvimwe zviitiko zvakakomba, kana pasina kumwe kurapwa kwakabudirira, kuisirwa moyo kunogona kudiwa. Zvisinei, izvi hazviwanzoitiki.
Ndezvipi zvinhu zvakakosha zvekungwarira?
Mwana ane chirwere ichi anoda kuongororwa nachiremba wemwoyo kweupenyu hwake hwese . Kunyangwe mushure mekuvhiyiwa, zvakakosha kushanyira makiriniki kuti anoongororwa panguva dzakatarwa.
Kana mwana wako aine chirwere ichi, chenjerera zviratidzo zvinotevera:
- Kana ganda rikava bhuruu kakawanda.
- Kana mwana achimhanya, achitamba, uye achitamba zvishoma nezvishoma.
- Kana muviri wako wazvimba.
- Kana uchinzwa moyo wako uchirova nekukurumidza.
Kana ukaona chero shanduko dzakadai, zivisa chiremba wako nekukasika .
Uyewo, mune dzimwe nguva, semusati mabuda mazino, chiremba anogona kurayira vana kuti vatore mishonga inorwisa mabhakitiriya kudzivirira hutachiona hwemwoyo. Gara uchitevedzera mirairo yachiremba nemazvo.
Mharidzo Yekuenda Nayo Kumba
- Ebstein's Anomaly chirwere chisingawanzoitiki chinokanganisa tricuspid valvu yemoyo.
- Dambudziko iri haribate munhu wese zvakafanana. Vamwe vanogona kurarama vasina zviratidzo, asi vamwe vanogona kubatwa zvakanyanya.
- Kuomerwa nekufema, kunzwa kuneta nekukurumidza, uye kutendeuka kuita bhuruu ndezvimwe zvezviratidzo zvikuru.
- Kurapwa kunoenderana nekuoma kwechirwere. Mishonga nekuvhiyiwa kwekugadzirisa kana kutsiva vharuvhu ndiyo nzira huru yekurapa.
- Mwana ane chirwere ichi anoda kutarisirwa nachiremba kwenguva refu. Kuenda kunoongororwa nguva dzose nemakiriniki kunogona kubatsira mwana kurarama hupenyu hune hutano.
- Kana muine mibvunzo kana kusava nechokwadi nezvemwana wenyu, musatya kutaura pachena nachiremba wenyu nezvazvo.











💬 Comments (0)
Hapana zvakataurwa parizvino. Isa mhinduro yako pano kekutanga.
Wedzera zvaunofunga