Ngaba ngamanye amaxesha uvuka kusasa uze uzive uvuvukile emehlweni akho? Okanye iinyawo zakho namaqatha akho ziyavuvuka, nto leyo eyenza kube nzima ukunxiba izihlangu zakho? Ngaba wakha waphawula ukuba umchamo wakho unamagwebu ngaphezu kwesiqhelo? Ezi ayizizo izinto ezingaqhelekanga nje. Kusenokuba kukho ingxaki ngezintso zakho emva kwezi mpawu. Namhlanje sithetha ngemeko ebalulekileyo kwezonyango ebangelwa kukudibana kweempawu ezifana nezi. Leyo yiNephrotic Syndrome.
Yintoni kanye kanye iNephrotic Syndrome?
Into yokuqala ekufuneka uyiqonde kukuba esi asisosifo sithile. Sibhekisa
kwingqokelela yeempawu ezinokwenzeka xa izintso zethu zingasebenzi kakuhle. Cinga ngezintso zethu njengesihluzo sobuchwephesha obuphezulu. Umsebenzi wazo ophambili kukucoca igazi lethu nokususa inkunkuma engafunekiyo kunye namanzi agqithisileyo emzimbeni njengomchamo. Lo msebenzi wokucoca wenziwa luthungelwano oluhle kakhulu lwemithambo yegazi kwizintso. Ezi sizibiza ngokuba yi-glomeruli. Kumntu ophilileyo, le nkqubo yokucoca ayivumeli izinto ezifana neeproteni ezibalulekileyo emzimbeni ukuba zidlule kuzo. Zigcinwa egazini. Kodwa ukuba ezi zihluzo zincinci ezibizwa ngokuba yi-glomeruli zonakele,
inani elikhulu leeproteni ezifunekayo ngumzimba ukuba zidlule kuzo kwaye ziqale ukuphuma nomchamo. Yiloo nto siyibiza ngokuba yi-nephrotic syndrome. Le meko inokuchaphazela abantu abadala kunye nabantwana, kodwa iindaba ezimnandi zezokuba kukho unyango lwayo.
Kutheni le meko isenzeka?
Izizathu zoku zinokwahlulwa zibe ziinxalenye ezimbini eziphambili.
Izizathu ezichaphazela izintso kuphela (Izizathu eziphambili)
Oku kuthetha ukuba i-nephrotic syndrome yenzeka ngenxa yesifo esenzeka kwizintso ngokwazo, ngaphandle kwempembelelo yesinye isifo.
- Isifo Sotshintsho Oluncinci: Esi sesona sizathu siphambili se-nephrotic syndrome ebantwaneni . Nangona izicubu zabo zezintso zibonakala ziqhelekile phantsi kwe-microscope, inkqubo yokuhluza ayisebenzi. Kukholeleka ukuba ibangelwa zizifo ezibangelwa ziintsholongwane , ii-allergies , okanye amayeza athile (ingakumbi ii-painkillers ezifana nee-NSAIDs ).
- I-Focal Segmental Glomerulosclerosis (FSGS): Le yimeko apho iiyunithi zokucoca (i-glomeruli) zezintso ziba namanxeba. Le yeyona nto ibangela i-nephrotic syndrome kubantu abadala . Iintsholongwane ezifana ne -HIV , amayeza athile, izinto zemfuza, kunye nokutyeba kakhulu zonke zinokubangela le meko .Izinto ezininzi, ezinje ngoxinzelelo lwegazi oluphezulu, zinokuchaphazela oku.
- I-Membranous Nephropathy: Oku kukuqina kwee-membrane ze-glomeruli. Oku kunokubangelwa zizifo ezifana nomhlaza, i-malaria, i-hepatitis B, kunye ne-lupus.
Izizathu zesibini zomonakalo wezintso ngenxa yezinye izifo
Oku kuthetha ukuba i-nephrotic syndrome yenzeka xa izintso zonakele ngenxa yesinye isifo emzimbeni.
- Isifo seswekile : Isifo seswekile sesona sizathu sixhaphakileyo sesifo se-nephrotic syndrome kubantu abadala. Isifo seswekile esingalawulwayo sinokukhokelela ekulimaleni kwezintso (i-diabetic nephropathy).
- I-Lupus: Esi sisifo esingapheliyo senkqubo yomzimba yokuzikhusela esinokubangela umonakalo omkhulu kwizintso.
- I-Amyloidosis: Uhlobo lweproteni ebizwa ngokuba yi-amyloid lunokuqokelelwa egazini, nto leyo ebangela umonakalo kwizintso.
Ziziphi iimpawu onokuba nazo?
Kukho iimpawu ezine eziphambili ze-nephrotic syndrome. Ukuze uziqonde ngokucacileyo ezi mpawu, jonga itheyibhile engezantsi.
| Uphawu | Kalula nje... |
|---|
| Iiproteni kwi-uria | Ukuphuma kweeprotheyini ezininzi kumchamo. Oku kunokubangela ukuba umchamo ubonakale unamagwebu ngaphezu kwesiqhelo . |
| I-hyperlipidemia | Amanqanaba aphezulu amafutha egazini kunye ne-cholesterol . Xa umzimba ulahlekelwa yiproteni, isibindi sivelisa amafutha amaninzi kunye ne-cholesterol, nto leyo ebangela oku . |
| Ukudumba komzimba (i-Edema) | Ukudumba, ingakumbi emilenzeni, emaqatheni nasezinyaweni . Ngamanye amaxesha izandla nobuso, ingakumbi ezijikeleze amehlo kusasa, nazo zinokudumba. |
| I-Hypoalbuminemia | Ukuncipha kohlobo lweproteni ebizwa ngokuba yi-albumin egazini. Le proteni yiyo egcina ulwelo kwimithambo yegazi. Xa lukhutshwa emchameni, ulwelo luyavuza kwiithishu kwaye umzimba uqala ukudumba. |
Le meko ibachaphazela njani abantwana abancinci?
I-Nephrotic syndrome yimeko engaqhelekanga ebantwaneni abancinci. Nangona kunjalo, ukuba umntwana ufumana le meko, iimpawu zinokwahluka kancinci.
- Ukudumba okujikeleze amehlo, ingakumbi xa uvuka kusasa.
- Ukudumba kobuso, izandla, imilenze, kunye nesisu.
- Umchamo onogwebu .
- Ukuziva udiniwe kwaye udiniwe ngaphezu kwesiqhelo.
Ii-corticosteroids lolona nyango lusetyenziswa kakhulu ebantwaneni. Ezi zihlala zilawula iimpawu kwaye zibangele ukuxolelwa.
Gqirha, uyixilonga njani le nto?
Ukuba unale mpawu, kubalulekile ukubona ugqirha ngokukhawuleza. Ugqirha uza kuqala akubuze ngeempawu zakho. Emva koko,
- Uvavanyo lomchamo: Oku kubalulekile ukuze kulinganiswe ukuba ingakanani iproteni ephuma kumchamo.
- Uvavanyo lweGazi: Jonga i-cholesterol egazini, amanqanaba e-albumin, kunye neminye imisebenzi yezintso.
- I-Biopsy Yezintso: Kwezinye iimeko, kusenokufuneka ukuba kuthathwe iqhekeza elincinci kakhulu lesicwili sezintso uze ulihlolisise nge-microscope. Oku kunceda ekufumaneni kanye kanye ukuba yintoni ebangela umonakalo kwizintso.
Ingakumbi ukuba iimpawu zeproteni engaphezulu kwe-3.5 grams ngosuku emchameni, amanqanaba aphantsi e-albumin egazini, kunye nokudumba komzimba ziyafana, yeyona nto iphambili ekuxilongweni kwe-nephrotic syndrome.
Zeziphi iingxaki ezinokwenzeka ukuba azinyangwa?
Ukuba le meko ayinyangwanga kakuhle, inokukhokelela kwezinye iingxaki zempilo ezinzulu.
- Umngcipheko ophezulu we-cholesterol nesifo sentliziyo: Amafutha aphezulu egazini kunye namanqanaba aphezulu e-cholesterol anyusa umngcipheko wesifo sentliziyo.
- Uxinzelelo lwegazi oluphezulu: Xa izintso zonakele, amandla azo okususa i-sodium (ityuwa) kunye nolwelo emzimbeni ayancipha, nto leyo ebangela ukuba uxinzelelo lwegazi lunyuke.
- Amahlwili egazi:Ngenxa yokuba iiproteni ezithintela ukujiya kwegazi zikhutshwa emchameni, umngcipheko wokujiya kwegazi emzimbeni uyanda.
- Iintsholongwane: Njengoko iiproteni ezifana nee-immunoglobulins, ezibalulekileyo kwinkqubo yomzimba yokuzikhusela, zilahleka, kukho ithuba elikhulu lokufumana izifo ezifana ne-pneumonia.
- Ukungasebenzi Kwezintso: Ukuba azinyangwa ixesha elide, izintso zinokungasebenzi ngokupheleleyo, zifune i-dialysis okanye ukufakelwa izintso ukuze ziphile.
Zithini iindlela zonyango zoku?
Isicwangciso sonyango sixhomekeke kwisizathu esiyintloko se-nephrotic syndrome yakho.
Iintlobo zamachiza
Ugqirha wakho angakunika amayeza alandelayo:
- Amayeza oxinzelelo lwegazi: Amayeza afana ne-ACE inhibitors kunye nee-ARB anciphisa uxinzelelo kwizintso kwaye anciphise ukukhutshwa kweproteni kumchamo.
- I-Diuretics: Ikwabizwa ngokuba "ziipilisi zamanzi," ezi zinceda ekunciphiseni ukudumba emzimbeni.
- Amayeza okwehlisa i-cholesterol.
- Izinto zokunciphisa igazi (i-Anticoagulants): Zinciphisa umngcipheko wokuqhekeka kwegazi.
- Amayeza okuthintela amajoni omzimba: Amayeza afana ne-corticosteroids alawula ukusebenza kwenkqubo yokuzikhusela komzimba kwaye anciphise umonakalo kwizintso.
Yingakho kubalulekile ukulawula ukutya
Kunye namayeza, ukutya kubaluleke kakhulu ekulawuleni esi sifo.
- Nciphisa ityuwa (i-sodium): Ukutya ityuwa eninzi kunokubangela ukugcinwa kwamanzi, ukudumba, kunye noxinzelelo lwegazi oluphezulu. Kuphephe ukutya okunetyuwa eninzi, njengeesoseji, inyama ecoliweyo, imifuno esemathinini, iisuphu, iibhisikithi kunye neesosi.
- Nciphisa amafutha kunye ne-cholesterol: Landela ukutya okunamafutha agcweleyo kunye ne-cholesterol encinci.
- Nciphisa ulwelo: Ngamanye amaxesha ugqirha wakho uya kukuxelela ukuba unciphise umlinganiselo wamanzi owaselayo ngosuku.
Khumbula, le miqathango yokutya kufuneka ilandelwe ngokwemiyalelo enikwe ngugqirha wakho okanye yingcali yesondlo.
Umyalezo Wokuya Ekhaya
- I-Nephrotic syndrome yingqokelela yeempawu ezibangelwa kukonakala kwenkqubo yokuhluza ethambileyo kwizintso.
- Iimpawu eziphambili kukudumba komzimba (ingakumbi emilenzeni nakwamehlo), umchamo onegwebu (ngenxa yeproteni eninzi), kunye ne-cholesterol ephezulu egazini.
- Le meko inokubangelwa nazezinye izifo ezifana nesifo seswekile kunye noxinzelelo lwegazi oluphezulu.
- Ukongeza kumayeza onyango, kubaluleke kakhulu ukulandela ukutya okunetyuwa encinci kunye namafutha amaninzi.
- Ukuba unale mpawu, ungaze uzityeshele . Bona ugqirha wakho ngokukhawuleza ukuze ufumane iingcebiso ezifanelekileyo kunye nonyango.
Isifo seNephrotic, iNephrotic Syndrome, isifo sezintso, ukudumba, iiproteni kumchamo, umchamo onegwebu, isifo sezintso ngesiSinhala, i-cholesterol
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