Ngaba wakha waphawula ukuba inxalenye emhlophe yamehlo abanye abantu, oko kukuthi, i-sclera emhlophe, iye yaba luhlaza okwesibhakabhaka kancinci? Mhlawumbi ukhe walubona olu tshintsho emehlweni akho. Oku kuqhelekile kakhulu kwiintsana ezincinci. Ngoko ke, kwezonyango, xa inxalenye emhlophe yeliso ifumana umbala oluhlaza okwesibhakabhaka, ongwevu okanye omfusa, siyibiza ngokuba yi-'Blue Sclera'. Uninzi lwexesha, oku akuyonto ibalulekileyo. Nangona kunjalo, ngamanye amaxesha oku kunokuba luphawu lwenye imeko yezonyango emzimbeni wethu. Ngoko ke namhlanje, masithethe ngayo yonke into ngendlela elula.
Yintoni kanye kanye i-'Blue Sclera'?
Ngamafutshane, inxalenye emhlophe yeliso lethu ibizwa ngokuba yi-sclera. Enyanisweni sisigqubuthelo esiqinileyo esenziwe ngemicu eqinileyo yezicubu ezidityanisiweyo. Umsebenzi walo ophambili kukukhusela iliso nokugcina imo yalo.
Khawucinge nje, kuya kwenzeka ntoni ukuba olu donga lumhlophe olubizwa ngokuba yi-sclera luba mncinci kancinci ngesizathu esithile? Ngelo xesha, izicubu ezimnyama (i-uvea) kunye nombala wemithambo yegazi engaphantsi kwayo zibonakala ngolu donga lumhlophe olubhityileyo. Kufana nokuba xa ubeka into eluhlaza okwesibhakabhaka phantsi ngelaphu elimhlophe elibhityileyo, ungabona umbala oluhlaza okwesibhakabhaka phezulu. Yiyo loo nto siyibiza ngokuba yi -Blue Sclera . Ngokwesiqhelo, le meko ayibangeli iintlungu zamehlo okanye ezinye iimpawu.
Ingaba le yimeko enzima rhoqo?
Hayi, uninzi lwexesha akunjalo. Ubunzima boku buxhomekeke kwisizathu samehlo aluhlaza okwesibhakabhaka.
- Iintsana eziselula: I-sclera yeentsana ezisandul’ ukuzalwa kunye neentsana eziselula ngokwemvelo incinci kancinci. Ngoko ke kuqhelekile ukuba amehlo amhlophe abonakale eluhlaza okwesibhakabhaka. Njengoko umntwana ekhula, le sclera iyanda, kwaye umbala oluhlaza okwesibhakabhaka uyanyamalala.
- Abantu abadala: Le meko inokwenzeka ngenxa yezizathu ezilula ezifana nokungabikho kwe-iron kwabanye abantu abadala.
Kodwa khumbula, ngamanye amaxesha oku kungaba luphawu lwesifo esinzulu. Ngoko ke, ukuba ubona naluphi na utshintsho emehlweni akho okanye kumntwana wakho, kungcono ukubona ugqirha ngaphandle kokulityeshela. Ugqirha wakho uya kwenza uvavanyo lwamehlo, uvavanyo lwegazi, okanye uvavanyo lwemfuza ukuze kuchongwe unobangela ochanekileyo.
Ziziphi izizathu eziphambili zamehlo aluhlaza okwesibhakabhaka?
Izizathu zeBlue Sclera zinokwahlulwahlulwa zibe ziindidi ezahlukeneyo. Masizijonge kwitheyibhile, ukuze kube lula ukuziqonda.
| Udidi lweMbango | Imizekelo kunye neenkcukacha |
|---|---|
| Iimeko zeMfuzo | Ezi ziimeko zokuzalwa ezinokudluliselwa kwizizukulwana ngezizukulwana.
|
| Ezinye Izifo Neemeko |
|
| Amayeza kunye nezinye izizathu zangaphandle |
|
Zithini iindlela zonyango zoku?
Kubaluleke kakhulu ukuqonda oku. I-Blue Sclera ayisosifo, kodwa luphawu. Ngenxa yoko, oogqirha abanyangi umbala oluhlaza okwesibhakabhaka wamehlo, kodwa sisifo esibangela amehlo aluhlaza.
- Ukuba ukrokrela ukuba une-iron enqongopheleyo , ugqirha wakho unokucebisa izongezo ze-iron okanye ukutya okune-iron eninzi. Xa amanqanaba akho e-iron ebuyela esiqhelweni, ubuluhlaza emehlweni akho bunokuphela kancinci kancinci.
- Unobangela we-Osteogenesis ImperfectaUkuba sisifo semfuza, njenge-Alzheimer's, unyango lujoliswe ekulawuleni esi sifo. Oku kungadinga uncedo lweqela loogqirha abaziingcali.
- Ukuba ibangelwa liyeza elithile, ugqirha uya kuqwalasela ukutshintsha okanye ukuyeka elo yeza.
Oko kuthetha ukuba unyango luxhomekeke ngokupheleleyo kwisizathu esiyintloko. Yiyo loo nto kubalulekile ukufuna iingcebiso zonyango kungekhona ukuzenza ngokwakho.
Ufanele ufune nini ingcebiso yezonyango ngokukhawuleza?
Ukuba ubona naluphi na utshintsho kumbala wamehlo akho amhlophe, kungcono ukubona ugqirha ngaphandle kokukhathazeka. Nangona kunjalo, ukuba amehlo aluhlaza okwesibhakabhaka ahamba neempawu ezilandelayo, kufuneka uye kwiSebe lezeMpilo eziNgxamisekileyo (ETU) lesibhedlele ngoko nangoko .
- Utshintsho olukhawulezileyo kumbono
- Umbono ofipheleyo
- Iinyembezi ezifana nolwelo ziyaphuma emehlweni.
- Uvakalelo ekukhanyeni (amehlo aluhlaza okwesibhakabhaka)
- Intlungu enkulu yamehlo
Ezi zinokuba ziimpawu zengxaki enkulu yamehlo, ngoko ke kubalulekile ukufuna unyango ngaphandle kokuchitha ixesha.
Umyalezo Wokuya Ekhaya
- I-Blue Sclera kuxa umhlophe weliso (i-sclera) ujika ube luhlaza okwesibhakabhaka, ngwevu, okanye ube mfusa.
- Oku kubangelwa kukucutheka kwe-sclera, okuvumela ukuba izicubu ezingaphantsi zibonakale.
- Nangona oku kudla ngokuba yimeko engenabungozi, ngamanye amaxesha kunokuba luphawu lwesifo esithile esifihlakeleyo, esifana nokungabikho kwesinyithi okanye iingxaki zemfuza.
- Olu nyango alujongani nombala oluhlaza okwesibhakabhaka wamehlo, kodwa lujongana nesifo esibangela oko.
- Ukuba ubona naluphi na utshintsho emehlweni akho, ingakumbi ukuba luhamba nezinye iimpawu ezifana neentlungu zamehlo okanye ukubona izinto ezingaqhelekanga, bonana nogqirha wakho ngoko nangoko.
👩🏽⚕️ Imibuzo eyongezelelweyo (Ii-FAQ)
💬 Iipilisi zeSelexipag / Uptravi ziyindlela ekhethekileyo yonyango olunikwe isifo esithile?
Eli asiloyeza eliqhelekileyo! Eli liyeza eliphumelele kakhulu nelibiza kakhulu emhlabeni (i-Prostacyclin receptor agonist) elinikwa amanqanaba okugqibela e-'Pulmonary Arterial Hypertension (PAH),' isifo esibulalayo apho kuphela imithambo yegazi esuka entliziyweni iye emiphungeni incipha, kwaye uxinzelelo lwegazi kuyo lunyuka ngendlela engaqhelekanga, nto leyo ebangela 'imiphunga nentliziyo zife'!
💬 Xa kungekho gazi liphumayo emiphungeni, ukuthatha ezi pilisi (Uptravi) kuyayivula njani imithambo yegazi?
Ikhemikhali ebizwa ngokuba yi-'Prostacyclin' ikhona ngokwemvelo emzimbeni ukuze yandise/ikhulise imithambo yegazi ethwala igazi ukuya emiphungeni (imithambo ye-Pulmonary), kodwa abaguli be-PAH abanayo. Xa le pilisi ingena emzimbeni, iya ngqo kwi-receptors (ii-IP receptors) kwimithambo yegazi yemiphunga ize icinezele iqhosha! Emva koko ingqondo ikhohliswa ukuba icinge ukuba 'iProstacyclin' ifikile, kwaye yonke imithambo yegazi exineneyo emiphungeni iphumla ngoko nangoko (iVasodilation), kwaye umthwalo entliziyweni uyanyamalala ngoko nangoko.
💬 Zithini iziphumo ebezingalindelekanga zokuthatha amayeza (iSelexipag) anikwa esi sifo sinzima?
Uninzi lweziphumo ebezingalindelekanga zoku zivela kwinto yokuba icinezela amaqhosha emithambo yegazi emzimbeni wonke (isiphumo seProstacyclin)! Ezona ziphumo bezingalindelekanga 'ziintloko ezibuhlungu' ezinganyamezelekiyo (ngenxa yokuba imithambo yegazi iba mikhulu), iintlungu eziqatha zemisipha kunye nemihlathi (intlungu yomhlathi / iMyalgia), kunye norhudo! Kwakhona, ukufunxa ngequbuliso (ukufunxa) kunokuba yingxaki enkulu.











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