Ngaba wakha wacinga ukuba izintso ezimbini ezingaphakathi emzimbeni wethu zifana nenkqubo yokucoca ephezulu? Yiloo nto kanye eyenzekayo. Umsebenzi ophambili wezintso kukucoca inkunkuma engafunekiyo egazini lethu size siyikhuphe emzimbeni njengomchamo. Kodwa khawucinge, kuthekani ukuba kukho into eyonakalisa esi sihluzo sixabisekileyo? Kulapho ke iingxaki ziqala khona. Namhlanje siza kuthetha ngemeko engaziwayo kangako, kodwa ebaluleke kakhulu eyonakalisa izihluzo ezikwizintso. Yiyo loo nto i-FSGS.
Kalula nje, yintoni i-FSGS?
Igama elipheleleyo le-FSGS yi-Focal Segmental Glomerulosclerosis. Nangona igama lisenokuvakala liyinkimbinkimbi, ibali lilula kakhulu. Masilihlalutye size siqonde.
Izintso zethu nganye zinezihluzo ezincinci ezimalunga nesigidi ezinceda ekuhluzeni igazi lethu. Ngokwezonyango, ezi zibizwa ngokuba yi-glomeruli . Zicinge njengesixhobo sokuhluza iti ekhitshini. Njengoko igazi lidlula kwezi zihluzo, zigcina izinto ezilungileyo ezifunekayo emzimbeni (izondlo, iiminerali) zibuyele egazini, kwaye zihluze inkunkuma engafunekiyo kunye namanzi agqithisileyo. Okwahlulwayo koko kuphuma njengomchamo.
Kwi-FSGS, ezi zihluzo zincinci (i-glomeruli) ziba namanxeba okanye ziqine. Oku kubizwa ngokuba yi-"sclerosis." Xa oku kuqhekeka, izihluzo azikwazi ukwenza umsebenzi wazo ngokufanelekileyo.
Ngoku makhe sijonge amanye amagama akwigama:
- I-Focal: Oku kuthetha ukuba lo monakalo awuchaphazeli zonke izihluzi ezikwizintso, zimbalwa kuphela ezichaphazelekayo.
- Inxalenye: Oku kuthetha ukuba nakwizihluzo ezonakeleyo, yinxalenye nje yesihluzo eyonakeleyo, hayi yonke isihluzo .
Ngamafutshane, i-FSGS yimeko apho ezinye zezihluzo ezikwizintso zonakala, nto leyo ebangela ukuba umsebenzi wazo uphazamiseke.
Ziziphi iintlobo eziphambili ze-FSGS?
Ii-FSGS zinokwahlulwa zibe ziintlobo ezintathu eziphambili. Masibone ukuba zeziphi.
| Uhlobo lwe-FSGS | Inkcazo |
|---|---|
| I-FSGS ePhambili | Akukho sizathu sicacileyo salolu hlobo. Le meko yenzeka ngaphandle kwesizathu esicacileyo. |
| I-FSGS yesibini | Olu hlobo lubangelwa yenye imeko yezonyango, usulelo, amayeza, okanye esinye isizathu sangaphandle. Umzekelo, inokubangelwa zizinto ezifana nesifo seswekile, ukutyeba kakhulu, usulelo olufana ne-HIV, amayeza athile, kunye nokusetyenziswa kweziyobisi. |
| I-FSGS yemfuza (yosapho) | Olu hlobo lubangelwa sisiphene semfuza, oko kuthetha ukuba lunokufunyanwa kubazali ukuya ebantwaneni. |
Zithini iimpawu zomntu one-FSGS?
Eyona ngxaki inkulu nge-FSGS kukuba ayinazo iimpawu ezicacileyo kwizigaba zokuqala . Idla ngokufunyanwa ngengozi ngexesha lovavanyo lwezonyango oluqhelekileyo okanye xa kuvavanywa enye imeko. Nangona kunjalo, kukho iimpawu ezimbalwa eziqhelekileyo.
- Ukudumba: Ukudumba, ingakumbi emilenzeni, emaqatheni, ezandleni nasebusweni. Olu luphawu lokuqala olubonwa ngabantu abaninzi.
- I-Proteinuria: Xa izihluzi zezintso zonakele, iiproteni ezifunekayo emzimbeni ziyahluzwa zize zikhutshwe emchameni. Oku kunokubangela ukuba umchamo wakho ubonakale ngathi unamagwebu (njengamanzi anesepha).
- Amanqanaba aphezulu e-cholesterol egazini.
- Ukuncipha kwe-albumin yeproteni egazini.
- Ukunyuka kobunzima ngequbuliso: Oku kungenxa yokugcinwa kwamanzi ngokungeyomfuneko emzimbeni.
- Uxinzelelo lwegazi oluphezulu (uxinzelelo lwegazi oluphezulu).
Xa ezi mpawu zininzi (ingakumbi ukudumba, iiproteni kumchamo, kunye neproteni ephantsi egazini) zisenzeka kunye, oogqirha bayibiza le meko ngokuthi yi-nephrotic syndrome .
Iimeko eziyingozi (iingxaki) ezinokubakho ngenxa yesi sifo
Ukuba i-FSGS ayilawulwa kakuhle, iingxaki ezinkulu zinokuvela ngokuhamba kwexesha. Eyona ngxaki inzima neyingozi kukungasebenzi kakuhle kwezintso . Oku kwenzeka xa izintso zingakwazi ukusebenza kakuhle. Le yimeko engxamisekileyo esongela ubomi.
Ukuba une-FSGS kwaye ufumana ezi mpawu zilandelayo, kuya kufuneka uye kwisebe likaxakeka lesibhedlele (ETU) ngoko nangoko :
- Uxinzelelo lwegazi oluphezulu olungalawulekiyo.
- Ukulahleka kwegazi (i-anemia).
- Isicaphucaphu, ukuhlanza, kunye nokuphelelwa ngumdla wokutya.
- Ukudumba okukhulu kwezandla, iinyawo, nobuso.
Ugqirha uyixilonga njani i-FSGS?
Emva kokumamela iimpawu zakho, ugqirha uza kukuthumela kwiimvavanyo ezininzi.
- Uvavanyo lwegazi: Jonga amanqanaba eeproteni, inkunkuma, kunye namafutha egazini.
- Uvavanyo lomchamo: Linganisa ubungakanani beproteni kunye negazi kumchamo.
- Uvavanyo lokusebenza kwezintso (iGlomerular Filtration Rate - GFR): Olu vavanyo lulinganisa indlela ezisebenza ngayo izintso zakho.
Kodwa nangona zonke ezi mvavanyo zinokubonisa ukuba kukho i-FSGS, kukho uvavanyo olunye ekufuneka lwenziwe ukuqinisekisa isifo nge-100% : i-biopsy yezintso .
Yintoni i-biopsy yezintso?
Oku kuquka ukuthatha iqhekeza elincinci kakhulu lesicwili esisezintsoni zakho usebenzisa inaliti encinci. Emva koko isicwili sihlolwa ngemakroskopu ukuze kubonwe ukuba akukho zikrwelo kwizihluzo zezintso. Oku kuthathwa njengomgangatho olungileyo wokuxilonga i-FSGS.
Ziziphi iindlela zonyango ze-FSGS?
Unyango lwe-FSGS luyahluka ngokwesigulana ngasinye. Luxhomekeke kwizinto ezifana nohlobo lwe-FSGS onayo, ubudala bakho, kunye nezinye iimeko zempilo onazo. Iinjongo eziphambili zonyango kukulawula iimpawu, ukugcina umgangatho wobomi obuhle, kunye nokunciphisa umonakalo kwizintso kunye nokuthintela ukungasebenzi kakuhle kwezintso.
Into ebalulekileyo kukuba umonakalo kwizintso obangelwa yi-FSGS awunakuguqulwa. Oku kuthetha ukuba ayisosifo esinganyangekiyo ngokupheleleyo. Nangona kunjalo, unyango lunokucothisa ukuqhubela phambili kwesi sifo.
Ugqirha angacebisa olu nyango lulandelayo:
Iintlobo zamachiza
- Amayeza alawula uxinzelelo lwegazi kwaye anciphise ukuphuma kweproteni kumchamo. Imizekelo: `(Izithinteli ze-enzyme eziguqula i-Angiotensin - ACE-Is)`, `(Izithinteli ze-Angiotensin receptor - ARBs)`.
- I-Diuretics ngamayeza anciphisa ukugcinwa kwamanzi emzimbeni.
- Amayeza okunciphisa umzimba ngamayeza alawula ukusebenza kwenkqubo yomzimba yokuzikhusela.
- Ii-steroids ezifana ne-`(Corticosteroids)`.
- Kwezinye iimeko, unyango olukhethekileyo olufana ne-`(Plasmapheresis)`.
Utshintsho kwindlela yokuphila
Njengamayeza, utshintsho olwenzayo kwindlela ophila ngayo nalo lubaluleke kakhulu.
- Ukutya: Kubaluleke kakhulu ukunciphisa ubungakanani betyuwa (i-sodium) kunye neproteni ekutyeni kwakho. Nxibelelana nogqirha wakho kunye nengcali yesondlo malunga noku.
- Ukuzilolonga: Zilolonge yonke imihla.
- Kuphephe ukutshaya: Ukuba utshaya, ukuyeka ngoko nangoko kubalulekile kwimpilo yezintso.
Ikamva liphethe ntoni kumntu ophila ne-FSGS?
I-FSGS sisifo esingapheliyo esingenanyango. Isifo siyahluka kumntu nomntu. Abanye abantu banokuphila nesi sifo belawulwa kakuhle ngonyango kwaye bangabi nangxaki iminyaka emininzi. Kwabanye, esi sifo sinokuba mandundu kancinci kancinci size sikhokelele ekungasebenzini kwezintso.
Ukuba oko kuyenzeka, ungadinga i-dialysis okanye ukufakelwa izintso ukuze uphile.
Kodwa nokuba imeko injani na, ngonyango olufanelekileyo, ukulandela imiyalelo kagqirha wakho, kunye nokugcina indlela yokuphila esempilweni, uninzi lwabantu abane-FSGS banokuphila ubomi obusebenzayo nobunempumelelo. Eyona nto ibalulekileyo kukuhlala unolwazi ngemeko yakho ngokufumana uhlolo lwezonyango rhoqo.
Umyalezo Wokuya Ekhaya
- I-FSGS sisifo esibangela ukuba izihluzo ezithambileyo ezintso ziqhekeke, nto leyo ethintela izintso ekucoceni igazi ngokufanelekileyo.
- Ukuba imilenze, iingalo, okanye ubuso bakho buyadumba ngaphandle kwesizathu esicacileyo, okanye ukuba ubona umchamo onamagwebu, musa ukuwutyeshela. Bona ugqirha wakho ngoko nangoko.
- Nangona esi sifo singenakunyangwa ngokupheleleyo, ngonyango olufanelekileyo kunye notshintsho kwindlela yokuphila, esi sifo sinokulawulwa kwaye umonakalo kwizintso ungancitshiswa.
- Kubalulekile ukusebenzisa amayeza achazwe ngugqirha ngokuchanekileyo nokulawula ukutya kwakho.
- I-FSGS ayisiyonto yokoyika, kodwa ngokuqinisekileyo yimeko ekufuneka uyixhalabele. Ukuba ujongwa kakuhle ngugqirha, ungaphila ubomi obuhle.











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