Ngaba umntwana wakho unesifo esingaqhelekanga esinje? Masifunde ngeRasmussen's Encephalitis!

Ngaba wakha weva ngesifo esingaqhelekanga esichaphazela icala elinye lobuchopho kwaye siba sibi ngakumbi ngokuhamba kwexesha? Mhlawumbi umntwana wakho omncinci unesifo sokuxhuzula rhoqo, ubuthathaka kwelinye icala lomzimba, kunye nobunzima bokuthetha? Kuyaqondakala ukuba woyike xa usiva ngento enjalo. Namhlanje siza kuthetha ngemeko engaqhelekanga kodwa ebalulekileyo. Ibizwa ngokuba yiRasmussen's Encephalitis.

Yintoni i-Rasmussen's Encephalitis?

Ngamafutshane, iRasmussen's Encephalitis kukudumba okuqhubekayo, okuhlala ixesha elide kwenye yee-hemispheres ezimbini zobuchopho bethu, oko kukuthi, kwelinye icala lobuchopho . Ngokuchanekileyo, iiseli zobuchopho ziyadumba kwaye zibe bomvu. Oku kukwabizwa ngokuba yiRasmussen syndrome.

Xa elinye icala lobuchopho livuvukele ngale ndlela, liqala ukubangela ukuxhuzula rhoqo. Ngokwezonyango, sikwabiza oku ngokuba yi-epilepsy. Oku akukokuxhuzula nje kuphela, kuqala ukonakalisa ingqondo kancinci kancinci, kwaye loo monakalo kunzima ukuwulungisa. Ekuhambeni kwexesha, ukusebenza kwelinye icala lomzimba kuyehla xa kuthelekiswa necala lobuchopho elonakeleyo. Khawuthelekelele, oku kuye kwachaphazela icala lasekunene lobuchopho, emva koko icala lasekhohlo lomzimba linokulahlekelwa ngamandla alo, libe nobunzima bokuthetha, kwaye lilahlekelwe yinkumbulo.

Esi sifo safunyanwa okokuqala ngugqirha ogama linguTheodore Rasmussen ngo-1958. Ngoko ke, sabizwa ngokuba yiRasmussen encephalitis njengesikhumbuzo sakhe.

Ingaba le meko inqabile kangakanani?

Esi sisifo esingaqhelekanga kakhulu . Ngokutsho kwabaphandi, ngabantu ababini kuphela kumawaka alishumi abantu abanokuba nesi sifo. Oko kuthetha ukuba sinqabile kakhulu.

Esi sifo sichaphazela kakhulu abantwana abancinci abaphakathi kweminyaka emi-2 neli-10 ubudala. Nangona kunjalo, ngamanye amaxesha ulutsha kunye nabantu abadala banokuba nale meko.

Zithini iimpawu zeRasmussen's Encephalitis?

Uphawu lokuqala lwesi sifo ludla ngokuba kukufanelana. Olu kufaneleka lunokuza ngeendlela ezahlukeneyo.

Iimpawu zokuqala

• Ukuxhuzula okukhulu, okuqhelekileyo kwe-tonic-clonic: Kule meko, izihlunu kumacala omabini omzimba ziyafinyela ngamandla, kwaye kusenokubakho ukulahleka kwengqondo.
• Ukuxhuzula okuqaphelekayo : Kwimeko enjalo, uyazi ukuba kwenzeka ntoni. Usenokuziva urhawuzelelwa sisandla esinye okanye unyawo, okanye ukungabi nanto kwindawo enye.
• Ukuxhuzula kolwazi oluphazamisekileyo kwifocal: Oku kukuxhuzula okuqala kwelinye icala lobuchopho, okubangela ukulahleka kancinci kwengqondo, okanye ukulahleka ngokupheleleyo kwengqondo.

Into ebalulekileyo kukuba, ukuba wena okanye umntwana wakho ninesifo sokuwa esifana nesi,Ufanele ubone ugqirha ngokukhawuleza. Yinto ekufuneka uyenze loo nto.

Enye into kukuba ubuthathaka obuncinci engalweni okanye emlenzeni womntwana bunokuba luphawu lokuqala lwesi sifo.

Iimpawu ezibonakala ngokuhamba kwexesha

Ukuxhuzula kokuqala kuyanda kancinci kancinci. Malunga nesiqingatha sabantu abane-Rasmussen encephalitis baba nesifo esibizwa ngokuba yi-`(Epilepsia Partialis Continua - EPC)`. Oku kuthetha ukuba ukuxhuzula kuqhubeka imizuzwana embalwa okanye imizuzu embalwa. Oku kuxhuzula kunzima kakhulu ukukulawula ngamayeza aqhelekileyo (ayinyangeki).

Ezi mpawu zilandelayo ziqala ukubonakala kwiinyanga ezimbalwa, okanye unyaka okanye emibini, emva kokufakwa kokuqala kwesilonda:

• Ukuwohloka kancinci kancinci kwezakhono zengqondo : Oku kuthetha ukuba izinto ezifana nokucinga, ukuqonda, kunye nenkumbulo zinokuncipha.
• Ukulahlekelwa kancinci kancinci kokushukuma kwelinye icala lomzimba (hemiparesis): Umzekelo, ingalo yasekunene kunye nomlenze wasekunene zinokuba ndindisholo. Ekuhambeni kwexesha, oku kunokuqhubekela phambili ekubeni kukhubazeke ngokupheleleyo (hemiplegia).
• I-Aphasia : Oku kwenzeka xa isifo sichaphazela icala lobuchopho elinoxanduva lokuthetha (ngokuqhelekileyo icala lasekhohlo).
• Ukulahlekelwa ngokupheleleyo kombono kwicala elinye (i-hemianopsia): Kufana nokulahlekelwa umbono kwicala elinye kuphela leliso.

Kubantu abaninzi, iinyanga zokuqala ezisi-8 ukuya kwezili-12 emva kokuqala kwe-Rasmussen encephalitis zezona zimbi kakhulu . Emva koko, esi sifo sinokubonakala sicotha okanye siphela. Nangona kunjalo, umonakalo engqondweni uhlala uhleli kwaye awunakuguqulwa.

Yintoni isizathu soku?

Inyaniso kukuba, izazinzulu azikayazi kakuhle into ebangela iRasmussen encephalitis . Kodwa zineengcamango ezimbini eziphambili:

1. Isifo sokuzikhusela komzimba : Kulapho inkqubo yethu yomzimba, inkqubo esikhusela kwizifo, ihlasela ngempazamo iiseli zethu ezilungileyo. Ngoko ke, iRasmussen encephalitis icingelwa ukuba sisifo esifanayo sokuzikhusela komzimba esihlasela icala elinye lobuchopho.

2. Usulelo : Kusenokwenzeka ukuba intsholongwane engaziwayo ingena engqondweni ize ibangele le meko. Nangona kunjalo, abaphandi baye bahlola ubuchopho babantu abaye banesifo, kodwa abakayifumani intsholongwane ethile.

Sifunyaniswa njani esi sifo? (Ukuxilongwa)

Oogqirha baxilonga iRasmussen encephalitis ngokusekelwe kwiimpawu zomntwana wakho kunye neziphumo zovavanyo olukhethekileyo oluninzi.

• I-MRI scan (Magnetic Resonance Imaging - MRI): Oku kungabonisa ukuba izicwili zobuchopho kwelinye icala lobuchopho bomntwana ziye zaphela okanye zancipha. Ukuba elinye icala lobuchopho liyaphela kancinci kancinci kwiinyanga okanye iminyaka emininzi, luphawu olukhulu lwesifo.
• Uvavanyo lwe-EEGI-Electroencephalography (EEG): Oku kunokunceda ekuxilongeni imeko. Uvavanyo lwe-EEG lurekhoda umsebenzi wombane engqondweni. Oku kunokunceda ekuqinisekiseni ukuba kwenzeka njani ukuxhuzula kunye nokuba ingqondo isebenza ngendlela engaqhelekanga na.

Ngoko ke, oogqirha bayaqinisekisa iRasmussen encephalitis ngokudibanisa iimpawu kunye nokufumanisa iziphumo, ezifana nokuwohloka kwelinye icala lobuchopho .

Ziziphi iindlela zonyango lwe-Rasmussen's Encephalitis?

Ngelishwa, akukabikho nyango lwe-Rasmussen encephalitis, ngoko ke injongo ephambili yonyango kukulawula iimpawu kunye nokunciphisa ukudumba engqondweni.

Oku kulandelayo kungenziwa njengonyango:

Amayeza okuthintela ukuxhuzula

La mayeza asenokungayiyeki ngokupheleleyo i-seizures ebangelwa yi-Rasmussen encephalitis. Nangona kunjalo, anokunceda ekunciphiseni ukuxhaphaka kunye nobunzima be-seizures .

Unyango lwe-immunotherapy

Unyango lwe-immunotherapy, oluquka ukunika amayeza atshintsha ukusebenza kwenkqubo yokuzikhusela komzimba, lunokunceda ukulawula uhlaselo nokunciphisa umonakalo engqondweni ovela kwinkqubo yokuzikhusela komzimba kwasekuqaleni kwesi sifo.

Utyando lobuchopho

Eyona ndlela isebenzayo yokulawula ukufana kwi-encephalitis yaseRasmussen lutyando lobuchopho . Oku kubizwa ngokuba yi-hemispherectomy. Olu tyando lubandakanya ukwahlula i-hemisphere echaphazelekayo yengqondo yomntwana, oko kukuthi, ukwahlula elo cala lobuchopho kwelinye icala, okanye ukulisusa ngokupheleleyo.

Kwiimeko ezininzi, abantwana abenza olu tyando sele benokulahlekelwa okukhulu kokusebenza kwicala elichaphazelekayo lengqondo. Ke ngoko, umngcipheko wokulahlekelwa ngakumbi kokusebenza emva kotyando uphantsi. Oogqirha bacinga ngotyando kuphela xa iingenelo zingaphezulu kakhulu kuneengozi .

Liyintoni ikamva lesi sifo? (Ingxelo yokuxela kwangaphambili)

Uqikelelo lwesifo se-encephalitis saseRasmussen lunokwahluka kumntu nomntu . Kwabanye abantu, esi sifo sinokuyeka ukusasazeka emva kotyando kwaye ukuxhaphaka kokuxhuzula kunokuzinza.

Nangona kunjalo, abantu abaninzi banokushiywa benesiphene esithile, ukulahleka kwengqondo kunye nenkumbulo, kunye nobunzima bokuthetha. Akunqabile kakhulu, esi sifo sinokusasazeka siye kwezinye iindawo zobuchopho.

Ngaba i-Rasmussen's Encephalitis ingathintelwa?

Ngenxa yokuba iRasmussen encephalitis sisifo esingaqhelekanga kwaye isizathu esichanekileyo asikaziwa, akukho nto sinokuyenza ukuyithintela .

Ngenxa yokuba yimeko engaqhelekanga, kunzima ukuba izazinzulu ziyifunde. Kodwa iindaba ezimnandi zezokuba kukho unyango olufumanekayo olunokunceda ukulawula ukuxhuzula nezinye iimpawu. Kusenokubakho nezilingo zonyango umntwana wakho anokuthi athathe inxaxheba kuzo. Kuqhelekile ukuziva uxinezelekile xa ufumana uxilongo olunje. Kodwa khumbula, iqela lezonyango lomntwana wakho lilapha ukukunceda wena nomntwana wakho ngazo zonke iindlela .

Masikhumbule (Umyalezo Wokuya Ekhaya)

I-Rasmussen's Encephalitis sisifo sengqondo esingaqhelekanga kakhulu, kodwa esinokuba yingozi kakhulu.

>

* Kwimeko enjalo, ukudumba kwenzeka kwelinye icala lobuchopho, okubangela ukuxhuzula rhoqo, ukukhubazeka kwelinye icala lomzimba, kunye nobunzima bokuthetha.

* Abantwana abancinci ngabona bachaphazeleka kakhulu.

* Ukuba ubona iimpawu, bonana nogqirha ngokukhawuleza.

Unyango lunokulawula iimpawu.

* Awuwedwa ngexesha elinje, cela uncedo koogqirha nakwabo basondeleyo kuwe.

Ndiyathemba ukuba olu lwazi luza kukunceda. Ukuba unemibuzo, ungathandabuzi ukuthetha nogqirha.

I- Rasmussen encephalitis, isifo sobuchopho, isifo sokuwa, ukuqina komzimba, abantwana, ukudumba kobuchopho, izifo zemithambo-luvo