Ngaba wakha wayibona indawo emnyama, efana nesangqa ejikeleze i-iris yeliso lomntu? Mhlawumbi ugqirha ukuxelele ngale nto. Abanye abantu basenokoyika ukuba oku kuya konakalisa umbono wabo. Kodwa oku akuyonto inobungozi kweliso. Nangona kunjalo, oku kungaba luphawu olubalulekileyo lwenye imeko embi eyenzekayo emzimbeni wethu. Namhlanje, masithethe ngale nto ngokulula.
Zithini iiKayser-Fleischer Rings (iirings zeKF)?
Ngamafutshane, iiringi zikaKayser-Fleischer ziiringi ezimnyama ezijikeleza inxalenye enemibala yamehlo ethu, i-iris. Ezi ringi zibangelwa bubhedu obuninzi emizimbeni yethu obuqokelelana emehlweni . Zinokubonakala ziluhlaza, zigolide, okanye zimdaka.
Eyona nto ingcono kukuba ezi rings aziyi kulimaza amehlo akho .
Le ring iqala njenge-arc kwinxalenye ephezulu yeliso. Emva koko isasazeka kancinci kancinci ize ibe yi-ring epheleleyo. Ezi rings zifumaneka kwindawo apho inxalenye emhlophe yeliso (i-sclera) idibana khona kunye nenxalenye ecacileyo engentla kwenxalenye enemibala yeliso (i-cornea).
Eyona nto ibalulekileyo kukuba kubantu baseSri Lanka abanamehlo amdaka ngebala, la makhonkco kaKayser-Fleischer awabonakali kakuhle. Kubantu abanamehlo akhanyayo, kulula ukuwabona la.
Zihluke njani ezi zinto kwezinye izigaqa zamehlo?
Kukho nezinye iimeko apho olu hlobo lwezangqa zamehlo luvela khona. Ngoko ke, kubaluleke kakhulu ukwahlula nokuqaphela ezi. Makhe sibone ukuba zeziphi umahluko ophambili.
| Uphawu | Iindandatho zeKayser-Fleischer | UArcus oSenile | Iiringi zeFleischer |
|---|---|---|---|
| Umbala | Luhlaza, lugolide, lumdaka (imibala emnyama) | Umbala omhlophe-ngwevu (umbala okhanyayo) | Umbala ophuzi-mdaka |
| Isizathu | Ukufakwa kwekopolo | Ukufakwa kwe-lipids | Ukufakwa kwentsimbi |
| Izifo ezinxulumene noko | Isifo sikaWilson, isifo sesibindi | I-cholesterol ephezulu, ukuguga | I-Keratoconus - ukuvezwa kweliso okumile okwekhowuni |
| Ukuchongwa | Ingcali yamehlo kufuneka yenze uhlolo lwesibane esikroliweyo. | Ibonakala emehlweni. | Kufuneka ihlolwe ngemakroskopu ekhethekileyo (uvavanyo lwesibane esiqhekekileyo). |
Ukujonga ezi rings ze-KF, ugqirha wamehlo usebenzisa imakroskopu ekhethekileyo ebizwa ngokuba yi- slit-lamp examination . Ngamanye amaxesha, kufuneka uvavanyo olunzulu olubizwa ngokuba yi-gonioscopy . Oku kuquka ukufiphaza iliso nokubeka ilensi ekhethekileyo phezu kweliso.
Yintoni eyona nto ibangela iiKayser-Fleischer Rings?
Eyona nto iphambili neyona ixhaphakileyo yoku sisifo sikaWilson .
Isifo sikaWilson sisifo semfuza esibangela ukuba umzimba uqokelele i-copper engaphezulu kuneemfuno zawo. Ngokwesiqhelo, isibindi sethu sisusa i-copper engaphezulu. Kodwa kumntu onesifo sikaWilson, loo nkqubo ayisebenzi kakuhle. Emva koko, le copper iqala ukuqokelelana esibindini, ebuchosheni, emehlweni nakwamanye amalungu omzimba.
- Isifo sesibindi: Ukuqokelelana kwekopolo kunokonakalisa isibindi kwaye kubangele isifo sesibindi.
- Iingxaki zemithambo-luvo nezengqondo: Xa ubhedu luqala ukuqokelelana engqondweni, kuvela iimpawu ezahlukeneyo zemithambo-luvo kunye neengxaki zengqondo. Umzekelo:
- Iingxaki zokunyakaza ezifana nokungcangcazela kwamalungu kunye nobunzima bokuhamba
- Ubunzima bokuthetha
- Ixhala kunye nokudakumba
- Utshintsho kwindlela yokuziphatha kunye nobuntu
Khawucinge nje, kubantu abaneempawu ze-neurological ngenxa yesifo sikaWilsonEzi rings ze-KF zinokubonwa kubantu abamalunga nama-95 kwabayi-100. Oku kubonakala kubantu abamalunga nama-50% abaneempawu zesibindi kuphela.
Ezinye izizathu
Ukongeza kwisifo sikaWilson, kukho nezinye izizathu ezininzi ze-KF rings. Ezi zizifo ezinxulumene nesibindi.
- I-Primary biliary cholangitis (PBC): Esi sisifo esingapheliyo esonakalisa imibhobho yenyongo esibindini.
- I-cholestasis yosana olusandul’ ukuzalwa: Ukugeleza kwenyongo esibindini seentsana ezisandul’ ukuzalwa.
Iphathwa njani le nto?
Eyona nto ibalulekileyo ekufuneka siyiqonde apha kukuba oogqirha abayinyangi i-ringworm ngokwayo, kodwa banyanga imeko yezonyango ebangele i-ringworm.
Unyango lwesifo sikaWilson
Kukho iinjongo ezimbini eziphambili zonyango.
1. Ukususa i-copper engaphezulu emzimbeni: Oku kubizwa ngokuba yi -copper chelation therapy . Oku kuthetha ukuba kunikwa amayeza akhethekileyo (ii-chelating agents) anamathela kwi-copper emzimbeni aze ayisuse ngomchamo. Imizekelo yezi ngamayeza afana ne-penicillamine kunye ne-trientine.
2. Ukunciphisa ukufunxwa kobhedu ekutyeni: Oku kwenziwa ngokunika izongezo ze-zinc . I-Zinc ithintela ukufunxwa kobhedu emathunjini emzimbeni.
Unyango lwezinye izifo zesibindi
Izifo ezifana ne-primary biliary cholangitis (PBC) azinakuphiliswa ngokupheleleyo. Nangona kunjalo, amayeza anikwa ukulawula iimpawu nokuthintela ukuqhubeka kwesi sifo. Kwi-cholestasis kwiintsana ezisandula ukuzalwa, kunikwa ubisi olukhethekileyo lwefomyula, amayeza okulwa nokurhawuzelelwa, kwaye kwiimeko ezinzima, utyando lokufakelwa isibindi lunokufuneka.
Asinakuthintela ukwakheka kwezi Kayser-Fleischer Rings?
Akukho ndlela yokuthintela ngokuthe ngqo ukwakheka kwezi rings, kuba iimeko ezifana nesifo sikaWilson ezibangela zona zizalwa zizezofuzo kwaye azinakuthintelwa.
Kodwa, eyona nto ingcono onokuyenza kukuyichonga kwangethuba .
Ukuba umntu okwintsapho yakho esondeleyo, njengomama, utata, okanye umntakwenu, unesifo sikaWilson, kubaluleke kakhulu ukuba uthethe nogqirha wakho ngaso uze uvavanywe . Ukufunyanwa kwangoko kunokukunceda uqale unyango ngaphambi kokuba kuvele iimpawu kwaye kuthintele iingxaki ezinkulu.
Ingaba ezi rings zihlala zihleli?
Hayi, le yindaba emnandi kakhulu. Iindandatho zikaKayser-Fleischer azihlali zihleli . Xa isifo esisisiseko, umzekelo isifo sikaWilson, sinyangwa ngokufanelekileyo, ubhedu olugqithisileyo emzimbeni luya kususwa. Emva koko ezi ndandatho emehlweni ziya kunyamalala kancinci kancinci zize zinyamalale ngokupheleleyo .
Ngoko ke akukho mfuneko yokoyika ukukubona oku. Eyona nto ibalulekileyo kukubona oku njengophawu kwaye uqale ukunyanga imeko esisiseko ngokukhawuleza. Ukuba ugqirha wamehlo uyakukhankanya oku ngexesha lovavanyo lwakho lwamehlo, uza kukuthumela kwingcali efanelekileyo ukuze ufumane unyango olongezelelweyo.
Umyalezo Wokuya Ekhaya
- Iindandatho zikaKayser-Fleischer azisiso isifo samehlo, kodwa luphawu lwangaphandle lwesifo esingaphantsi (ingakumbi isifo sikaWilson) esibangelwa yikopolo eninzi emzimbeni.
- Ezi rings aziyi kulimaza amehlo akho.
- Ezi zidla ngokufunyanwa okokuqala xa ugqirha wamehlo ehlola amehlo nge-microscope ekhethekileyo.
- Ezi rings zinokususwa phantse ngokupheleleyo ngonyango olufanelekileyo lwesifo esisisiseko.
- Ukuba kukho umntu kusapho lwakho onesifo sikaWilson, nokuba akukho zimpawu, kubaluleke kakhulu ukubona ugqirha uze uthethe ngaso.











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