Unoziva zvinhu izvi here nezve ventricle yekuruboshwe yemoyo wako? (Kusasimba kweVentricle Yekuruboshwe - LVNC) Ngatikurukurei!

Nhasi tichataura nezvemamiriro ezvinhu akaomarara zvishoma, asi anogona kunge akakosha zvikuru emwoyo. Ungave usati wambonzwa nezvazvo. Inonzi Left Ventricular Non-Compaction (LVNC) sekudanwa kwazvinoitwa navanachiremba. Zita racho ringanzwika sedambudziko guru, asi musazvidya mwoyo, ngatirambei takareruka.

Saka chii chinonzi left ventricular noncongestive heart failure (LVNC)?

Zvichitaurwa zviri nyore, ichi chirwere chinoitika kana kamuri rezasi riri kuruboshwe rwemoyo wedu, iyo Left Ventricle, risingakure zvakanaka. Funga nezvazvo, kazhinji iyi ventricle yekuruboshwe yemoyo wedu inyama yakasimba kwazvo, yakatsetseka. Ndiyo chikamu chikuru chinopomba ropa kumuviri wedu wese. Asi kune munhu ane iyi `(LVNC)`, ventricle yekuruboshwe yakaita sechipanji, yakakora zvishoma, uye yakarongwa semambure. Ine hunhu hwakaita semakomo, semukati mechingwa.

Izvi zvinowanzoonekwa sechirwere chemwoyo chawakazvarwa nacho. Izvi zvinoreva kuti unogona kunge uine chirwere ichi mumoyo mako kubva panguva yawakazvarwa . Kana chikasarapwa zvakanaka, chirwere ichi (LVNC)` chinogona kukonzera matambudziko makuru emwoyo, kureva chirwere chemwoyo.

Dambudziko iri reLVNC rinokanganisa sei mashandiro emoyo?

Zvino tarisai, ventricle yekuruboshwe yemwoyo wedu ine basa rakakosha zvikuru. Ndiyo iyi inopomba ropa rine oxygen kubva mumapapu kuenda kumuviri wese. Sezvinongoita mota yemvura. Zvisinei, kana mamiriro aya e`(LVNC)` akaitika, ventricle yekuruboshwe, yakaita sechipanji, haigone kudzika kana kuzorora zvakanaka. Kureva kuti, ine dambudziko rekusunga nekusundidzira ropa mberi, kana kuzorora zvakare kuti rizadze neropa. Saka, mhedzisiro ndeyekuti basa rekupomba ropa kumuviri wese hariitike zvakanaka . Ndosaka matambudziko akasiyana-siyana achitanga kumuka.

Dambudziko iri rinonzi LVNC hariwanzoitiki kangani?

Ichi chirwere chisingawanzoitiki. Sekureva kwenyanzvi dzezvekurapa, vanhu vanosvika gumi nevaviri chete pamamiriyoni vanoonekwa vaine chirwere ichi gore rega rega. Zvisinei, nhamba chaiyo inogona kunge yakakura zvikuru . Chikonzero ndechekuti vamwe vanhu havaratidzi zviratidzo. Zvadaro havaendi kuna chiremba, saka havaongororwi.

Ndezvipi zviratidzo zveLVNC?

Ichi ndicho chinhu chakakosha. Vamwe vanhu vangasaratidza zviratidzo . Zvisinei, vamwe vanogona kuva nematambudziko makuru emwoyo. Semuenzaniso, kufa kamwe kamwe kwemwoyo kunogona kuitika. Vanhu vanosvika zvikamu zviviri muzvitatu vane LVNC vari panjodzi yekukundikana kwemoyo .

Zvakanaka, ngationei kuti munhu ane `(LVNC)` angaratidza zviratidzo zverudzii:

Zviratidzo zvinowanzoonekwa :

• Kugwamba kweropa kunogona kuumbwa. Izvi zvine njodzi huru, nekuti kana kugwamba uku kukaenda kuuropi kana kumapapu, zvinogona kuva dambudziko guru.
• Ungave nedambudziko rekufema wakarara pamubhedha.
• Kufenda .
• Kurova kwemoyo - Izvi zvinogona kunzwa sekunge ngoma iri kurova mukati mechipfuva, kana kuti sekuti moyo uri kumhanya.
• Kusakwanisa kuita maekisesaizi, kushaya mweya kunyangwe kana ukashandisa simba shoma (Dyspnea) .
• Kusarongeka kwemoyo (arrhythmia) .
• Kuzvimba kwemakumbo (Lymphedema) - kunyanya muzvitsitsinho.
• Kushaya mweya / Kushaya mweya - Kunzwa sekunge wapererwa nemweya kunyangwe ukashanda nesimba zvishoma.

Sei chirwere ichi cheLVNC chichiitika? Ndezvipi zvinokonzera?

Kazhinji, chirwere ichi che`(LVNC)` chinokonzerwa nekuchinja kwemajini (Gene mutation) kunoitika usati waberekwa. Ichi chinhu chakaoma zvikuru. Kuchinja kwemajini uku kunogona kuitika zvisina tsarukano, zvichireva kuti pasina chikonzero, kana kuti kunogona kugarwa nhaka kubva kuvabereki vako. Izvi zvinoreva kuti chinogona kuva chimwe chinhu chinoitika mumhuri. Ingofunga, dzimwe mhuri dzine huwandu hwakawanda hwechirwere chemwoyo cherudzi urwu.

Uyewo, chikamu chidiki chevakadzi chinogona kuva neLVNC kekutanga panguva yekuzvitakura pasina chikonzero chakajeka. Vanachiremba vanofunga kuti izvi zvinogona kunge zvichikonzerwa nekumanikidzwa kwakanyanya kwetsandanyama yemwoyo panguva yekuzvitakura. Kune vamwe vakadzi, zviratidzo izvi zvinopera mushure mekusununguka. Asi kune vamwe, LVNC inogona kuva nemigumisiro yenguva refu.

Vanachiremba vanoongorora sei chirwere ichi cheLVNC?

Chiremba achaita bvunzo dzakawanda kuti aone kana uine chirwere ichi che ""(LVNC)``. Ngationei kuti chii:

• Echocardiogram: Izvi zvinotarisa kuti mwoyo wako uri kupomba ropa zvakanaka sei, kuti mavharuvhu ari kushanda zvakanaka sei, uye kana paine matambudziko nemavharuvhu. Zvakafanana ne ultrasound scan yemoyo. Apa ndipo paunotanga kuona hunhu hwe left ventricle.
• Electrocardiogram (ECG): Iyi inoyera mashandiro emagetsi emwoyo wako. Inogona kuona chero matambudziko ane chekuita nekumhanya kwemoyo wako.
• Kuongororwa kwemifananidzo kwakakosha: Izvi zvinosanganisira cardiac CT scans uye magnetic resonance imaging (MRI). Izvi zvinogona kuratidza chimiro chemoyo, zvakaita sekuti mwoyo wakagadzirwa sei uye ukobvu hwemadziro awo. MuLVNC, chitarisiko chakaita sechipanji chinonyatsoonekwa pamaskeni aya.
• Coronary angiogram: Iyi inoongorora kuti ropa rinoyerera sei kuburikidza netsinga dzemwoyo dzinoendesa ropa kumoyo, uye kana paine zvivhariso. Dzimwe nguva bvunzo iyi inogonawo kudiwa kuti ionekwe kuti hapana zvimwe zvirwere zvemoyo.

Ndeapi marapirwo echirwere ichi cheLVNC?

Kurapwa kweLVNC kunosiyana zvichienderana nezviratidzo zvako. Havasi vese vanorapwa nenzira imwechete. Semuenzaniso, kana uine chirwere chemwoyo, chiremba wako anogona kukupa mishonga yakaita se:

• Mishonga inodzivirira enzyme inochinja angiotensin (ACE inhibitors): Semuenzaniso, benazepril (Lotensin®) kana lisinopril (Prinivil®, Zestril®) kana sacubitril-valsartan (Entresto®) (mishonga inodzivirira angiotensin-neprilysin). Iyi mishonga inoshanda nekuzorodza nekuvhura mitsipa yeropa (tsinga netsinga) kuti zvive nyore kuti ropa riyerere nepakati payo. Izvi zvinoderedza basa remoyo.
• Beta-blockers: Semuenzaniso, metoprolol (Lopressor®, Toprol XL®) kana atenolol (Tenormin®). Izvi zvinodzivirira mamwe mahormone (semuenzaniso adrenaline), zvinoderedza BP uye zvinodzora kurova kwemoyo.
• Digoxin (Digoxin®, Lanoxin®): Izvi zvinodzora kurova kwemoyo wako, zvinowedzera simba remwoyo wako, uye zvinovandudza kutenderera kweropa.
• Mishonga inobvisa mvura mumuviri kana kuti "mapiritsi emvura": Izvi zvinoshanda nekuita kuti muviri ubudise munyu nemvura yakawandisa kuburikidza neweti. Izvi zvinoderedza kuzvimba uye zvinoderedza basa remoyo.

Dzimwe nguva, kana paine njodzi yekumira kwemwoyo kamwe kamwe, chiremba anogona kukurudzira kuisa mudziyo unonzi Implantable Cardioverter Defibrillator (ICD) pasi peganda remoyo. Uyu mudziyo mudiki unoshandiswa nebhatiri. Unoona mutinhimira unokurumidza, unouraya mumoyo uye unokonzeresa kuvhunduka kwemoyo kuti udzorere mutinhimira wakajairika. Muzviitiko zvakakomba, kana mamwe marapirwo akasabudirira, kuisirwa moyo kunogona kudiwa.

Dambudziko iri reLVNC rinogona kurapwa zvachose here? Rinogona kugadziriswa here?

Kwete. Parizvino hapana mushonga weLVNC . Kureva kuti, hazvigone kuchinjwa. Asi musazvidya mwoyo. Kurapwa kunogona kuvandudza hupenyu hwenyu uye kuderedza matambudziko anogona kuitika nekuda kwechirwere chemwoyo . Uye, sezvandambotaura, muzviitiko zvakanyanya, kuisirwa moyo kunogona kudiwa.

Tingadzivisa sei mamiriro ezvinhu aya eLVNC?

Hapana nzira yekudzivirira LVNC. Izvi zvinokonzerwa nekuti inowanzokonzerwa nezvinhu zvemajini. Zvisinei, kana uine gene mutation inokonzera chirwere ichi, kana kuti uchifunga kuti ungave nacho (semuenzaniso, kana mumwe munhu mumhuri mako aine chirwere ichi), kuongororwa kwemajini kunogona kubatsira zvikuru.Nyanzvi yezvemajini ichakutsanangurira iwe nemhuri yako zvabuda muongororo yako. Vachakubatsira kunzwisisa zvinorehwa nekuva neLVNC uye njodzi yako yekuipfuudza kuvana vako.

Pane zvimwe zvirwere zvine chekuita nechirwere ichi cheLVNC here?

Ehe. Dzimwe nguva chirwere ichi chinonzi `(LVNC)` chinogonawo kuonekwa sechikamu chemamwe mamiriro ezvinhu emumajini (syndromes). Izvi zvakaoma zvishoma, asi vanachiremba vanofungawo nezvemamiriro aya pavanoongorora `(LVNC)`. Heano mimwe mienzaniso mishoma:

• Chirwere cheBarth
• Chirwere cheNoonan
• Roifman syndrome
• Toriello Carey syndrome

Ramangwana remunhu ane chirwere cheLVNC rakaita sei? Inguvai yekurarama?

Maonero emunhu ane chirwere cheLVNC anogona kusiyana. Zvinosiyana kubva pamunhu kusvika pamunhu. Kana munhu achirapwa zvakanaka, zviratidzo zvinogona kudzorwa , uye vamwe vanhu vanorarama hupenyu hurefu.

LVNC chirwere chinogona kuuraya, asi hazvisirizvo nguva dzose . Vanhu vazhinji vane LVNC havafi nechirwere ichi. Chinhu chakakosha ndechekuona chiremba wemwoyo nguva dzose uye kuongororwa . Iye anogona kukubatsira kugadzirisa hutano hwemwoyo wako uye kuderedza njodzi yekusangana nematambudziko.

Kana ini kana mwana wangu aine chirwere cheLVNC, mibvunzo ipi yandinofanira kubvunza chiremba?

Kana iwe kana mwana wako aine chirwere che (LVNC), kana kuti kana muine zvinokunetsai, zvakanaka kubvunza chiremba wenyu mibvunzo yakaita seiyi:

• Chii chingangove chikonzero chikuru chechirwere cheLVNC chemwana wangu/wangu? (kureva kuti, majini here kana chimwe chinhu)
• Munokurudzira kuongororwa kwemajini eLVNC here? Kana zvakadaro, zvingave zvakakosha here kune vamwe vemumhuri?
• Ndedzipi bvunzo dzinofanira kuitwa ini/mwana wangu kuti ndione kana ndine chirwere cheLVNC? Chii chandingatarisira kubva kwavari?
• Ndedzipi nzira dzekurapa LVNC? Ndeupi mushonga wakanakira ini/mwana wangu? Pane migumisiro yakaipa here pakurapa uku?
• Kana ini kana mwana wangu tikangoerekana tamira mwoyo, zviratidzo zvacho ndezvipi? Ndinofanira kuitei nekukasika?

Mibvunzo iyi ichakubatsirai kukurukura nachiremba wenyu uye kunzwisisa zviri nani mamiriro enyu ezvinhu.

Saka, ndezvipi zvinhu zvakakosha zvatinofanira kurangarira kubva munyaya iyi?

Mwoyo usingashande we ventricular yekuruboshwe (LVNC) chirwere chemwoyo chisingawanzoitiki, chinowanzo berekwa nacho. Apa ndipo apo ventricle yekuruboshwe yemoyo isingakure zvakanaka. Pane kuva tsandanyama dzakapfava uye dzakasimba, inova gobvu uye yakaita sesponji. Izvi zvinoita kuti mwoyo usapombe ropa zvakanaka.

Kana uine `(LVNC)`,Chinhu chinonyanya kukosha ndechekuona chiremba wemwoyo nguva dzose uye kutevedzera mazano avo. Kunyangwe pasina mushonga weizvi, kurapwa kwaunopihwa nachiremba wako kunogona kuderedza njodzi yekusangana nematambudziko uye kuvandudza hupenyu hwako. Zvakakosha kuti usatye wowana kurapwa kwakakodzera . Yeuka, hausi wega, uye vanachiremba varipo kuti vakubatsire.

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