Ubusazi ukuba ngamanye amaxesha iingxaki zempilo ezingalindelekanga zinokuvela ngexesha lokukhulelwa? Namhlanje siza kuthetha ngesimo esinokuba yingozi kakhulu ekufuneka sazi ngaso, nokuba singalindelekanga kancinci. Nangona oku kungenzeki kubantu abaninzi, ukuba kuyenzeka, kufuna unyango olukhawulezileyo.
Yintoni le nto kuthiwa sisifo sesibindi esinamafutha (AFLP) ngexesha lokukhulelwa?
Ngamafutshane, i-Acute Fatty Liver of Pregnancy (AFLP) yimeko engaqhelekanga kodwa imbi kakhulu. Oku kwenzeka xa isibindi sakho sigcwala kakhulu ngamafutha ngexesha lokukhulelwa. Oku kunokubangela ukungasebenzi kwesibindi kunye nezinye iingxaki ezisongela ubomi. Enyanisweni, kuthathwa njengengxamiseko yezonyango . Ukuba oku kuyenzeka, eyona nto ingcono onokuyenza kukuzala umntwana ngokukhawuleza.
Ixhaphake kangakanani i-AFLP?
Ungakhathazeki, oku akuqhelekanga kakhulu. Esi simo sibizwa ngokuba yi-AFLP asiqhelekanga kangako. Kuthiwa sichaphazela umntu omnye kuphela kwabayi-10,000 ukuya kwabayi-20,000 abakhulelweyo ngonyaka. Ngoko ke asiyonto uyibona rhoqo.
Zithini iimpawu ze-AFLP? (Qaphela ezi)
I-AFLP idla ngokuqala kwikota yesithathu yokukhulelwa ekupheleni – malunga neeveki ezingama-36 – kwaye idla ngokufunyaniswa. Nangona kunjalo, ngamanye amaxesha inokwenzeka kwangethuba, okanye ide ifike umntwana.
Kukho ezinye iimpawu eziqhele ukubonwa kule meko:
- Isicaphucaphu nokuhlanza: Nangona oku kunokubonakala kuqhelekile ngexesha lokukhulelwa, ngamanye amaxesha kunokuba luphawu lwe-AFLP.
- Intlungu yesisu: Le ntlungu yenzeka ngakumbi kwinxalenye ephezulu ngasekunene yesisu.
- Ukudinwa kakhulu: Akupheleli nje ekudinweni, kodwa kukuziva udinwe kakhulu.
- Ukuziva ungonwabanga emzimbeni: Ukuziva ungonwabanga emzimbeni, ngokungathi unesifo.
- I-Anorexia: Ukulahlekelwa yiminqweno yokutya.
- Ukuziva unxaniwe kakhulu: Nokuba usela amanzi angakanani na, kusavakala ngathi akwanele.
- I-Jaundice: Ulusu lwakho kunye namehlo amhlophe ajika abe tyheli. Olu luphawu olucacileyo.
- Ukudideka okanye ukungakwazi ukugxila: Ubunzima bokugxila, ukuziva ungaphumli.
Khumbula, iimpawu ze-AFLP zinokufana nezezinye iimeko zonyango. Ngoko ke kubalulekile ukuthetha nogqirha wakho ngazo naziphi na iimpawu ezingaqhelekanga ozifumanayo ngexesha lokukhulelwa. I-AFLP yingxamiseko yezonyango efuna unyango olukhawulezileyo.
Kutheni le nto i-AFLP yenzeka? Yintoni isizathu?
Abaphandi abakayazi kakuhle into ebangela i-AFLP. Omnye wemisebenzi ephambili yesibindi sethu kukuqhekeza ii-fatty acids. Kwi-AFLP, kukho ingxaki ngokukwazi kwesibindi ukuqhekeza ezi fatty acids, nto leyo ebangela ukuba amafutha amaninzi aqokeleleke esibindini. La mafutha emva koko avaleleke ngaphakathi esibindini, nto leyo ephazamisana nokusebenza kwesibindi okuqhelekileyo. Oku kunokuba yingozi ebomini ukuba akunyangwa.
Ngaba kukho unxibelelwano lwemfuza? (Ukunqongophala kwe-LCHAD)
Ezinye izifundo zibonise ukuba i-AFLP inokuba nefuthe kwimfuza . Oko kukuthi, inokubangelwa kukungabikho kwe-enzyme ebizwa ngokuba yi -long-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency .
Olu nqongophala (LCHAD) luyingxaki engaqhelekanga kakhulu, (autosomal recessive) . Ngamafutshane, ukuze umntwana azuze oku, bobabini abazali kufuneka bafumane i-gene efanelekileyo. Umntwana onqongophala (LCHAD) akanakuyicola kakuhle i-fatty acids. Emva koko la ma-fatty acids angena egazini likamama nge-placenta. Oku kunokubangela ukuba amafutha aqokeleleke kwisibindi sikamama. Khawuthelekelele indlela utshintsho kwi-metabolism yomzimba womntwana oluchaphazela ngayo umama!
Ziziphi izinto ezibangela umngcipheko wokuphuhlisa i-AFLP?
Ngoku siyazi ukuba le meko, ebizwa ngokuba yi-AFLP, inokuba yimfuza. Oko kuthetha ukuba inokuzuzwa kubazali. Ukongeza, kukho nezinye izinto ezininzi ezinobungozi:
- Ukuba oku kukukhulelwa kwakho kokuqala.
- Ukuba ulindele amawele okanye ngaphezulu.
- Ukuba ulindele inkwenkwe.
- Ukuba unesifo seswekile.
- Ukuba une-cholestasis yesibindi yokukhulelwa.
- Ukuba une-preeclampsia.
- Ukuba utyebile kakhulu.
Kodwa, nangona kukho zonke ezi zinto zinobungozi, ugqirha wakho akanakukwazi ukuqikelela ukuba uza kuba ne-AFLP na. Kwaye asinto onokuyiqikelela okanye ungayithintela. Yiloo nto eyenza ixhalabise ngakumbi.
Ziziphi iingxaki ezinokubakho ze-AFLP? (Oku kunokuba yingozi)
Isifo sesibindi esinamafutha aqatha (AFLP) ngexesha lokukhulelwa singabulala . Wena nomntwana wakho nisengozini yeengxaki ezahlukeneyo. Ezinye zazo zezi:
- Ukungasebenzi kakuhle kwesibindi.
- Ukungasebenzi kakuhle kwezintso.
- Ukungasebenzi kakuhle kwemiphunga.
- Usulelo.
- Ukopha igazi.
Kuyoyikisa ukuva ezi zinto, akunjalo? Yiyo loo nto kubalulekile ukuba uqaphele le meko.
Ungayichonga njani imeko ye-AFLP?
Ngenxa yokuba i-AFLP inokubangela ukungasebenzi kakuhle kwamalungu omzimba,Kubalulekile ukufumanisa isifo kwangethuba kwaye uqale unyango ngokukhawuleza. Ukuxilongwa okuchanekileyo yi -biopsy yesibindi . Kulapho ugqirha wakho ehlola khona izicwili zesibindi sakho phantsi kwe-microscope. Nangona kunjalo, oku akusoloko kukhuselekile ukwenza ngexesha lokukhulelwa. Ke ngoko, ugqirha wakho unokuxilonga i-AFLP ngokusekelwe kwiimpawu zakho kunye nembali yakho yempilo.
Uvavanyo lwegazi lukhangela ntoni?
Ugqirha wakho uza kuyalela uvavanyo lwegazi ukuze kuhlolwe i-AFLP. Ngamanye amaxesha ugqirha wakho unokurhanela i-AFLP ngokusekelwe kwiziphumo zovavanyo lwegazi lokusebenza kwesibindi . Olu vavanyo ludla ngokubonisa izinto ezinje:
- Iienzymes zesibindi eziphakamileyo.
- Iingxaki ngenkqubo yakho yokujiya kwegazi.
- Amanqanaba aphezulu e-ammonia, i-uric acid, kunye neproteni egazini.
- Amanqanaba eswekile egazini aphantsi.
- Iimpawu zomonakalo kwizintso.
Ezinye iimvavanyo
Ukuqinisekisa ukuxilongwa, ugqirha wakho unokuyalela ukuba kwenziwe i -ultrasound scan okanye i -CT scan . Ezi zinokubonelela ngemifanekiso eneenkcukacha zesibindi.
Inyangwa njani i-AFLP? (Unyango olukhawulezileyo lubalulekile!)
Ukuze uphephe iingxaki ezisongela ubomi, ugqirha wakho uya kukucebisa ukuba ubelekise umntwana wakho ngokukhawuleza . Emva kokuba umntwana kunye ne-placenta zisusiwe, isibindi sakho siya kuqala ukubuyela esimeni. Olu lolona nyango luphambili nolukuphela kwalo kule meko.
Ngaba kukho into endinokuyenza ukunciphisa umngcipheko wam we-AFLP?
Le yingxaki abantu abaninzi abanayo. I-AFLP yimeko engaqhelekanga. Kwaye, akukho nto unokuyenza ukuyithintela okanye ukuyifumanisa kwangaphambili . Le yinxalenye engathandekiyo yesi sifo.
Kuza kwenzeka ntoni ukuba ndine-AFLP?
Ukuba une-AFLP, kufuneka ubeleke umntwana wakho ngoko nangoko . Ukusebenza kwesibindi sakho kuya kuqala ukubuyela esiqhelweni kwiintsuku ezili-10 emva kokubeleka. Kuya kufuneka ujongwe ngoogqirha besibhedlele de iziphumo zovavanyo lwesibindi sakho zibuyele esiqhelweni.
Akunakwenzeka ukutsho ngqo ukuba yintoni na ingozi yakho yokuphinda ube ne-AFLP. Ugqirha wakho unokucebisa uvavanyo lwemfuza ukuze kubonwe ukuba kukho na ukungaqheleki kwi-fatty acids okunokuba negalelo ekuphuhlisweni kwe-AFLP. Banokucebisa nokuba ukuba ukhulelwa kwakhona kwixesha elizayo, kufuneka ukhulelwe yingcali yamayeza okukhulelwa ukusuka kumama ukuya kumntwana ongekazalwa .
Yintoni ingxaki ngomntwana?
Ubunzima bemeko kumama buhlala bumisela ukuba ichaphazela kangakanani na umntwana. Abanye abantwana basengozini yokuba nesifo esibizwa ngokuba yi -nonketotic hypoglycemia (ukungakwazi ukucubungula kakuhle ii-amino acids). Abanye banokuba neemeko ezifana ne -dilated cardiomyopathy (imisipha yentliziyo ebuthathaka) okanye i-neuropathy (umonakalo wemithambo-luvo). Nangona kunjalo, kwiimeko ezininzi, umngcipheko kumntwana ungaphantsi komngcipheko kumama.
Ndifanele ndibonane nogqirha nini?
Kubalulekile ukwabelana ngembali yakho epheleleyo yezonyango nogqirha wakho ngexesha lokukhulelwa kwaye ubazise ngazo naziphi na iimpawu onazo. Ukunyaniseka kuya kukunceda ufumane unyango olufanelekileyo olufunekayo.
Ukuba ufumana naziphi na kwezi mpawu zilandelayo ngexesha lokukhulelwa, bonana nogqirha ngokukhawuleza :
- Intlungu yesisu okanye yesinqe engapheliyo.
- Ukudinwa kakhulu okanye ukungabi namandla.
- Ukucaphuka nokuhlanza okungapheliyo.
- Intloko ebuhlungu engasoze iphele.
Ezi zisenokuba ziimpawu zokukhulelwa eziqhelekileyo, kodwa zinokuba luphawu lwento enzulu. Ngoko ke musa ukurhanela.
Ndingayibuza yiphi imibuzo ugqirha wam?
Khawucinge nje, ukuba ugqirha wakho ebekuxelela ukuba une-AFLP... kuqhelekile ukuba ube nemibuzo emininzi. Usenokufuna ukuzibuza imibuzo efana nale:
- "Gqirha, ngaba kufuneka ndibeleke umntwana ngoku?"
- "Ingaba ubomi bam busengozini?"
- "Ingaba ubomi bomntwana wam busemngciphekweni?"
- "Ngaba le meko ye-AFLP iza kuba ngcono?"
- "Luhlobo luni lonyango endiludingayo?"
- "Ingaba oku kuya kuphinda kwenzeke ukuba ndikhulelwe kwakhona?"
- "Kutheni oku kwenzeke kum, gqirha?"
Buza yonke imibuzo onokuyicinga ngolu hlobo. Musa ukuzibamba.
Yintoni umahluko phakathi kwe-AFLP kunye ne-HELLP syndrome?
I-HELLP syndrome ( i-Hemolysis, ii-Enzymes zesibindi eziphakamileyo , kunye ne-Low Platelet Count Syndrome)** yimeko eyenzeka ngexesha lokukhulelwa kwaye ifana ne-AFLP. Umahluko ophambili phakathi kwezi meko zimbini kukuba iziphumo zovavanyo lwegazi zitshintsha njani ngokuhamba kwexesha. I-AFLP idla ngokubandakanya iingxaki zokujiya kwegazi kunye notshintsho kumanqanaba eeplatelet. Nangona kunjalo, i-HELLP syndrome idla ngokubandakanya ukwehla kancinci kancinci kwenani leeplatelet.
Ukongeza, abantu abane-AFLP banamathuba amaninzi okuba:
- Ukuphazamiseka okukhulu kwiimvavanyo zokusebenza kwesibindi.
- Nakuphi na ukungaqheleki kwamanqanaba eswekile egazini.
- Iimpawu zokungasebenzi kakuhle kwezintso.
- Amanqanaba aphezulu e-bilirubin (i-bilirubin yimveliso elahliweyo) kwiimvavanyo.
- I-Acidosis (ukwanda kwe-asidi egazini).
- (I-Proteinuria)(Ubukho beprotheyini kumchamo).
- Utshintsho ekusebenzeni kwengqondo (umz., ukungakwazi ukucinga kakuhle, ukudideka).
Ingaba kuqhelekile ukuba nesibindi esinamafutha ngexesha lokukhulelwa?
Kwanakwibantu abangakhulelwanga, isifo sesibindi esinamafutha sisifo esixhaphakileyo nesinokunyangwa. Uninzi lwabantu lunamafutha athile esibindini sabo. Nangona kunjalo, ukuba la mafutha ayaqokelelana, anokubangela ukuba isibindi singaphumeleli. Oku kuyingozi kakhulu ngexesha lokukhulelwa , kuba isibindi yindlela yomzimba yokususa iityhefu. Ukuba isibindi sakho (okanye isibindi somntwana wakho) asisebenzi kakuhle, izinto ezinobungozi zinokuqokelelana egazini lakho.
Okokugqibela, nantsi into endifuna ukuyithetha kuwe (Umyalezo Wokubuyela Ekhaya)
I-AFLP, okanye isifo sesibindi esinamafutha esiqatha sokukhulelwa, yimeko engaqhelekanga kodwa enzulu. Ayinakuthintelwa okanye iqikelelwe. Oku kuthetha ukuba kubalulekile ukuthetha nogqirha wakho ngembali yakho yempilo kunye nazo naziphi na iimpawu ezingaqhelekanga onokuzifumana ngexesha lokukhulelwa kwakho. Ezi ngxoxo ziya kunceda ugqirha wakho ukuba abone iingxaki ezinokubakho aze akunike unyango olufunayo.
Musa ukoyika, kodwa lumka . Nika ingqalelo emzimbeni wakho. Ukuba uziva into engaqhelekanga okanye eyahlukileyo, funa ingcebiso kagqirha ngoko nangoko. Eyona nto ibalulekileyo kukuba wena nomntwana wakho nihlale nisempilweni.
Isibindi esinamafutha ngexesha lokukhulelwa, i-AFLP, iingxaki zokukhulelwa, isifo sesibindi, i-jaundice, ukuzala, ukungabikho kwe-LCHAD











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