Ngaba nawe unazo ezi mpawu zingaqhelekanga? Masifunde ngesifo sikaBehçet ngokulula!

Ngaba wakha weva ngeSifo sikaBehçet? Eli gama lisenokuvakala lingaqhelekanga. Kodwa eneneni yimeko enzima, kodwa elawulekayo enokuchaphazela iindawo ezahlukeneyo zomzimba wethu. Ngoko ke, masithethe ngayo ngokweenkcukacha namhlanje, ngokulula nje, njengokuthetha nomhlobo.

Yintoni isifo sikaBehçet?

Ngamafutshane, isifo sikaBehçet kukudumba okungapheliyo kwemithambo yegazi emizimbeni yethu. Oogqirha bakwabiza ngokuba yi-"vasculitis." Esi sisifo apho imithambo yegazi idumba, ibe bomvu, kwaye ibe buhlungu. Sinokuchaphazela zombini imithambo yegazi emikhulu (imithambo yegazi) kunye nemithambo yegazi emincinci (imithambo yegazi). Esi sifo ngamanye amaxesha sibizwa ngokuba yi-"Silk Road disease" kuba siqhelekile kwiindawo ezikufutshane neSilk Road kwimbali.

Ngubani onokuba nethuba elikhulu lokufumana esi sifo?

Isifo sikaBehçet sinokuchaphazela nabani na emhlabeni. Nangona kunjalo, sixhaphake kakhulu kwamanye amazwe. Umzekelo, sixhaphake kakhulu kumantla eTurkey, kumazwe ajikeleze uLwandle lweMeditera, uMbindi Mpuma kunye neMpuma Asia. Asixhaphakanga kangako kumazwe afana ne-United States. Iimpawu zihlala ziqala ukubonakala phakathi kweminyaka engama-20 ukuya kwengama-30. Nangona kunjalo, sinokubakho nakweyiphi na iminyaka. Nangona ekuqaleni kwakucingwa ukuba sichaphazela amadoda nabafazi ngokulinganayo, ezinye izifundo zibonisa ukuba amadoda anamathuba amancinci okufumana esi sifo .

Zithini iimpawu zesi sifo? Siziva njani?

Le yeyona nto ibalulekileyo. Iimpawu zesifo sikaBehçet zinokuhluka kumntu nomntu. Oku kuthetha ukuba iimpawu onazo zisenokungafani nezomnye umntu. Kodwa kukho iimpawu ezimbalwa eziphambili eziqhelekileyo.

Izilonda zomlomo

Olu luphawu lokuqala olubonwa ngabantu abaninzi . Lufana nezilonda ezidla ngokufumaneka emlonyeni wethu, kodwa zikhulu, zihlala zikho, kwaye zibuhlungu ngakumbi . Abanye abantu banokuba nezi zilonda emlonyeni ngaphambi kokuba kuvele ezinye iimpawu. Zinokuvela emilebeni, elulwimini, nangaphakathi ezidleleni.

Khawucinge nje, uhlala ufumana izilonda emlonyeni, zibuhlungu kangangokuba awukwazi nokutya okanye ukusela, kwaye nokuba sele uthathe amayeza, ziyabuya emva kweentsuku ezimbalwa. Yimeko efana naleyo.

Izilonda zesini

Njengezilonda zomlomo, izilonda zesini nazo zinokubakho. Ezi zinokuba buhlungu. Zinokubakho nakwisinqe samathumbu kumadoda nakwisinqe sabasetyhini. Nangona kunjalo, azixhaphakanga njengezilonda zomlomo.

Ukudumba kwamehlo

Ukudumba kwamehlo kukwaluphawu olubi kakhulu lwesi sifo. Oku kunokubangela ukuba amehlo abe bomvu, aqaqambe, angaboni kakuhle, abonakale ekhanya, aze amehlo abe namanzi . Ukuba anganyangwa kakuhle, oku kunokubangela ukuba amehlo angaboni kakuhle.Kukho ithuba. Kukho iingxelo zokuba olu hlobo lomonakalo wamehlo luqheleke kakhulu kumazwe afana neMbindi Mpuma neJapan.

Iingxaki zolusu

Iingxaki zolusu nazo zixhaphakile. Ngamanye amaxesha, amaqhuqhuva afana namaqhuqhuva kunye namaqhuqhuva abomvu (i-erythema nodosum) anokuvela. La maqhuqhuva abuhlungu xa uwachukumisa. Ngamanye amaxesha, izilonda zolusu zinokuvela. Ezinye zezi zingaphezulu, ngelixa ezinye zinokuba nzulu. Olunye uphawu olungaqhelekanga kukuba ukuba ulusu lukrwelwe okanye luhlatywe, indawo iya kuba bomvu kwaye iqhuqhuva elincinci liya kuvela kwiintsuku ezimbalwa . Oogqirha bakubiza oku ngokuthi "luvavanyo lwe-positive pathergy."

Intlungu yamalungu

Iintlungu zamalungu nazo zixhaphakile phakathi kwaba baguli. Zichaphazela amaqatha, amadolo, iingqiniba, kunye namaqakala ngokukodwa . Amalungu anokuba nokudumba, abomvu, kwaye abuhlungu xa echukunyiswa. Nangona kunjalo, ngokuqhelekileyo abangela umonakalo omncinci osisigxina kumalungu.

Ukudumba kwemithambo yegazi

Ukudumba ngaphakathi kwemithambo yegazi kunokubangela ukuqhekeka kwegazi, ukuvaleka , okanye ukuvaleka ngokupheleleyo kwemithambo yegazi. Oku kunokuchaphazela zombini imithambo engaphezulu, ekufutshane nolusu, kunye nemithambo enzulu, engaphakathi emzimbeni. Ngamanye amaxesha, umthambo omkhulu emzimbeni wethu, i-vena cava, unokuchaphazeleka, nto leyo enokukhokelela kwiingxaki zempilo ezinzulu. Ezi ngxaki zemithambo yegazi zibangelwa kukudumba, kungekhona sisiphene kwinkqubo yokuqunjelwa kwegazi.

Ukubandakanyeka kwengqondo

Ngamanye amaxesha esi sifo sinokuchaphazela nobuchopho. Ngokukodwa, ii-membrane ezigubungela ubuchopho (i-meninges). Emva koko iimpawu ezinje ngomkhuhlane, intloko ebuhlungu, ukuqina kwentamo, ubunzima bokulungelelanisa intshukumo xa uhamba zinokubonakala. Ngamanye amaxesha , i-stroke nayo inokwenzeka. Oku kwenzeka xa umthambo wegazi engqondweni uvalekile okanye uqhuma.

Iimpawu zendlela yesisu (GI)

Iingxaki zinokubakho nakwinkqubo yokugaya ukutya, oko kukuthi, emathunjini. Ungabona izinto ezifana nokuqaqamba kwesisu kunye negazi esitulweni . Oku kungenxa yokuba amanxeba emlonyeni nakwindawo yangasese, kunye namanxeba angaphakathi emathunjini. La manxeba emathunjini ayingozi kancinci, kuba anokubangela ukopha emathunjini okanye ukuqhekeka.

Iziphumo kwamanye amalungu omzimba

Nangona kunqabile kakhulu, esi sifo sinokuchaphazela nezinye izitho zomzimba, ezifana nemiphunga, izintso, kunye nemithambo yegazi emikhulu (i-aorta).

Kutheni isifo sikaBehçet senzeka? Yintoni unobangela?

Isizathu esichanekileyo sesi sifo asikaziwa okwangoku . Izazinzulu zisaphanda ngaso. Enye ingcamango kukuba kusenokwenzeka ukuba "sisifo sokuzikhusela komzimba." Ngamafutshane, kuthetha ukuba inkqubo yethu yomzimba yokuzikhusela, inkqubo esikhusela kwizifo, ihlasela iiseli zethu eziphilileyo ngempazamo.. Olu hlaselo lubangela ezi meko zokudumba zikhankanyiweyo apha ngasentla. Ezinye iimpawu zemfuza, ezifana ne-`(HLA-B5)` kunye ne-`(HLA-B51), ziyabonakala kwabanye abantu abanesifo. Nangona kunjalo, ayinguye wonke umntu oneempawu zemfuza ofumana isifo sikaBehçet. Ke ngoko, ii-gene zodwa azinakuthiwa zingunobangela. Abaphandi bakwakholelwa ukuba kubantu abanesifo semfuza, kukho uluvo lokuba esi sifo sinokuvela ngenxa yosulelo (ibhaktiriya okanye intsholongwane) . Oku kuthetha ukuba zombini izinto zemfuza kunye nendalo zinokusichaphazela.

Ngubani osengozini enkulu yokuhlaselwa sesi sifo?

Abanye abantu basengozini enkulu yokufumana esi sifo kunabanye:

• Abantu abahlala kwiindawo apho esi sifo sixhaphake khona (umz. eTurkey, eMbindi Mpuma).
• Abantu abaphakathi kweminyaka engama-20 ukuya kwengama-40 ubudala .
• Abantu abanezakhi zofuzo ezithile (i-HLA-B5 okanye i-HLA-B51)
• Amadoda (amadoda asengozini enkulu yokufumana esi sifo kunabafazi).

Sichongwa njani esi sifo ngokuchanekileyo? (Ukuxilongwa)

Akukho vavanyo lunye lwelabhoratri olunokuchongwa isifo sikaBehçet. Oogqirha bachonga isifo ngokusekwe kwiimpawu zakho. Eyona nto bayifunayo kuku:

• Ukuphinda rhoqo (ngokwesiqhelo ngaphezulu kwezihlandlo ezithathu ngonyaka) kwezilonda zomlomo .
• Ukongeza, kufuneka kubekho ubuncinane ezimbini kwezi mpawu zilandelayo :
• Ukwenzakala kwindawo yesini.
• Ukudumba kwamehlo.
• Iingxaki zolusu.
• Uvavanyo olubonisa ukuba kukho isifo esibangela ukuba umntu angakwazi ukuzikhusela - Oku kuthetha ukuba kuvela irhashalala ebomvu efana ne-blister kwiintsuku ezimbalwa emva kokuba ulusu luhlatyiwe okanye luhlatyiwe. Oku kunika umbono wokuba inkqubo yomzimba yokuzikhusela isebenza kakuhle kangakanani.

Ukuze uxilonge esi sifo ngokuchanekileyo, kuyimfuneko ukuthintela ezinye izifo ezibangela izilonda emlonyeni ezifana nesifo sikaBehçet . Umzekelo, `(systemic lupus)`, `(isifo sikaCrohn)` (imeko yokudumba kwamathumbu), kunye nezinye iintlobo ze `(vasculitis)`. Ugqirha wakho unokuyalela uvavanyo lwegazi ukunceda ukuthintela ezi zifo.

Ngaba esi sisifo esizuzwe njengelifa?

Akukho bungqina bucacileyo bokuba isifo sikaBehçet sidluliselwa kwilifa . Uninzi lweziganeko zenzeka ngokungacwangciswanga, ngaphandle kwembali yosapho. Nangona ipesenti encinci kakhulu yeziganeko ibikwe kumalungu aliqela osapho olunye, akukho ndlela icacileyo yelifa.

Zithini iindlela zokunyanga oku? (Unyango)

Akukho nyango lwesi sifo okwangoku . Nangona kunjalo, kukho amayeza aliqela anokunceda ukulawula iimpawu:

• Ii-Corticosteroids (umz., i-prednisone): Ezi zezona ndlela ziphambili zonyango. La mayeza anciphisa ukudumba kunye nokusebenza ngokugqithisileyo kwenkqubo yomzimba yokuzikhusela.
• I-Colchicine (i-Colcrys®): Oku kunceda kwizilonda zomlomo, izilonda zesini, kwaye ngamanye amaxesha intlungu yamalungu.
• Ezinye izidakamizwa ze-immunosuppressant : Imizekelo ibandakanya i-methotrexate (i-Trexall®, i-Rasuvo®), i-azathioprine (i-Imuran®, i-Azasan®), i-cyclophosphamide (i-Cytoxan®, i-Neosar®), kunye ne-cyclosporine (i-Gengraf®, i-Neoral®, i-Sandimmune®). Kwiimeko ezinzima kakhulu, i-anti-TNF (i-Tumor Necrosis Factor) yezinto eziphilayo ezifana ne-infliximab (Remicade®), i-etanercept (Enbrel®), kunye ne-tocilizumab (Actemra®) nazo zisetyenziswa.

Kubalulekile: La mayeza okunciphisa amasosha omzimba anokunciphisa amandla omzimba wakho okulwa nezifo, nto leyo eyonyusa umngcipheko wakho wokufumana ezinye izifo.

• I-Apremilast (Otezla®) : Le yipilisi ethathwa ngomlomo. Ivunyiwe ukunyanga izilonda emlonyeni kubantu abanesifo sikaBehçet.

Ngokuxhomekeke ekubeni imeko yakho imbi kangakanani na, ugqirha wakho unokuzama ukulawula iimpawu ngezinto ezifana namaconsi amehlo, ii-mouthwash, kunye ne-skin ointments ngaphambi kokusebenzisa la mayeza.

Luhlobo luni lwethemba onokuba nalo ngelixa uphila nesi sifo?

Isifo sikaBehçet sisifo esinganyangekiyo . Oku kuthetha ukuba, nangona unyango lunyangwa, ngamanye amaxesha lunokuphela luze luphinde luvele. Oku kwenza kube nzima ukutsho ukuba unyango luphumelela kangakanani na. Izigulane ezininzi kuya kufuneka zijongane nezi mpawu ngamanye amaxesha ebomini bazo bonke. Nangona kunjalo, uninzi lwabantu lunokuphila ubomi obuqhelekileyo nobupheleleyo .

Indlela yokujamelana ngempumelelo nesi sifo?

Kukho iindlela ezahlukeneyo zokunceda xa uphila nesi sifo:

• Ukulinganisela phakathi kokuphumla nomsebenzi : Ukuzilolonga rhoqo kuya kwenza umzimba wakho uzive uphilile, kunciphise iintlungu zamalungu kunye nezinye iindawo ezinengxaki. Kwakhona, ukuthatha ixesha lokuphumla xa iimpawu zinzima kulungile kwimpilo yakho yengqondo kwaye kunokunciphisa impembelelo yeempawu.
• Amava ahlukeneyo kunye noluntu : Oku kuthetha ukufumana nokuthetha nabanye abantu abanemeko efanayo. Oku kunokuba nzima kuba imeko ayiqhelekanga. Kodwa ugqirha wakho unokukunceda ufumane abantu abaye baba namava afanayo.

Ngaba esi sifo singabulala?

Izinga lokufa kwesi sifo limalunga ne-5%.Izizathu eziphambili zokufa kukugqobhoka kwamathumbu, ukubetheka, kunye nokuqhekeka kwe-aneurysms. Nangona isifo sikaBehçet singabulali ngokuthe ngqo, sinokubangela iingxaki ezahlukeneyo zempilo kunye neemeko zempilo emzimbeni wonke, uninzi lwazo ezibuhlungu. Nangona kunjalo, kunokwenzeka ukulawula esi sifo ngempumelelo kwaye uphile ubomi obuqhelekileyo . Ingakumbi ukuba uzilolonga rhoqo, uphumle, kwaye uthethe nabanye abadlula kwinto efanayo.

Okokugqibela, khumbula ezi zinto!

Isifo sikaBehçet sinokuba yimeko enzima nengakhululekiyo. Kodwa khumbula:

• Esi sisifo esilawulekayo .
• Ukuba unale mpawu, funa ingcebiso kagqirha ngoko nangoko .
• Ungazama ukuphila ubomi obuqhelekileyo ngonyango olufanelekileyo kunye notshintsho kwindlela ophila ngayo.
• Musa ukubandezeleka wedwa, qhagamshelana namaqela enkxaso okanye ezinye izigulane .

Ndiyathemba ukuba olu lwazi luluncedo kuwe. Hlala usempilweni!