Dzimwe nguva unonzwa dzungu here kana kuti une musoro wakaremara? Kana kuti pane mumwe munhu waunoziva akaerekana abatwa nechirwere chemwoyo here? Dzimwe nguva chikonzero chezvinhu izvi chinogona kunge chiri chirwere chemajini chisingawanzoitika chatisinganzwi zvakawanda nezvacho. Chimwe chezvirwere zvakadaro iShort QT Syndrome, kana kuti sekudanwa kwazvinoitwa navanachiremba, Short QT Syndrome (SQTS) . Kunyangwe zita racho ringanzwika serakaoma zvishoma, ngatitaurei nezvazvo zviri nyore.
Chii chinonzi nguva yeQT? Masaini emagetsi emoyo!
Zvakanaka, ngatitangei tatarisa kuti iyi QT interval chii. Waizviziva here kuti moyo wedu unorova tichishandisa sisitimu yemagetsi? Zvakafanana newaya iri mumba kuti ibatidze mwenje. Imhaka yemagetsi aya ndiyo inoita kuti makamuri emoyo agumbuke uye awedzere kurongeka, izvo zvinopomba ropa.
Pamwe wakamboona chiremba achiita bvunzo yeECG (Electrocardiogram) pavanoongorora moyo wako. Vanokuita bvunzo iyi nekukurara pamubhedha uye vachinamira zvidhindo zvidiki pachipfuva nemaoko ako. Ndizvo zvinonyora mashandiro emagetsi emoyo. Chiremba paanotarisa chinyorwa ichi, anoona patani yemafungu inonzi P, Q, R, S, T. Tsamba imwe neimwe inokuudza mashandiro ari kuita zvikamu zvakasiyana zvemoyo.
Zvichitaurwa zviri nyore:
- P wave: Chiratidzo chemagetsi chinoita kuti makamuri epamusoro emoyo, iyo atria, agumbuke.
- QRS complex: Chiratidzo chemagetsi chinoita kuti makamuri epasi emwoyo, anonzi maventricles, agumbuke. Izvi ndizvo zvinonyanya kupomba ropa kuenda kumuviri.
- T wave: Maventricle apedza kugwinha, asununguka zvakare, uye ari kugadzirira kurova kunotevera. Zvakafanana nekumhanya wozorora zvishoma.
Zvino hechino chinhu chakakosha. Nguva yeQT inguva kubva pakutanga kweQRS complex kusvika kumagumo eT wave. Aya ndiwo maitiro anoita vanachiremba kuyera kuti zvinotora nguva yakareba sei kuti makamuri epasi emoyo wako ('ventricles') agadzirire kurova kunotevera mushure mekurova kumwe chete. Kazhinji, nguva yeQT mumoyo une hutano iri pakati pemasekondi 0.35 ne0.45. Zvisinei, kune munhu ane SQTS , nguva ino isingasviki masekondi 0.34. Izvi zvinoreva kuti moyo wava kutanga kurova zvakare usati wagona kuzorora.
Ndeupi musiyano uripo pakati peShort QT Syndrome (SQTS) neLong QT Syndrome?
Izvi zvingave zvakakoshawo kwauri. Pamwe chete neSQTS, kune chimwe chirwere chinonzi Long QT Syndrome (LQTS) . Zvakafanana nerumwe rutivi rwemari, handiti?
- Syndrome Pfupi yeQT (SQTS): Nguva yeQT ipfupi zvisingawanzoitiki (kazhinji isingasviki masekondi 0.34).
- Long QT Syndrome (LQTS): Nguva yeQT inorebeswa zvisina kujairika (kazhinji inodarika masekondi 0.45).
Matambudziko ese aya anogona kukonzera matambudziko anokanganisa rhythm yemoyo. Zvisinei, zvikonzero nekurapa zvinogona kunge zvakasiyana. Nhasi tichangotaura nezveSQTS chete.
Ndiani anogona kugadzira SQTS?
Ichi chirwere chisingawanzoitiki . Hazvizivikanwe kuti vanhu vangani pasi rose vane chirwere ichi, asi hazviwanzoitiki. Imwe tsvakiridzo yakawana kuti zviratidzo zveSQTS zvinogona kuonekwa kune vamwe vanhu mugore rekutanga rehupenyu. Zvadaro, zvinonzi zviratidzo zvinogona kuoneka zvakare muhudiki uye kunyange mukukura. Izvi zvinoreva kuti zvinogona kukanganisa vanhu vemazera ese.
Ndezvipi zvikonzero zveSQTS?
SQTS chirwere chinokonzerwa nemajini . Sekunge ruvara rwemaziso ako uye magadzirirwo ebvudzi rako zvinotemerwa nemajini ako, chirwere ichi chinogonawo kukonzerwa nekuchinja kwemajini.
Pane nzira mbiri idzi dzinogona kuitika nadzo:
1. Nhaka kubva kuvabereki: Kana amai vako kana baba vako vaine rudzi urwu rwemajini, unogonawo kuitora nhaka.
2. Kuchinja kwemajini pasina chikonzero: Dzimwe nguva, kuchinja kwemajini uku kunogona kuitika mumuviri wako pasina chikonzero, kunyangwe pasina mumwe munhu mumhuri yako ane izvozvo.
Kuchinja kwemajini uku kunoshandura mashandiro ezvinhu zvinonzi maion channels mumasero emwoyo. Maion channels aya anobatsira kuti masaini emagetsi emoyo afambe zvakanaka. Kana paine dambudziko nawo, nguva yeQT inopfupika.
Ndezvipi zviratidzo zveSQTS?
Havasi vese vane SQTS vane zviratidzo zvakafanana. Vamwe vanhu vanogona kunge vasina zviratidzo zvachose. Zvisinei, vanhu vazhinji vanowana zvimwe zviratidzo.
Chinhu chakakosha ndechekuti zviratidzo izvi zvinogona kufanana nezvezvimwe zvirwere zvemoyo. Saka, kana ukasangana nechimwe chinhu chakadai, zvakanaka kuti uende kunoonekwa nachiremba wonoongororwa.
Zviratidzo zvikuru zvinogona kuonekwa ndezvi:
- Atrial Fibrillation (AFib): Ichi ndicho chiratidzo chinowanzoitika. Zvinonzi chinokanganisa vanhu vana pavanhu vashanu vane SQTS. AFib inguva apo makamuri epamusoro emwoyo (atria) asingarove zvakanaka, asi "anobhururuka." Izvi zvinoita kuti mwoyo urove zvisina kurongeka.
- Kurova kwemoyo: Munhu mumwe chete pavanhu vatatu anogona kuona chiratidzo ichi. Zvinganzwa sekunge mumwe munhu ari kurova mukati mechipfuva chake, kana kuti zvinganzwa sekunge ari kunzwa kurova kwechipfuva chake.
- Dzungu uye kufenda kana kuvhiringidzika kwepfungwa: Izvi zvinogona kukanganisa munhu mumwe chete pavanhu vana. Zvinogona kukonzera kunzwa kusuruvara uye dzimwe nguva kurasikirwa nepfungwa.
Zvinosuwisa kuti vamwe vanhu (vanenge vaviri pavashanu) vanotanga kuziva kuti vane SQTS mushure mekumira kwemoyo kana kufa kamwe kamwe kwemoyo. Izvi zvinokonzerwa nekurova kwemoyo kusina kurongeka (arrhythmia) mumakamuri epasi emoyo, zvakaita se ventricular fibrillation kana ventricular tachycardia, izvo zvinoita kuti moyo umire kurova kamwe kamwe. Ichi chirwere chakakomba zvikuru.
Fungidzira, kune jaya rine makore makumi maviri nemashanu ekuberekwa rinonzi Asanka. Aive mutambi akanaka uye ane hutano hwakanaka. Rimwe zuva, achitamba cricket neshamwari dzake, akangoerekana awira pasi akabata chipfuva chake. Akamhanyiswa kuchipatara, asi haana kukwanisa kuponeswa. Kuongororwa kwakazotevera kwakaratidza kuti Asanka aive neSQTS. Zvinosuwisa kunzwa zvinhu zvakadaro, asi zvakakosha kuziva zvinhu izvi.
SQTS inoonekwa sei?
Kana uchifungidzira kuti une SQTS, chiremba achatanga nekubvunza nezvezviratidzo zvako uye kana paine munhu mumhuri mako ane chirwere chemwoyo. Zvadaro vanogona kuita bvunzo dzinotevera:
- ECG (Electrocardiogram): Iyi ndiyo bvunzo inonyanya kukosha. Inoyera nguva yeQT. Kazhinji, kana nguva yeQT iri pasi pemasekondi 0.34 uye paine zvimwe zviratidzo, SQTS inofungidzirwa. Dzimwe nguva, kunyangwe nguva yeQT iri pakati pemasekondi 0.34 ne0.36, SQTS inogona kufungwa nezvayo kana paine zvimwe zviratidzo (semuenzaniso, nhoroondo yemhuri yeSQTS, kushaya simba kusingatsananguriki).
- Kuongororwa kwemajini: Kuongororwa uku kunoitwa kuti kuonekwe kana paine shanduko dzemajini dzinokonzera SQTS. Izvi zvinogona kubatsira kusimbisa chirwere ichi uye kuona kana vamwe vemumhuri vari panjodzi.
Dzimwe nguva, ungasava nezviratidzo uye netsaona ukaona kuti nguva yako yeQT inopfupikiswa kana uine ECG nekuda kwechimwe chikonzero.
Ndeapi marapirwo eSQTS?
Kunyange zvazvo SQTS iri chirwere chakakomba, chinorapika. Chinorapwa nachiremba wemwoyo. Zvichienderana nemamiriro ako ezvinhu, chiremba wako anogona kukupa mazano ekurapa anotevera:
- Implantable Cardioverter Defibrillator (ICD): Uyu ndiwo mushonga wakavimbika kune vakuru vane SQTS. ICD muchina mudiki unoiswa pasi peganda rechipfuva wobatanidzwa nemoyo. Muchina uyu unogara uchitarisa rhythm yemoyo. Kana kurova kwemoyo kusina kurongeka (arrhythmia) kukaitika, ICD inongoerekana yakonzera kuvhunduka kwemoyo kuti idzorere rhythm. Zvakafanana ne emergency lifeguard.
- Mishonga: Kune mishonga yekurwisa arrhythmia inodzora rhythmia yemoyo. Semuenzaniso, quinidine inowanzo shandiswa paSQTS. Chiremba wako anogonawo kunyora mishonga yakaita seflecainide (Tambocor™) , ibutilide (Corvert® ), propafenone , amiodarone , sotalol , kana beta-blockers (semuenzaniso, metoprolol (Toprol XL®, Lopressor®) , carvedilol (Coreg®) ).
Zvakakosha: Mishonga iyi inofanira kutorwa chete kana yakanyorerwa nachiremba wako, uye sezvaanokuudza. Kushandisa mishonga wega kunogona kuva nemigumisiro ine njodzi.
Njodzi yeSQTS inogona kuderedzwa here?
Nekuti SQTS chirwere chinokonzerwa nemajini, hapana nzira yekudzivirira kuti chisatange. Hachisi chinhu chatinogona kudzora.
Zvisinei, kana ukaonekwa uine SQTS, zvakakosha kuti ugare uchiona chiremba wemwoyo uye utevedzere mazano avo. Vanogona kutarisa hutano hwemwoyo wako uye kubatsira kuderedza njodzi yematambudziko akakomba, kunyanya kufa kamwe kamwe kwemoyo, anogona kuitika nekuda kweSQTS.
Unogona kurarama kwenguva yakareba sei uine SQTS?
Uyu mubvunzo unobvunzwa nevanhu vazhinji. Nguva yaunogona kurarama neSQTS inogona kusiyana kubva pamunhu kusvika pamunhu. Kune vamwe vanhu, SQTS inogona kukonzera rufu rwemwoyo kamwe kamwe. Zvinofungidzirwa kuti vanhu vane SQTS vane mukana we40% wekufa kamwe kamwe kwemwoyo pavanosvika makore makumi mana. Njodzi iyi yakanyanya muvacheche vane makore 0-1 uye vechidiki vane makore 20-40. Kana izvi zvikaitika kumwana ari pakati pemakore ekuzvarwa neachangoberekwa negore rimwe chete, vanachiremba vanogonawo kuidana kuti Sudden Infant Death Syndrome (SIDS) .
Asi, musavhunduke neizvi. Chinhu chakakosha chekurangarira ndechekuti havasi vese vane nguva pfupi yeQT (isingasviki 360 milliseconds) vari paECG vane SQTS, uye havasi vese vari panjodzi yekufa kamwe kamwe nemoyo. Vamwe vanhu vane SQTS vanogona kurarama hupenyu hwakajairika vasina zviratidzo. Nekuti SQTS chirwere chisingawanzoitiki, vaongorori vachiri kuferefeta kuti chinokanganisa sei hupenyu hwavo.
Chiremba wako anogona kukubatsira kugadzirisa dambudziko rako uye kuderedza njodzi yekusangana nematambudziko nekupa nzira dzakakodzera dzekurapa.
Chii chimwe chaungada kubvunza chiremba wako?
Kana uchifungidzira kuti une SQTS, kana kuti wakamboonekwa kuti unayo, zvakanaka kubvunza chiremba wako mibvunzo iyi:
- Ndezvipi zviratidzo zveSQTS? Zviratidzo zvangu zvinoenderana neizvi here?
- Ndedzipi bvunzo dzandinofanira kuita kuti ndione kana ndine chirwere cheSQTS?
- Ndedzipi nzira dzekurapa dzandinadzo? Ndeipi nzira yakandinakira?
- Ndezvipi zvandingashandura mararamiro angu kuti ndirambe ndiine hutano hwakanaka? (semuenzaniso, kudzivisa mimwe mishonga, mamwe mabasa)
- Pane mukana wekuti vana vangu vagare nhaka yeSQTS here? Pane bvunzo dzekutsvaga here?
Pamusoro pemibvunzo iyi, usatya kutaura nachiremba wako nezvechero chauri kufunga kana kuti chausingafungi nezvacho.
Heino pfupiso yezvatakakurukura (Mharidzo Yekuenda Kumba):
Zvakanaka saka, ngatirangarirei zvatakataura nezvazvo:
- Short QT Syndrome (SQTS) chirwere chisingawanzoitiki, chine majini.
- Chinoitika apa ndechekuti nguva yeQT, iyo inguva inoshanda mumoyo, inova pfupi zvisingawanzoitiki. Zvichitaurwa zviri nyore, inoderedza nguva inotora makamuri epasi emoyo kugadzirira kurova kunotevera mushure mekurova kumwe chete.
- Izvi zvinogona kukonzera zviratidzo zvakaita sedzungu, kupera simba, uye kuomarara kwechipfuva.
- Dzimwe nguva, panogona kunge pasina zviratidzo zvachose.
- SQTS chirwere chakakomba chinogona kukonzera kumisa kwemwoyo kamwe kamwe uye kunyange rufu.
- Zvisinei, izvi zvinogona kuongororwa neECG uye bvunzo dzemajini.
- Izvi zvinogona kurapwa nemidziyo yeICD nemishonga.
- Kana muine kusava nechokwadi nezveizvi, kana kana paine mumwe munhu mumhuri yenyu ane chirwere chemwoyo cherudzi urwu, iva nechokwadi chekuona chiremba kuti akupe mazano.
Yeukai, zvakakosha kuziva zvinhu izvi uye kutsvaga mazano echiremba nenguva. Tinokushuvirai hutano hwakanaka!
` Short QT syndrome, SQTS, chirwere chemwoyo, ECG, QT interval, chirwere chemajini, kumisa mwoyo kamwe kamwe, ICD











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