Pane dambudziko here nehurongwa hwemagetsi hwemwoyo wako? Ngatikurukurei nezveLong QT Syndrome (LQTS).

Wakambonzwa nezvemagetsi emwoyo here? Mwoyo yedu inoshanda semuchina mudiki. Ine magetsi, ayo anodzora kurova kwemoyo. Dzimwe nguva, shanduko diki dzinogona kuitika mune iyi system yemagetsi. Imwe shanduko yakadaro inonzi Long QT Syndrome, kana kuti `(Long QT Syndrome - LQTS)`. Usazvidya moyo, ngatitaurei nezvazvo zviri nyore.

Chii chinonzi Long QT Syndrome? Zvichitaurwa zviri nyore...

Fungidzira kuti kana mwoyo wako warova kamwe chete, zvinotora "zororo" zvishoma usati warova zvakare, sekunge bhatiri richichajwazve. Nguva yaunotora kuti "uzorore" kana kuchajwazve inguva yakareba zvishoma kupfuura zvakajairika, inova ndiyo yatinodaidza kuti long QT syndrome.

Kana wakamboitwa ECG, inova bvunzo inotarisa mashandiro emagetsi emwoyo, pane chikamu chayo chinonzi QT interval. Izvi zvinoratidza kuti zvinotora nguva yakareba sei kuti makamuri epasi emwoyo wako, anonzi maventricles, akwanise kukwenya ozorora, kana "kuchajazve" sezvandambotaura.

Kushanda kwemagetsi kwemwoyo yedu kunobatsirwa nezvidimbu zvidiki zvemagetsi zvinonzi `ions`. MaIon akadai sesodium, calcium, potassium, uye chloride anobatsira mune izvi. MaIon aya anopinda nekubuda mumasero emwoyo kuburikidza nenzira dzakakosha dzinonzi `ion channels`. Zvino, mune iyi `(Long QT Syndrome)`, pangave paine dambudziko nemaIon channels aya, kana kuti pane kushomeka kwawo. Ipapo moyo unononoka "kuchaja". Kana nguva yeQT yawedzerwa, pane njodzi yakawedzerwa yechirwere chemwoyo chinokurumidza zvikuru chinonzi `Torsades de Pointes`, chinogona kutyisidzira hupenyu.

Kune marudzi eLong QT Syndrome here?

Ehe, kune mhando mbiri huru. Imwe inogarwa nhaka , zvinoreva kuti inopfuudzwa kuburikidza nemajini. Imwe inowanikwa , zvinoreva kuti inokonzerwa nezvimwe zvinhu, zvakaita semishonga yakati wandei.

Mhando dzekuzvarwa nadzo:

Izvi zvinonyanya kukonzerwa nekusakwana kwemajini mu 'ion channels' dzandataura.

• Kusarongeka kwenzira dzeIon: Iyi ndiyo mhando inonyanya kuwanikwa. Kune mhando dzakasiyana dzakadai se`LQT1, LQT2, LQT3, LQT4, LQT5`. Idzi dzinorongwa zvichienderana nerudzi rwenzira dzeIon dziripo. Njodzi yechirwere chemwoyo mune ramangwana inogona kusiyana zvichienderana nerudzi rwacho.
• Jervell naLange-Nielsen Syndrome: Muchirwere ichi, vabereki vese vanogona kutakura jini risingawanzoitiki, asi vangasave nezviratidzo. Ichi chirwere chisingawanzoitiki. Nekuti hazvigoneke kuti vabereki vese vatakure jini iri, mwana wega wega ane mukana we25% wekurigara nhaka. Vanhu vane chirwere ichi vanogona kuzvarwa vari matsi.
• Chirwere cheRomano-Ward:Muchiitiko ichi, mumwe mubereki anowanzova ne "Long QT Syndrome" uye mumwe haana. Mwana wega wega ane mukana we50% wekugara nhaka jini iri risingawanzoitiki. Muchiitiko ichi, kunzwa kwakajairika.
• Timothy Syndrome: Iyi inyaya isingawanzoitiki. Inogona kukanganisa kwete mwoyo chete, asiwo dzimwe nhengo dzemuviri.

Dambudziko iri rakajairika zvakadii?

Chirwere cheLong QT Syndrome chinowanzoitika zvisingawanzoitiki . Semuenzaniso, muUnited States, zvinofungidzirwa kuti munhu mumwe chete pavanhu zviuru zviviri ane chirwere ichi.

Ndezvipi zviratidzo zveLong QT Syndrome?

Aya ndiwo zviratidzo zvinowanzoonekwa:

• Syncope: Kurasikirwa nepfungwa kamwe kamwe.
• Kubatwa nepfari: Vamwe vanhu vanogona kusangana nepfari.
• Kumira kwemwoyo: Izvi zvine njodzi zvikuru.
• Rufu rusingatarisirwi:

Zviratidzo izvi zvinoitika kana chirwere chemwoyo chinonzi `Torsades de Pointes' chandambotaura nezvacho chikaitika. Panguva ino, mwoyo haugone kupomba ropa nemazvo. Kana uropi hukasawana ropa rakakwana, zvinhu zvakaita sekufenda uye pfari zvinoitika. Kana chirwere ichi chikaramba chiripo, rufu rwechimbichimbi runogona kuitika. Zvisinei, kana kurova kwemoyo kukadzokera pakare, zviratidzo zvinomira.

Zviratidzo zvinonyanya kuoneka kana:

• Paunenge uchirovedza muviri (kana maminitsi mashoma mushure mekurovedza muviri).
• Munguva yekukurudzirwa kwakasimba kwepfungwa , kunyanya kana ukangoerekana watya kana kuvhunduka.
• Panguva yekurara kana kuti paunongoerekana wamuka .

Zvakakosha kuti vanhu vanosvika 50% vane Long QT Syndrome vangasazombova nezviratidzo . Uye, kune munhu mumwe chete pavanhu gumi, kumisa kwemoyo ndicho chiratidzo chekutanga chechirwere ichi. Izvi zvinogona kuuraya kana zvikasarapwa nekukurumidza.

Zviratidzo zvinowanzotanga munhu akura . Kana uine zviratidzo, zvinogona kudzoka. Zviratidzo zvinowanzoonekwa usati wasvitsa makore makumi matatu. Zvisinei, vamwe vanhu vanogona kutanga zviratidzo mumakore avo ekuma50 zvichikwira.

Chii chinokonzera Long QT Syndrome?

Sezvandambotaura, izvi zvinogona kutorwa kubva kuvabereki vako (vakaberekwa navo) kana kuwanikwa nekuda kwemishonga yakati . MuLong QT Syndrome, pane kusarongeka kwegene code ye ion channels dzako. Aya ma ion channels asina kujairika anokonzera kunonoka kwekudzoka kwemoyo wako. Izvi zvinogona kutungamira ku arrhythmia inotyisidzira hupenyu.

Mimwe mishonga inogona kukonzera "Long QT Syndrome" kuvanhu vane fungidziro ye "ion channels" dzavo. Vangasatombozviziva, asi kana vakatora mishonga iyoyo ndipo panoitika "Long QT".

Mishonga inogona kukonzera acquired long QT syndrome:

• Mimwe mishonga yekurwisa marwadzo emwoyo (Antiarrhythmics)
• Mimwe mishonga yekuora mwoyo
• Mimwe mishonga inobvisa mvura mumuviri (mishonga inoita kuti munhu awedzere kuita weti)
• Mamwe maantibayotiki
• Zvinodzivisa kana zvinodzivisa maSerotonin receptor
• Vadzivisi veHistamine receptor

Zvimwe zvikonzero zve acquired long QT syndrome:

• Mamwe marudzi echepfu
• Anorexia nervosa (chirwere chepfungwa chine chekuita neanorexia)
• Mamwe `bradyarrhythmias` (kurova kwemoyo kunonoka zvisingawanzoitiki)
• Kuderera kwecalcium, magnesium, kana potassium mumuviri
• Kukuvadzwa kwehurongwa hwako hwetsinga

Ndiani ari panjodzi huru yekuva nechirwere ichi?

Vanhu vanotevera vari panjodzi huru yekubatwa ne "Long QT Syndrome":

• Kune vana vasinganzwi kubva pakuzvarwa.
• Vana nevechidiki vane nhoroondo yemhuri yekufa kamwe kamwe kana kufenda zvisina tsarukano (syncope).
• Kune hama dzeropa dzine ``Long QT Syndrome``.
• Kune avo vane `Cardiomyopathy` (chirwere chetsandanyama dzemwoyo) kana chirwere chemwoyo chekuzvarwa nacho.
• Kune avo vane mamwe ma electrolytes mashoma mumuviri nekuda kwechimwe chirwere.
• Kune avo vanotora mishonga inokanganisa nzira dze ion mumoyo.

Ndinofanirawo kuongororwa chirwere cheLong QT Syndrome here?

Long QT Syndrome chirwere chemajini chinogona kupfuudzwa kubva kuchizvarwa kuenda kune chimwe chizvarwa. Kana mumwe wehama dzako dzekutanga (vabereki, vanun'una, vana) aine Long QT Syndrome, zvakanaka kuti uedze kuongororwa majini .

Hama dzese dzepadanho rekutanga (vanin'ina, vabereki, nevana) dzinofanira kuvhenekwa ECG. Zvakakoshawo kuti chero ani zvake ane nhoroondo yemhuri yepfari kana kufenda aite bvunzo iyi.

Danho rekutanga nderekuzivisa chiremba wako kuti mhuri yako ine chirwere ichi. Angangoita kuti aite bvunzo dzinodiwa kuti aongorore moyo wako. Kana bvunzo idzodzo dzikaitika kuti une chirwere ichi, unofanira kuona chiremba wemwoyo anoziva nezveLong QT Syndrome.

Ndezvipi zvinetso zveLong QT Syndrome?

``Long QT Syndrome`` inogona kukonzera kusagadzikana kwemoyo kunotyisidzira hupenyu kwandataura. Izvi zvinogona kutokonzera rufu rwechimbichimbi.

Long QT Syndrome inoonekwa sei?

Vanachiremba vanogona kuongorora chirwere cheLong QT Syndrome nekuongororwa kuri nyore kweECG. Kuti vaongorore chirwere ichi, vanoyera nguva yeQT paECG. Kana nguva yako yeQT yakareba kupfuura 450 milliseconds, unogona kunge uine Long QT Syndrome.

Chiremba wako achakubvunza nezvezvinhu izvi:

• Pane nhoroondo yemhuri ye "Long QT Syndrome" here?
• Pane nhoroondo yemhuri yakambofenda, pfari, kana kuti cardiac attack isingatsananguriki here?
• Wakambonzwa kufenda, pfari, kana kuti cardiac arrest, kunyanya panguva yekurovedza muviri here?

Ndezvipi zviedzo zvinoshandiswa kuongorora chirwere cheLong QT Syndrome?

Kuwedzera kuECG, bvunzo idzi dzinogonawo kuitwa:

• Kuongororwa kweropa.
• Kuongororwa kwemajini.
• Kuedza kushushikana kwemuviri.
• Ambulatory monitor: Izvi zvinotarisa mashandiro emoyo wako kwemazuva akati wandei.

Long QT Syndrome inorapwa sei?

Kune mishonga, zvishandiso, kana kuvhiyiwa kunogona kubatsira kudzora zviratidzo uye kudzivirira kufa kamwe kamwe kweLong QT Syndrome. Kunyange zvazvo kurapwa uku kusingakwanise kurapa chirwere chacho zvizere, kunogona kukudzivirira kubva pakuita kwemoyo zvisina kujairika.

Mishonga

Vanhu vazhinji vane Long QT Syndrome (kunyangwe vasina zviratidzo) vanotora beta-blocker, yakaita se nadolol. Mimwe mishonga inogona kupfupisa nguva yako yeQT kana kuvandudza mazinga e electrolyte. Chiremba wako achakuudza kuti ndeipi mishonga yakakunakira.

Zvishandiso

Vamwe varwere vane ``Long QT Syndrome'' vangadawo michina yakaita seiyi:

• Mushonga weCardioverter Defibrillator (ICD): Mushonga wecardioverter defibrillator (ICD) unogona kuiswa muvanhu vane nhoroondo yekumira kwemwoyo kana kuti vachiri kuratidza zviratidzo kunyangwe vachirapwa nebeta-blocker. Muchina uyu unoona kusagadzikana kwemoyo uye unokonzeresa kuvhunduka kwemoyo kuti udzivise kufa kamwe kamwe.
• Chinopa simba remoyo: Chishandiso ichi chinobatsira vanhu vane kurova kwemoyo kunonoka zvisingaite.

Kuvhiya

Vamwe varwere vane Long QT Syndrome vangangoda kuvhiyiwa Left Cardiac Sympathetic Denervation (LCSD) kana kuvhiyiwa sympathectomy. Iyi inzira isinganyanyi kukuvadza tsinga dzetsinga dziri mutsinga dzetsinga dzinobviswa.

Ndezvipi zvinetso/migumisiro yekurapwa?

Migumisiro kana matambudziko zvinogona kuitika zvinoenderana nerudzi rwekurapwa kwaunowana.

• Beta-blocker:
• Kuderera kweropa.
• Dzungu.
• Musoro .
• Kuneta.
• ICD (Implantable Cardioverter Defibrillator):
• Zvikanganiso zvemudziyo.
• Mapapu akaputsika.
• Kubuda ropa.
• Utachiona.
• Chinopa simba remoyo:
• Mapapu akaputsika.
• Kubuda ropa.
• Utachiona.
• Zvikanganiso zvemudziyo.
• LCSD (Kuvhiyiwa Kwemwoyo Kunopa Rutsigiro):
• Horner syndrome.
• Mapapu akaputsika.
• Kusviba kana kudikitira pachiso.

Ko Long QT Syndrome inogona kudzivirirwa here?

Haugone kudzivirira kana ukaitora kubva kuvabereki vako. Zvisinei, kune avo vasingaitore, unogona kudzivirira zvirwere zvinokonzera acquired (long QT syndrome) gare gare. Semuenzaniso, chenjerera nemishonga yakati.

Chii chinoitika kana ndine Long QT Syndrome?

Kana munhu aine chirwere che "Long QT Syndrome" zvakanaka , huwandu hwevanhu vanofa nechirwere ichi hunosvika 1%. Kana munhu asina kurapwa, mamiriro acho ezvinhu akaoma. Vanhu vanosvika 21% vane zviratidzo vasingarapwe vanofa mukati megore rimwe chete kubva pakutanga kwechirwere ichi.

Asi yeukai, vanhu vane "Long QT Syndrome" vanogona kurarama hupenyu hwakazara . Vanogona kubata pamuviri nekubereka vana.

Long QT Syndrome inogara kwenguva yakareba sei?

Chirwere cheLong QT Syndrome chinogara kwenguva refu. Zvisinei, zviratidzo uye njodzi yezvinetso zvinogona kudzikira nekufamba kwenguva.

Ndinozvitarisira sei?

Long QT Syndrome inogona kukanganisa zvakawanda muhupenyu hwako hwezuva nezuva. Unofanira kubvunza chiremba wako usati waita zvimwe zvinhu.

Ruzha uye kushushikana

Vamwe vanhu vane Long QT Syndrome vanogona kukanganiswa neruzha rukuru kana kushushikana mupfungwa. Kunyange zvazvo usingakwanise kudzora ruzha rwese nekushushikana kwakakupoteredza, unogona kuedza kudzikamisa.

• Udza shamwari dzako nemhuri yako kuti hazvina kunaka kukumutsa kamwe kamwe.
• Panzvimbo pekurira zvine ruzha zvinorira panguva imwe chete, shandisa alarm ine ruzha runonakidza.
• Deredza ruzha rwezvinhu zvinogona kukuvhundutsa.

Kurovedza muviri

Mamwe marudzi eLong QT Syndrome anowanzo kukonzera matambudziko pakurovedza muviri. Chiremba wako achakuudza kuti ndeapi mabasa akakodzera kwauri, zvichienderana nerudzi rwejini raunaro risingawanzoitiki. Nekuti kurovedza muviri kunogona kukonzera kusagadzikana kwerhythmias kunouraya, unofanira kutaura nachiremba wako usati wasarudza kutamba mitambo yemakwikwi. Kana ukasarudza kutamba mitambo, ungangoda kutora matanho ekudzivirira.

Kushambira kunogona kuva nengozi kune vamwe vanhu vane ``Long QT Syndrome''. Kana ukafenda uchishambira, unogona kunyura.

Mishonga

Mishonga yakawanda inogona kuwedzera nguva yeQT. Mishonga iyi inogona kukanganisa vanhu vane ``Long QT Syndrome`` kupfuura vasina. Kana uine ``Long QT Syndrome``, unofanira kuita zvinotevera:

• Udza vanachiremba vako vese kuti une "Long QT Syndrome".
• Taura nachiremba wako usati watora chero mushonga wakanyorerwa kune zvimwe zvirwere.
• Dzivisa kutora mishonga inotengeswa pasina kunyorerwa chiremba (OTC) (kunze kweaspirin kana paracetamol) usina kutaura nachiremba wako.

Kana uine "Long QT Syndrome", mhando idzi dzemishonga dzinogona kukanganisa:

• Mishonga yeAntihistamines (mishonga yekurapa allergies)
• Mishonga yekuderedza kushushikana (mishonga yekuderedza kushushikana)
• Mishonga yezvinetso zvepfungwa
• Mishonga yezvirwere zvemwoyo
• Mishonga inorwisa mabhakitiriya
• Mishonga inorwisa fungus
• Mishonga yekudzivirira hutachiona
• Mishonga yezvirwere zvemudumbu
• Mishonga Inorwisa Kubata Chipfukuto
• Diuretics (mishonga inokonzera weti yakawanda)
• Mishonga yeBP yakakwira
• Mishonga yekurwadziwa kwemusoro
• Mishonga inoderedza cholesterol

Ndinofanira kuona chiremba wangu rini?

Unofanira kuona chiremba kana wava kutanga kuva nezviratidzo uye kamwe chete pagore mushure mezvo. Chiremba wemagetsi ndiyo sarudzo yakanakisisa.

Kana mwana wako aine chirwere che "Long QT Syndrome", unofanira kuona chiremba wako kanopfuura kamwe chete pagore kuti uve nechokwadi chekuti ari kuwana mushonga wakakodzera zvichienderana nehuremu hwake hwazvino.

Kana wakaisirwa mudziyo, unofanira kuona chiremba wako kamwe chete pagore kuti uve nechokwadi chekuti uri kushanda nemazvo.

Ndinofanira kuenda kuEmergency Treatment Unit (ETU) riini?

Munhu ane chirwere chemwoyo chinomira anoda rubatsiro rwechiremba nekukurumidza . Mumwe munhu ari pedyo anofanira kutanga CPR (cardiac resuscitation) uye ofonera 911 (kana nhamba yako yekukurumidzira yemuno).

Mibvunzo ipi yandinofanira kubvunza chiremba wangu?

Mimwe mibvunzo yaunogona kubvunza chiremba wako:

• Rudzii rwe "Long QT Syndrome" rwandinarwo?
• Ndeapi marapirwo chaiwo amunokurudzira kwandiri?
• Ndinofanira kukuonai kangani?
• Ndeapi mishonga nemabasa andinofanira kudzivisa nerudzi rwangu rwe "Long QT Syndrome"?

Pakupedzisira, Mharidzo Yekuenda Nayo Kumba

Zvakajairika kuti unzwe kunetseka kana ukaona kuti une chirwere chemwoyo. Asi kubvunza chiremba wako mibvunzo uye, kana zvichidikanwa, kutaura neanopa mazano kunogona kukubatsira kuti unzwe wakasununguka. Zvakakosha kutevedzera mirairo yachiremba wako, kunwa mishonga yako nenguva, uye kuchengeta nguva yako yekusangana.

Zvinogonawo kuva zororo kuzivisa mhuri yako neshamwari kuti une Long QT Syndrome. Kana ukaona zviratidzo vari newe, vanogona kufona kuti vakubatsire nekukurumidza. Zviri nani, kana vachiziva maitiro ekuita CPR, zvinogona kuponesa hupenyu hwako. Usazvidya mwoyo, nekutarisira kwakanaka, iwewo unogona kurarama hupenyu hwakanaka.

Long QT Syndrome, LQTS, chirwere chemwoyo, QT interval, kurova kwemoyo, arrhythmia, zvirwere zvemajini