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Singathetha ngeBirdshot Chorioretinopathy namhlanje?

Singathetha ngeBirdshot Chorioretinopathy namhlanje?

Ngaba wakha waziva ngathi ubona izinto ezincinci ezimnyama zintanta phambi kwamehlo akho? Okanye mhlawumbi umbono wakho awucacanga? Ezi zinokuba zizinto eziqhelekileyo, kodwa ngamanye amaxesha zinokuba luphawu lwengxaki engaphakathi kweliso lakho. Namhlanje siza kuthetha ngesinye sezifo zamehlo ezingaqhelekanga ezinokulawulwa ukuba zinyangwa ngokufanelekileyo.

Yintoni le (i-Birdshot Chorioretinopathy)?

Ngamafutshane, iBirdshot Chorioretinopathy, okanye iBSCR ngamafutshane, sisifo esingaqhelekanga sokudumba esifumaneka ngaphakathi kweliso. Asikuko ukuba sisifo esingapheliyo , oko kuthetha ukuba asipheli ngexesha elifutshane, kodwa sisifo esiqhubekayo. Ukuba asinyangwa kakuhle, sinokukhokelela kutshintsho oluhlala luhleli lombono okanye ukulahleka ngokupheleleyo kombono .

(BSCR) sisifo esibi kakhulu esikwiqela lezifo ezibizwa ngokuba yi-"Uveitis", ezonakalisa izicwili ezingaphakathi kweliso. Ngokuyintloko sibandakanya ukudumba kwezi zinto zilandelayo:

  • I-Retina : Le yinwebu ebonakala ekukhanyeni ngasemva kweliso lethu. Ifana nefilimu ekwikhamera. Imifanekiso esiyibonayo irekhodwa apha.
  • I-Choroid : Le ikwindawo engaphantsi kwe-retina. Le yi-membrane edibanisa i-retina nenxalenye emhlophe yeliso, kwaye inika igazi kwi-retina, oko kukuthi, iyondla.

Eyona nto ibalulekileyo kwesi sifo kukuvela kwamabala amancinci, angqukuva, anombala okhrimu kwindawo enzulu ye-retina kunye nomaleko ongaphezulu we-choroid. Iimpawu zokuqala zihlala ziquka izinto ezimnyama ezidada phambi kwamehlo (ii-floaters) , umbono ofipheleyo , okanye zombini. Le meko idla ngokuchaphazela amehlo omabini .

Ekuhambeni kwexesha, lo monakalo unokukhokelela kwiimeko ezifana ne -cystoid macular edema okanye i-glaucoma . Nangona kungekho nyango, i-Birdshot Chorioretinopathy sisifo esinokunyangwa . Ukufunyanwa kwangoko kubalulekile ukuze unyango luphumelele.

Ngubani ofumana i-Birdshot Chorioretinopathy?

Enyanisweni, esi sifo sinokukhula nakubani na. Kodwa sixhaphake kakhulu kubantu abadala abamhlophe abaneminyaka ephakathi kwama-40 nama-60. Kunqabile kakhulu ukuba abantwana babe nesi sifo.

Ngaba zikhona ezinye izifo ezifana nale (Birdshot Chorioretinopathy)?

Ewe, ezinye izifo ezininzi, kuquka nezinye izifo ezikwiqela le-Uveitis, zinokuba neempawu ezifanayo neze-Birdshot Chorioretinopathy. Ke ngoko, kubaluleke kakhulu ukufumana uxilongo oluchanekileyo ukuze ufumane unyango olufanelekileyo. Ezinye zezifo ezinokufana ne-BSCR zezi:

  • I-Lymphoma (uhlobo lomhlaza)
  • I-Sarcoidosis (isifo esibangela ukudumba okuncinci kwiindawo ezahlukeneyo zomzimba)
  • `(Sympathetic ophthalmia)` (Uhlobo olungaqhelekanga lwe-uveitis olubangelwa kukwenzakala kwamehlo)
  • I-Syphilis (isifo esidluliselwa ngesondo)
  • `(Isifo se-ocular histoplasmosis esicingelwayo (POHS))` (Imeko echaphazela amehlo ebangelwa lusulelo lwefungus)
  • `(Isifo Sephepha)` (Isifo Sephepha)
  • `(Isifo seVogt-Koyanagi-Harada)` (isifo esichaphazela inkqubo yemithambo-luvo, esichaphazela umbono nokuva)

Kukwakho neqela lezifo ezibangelwa kukudumba ezibizwa ngokuba yi-"White dot syndromes", ezinokubonisa iimpawu ze-BSCR. Ezi zibangela "izilonda" kwi-retina nakwi-choroid. Eminye imizekelo yile:

  • `(I-Acute posterior multifocal placoid pigment epitheliopathy (i-APPMPPE))`
  • `(I-Multifocal choroiditis kunye ne-panuveitis (MCP))`
  • `(Isifo samachaphaza amhlophe amaninzi e-evanescent (MEWDS))`
  • `(I-Punctate inner choroidopathy (PIC))`

Kutheni oku kubizwa ngokuba yiBirdshot Chorioretinopathy?

Esi sisifo esitsha ngokwenene, esachazwa okokuqala ngo-1949. Kwakungekho de kwaba ngu-1980 apho oogqirha ababini bamehlo basibiza ngegama elithi "(Birdshot Chorioretinopathy)". Isizathu soku kukuba la mabala asasazeke kulo lonke i-retina, anombala okhrimu noorenji . Eli gama livela kwinto yokuba ipateni yala mabala ifana nepateni yeembumbulu ezincinci (i-birdshot) ezisetyenziselwa ukudubula iintaka. Khawuthelekelele, kukho amabala ngaphakathi kweliso, njengeembumbulu ezisasazekileyo xa kudubula umpu.

Ngaba kukho amanye amagama alo mba?

Ewe, kukho amanye amagama aliqela asetyenziswa kwesi sifo (i-Birdshot Chorioretinopathy):

  • `(I-Birdshot chorioretinitis)`
  • `(i-Birdshot retinochoroiditis)`
  • `(i-Birdshot retinochoroidopathy)`
  • `(Umkhuhlane we-Birdshot)`
  • `(BSCR)` (igama elifutshane)
  • `(I-Posterior uveitis)` (i-uveitis eyenzeka ngasemva kweliso)
  • `(I-Vitiliginous choroiditis)`

Ixhaphake kangakanani i-Birdshot Chorioretinopathy?

Esi sisifo esingaqhelekanga . Abaphandi bakholelwa ukuba sichaphazela abantu abangaphantsi komnye kwikhulu lamawaka. Oku kuthetha ukuba naseSri Lanka, basenokuba khona abantu abanaso esi sifo, kodwa inani lincinci kakhulu.

Yintoni ebangela i-Birdshot Chorioretinopathy?

Abaphandi abakayazi eyona nto ibangela esi sifo, kodwa bacinga ukuba sisifo esibangelwa kukuzikhusela komzimba . Ngamafutshane, inkqubo yokuzikhusela yomzimba wethu, inkqubo yokuzikhusela yomzimba, ihlasela ngempazamo izicubu zethu ezisempilweni.

Ngaphezulu kwama-90% abantu abafunyaniswe benale gene (BSCR) bane-antibody gene (imolekyuli evuselela inkqubo yomzimba yokuzikhusela) ebizwa ngokuba yi-`(HLA-A29)` emizimbeni yabo. Le yinto ezuzwe ngabazali. Nangona kunjalo, i-`(HLA-A29)` ayifuneki ukuze ikhule (Birdshot Chorioretinopathy). Kwakhona, kunokwenzeka ukuba ube nale gene ye-antibody kodwa ungaphumi kwesi sifo.

Zithini iimpawu zeBirdshot Chorioretinopathy?

Iimpawu zesi sifo zinokwahluka kumntu nomntu.Isifo esiqhubekayo sisifo esiba mandundu kancinci kancinci kangangeenyanga ukuya kwiminyaka.

Iimpawu zokuqala ze-Birdshot Chorioretinopathy zihlala zilandelayo:

  • Ukubona izinto ezimnyama zidada phambi kwamehlo (iiflethi)
  • Umbono ofipheleyo

Le meko ayidli ngokubangela iintlungu okanye ukubomvu kwamehlo . Nangona kunjalo, unokufumana oku kulandelayo:

  • Umbono uyatshintsha okanye umbono awuboni kakuhle.
  • Ukubona okuphantsi okanye ubunzima bokujonga umgama.
  • Uxinzelelo oluphezulu emehlweni (uxinzelelo oluphezulu lwegazi emehlweni).
  • Ukungaboni kakuhle ebusuku (nyctalopia) (ukubona kakubi ebusuku).
  • Iingxaki zokubona imibala (`(ukungaboni imibala)`), ubunzima bokwahlula imibala ethile (`(dyschromatopsia)`.
  • Uvelwano ekukhanyeni okuqaqambileyo okanye ekukhanyeni okuqaqambileyo (photophobia).

Abanye abantu banokuba notshintsho olungaqhelekanga embonweni okanye iingxaki zengqondo. Umzekelo:

  • Impembelelo yefeni esilingini : Xa uvala amehlo akho, kubonakala ngathi ifeni esilingini okanye i-windmill iyajikeleza.
  • Ukubona ukukhanya okanye ukukhanya okuqaqambileyo (photopsia) okanye ukubona iimilo ezigqwethekileyo (metamorphopsia) .
  • Umbono ofipheleyo, okhanyayo, ngokungathi ujonge emanzini okanye kwiglasi engcolileyo .

Kwiimeko ezinzima kakhulu, iimeko ezifana ne-cataracts okanye i-glaucoma zinokuvela. Ezi zinokubangela ukulahleka okukhulu kokubona nasemva konyango lokudumba. I-Birdshot Chorioretinopathy inokubangela iingxaki kumbindi we-retina, njenge-cystoid macular edema kunye ne-epiretinal membranes.

Ifunyanwa njani i-Birdshot Chorioretinopathy?

Esi sifo ngamanye amaxesha sinokuba nzima ukusifumanisa kuba sisifo esingaqhelekanga kwaye amabala ahlukileyo asenokungabonakali kwizigaba zokuqala zesi sifo.

Iingcali zamehlo zihlala zixilonga i-BSCR ngokuhlolwa kwamehlo. Zikwahlola igazi ukujonga ukuba unayo na i-HLA-A29 antibody.

Oogqirha banokusebenzisa iintlobo ngeentlobo zovavanyo ukukujonga ngokuhamba kwexesha. Kubalulekile ukuhlala unxibelelana nogqirha wakho ukuze ufumane unyango olufunayo.

Ngaba ikho indlela yokunyanga i-Birdshot Chorioretinopathy ngokupheleleyo?

Ngelishwa, akukho nyango lupheleleyo lwesi sifo. Nangona kunjalo, ukuba esi sifo sifunyenwe kwaye sinyangwa kwangethuba , iimpawu zinokuncitshiswa kwaye esi sifo sinokuthintelwa ukuba singabi mandundu.

Khumbula: eyona nto ibalulekileyo kukufumanisa isifo kwangethuba uze uqale unyango!

Ngubani onokuba kwiqela lam lonyango?

Iqela lakho lokhathalelo liza kukucebisa unyango, likujonge, kwaye lilungise amayeza akho ngokwemeko yakho kunye nemiphumo emibi. Iqela lakho lingabandakanya:

  • Ingcali yamehlo : Ugqirha oyintloko osebenza ngamehlo.
  • Ingcali yezifo ze-Nephrologist : Kuba ezinye iindlela zonyango zichaphazela izintso.
  • Ingcali yezifo zamehlo: Ugqirha oqeqeshwe ngokukhethekileyo kwiingxaki zenkqubo yokuzikhusela yamehlo.
  • Ingcali yeRheumatology: Ugqirha ogxile kwizifo ezinxulumene nokudumba emzimbeni, kuba oku kukwasisifo sokudumba.
  • Ugqirha wamathambo : Kuba ezinye iindlela zonyango zichaphazela amathambo.

Inyangwa njani i-Birdshot Chorioretinopathy?

Unyango lwesi sifo luxhomekeke kubukhulu bemeko yakho kunye nendlela etshintsha ngayo ngokuhamba kwexesha. Injongo ephambili yonyango kukunciphisa ukudumba emehlweni akho kunye nokuthintela okanye ukubuyisela umbono olahlekileyo .

Oogqirha badla ngokuqala banike iidosi eziphezulu ze-corticosteroids (uhlobo lwamayeza e-steroid) ukulawula ukudumba kwamehlo. Emva koko, idosi incitshiswa kancinci kancinci ukunciphisa umngcipheko weziphumo ebezingalindelekanga. Ungafumana ii-steroids ngeendlela ezilandelayo:

  • Amaconsi amehlo
  • Amayeza omlomo
  • Isixhobo esincinci esifakelwa ngaphakathi kweliso ngotyando (intravitreal implant)
  • Inaliti
  • Inikwa emthanjeni (nge-IV - ngemithambo yegazi)

Abantu abaninzi kufuneka bathathe amayeza okunciphisa amajoni omzimba ixesha elide . La mayeza ayayithintela inkqubo yakho yomzimba ukuba ingahlaseli amehlo akho. Elinye okanye ngaphezulu kwezi zilandelayo lingasetyenziswa:

  • `(Iiarhente ze-alkylating)`
  • `(Amayeza e-Antimetabolite)`
  • `(Iiarhente zebhayoloji)` (amayeza ebhayoloji)
  • `(Ukudluliselwa kweeseli ze-T/izithinteli ze-calcineurin)`

Ngaba unyango lweBirdshot Chorioretinopathy (Birdshot Chorioretinopathy) lunokubangela iziphumo ebezingalindelekanga?

Ewe, ukusetyenziswa ixesha elide kwee-steroids kunye ne-immunosuppressants kunokubangela iziphumo ebezingalindelekanga ezibi kakhulu . Umzekelo, iingxaki zesisu (izilonda, izilonda) okanye iingxaki zamathambo (i-osteoporosis) zinokubakho. La mayeza anokunyusa umngcipheko wokuba ne-cataracts okanye i-glaucoma.

Ugqirha wakho uza kukujonga ukuba azikho na iziphumo ebezingalindelekanga aze akunike amanye amayeza ukuba kuyimfuneko. Ukuba uthatha ii-steroids ezithathwa ngomlomo, ugqirha wakho uza kukujonga ukuba amathambo akho alahlekile na (i-osteoporosis) kunye nomngcipheko wakho wokuqhekeka.

Ugqirha wakhoKungacetyiswa ukuba kuhlolwe uxinano lwamathambo. Amayeza (ii-bisphosphonates) anganikwa ukuthintela ukulahleka kwamathambo.

Luhlobo luni lokubekwa esweni ixesha elide endiludingayo (BSCR)?

Qaphela naluphi na utshintsho okanye iingxaki kwimeko yakho. Ugqirha wakho uza kwenza uvavanyo lwegazi nomchamo ukujonga ukuba izintso zakho, isibindi kunye nomongo wethambo zisebenza kakuhle kangakanani na. Kuya kufuneka uhlolwe amehlo rhoqo, uvavanyo lwentsimi yokubona, kunye ne-optical coherence tomography (OCT) scans.

Ndingawunciphisa na umngcipheko wam wokuba ne-Birdshot Chorioretinopathy?

Okwangoku akukho ndlela eyaziwayo yokuthintela esi sifo. Kwiimeko ezininzi, kukholelwa ukuba sibangelwa yi-antibody gene ethile (i-antigen) efunyanwa kumalungu osapho.

Ukuhlolwa kwamehlo rhoqo kunokunceda ekufumaneni iimpawu zokuqala zesifo, ukuze ufumane unyango olukhawulezileyo ukuba kuyimfuneko. Xelela ugqirha wakho ukuba kukho umntu kusapho lwakho oneengxaki zamehlo.

Iyintoni imbono ye-Birdshot Chorioretinopathy?

Imbonakalo yesi sifo iyahluka kumntu nomntu . Ixhomekeke kubukhali bemeko kunye nempumelelo yonyango. Kwiimeko ezibuthathaka, unyango lunokunceda ekugcineni okanye ukuphucula umbono.

Ndifanele ndifumane nini ingcebiso kagqirha malunga (ne-Birdshot Chorioretinopathy)?

Kubalulekile ukufuna ukuxilongwa ngokukhawuleza kunye nonyango kwingcali yamehlo ye-Birdshot Chorioretinopathy. Nokuba umbono wakho ubonakala ulungile, uvavanyo lwamehlo lunokufumanisa ukudumba okuphantsi.

Xelela ugqirha wakho ngazo naziphi na iziphumo ebezingalindelekanga, utshintsho kwiimpawu, okanye umbono ovela kumayeza akho. Unganikwa elinye iyeza ukuba kuyimfuneko. Ugqirha wakho uza kuthetha nawe malunga neendlela ezikulungeleyo.

Umyalezo Wokugqibela Wokuya Ekhaya

(I-Birdshot Chorioretinopathy) sisifo esingaqhelekanga kodwa esinokunyangwa . Ngoko ke ungoyiki. Eyona nto ibalulekileyo kukujonga amehlo akho rhoqo kwaye ulandele iingcebiso zikagqirha wakho . Ekuhambeni kwexesha, ugqirha wakho uya kukuxelela indlela yokukhusela umbono wakho kunye nokuthintela iingxaki. Emva koko uya kukwazi ukubona ihlabathi ngokucacileyo ixesha elide. Nyamekela amehlo akho, kuba axabiseke kakhulu!


I- Birdshot Chorioretinopathy, Izifo Zamehlo, Ukuphazamiseka Kokubona, I-Uveitis, I-Retina, Izifo Zokuzikhusela Ngokwasemzimbeni, Unyango Lwamehlo

Frequently Asked Questions (FAQ)

Ngaba kukho amanye amagama alo mba?

Ewe, kukho amanye amagama aliqela asetyenziswa kwesi sifo (i-Birdshot Chorioretinopathy):

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Singathetha ngeBirdshot Chorioretinopathy namhlanje?

Singathetha ngeBirdshot Chorioretinopathy namhlanje?

Ngaba wakha waziva ngathi ubona izinto ezincinci ezimnyama zintanta phambi kwamehlo akho? Okanye mhlawumbi umbono wakho awucacanga? Ezi zinokuba zizinto eziqhelekileyo, kodwa ngamanye amaxesha zinokuba luphawu lwengxaki engaphakathi kweliso lakho. Namhlanje siza kuthetha ngesinye sezifo zamehlo ezingaqhelekanga ezinokulawulwa ukuba zinyangwa ngokufanelekileyo.

Yintoni le (i-Birdshot Chorioretinopathy)?

Ngamafutshane, iBirdshot Chorioretinopathy, okanye iBSCR ngamafutshane, sisifo esingaqhelekanga sokudumba esifumaneka ngaphakathi kweliso. Asikuko ukuba sisifo esingapheliyo , oko kuthetha ukuba asipheli ngexesha elifutshane, kodwa sisifo esiqhubekayo. Ukuba asinyangwa kakuhle, sinokukhokelela kutshintsho oluhlala luhleli lombono okanye ukulahleka ngokupheleleyo kombono .

(BSCR) sisifo esibi kakhulu esikwiqela lezifo ezibizwa ngokuba yi-"Uveitis", ezonakalisa izicwili ezingaphakathi kweliso. Ngokuyintloko sibandakanya ukudumba kwezi zinto zilandelayo:

  • I-Retina : Le yinwebu ebonakala ekukhanyeni ngasemva kweliso lethu. Ifana nefilimu ekwikhamera. Imifanekiso esiyibonayo irekhodwa apha.
  • I-Choroid : Le ikwindawo engaphantsi kwe-retina. Le yi-membrane edibanisa i-retina nenxalenye emhlophe yeliso, kwaye inika igazi kwi-retina, oko kukuthi, iyondla.

Eyona nto ibalulekileyo kwesi sifo kukuvela kwamabala amancinci, angqukuva, anombala okhrimu kwindawo enzulu ye-retina kunye nomaleko ongaphezulu we-choroid. Iimpawu zokuqala zihlala ziquka izinto ezimnyama ezidada phambi kwamehlo (ii-floaters) , umbono ofipheleyo , okanye zombini. Le meko idla ngokuchaphazela amehlo omabini .

Ekuhambeni kwexesha, lo monakalo unokukhokelela kwiimeko ezifana ne -cystoid macular edema okanye i-glaucoma . Nangona kungekho nyango, i-Birdshot Chorioretinopathy sisifo esinokunyangwa . Ukufunyanwa kwangoko kubalulekile ukuze unyango luphumelele.

Ngubani ofumana i-Birdshot Chorioretinopathy?

Enyanisweni, esi sifo sinokukhula nakubani na. Kodwa sixhaphake kakhulu kubantu abadala abamhlophe abaneminyaka ephakathi kwama-40 nama-60. Kunqabile kakhulu ukuba abantwana babe nesi sifo.

Ngaba zikhona ezinye izifo ezifana nale (Birdshot Chorioretinopathy)?

Ewe, ezinye izifo ezininzi, kuquka nezinye izifo ezikwiqela le-Uveitis, zinokuba neempawu ezifanayo neze-Birdshot Chorioretinopathy. Ke ngoko, kubaluleke kakhulu ukufumana uxilongo oluchanekileyo ukuze ufumane unyango olufanelekileyo. Ezinye zezifo ezinokufana ne-BSCR zezi:

  • I-Lymphoma (uhlobo lomhlaza)
  • I-Sarcoidosis (isifo esibangela ukudumba okuncinci kwiindawo ezahlukeneyo zomzimba)
  • `(Sympathetic ophthalmia)` (Uhlobo olungaqhelekanga lwe-uveitis olubangelwa kukwenzakala kwamehlo)
  • I-Syphilis (isifo esidluliselwa ngesondo)
  • `(Isifo se-ocular histoplasmosis esicingelwayo (POHS))` (Imeko echaphazela amehlo ebangelwa lusulelo lwefungus)
  • `(Isifo Sephepha)` (Isifo Sephepha)
  • `(Isifo seVogt-Koyanagi-Harada)` (isifo esichaphazela inkqubo yemithambo-luvo, esichaphazela umbono nokuva)

Kukwakho neqela lezifo ezibangelwa kukudumba ezibizwa ngokuba yi-"White dot syndromes", ezinokubonisa iimpawu ze-BSCR. Ezi zibangela "izilonda" kwi-retina nakwi-choroid. Eminye imizekelo yile:

  • `(I-Acute posterior multifocal placoid pigment epitheliopathy (i-APPMPPE))`
  • `(I-Multifocal choroiditis kunye ne-panuveitis (MCP))`
  • `(Isifo samachaphaza amhlophe amaninzi e-evanescent (MEWDS))`
  • `(I-Punctate inner choroidopathy (PIC))`

Kutheni oku kubizwa ngokuba yiBirdshot Chorioretinopathy?

Esi sisifo esitsha ngokwenene, esachazwa okokuqala ngo-1949. Kwakungekho de kwaba ngu-1980 apho oogqirha ababini bamehlo basibiza ngegama elithi "(Birdshot Chorioretinopathy)". Isizathu soku kukuba la mabala asasazeke kulo lonke i-retina, anombala okhrimu noorenji . Eli gama livela kwinto yokuba ipateni yala mabala ifana nepateni yeembumbulu ezincinci (i-birdshot) ezisetyenziselwa ukudubula iintaka. Khawuthelekelele, kukho amabala ngaphakathi kweliso, njengeembumbulu ezisasazekileyo xa kudubula umpu.

Ngaba kukho amanye amagama alo mba?

Ewe, kukho amanye amagama aliqela asetyenziswa kwesi sifo (i-Birdshot Chorioretinopathy):

  • `(I-Birdshot chorioretinitis)`
  • `(i-Birdshot retinochoroiditis)`
  • `(i-Birdshot retinochoroidopathy)`
  • `(Umkhuhlane we-Birdshot)`
  • `(BSCR)` (igama elifutshane)
  • `(I-Posterior uveitis)` (i-uveitis eyenzeka ngasemva kweliso)
  • `(I-Vitiliginous choroiditis)`

Ixhaphake kangakanani i-Birdshot Chorioretinopathy?

Esi sisifo esingaqhelekanga . Abaphandi bakholelwa ukuba sichaphazela abantu abangaphantsi komnye kwikhulu lamawaka. Oku kuthetha ukuba naseSri Lanka, basenokuba khona abantu abanaso esi sifo, kodwa inani lincinci kakhulu.

Yintoni ebangela i-Birdshot Chorioretinopathy?

Abaphandi abakayazi eyona nto ibangela esi sifo, kodwa bacinga ukuba sisifo esibangelwa kukuzikhusela komzimba . Ngamafutshane, inkqubo yokuzikhusela yomzimba wethu, inkqubo yokuzikhusela yomzimba, ihlasela ngempazamo izicubu zethu ezisempilweni.

Ngaphezulu kwama-90% abantu abafunyaniswe benale gene (BSCR) bane-antibody gene (imolekyuli evuselela inkqubo yomzimba yokuzikhusela) ebizwa ngokuba yi-`(HLA-A29)` emizimbeni yabo. Le yinto ezuzwe ngabazali. Nangona kunjalo, i-`(HLA-A29)` ayifuneki ukuze ikhule (Birdshot Chorioretinopathy). Kwakhona, kunokwenzeka ukuba ube nale gene ye-antibody kodwa ungaphumi kwesi sifo.

Zithini iimpawu zeBirdshot Chorioretinopathy?

Iimpawu zesi sifo zinokwahluka kumntu nomntu.Isifo esiqhubekayo sisifo esiba mandundu kancinci kancinci kangangeenyanga ukuya kwiminyaka.

Iimpawu zokuqala ze-Birdshot Chorioretinopathy zihlala zilandelayo:

  • Ukubona izinto ezimnyama zidada phambi kwamehlo (iiflethi)
  • Umbono ofipheleyo

Le meko ayidli ngokubangela iintlungu okanye ukubomvu kwamehlo . Nangona kunjalo, unokufumana oku kulandelayo:

  • Umbono uyatshintsha okanye umbono awuboni kakuhle.
  • Ukubona okuphantsi okanye ubunzima bokujonga umgama.
  • Uxinzelelo oluphezulu emehlweni (uxinzelelo oluphezulu lwegazi emehlweni).
  • Ukungaboni kakuhle ebusuku (nyctalopia) (ukubona kakubi ebusuku).
  • Iingxaki zokubona imibala (`(ukungaboni imibala)`), ubunzima bokwahlula imibala ethile (`(dyschromatopsia)`.
  • Uvelwano ekukhanyeni okuqaqambileyo okanye ekukhanyeni okuqaqambileyo (photophobia).

Abanye abantu banokuba notshintsho olungaqhelekanga embonweni okanye iingxaki zengqondo. Umzekelo:

  • Impembelelo yefeni esilingini : Xa uvala amehlo akho, kubonakala ngathi ifeni esilingini okanye i-windmill iyajikeleza.
  • Ukubona ukukhanya okanye ukukhanya okuqaqambileyo (photopsia) okanye ukubona iimilo ezigqwethekileyo (metamorphopsia) .
  • Umbono ofipheleyo, okhanyayo, ngokungathi ujonge emanzini okanye kwiglasi engcolileyo .

Kwiimeko ezinzima kakhulu, iimeko ezifana ne-cataracts okanye i-glaucoma zinokuvela. Ezi zinokubangela ukulahleka okukhulu kokubona nasemva konyango lokudumba. I-Birdshot Chorioretinopathy inokubangela iingxaki kumbindi we-retina, njenge-cystoid macular edema kunye ne-epiretinal membranes.

Ifunyanwa njani i-Birdshot Chorioretinopathy?

Esi sifo ngamanye amaxesha sinokuba nzima ukusifumanisa kuba sisifo esingaqhelekanga kwaye amabala ahlukileyo asenokungabonakali kwizigaba zokuqala zesi sifo.

Iingcali zamehlo zihlala zixilonga i-BSCR ngokuhlolwa kwamehlo. Zikwahlola igazi ukujonga ukuba unayo na i-HLA-A29 antibody.

Oogqirha banokusebenzisa iintlobo ngeentlobo zovavanyo ukukujonga ngokuhamba kwexesha. Kubalulekile ukuhlala unxibelelana nogqirha wakho ukuze ufumane unyango olufunayo.

Ngaba ikho indlela yokunyanga i-Birdshot Chorioretinopathy ngokupheleleyo?

Ngelishwa, akukho nyango lupheleleyo lwesi sifo. Nangona kunjalo, ukuba esi sifo sifunyenwe kwaye sinyangwa kwangethuba , iimpawu zinokuncitshiswa kwaye esi sifo sinokuthintelwa ukuba singabi mandundu.

Khumbula: eyona nto ibalulekileyo kukufumanisa isifo kwangethuba uze uqale unyango!

Ngubani onokuba kwiqela lam lonyango?

Iqela lakho lokhathalelo liza kukucebisa unyango, likujonge, kwaye lilungise amayeza akho ngokwemeko yakho kunye nemiphumo emibi. Iqela lakho lingabandakanya:

  • Ingcali yamehlo : Ugqirha oyintloko osebenza ngamehlo.
  • Ingcali yezifo ze-Nephrologist : Kuba ezinye iindlela zonyango zichaphazela izintso.
  • Ingcali yezifo zamehlo: Ugqirha oqeqeshwe ngokukhethekileyo kwiingxaki zenkqubo yokuzikhusela yamehlo.
  • Ingcali yeRheumatology: Ugqirha ogxile kwizifo ezinxulumene nokudumba emzimbeni, kuba oku kukwasisifo sokudumba.
  • Ugqirha wamathambo : Kuba ezinye iindlela zonyango zichaphazela amathambo.

Inyangwa njani i-Birdshot Chorioretinopathy?

Unyango lwesi sifo luxhomekeke kubukhulu bemeko yakho kunye nendlela etshintsha ngayo ngokuhamba kwexesha. Injongo ephambili yonyango kukunciphisa ukudumba emehlweni akho kunye nokuthintela okanye ukubuyisela umbono olahlekileyo .

Oogqirha badla ngokuqala banike iidosi eziphezulu ze-corticosteroids (uhlobo lwamayeza e-steroid) ukulawula ukudumba kwamehlo. Emva koko, idosi incitshiswa kancinci kancinci ukunciphisa umngcipheko weziphumo ebezingalindelekanga. Ungafumana ii-steroids ngeendlela ezilandelayo:

  • Amaconsi amehlo
  • Amayeza omlomo
  • Isixhobo esincinci esifakelwa ngaphakathi kweliso ngotyando (intravitreal implant)
  • Inaliti
  • Inikwa emthanjeni (nge-IV - ngemithambo yegazi)

Abantu abaninzi kufuneka bathathe amayeza okunciphisa amajoni omzimba ixesha elide . La mayeza ayayithintela inkqubo yakho yomzimba ukuba ingahlaseli amehlo akho. Elinye okanye ngaphezulu kwezi zilandelayo lingasetyenziswa:

  • `(Iiarhente ze-alkylating)`
  • `(Amayeza e-Antimetabolite)`
  • `(Iiarhente zebhayoloji)` (amayeza ebhayoloji)
  • `(Ukudluliselwa kweeseli ze-T/izithinteli ze-calcineurin)`

Ngaba unyango lweBirdshot Chorioretinopathy (Birdshot Chorioretinopathy) lunokubangela iziphumo ebezingalindelekanga?

Ewe, ukusetyenziswa ixesha elide kwee-steroids kunye ne-immunosuppressants kunokubangela iziphumo ebezingalindelekanga ezibi kakhulu . Umzekelo, iingxaki zesisu (izilonda, izilonda) okanye iingxaki zamathambo (i-osteoporosis) zinokubakho. La mayeza anokunyusa umngcipheko wokuba ne-cataracts okanye i-glaucoma.

Ugqirha wakho uza kukujonga ukuba azikho na iziphumo ebezingalindelekanga aze akunike amanye amayeza ukuba kuyimfuneko. Ukuba uthatha ii-steroids ezithathwa ngomlomo, ugqirha wakho uza kukujonga ukuba amathambo akho alahlekile na (i-osteoporosis) kunye nomngcipheko wakho wokuqhekeka.

Ugqirha wakhoKungacetyiswa ukuba kuhlolwe uxinano lwamathambo. Amayeza (ii-bisphosphonates) anganikwa ukuthintela ukulahleka kwamathambo.

Luhlobo luni lokubekwa esweni ixesha elide endiludingayo (BSCR)?

Qaphela naluphi na utshintsho okanye iingxaki kwimeko yakho. Ugqirha wakho uza kwenza uvavanyo lwegazi nomchamo ukujonga ukuba izintso zakho, isibindi kunye nomongo wethambo zisebenza kakuhle kangakanani na. Kuya kufuneka uhlolwe amehlo rhoqo, uvavanyo lwentsimi yokubona, kunye ne-optical coherence tomography (OCT) scans.

Ndingawunciphisa na umngcipheko wam wokuba ne-Birdshot Chorioretinopathy?

Okwangoku akukho ndlela eyaziwayo yokuthintela esi sifo. Kwiimeko ezininzi, kukholelwa ukuba sibangelwa yi-antibody gene ethile (i-antigen) efunyanwa kumalungu osapho.

Ukuhlolwa kwamehlo rhoqo kunokunceda ekufumaneni iimpawu zokuqala zesifo, ukuze ufumane unyango olukhawulezileyo ukuba kuyimfuneko. Xelela ugqirha wakho ukuba kukho umntu kusapho lwakho oneengxaki zamehlo.

Iyintoni imbono ye-Birdshot Chorioretinopathy?

Imbonakalo yesi sifo iyahluka kumntu nomntu . Ixhomekeke kubukhali bemeko kunye nempumelelo yonyango. Kwiimeko ezibuthathaka, unyango lunokunceda ekugcineni okanye ukuphucula umbono.

Ndifanele ndifumane nini ingcebiso kagqirha malunga (ne-Birdshot Chorioretinopathy)?

Kubalulekile ukufuna ukuxilongwa ngokukhawuleza kunye nonyango kwingcali yamehlo ye-Birdshot Chorioretinopathy. Nokuba umbono wakho ubonakala ulungile, uvavanyo lwamehlo lunokufumanisa ukudumba okuphantsi.

Xelela ugqirha wakho ngazo naziphi na iziphumo ebezingalindelekanga, utshintsho kwiimpawu, okanye umbono ovela kumayeza akho. Unganikwa elinye iyeza ukuba kuyimfuneko. Ugqirha wakho uza kuthetha nawe malunga neendlela ezikulungeleyo.

Umyalezo Wokugqibela Wokuya Ekhaya

(I-Birdshot Chorioretinopathy) sisifo esingaqhelekanga kodwa esinokunyangwa . Ngoko ke ungoyiki. Eyona nto ibalulekileyo kukujonga amehlo akho rhoqo kwaye ulandele iingcebiso zikagqirha wakho . Ekuhambeni kwexesha, ugqirha wakho uya kukuxelela indlela yokukhusela umbono wakho kunye nokuthintela iingxaki. Emva koko uya kukwazi ukubona ihlabathi ngokucacileyo ixesha elide. Nyamekela amehlo akho, kuba axabiseke kakhulu!


I- Birdshot Chorioretinopathy, Izifo Zamehlo, Ukuphazamiseka Kokubona, I-Uveitis, I-Retina, Izifo Zokuzikhusela Ngokwasemzimbeni, Unyango Lwamehlo

Frequently Asked Questions (FAQ)

Ngaba kukho amanye amagama alo mba?

Ewe, kukho amanye amagama aliqela asetyenziswa kwesi sifo (i-Birdshot Chorioretinopathy):

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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