Yintoni iHemangioblastoma? Makhe sithethe ngayo!

Ngaba wakha waliva igama elithi `Hemangioblastoma`? Lisenokuvakala linzima kancinci, kodwa luhlobo lwethumba elincinci elinokukhula emzimbeni wethu, ingakumbi engqondweni, emgogodleni, okanye ngaphakathi kweliso. Ungakhathazeki, siza kuthetha ngalo ngokulula, ngendlela onokuyiqonda.

Ingaba ngumhlaza lo?

Abantu abaninzi bayoyika ngoko nangoko xa besiva igama elithi 'ithumba', becinga, "Owu, andazi ukuba lo ngumhlaza na." Ndiyavuya ukukuxelela, le 'Hemangioblastoma' ayilomhlaza. Ngokwezonyango, ezi ziithumba ezingenabungozi okanye "ezingenabungozi". Oko kuthetha ukuba azisasazeki kwezinye iindawo zomzimba njengomhlaza.

Nangona kunjalo, nangona ezi zingengomhlaza, zinokubangela iingxaki ezincinci. Esinye kukuba ngamanye amaxesha zinokuba khona ezingaphezulu kwesinye kwezi zifo emzimbeni. Esinye isizathu kukuba njengoko esi sifo sikhula kancinci kancinci, siqala ukucinezela izicubu ezibalulekileyo kunye nemithambo-luvo ejikelezileyo. Kulapho ke zonke iintlobo zeempawu ziqala ukubonakala khona. Kufana nokuba nento enkulu kwigumbi elincinci kwaye akukho ndawo yaneleyo yokuyigcina yonke.

Ngubani onokuthi aphuhlise oku ngakumbi?

Ngoku usenokuba uzibuza, "Ngubani onokuba nale meko?" Enyanisweni, imeko ebizwa ngokuba yi-'Hemangioblastoma' inokuvela nakubani na, nangaliphi na ixesha. Nangona kunjalo, ngokutsho koogqirha, le meko ixhaphake kakhulu kubantu abadala abaselula .

Ukongeza, kukho elinye ityala elikhethekileyo. Eso sisifo semfuza esibizwa ngokuba yi-'Von Hippel-Lindau (VHL) disease'. Esi sisifo esingaqhelekanga, esizuzwa njengelifa. Abantu abanesifo se-'(VHL)' banamathuba amaninzi okufumana iithumba ze-'Hemangioblastoma' kunabanye. Cinga nje, ngokwezibalo, malunga nama-60% abantu abanesifo se-'(VHL)' banokuvelisa ezi thumba ngaphakathi kweliso. Kwakhona, malunga nama-80% kuthiwa banokuba nazo ezi thumba ebuchotsheni okanye emgogodleni. Ngoko ke, kukho unxibelelwano olukhulu phakathi kwesifo se-'(VHL)' kunye ne-'Hemangioblastoma'.

I-hemangioblastoma ichaphazela njani umzimba?

Ngoku makhe sibone indlela eli thumba elichaphazela ngayo imizimba yethu. Isiphumo salo sixhomekeke kakhulu kwindawo elikuyo ithumba kunye nobukhulu balo.

Ngokukodwa, ukuba le thumba ikhula engqondweni okanye emgogodleni, inokuthintela ukuhamba kwe-'Cerebrospinal fluid (CSF)', ebalulekileyo kwingqondo yethu nakwi-spinal cord. Le '(CSF)', ngokufutshane, lulwelo olucacileyo, olufana namanzi olujikeleze ingqondo yethu kunye ne-spinal cord, olubanika umqamelo kunye nokondla. Ukuba ukuhamba kwe-'(CSF)' kuthintelwe yi-tumor, uxinzelelo ngaphakathi kwengqondo lunokwanda, okubangela iimpawu ezifana neentloko ezibuhlungu. Kwakhona, ngokuxhomekeke kwindawo ye-tumor, imithambo-luvo kuloo ndawo inokucinezelwa, okubangela ukuba imithambo-luvo isebenze.

Kuqheleke kangakanani oku?

Enyanisweni, i-'Hemangioblastoma' ayilohlobo luqhelekileyo lwethumba. Ukuba sithatha inani lilonke leethumba ezikhula engqondweni, i-'Hemangioblastoma' ibandakanya i-0.5% yazo, eliyipesenti ephantsi kakhulu, malunga nenye kwikhulu elinamabini. Ukuba sithatha iintlobo zezicubu ezikhula kumqolo, zimalunga ne-2%. Ukuba sijonga izibalo kwilizwe elifana neMelika, kuthiwa malunga nama-24 kwi-100,000 abantu abadala bane-tumor ethile engqondweni okanye kwinkqubo yemithambo-luvo. Ngoko ke i-'Hemangioblastoma' lipesenti elincinci kakhulu lazo. Ke ngoko, esi asisosifo esichaphazela wonke umntu.

Zithini iimpawu?

Iimpawu zale thumba ethi `Hemangioblastoma` zinokwahluka kancinci ngokuxhomekeke ekubeni ivela phi. Makhe sibone ukuba isebenza njani loo nto.

Ukuba une-hemangioblastoma yomgogodla:

Ukuba le thumba ikhula kwi-spinal cord yakho, i-nerve cord ngaphakathi komqolo wakho, unokufumana iimpawu ezifana nezi:

• Ukuqhinwa okanye ukungakwazi ukuzibamba lindle.
• Ubunzima bokuchama (ukugcinwa komchamo) okanye ukungakwazi ukulawula ukuchama (ukungakwazi ukuzibamba komchamo).
• Ukuziva ngathi kukho ukungaziva okanye ukurhawuzelela kwamalungu okanye amalungu omzimba.
• Ubuthathaka bemisipha , nto leyo eyenza kube nzima ukuhamba ngamanye amaxesha.

Ukuba uneHemangioblastoma engqondweni:

Ukuba ithumba elifana neli likhula ngaphakathi engqondweni, lithathwa njengethumba lobuchopho. Emva koko ungabona iimpawu ezifana nezi:

• Iingxaki zokulinganisela , njengomntu onxilileyo, zinokubakho.
• Intloko ebuhlungu rhoqo, ngamanye amaxesha iba mandundu kusasa.
• Isicaphucaphu okanye ukuhlanza , ingakumbi kusasa.

Ukuba une-hemangioblastoma kwi-retina:

Ukuba kuvela ithumba kwi-retina, umaleko wezicubu ezingasemva kweliso ezirekhoda imifanekiso esiyibonayo, ithathwa njengethumba lamehlo. Nazi ezinye izinto ezinokwenzeka:

• Ukuqhekeka kwe-retina, okunokubangela ukulahleka kombono.
• Ukulahlekelwa kancinci kancinci okanye ngokupheleleyo kokubona .
• Intlungu yamehlo kunye nokudumba .

Zithini izizathu?

Kwiimeko ezininzi, kunzima ukufumana unobangela ocacileyo nocacileyo wophuhliso lwe-'Hemangioblastoma'. Oko kukuthi, zinokwenzeka ngaphandle kwesizathu esithile (ezingaqhelekanga). Nangona kunjalo, njengoko bekutshiwo ngaphambili, kufunyenwe ukuba malunga nesigulane esinye kwabane sinesifo semfuza esibizwa ngokuba yi-'Von Hippel-Lindau (VHL)' esibangela esi sifo. Oko kukuthi, abantu abane-'(VHL)' basengozini enkulu yokuphuhlisa esi sifo.

Uyibona njani le nto? (Ukuxilongwa)

Ukuba unenye okanye ngaphezulu kwezi mpawu zikhankanyiweyo apha ngasentla, xa ubona ugqirha, uza kuqala akubuze ngeempawu zakho. Uza kubuza nangezinye iimeko zakho zempilo kunye nokuba kukho umntu kusapho lwakho okhe waba neemeko ezifanayo (imbali yosapho). Emva koko, kunokwenziwa uvavanyo oluninzi ukuqinisekisa ukuxilongwa kunye nokufumanisa indawo kunye nobukhulu bethumba.

• I-CT scan (i-Computed Tomography scan): Le nkqubo isebenzisa uthotho lwee-X-rays kunye nekhompyutha ekhethekileyo ukuthatha imifanekiso enqamlezileyo yezicubu ezahlukeneyo emzimbeni.
• I-MRI (Magnetic Resonance Imaging): Oku kusebenzisa amandla emagnethi aqinileyo kunye namaza erediyo ukuvelisa imifanekiso ecacileyo neneenkcukacha zezitho zomzimba kunye nezicubu ezithambileyo ngaphakathi emzimbeni. Olu luvavanyo olubaluleke kakhulu ekuxilongeni iimeko ezifana ne-hemangioblastoma.
• I-Angiography: Oku kuquka ukufaka idayi ekhethekileyo kwimithambo yegazi ukuze iithumba ezifana ne-hemangioblastoma kwimithambo yegazi zibonakale ngakumbi kwi-X-ray okanye kwi-MRI/CT scan. Ngenxa yokuba ezi thumba zikhula kwimithambo yegazi (iithumba zemithambo yegazi), olu vavanyo lunokunika umbono olungileyo wokunikezelwa kwegazi.

Luthini unyango?

Kulungile, ngoku makhe sibone ukuba loluphi unyango olufumanekayo lwe-'Hemangioblastoma.' Indlela yonyango imiselwa zizinto ezininzi, ezinje ngobukhulu bethumba, indawo elikuyo, kunye nempilo yakho iyonke.

• Utyando lokususa ithumba: Le yindlela ecetyiswa kakhulu ngoogqirha. Kule ndlela, ugqirha okanye umongikazi wenza utyando eluswini aze asebenzise izixhobo zotyando ukususa ithumba. Injongo ephambili apha kukususa ithumba elininzi kangangoko kunokwenzeka ngelixa kuncitshiswa umonakalo kwizicwili eziphilileyo ezingqongileyo, ingakumbi imithambo-luvo.
• Unyango ngemitha: Ngamanye amaxesha, ukuba utyando alukwazi ukususa ngokupheleleyo ithumba, okanye ukuba ithumba libuyile, kusetyenziswa unyango ngemitha. Oku kubandakanya ukusebenzisa imisebe yemitha ejolise ngqo, enamandla ukutshabalalisa iiseli zethumba okanye ukunciphisa ithumba. Kukho iindlela ezikhethekileyo zolu hlobo olubizwa ngokuba yi-stereotactic radiosurgery. Ixesha elingakanani kunye nokuba unyango ngemitha lunikwa lixhomekeke kwizinto ezifana nendawo yethumba kunye nembali yakho yezonyango yangaphambili.
• Ukuqwalaselwa: Ngamanye amaxesha, ukuba ithumba lincinci kakhulu, akukho zimpawu, okanye ukuba indawo elikuyo ithumba yenza kube yingozi kakhulu ukulisusa ngotyando, oogqirha banokucebisa ukuba ungenzi nto okwangoku, kodwa lijonge rhoqo nge-MRI scans kunye notyelelo olulandelayo. Oku kukujonga ukuba ithumba liyakhula okanye ukuba uneempawu ezintsha. Ukuba unezihlunu ezininzi kwaye zikhula kancinci kancinci, unokufuna ukuqwalasela le ndlela.
• Unyango lwamayeza:Uphando ngoku luyaqhubeka malunga namayeza anokuthintela ukukhula kwezi thumba okanye azinciphise. Ingakumbi kwabo banesifo se-`(VHL)`, iyeza elibizwa ngokuba yi-`(Belzutifan)` okwangoku libonisa iziphumo eziphumelelayo zezi thumba ezinxulumene ne-`(VHL)`, kuquka ne-`Hemangioblastoma`. Nangona kunjalo, ezi ziseziindlela ezintsha zonyango, azifanelekanga kuye wonke umntu, kwaye kufuneka zithathwe kuphela ngokwengcebiso kagqirha.

Ngaba inganyangeka ngokupheleleyo?

Lo ngumbuzo obalulekileyo kubantu abaninzi. Isigulana ngasinye esine-'Hemangioblastoma' sahlukile, ngoko ke kunzima ukunika impendulo enye kumntu wonke.

Khawucinge nje, ukuba umntu une-"Hemangioblastoma" enye kuphela, kwaye inokususwa ngokupheleleyo nangokukhuselekileyo ngotyando, amathuba okuba ikhule kwakhona kwindawo enye aphantsi kakhulu. Oko kuthetha ukuba kukho amathuba aphezulu okuchacha.

Kodwa abanye abantu banokuba neethumba ezingaphezu kwesinye (ingakumbi abo bane-VHL). Okanye, ithumba lisenokuba nzulu engqondweni okanye kwindawo ebuthathaka ekunzima ukuyisusa. Kwiimeko ezinjalo, ukuthetha ngokuchacha ngokupheleleyo kunzima ngakumbi. Ke ngoko, kubalulekile ukuthetha neqela lakho lezonyango malunga nento onokuyilindela ngokusekelwe kwimeko yakho.

Ngaba zikho ezinye izinto ezibangela umngcipheko?

Ewe, njengoko besitshilo amaxesha amaninzi ngaphambili, ukuba unesifo semfuza i-'Von Hippel-Lindau (VHL), umngcipheko wakho wokuba ne-'Hemangioblastoma' uphezulu kakhulu. Ngoko ke, ukuba ugqirha ufumanisa i-'Hemangioblastoma', ingakumbi ukuba uselula okanye uneethumba ezininzi, banokuvavanya nesifo se-'(VHL)'.

Ithini ingqikelelo yokuchacha?

Ingqikelelo yokuba i-hemangioblastoma inokuba yingozi idla ngokuba ntle, ingakumbi ukuba iqela lezonyango liyakwazi ukuyisusa ngokupheleleyo ithumba. Kwakhona, ukuba ithumba alizange libangele iimpawu zexesha elide, njengokonakala kwemithambo-luvo okungapheliyo, amathuba okuchacha aphezulu.

Nokuba sele isusiwe ithumba, kuya kufuneka ubone ugqirha wakho ukuze ahlolwe rhoqo . Olu vavanyo lunokubandakanya izinto ezifana ne-MRI scan. Ukwenza oku kuya kunceda ekuchongeni nasekunyangeni naziphi na iziganeko zokubuyela kwesi sifo kwakhona (ingakumbi kubantu abane-VHL) kwangethuba. Ngoko ke, ukulandela imiyalelo kagqirha wakho ngokuchanekileyo nokuya kwiikliniki ngexesha kubaluleke kakhulu kwimpilo-ntle yakho.

Yeyiphi imibuzo omele uyibuze ugqirha?

Ukuba une-hemangioblastoma, okanye ucinga ukuba unokuba nayo, kungcono ukubuza ugqirha wakho imibuzo efana nale:

• "Yintoni enokubangela ukuba iimpawu zam zibe yingozi?"
• "Lingakanani ithuba lokuba ndibe nenye imeko yezonyango engabonakaliyo (umzekelo, isifo se-VHL) eyabangela ukuba ndibe ne-'Hemangioblastoma'?"
• "Zithini iindlela zonyango lwe-'Hemangioblastoma' yam? Zithini iingenelo kunye neengozi zonyango ngalunye?"
• "Zeziphi iziphumo ebezingalindelekanga endinokuzilindela emva kolu nyango?"
• "Lithini ithuba lokuba i-`Hemangioblastoma` iphinde ivele emva kokuba ithumba lisusiwe?"
• "Ndifanele ndiye kangaphi ukuza kuhlolwa?"

Kuya kuba luncedo kakhulu kuwe ukuqonda kakuhle imeko yakho ngokubuza le mibuzo. Ungoyiki ukuthetha nogqirha wakho ngayo yonke into esengqondweni yakho, nokuba incinci kangakanani na. Kulapho ke kuphela apho uya kukwazi ukufumana unyango olungcono.

Khumbula njengesishwankathelo (Umyalezo Wokuya Ekhaya)

Kulungile, masishwankathele oko sithethe ngako.

I-Hemangioblastoma yithumba elingengomhlaza (elingenobungozi) elivela kwimithambo yegazi. Lifumaneka kakhulu engqondweni yakho, emgogodleni, okanye kwi-retina .

Njengoko le thumba ikhula, inokutyhala izicwili ezingqongileyo kwaye ibangele iimpawu zemithambo-luvo.

Amaxesha amaninzi, oogqirha baya kuyisusa le thumba ngotyando. Ukuba le thumba isusiwe ngokupheleleyo, amathuba okuba ibuye kwakhona aphantsi . Nangona kunjalo, abantu abaneengxaki zemfuza ezifana ne-'Von Hippel-Lindau (VHL)' basengozini enkulu yokuphuhlisa la mathumba, mhlawumbi namathumba amaninzi, kwaye banamathuba amaninzi okubuya.

Ngoko ke, ukuba uneempawu ezikhankanyiweyo kweli nqaku, ingakumbi ukuba ziyaqhubeka okanye ziyanda, kungcono ukubona ugqirha ngokukhawuleza ukuze ufumane ingcebiso. Khumbula, okukhona uxilongo lusenzeka kwangoko, kokukhona unyango luya kuphumelela. Ungakhathazeki, ngonyango olufanelekileyo nolwalathiso, ezi meko zinokulawulwa kwaye ziphile ngempumelelo.

i- hemangioblastoma, iithumba zobuchopho, iithumba zomthambo womqolo, iithumba zamehlo, i-Von Hippel-Lindau, iithumba ezingengobungozi, iithumba zemithambo yegazi