Ngaba wakha wayibona ibala elibomvu-mdaka emzimbeni womntwana wakho okanye owakho? Mhlawumbi uyiphulule kancinci le ndawo ngomnwe wakho, kwaye ngequbuliso ibala lajika laba bomvu, laqala ukurhawuzelela, kwavela ithumba elincinci phezulu. Ukuba le nto uyayazi, kubaluleke kakhulu ukuba uqaphele imeko esithetha ngayo namhlanje.
Ngamafutshane, yintoni i-Urticaria Pigmentosa?
I-Urticaria Pigmentosa luhlobo lweehives ezenzeka eluswini. Ixhaphake kakhulu kubantwana abancinci nakubantu abadala abancinci. Enyanisweni luhlobo lwemeko ebizwa ngokuba yi-'mastocytosis'.
Ngoku usenokuba uzibuza ukuba yintoni i-'mastocytosis'. Kulula kakhulu. "iiseli ze-mast" luhlobo olukhethekileyo lweeseli kwinkqubo yethu yokuzikhusela yomzimba. Zifana noonogada bomzimba. Xa ngesizathu esithile ezi seli ze-mast ziqokelelana kakhulu kwindawo enye yesikhumba, siyibiza ngokuba yi-Urticaria Pigmentosa. Nangona kunjalo, ezi seli ze-mast zinokuqokelelana kungekuphela nje eluswini, kodwa ngamanye amaxesha nakwezinye izitho ezifana namathambo namathumbu. Emva koko ijika ibe yimeko ebizwa ngokuba yi-"systemic mastocytosis". Kodwa ungakhathazeki, uninzi lwexesha, i-Urticaria Pigmentosa ebantwaneni iphelela eluswini.
Kwesi sifo, xa kuvela ibala elimdaka eluswini, liba bomvu, lidumbe, lirhawuzelele, lize liphakame ngokungathi litshayiswe yimoto. Ngokwezonyango, olu phawu lubizwa ngokuba "luphawu lukaDarier."
Kutheni kusenzeka into enje?
Isizathu esiphambili sale nto yi- "mast cells" ebesithethe ngayo ngaphambili. Ezi luhlobo lweeseli ezimhlophe zegazi eziveliswa kumongo wethu wethambo. Ezi seli zifumaneka kuyo yonke imizimba yethu, ingakumbi apho sidibana khona nehlabathi langaphandle, njengesikhumba, imiphunga, kunye namathumbu. Xa into efana nentsholongwane ingena emzimbeni, ezi seli zemast zikhupha ikhemikhali ebizwa ngokuba yi-"histamine" ukunceda ukukhusela umzimba.
I-Urticaria Pigmentosa ibangelwa kukuguquka kwezakhi zofuzo okubangela ukuba ezi seli ze-mast ziqokeleleke kakhulu eluswini. Olu tshintsho lwezakhi zofuzo ludla ngokwenzeka xa umntwana esesesibelekweni. Nangona kunjalo, asinto ezuzwa ngabazali ukuya ebantwaneni . Isizathu esichanekileyo sale nguqu asikafunyanwa.
Ukuba abantu abadala bafumana le meko, inokuba nzima ngakumbi. Ibizwa ngokuba yi-'indolent systemic mastocytosis'. Kule meko, ii-mast cells ziqokelelana kwiindawo ezifana nomongo wethambo ukongeza kulusu. Kunqabile kakhulu, le meko inokukhula ibe yimeko yomhlaza ebizwa ngokuba yi-'mast cell leukemia'. Kodwa kwakhona, ezi zizinto ezinqabileyo kakhulu . I-99% ye-Urticaria Pigmentosa eyenzeka ebantwaneni ayinzima kangako.
Zithini iimpawu zesi sifo?
Uphawu oluphambili nolucacileyo luluphawu lukaDarier esithethe ngalo. Oko kukuthi, amabala amdaka aba bomvu aze arhawuzelele xa ekhuhliwe. Ukongeza, abanye abantu banokufumana ezi mpawu zilandelayo.
| Uphawu | Ingcaciso elula |
|---|---|
| Ukubetha kwentliziyo | Isantya sentliziyo siyanda ngokungathi uziva usoyika. |
| Urhudo (intlungu yesisu) | Isenokubangelwa kukusebenza kweeseli zemast kwinkqubo yokugaya ukutya. |
| Ukuhlanjwa ngamanzi | Ububomvu obukhawulezileyo bobuso nomzimba ongasentla. |
| Ubunzima bokuphefumla (Ukuphefumula kancinci) | Isandi esithi 'itshizi-tshizi' xa uphefumla, esifana neso sabantu abane-asthma. |
| Ukuquleka | Ukulahlekelwa zingqondo ngenxa yokwehla ngequbuliso koxinzelelo lwegazi. |
| Intloko ebuhlungu | Intloko ebuhlungu. |
Ngaphezulu kwama-75% ezigulane ze-Urticaria Pigmentosa ngabantwana abangaphantsi kweminyaka eli-10 ubudala. Kuninzi lwabantwana, le meko iphelela eluswini kwaye iyaphucuka xa bekhula.
Ugqirha uyixilonga njani le nto?
Kwiimeko ezininzi, ugqirha wakho unokusifumanisa esi sifo ngokulula ngokujonga amabala eluswini lwakho aze ajonge uphawu lukaDarier. Akukho mfuneko yolunye uvavanyo.
Nangona kunjalo, ukuba kukho amathandabuzo malunga nokuba le meko ayiphelelanga nje eluswini kodwa ichaphazele nezinye iindawo zomzimba, ugqirha unokucebisa ukuba kwenziwe ezi mvavanyo zilandelayo.
- Uvavanyo lwegazi (`Ubalo lwegazi`): Funda ngeentlobo ezahlukeneyo kunye nobungakanani beeseli egazini.
- Uvavanyo lwe-serum tryptase: Lujonga ukuba kukho i-enzyme egazini ekhutshwa ziiseli ze-mast.
- Uvavanyo lobuninzi bamathambo: Jonga ukuba amathambo akho aqine kangakanani.
- Uvavanyo lomongo wethambo: Lujonga ukuba umongo wethambo uvelisa iiseli eziphilileyo na.
Iindlela zonyango kunye nendlela yokulawula isifo
Iindaba ezimnandi zezokuba kubantwana abaninzi, i-Urticaria Pigmentosa iyaphela yodwa njengoko bekhula . Akukho nyango luthile lokuthintela ukwakheka kwamabala amatsha. Amabala akhoyo angathatha iminyaka ukuba aphele.
Logama nje imeko iphelela eluswini, akukho nyango lubalulekileyo olufunekayo. Ugqirha wakho unokucebisa oku kulandelayo ukunceda ukulawula iimpawu zakho:
- Ii-antihistamines ezithethwa ngomlomo: Lawula ukurhawuzelela nokudumba.
- Iikhrimu zeCorticosteroid: Faka kwiindawo ezirhawuzelelayo.
- I-Cromolyn sodium: Iyeza elinikwa ukunyanga iimpawu ezinje ngokuhlanza kunye norhudo.
- I-EpiPen: Isixhobo esinikwa abantu abane-allergy enzima kakhulu (i-anaphylactic reaction) ukuba basisebenzise xa kukho imeko engxamisekileyo. Asinguye wonke umntu osidingayo esi sixhobo.
Izinto ekufuneka ziphetshwe ngokukodwa
Eyona nto ibalulekileyo kwesi sifo kukuphepha izinto ezibangela ukuba iimpawu zibe mandundu, oko kukuthi, izinto ezibangela ukuba amabala arhawuzelele aze abe bomvu.
| Amayeza ekufuneka uwaphephe | Ezinye izinto ekufuneka uziphephe |
|---|---|
| I-aspirin | Ukuzilolonga (ingakumbi okunzima) |
| Utywala | Ukuhlikihla ulusu ngamandla ngeetawuli |
| Izithomalalisi zentlungu ezifana ne-morphine kunye ne-codeine (`Opiates`) | Ukuhlamba emanzini ashushu |
| I-Thiamine (iVithamin B1) | Iziselo ezishushu |
| I-Quinine (`i-Quinine` - iyeza lemalariya) | Ukuvezwa lilanga kakhulu |
| I-Dextromethorphan (iyeza lokukhwehlela) | Ukuvezwa kumkhuhlane omkhulu |
| Amanye amayeza okubulala iintlungu kunye needayi ze-X-ray | Ukutya okuneziqholo, okushushu |
Kubalulekile: Ukuba wena okanye umntwana wakho kufuneka nithathe amayeza esinye isifo, qiniseka ukuba wazisa ugqirha wakho nge-Urticaria Pigmentosa.
Ngaba iingxaki zinokwenzeka?
Amaxesha amaninzi, le meko inokuqhubela phambili iye kwi-'systemic mastocytosis'. Abantu abanjalo basengozini enkulu yokufumana i-allergy enzima ebizwa ngokuba yi-'anaphylactic shock', enokuba yingozi ebomini. Ukuba ufumana iimpawu ezifana nobunzima bokuphefumla kunye nokulahlekelwa zingqondo , kufuneka uye kwisebe likaxakeka lesibhedlele (ETU) ngoko nangoko .
Ezinye iingxaki ze-mastocytosis yenkqubo ziquka:
- I-Osteoporosis: Ukubuthathaka kwamathambo.
- I-Cytopenia: Ukuncipha kwemveliso yeeseli zegazi emzimbeni.
- Iingxaki zesibindi.
- Umhlaza (unqabile kakhulu).
Kwakhona, ezi ziingxaki ezingaqhelekanga kakhulu. Zinqabile kakhulu kubantwana abane-Urticaria Pigmentosa.
Umyalezo Wokuya Ekhaya
- I-Urticaria Pigmentosa yimeko yesikhumba echaphazela kakhulu abantwana. Ayisuleli okanye ayizuzwa kubazali.
- Uphawu oluphambili kukuba xa ibala elimdaka likhuhlwe, liba bomvu, lidumbe, kwaye lirhawuzelele (`uphawu lukaDarier`).
- Musa ukoyika ngokungeyomfuneko, kuba le meko iza kuba ngcono ngokwayo kubantwana abaninzi njengoko bekhula.
- Eyona ndlela ilungileyo yokulawula kukuphepha ukutya, amayeza, kunye nemisebenzi eyenza iimpawu zibe mandundu.
- Ukuba wena okanye umntwana wakho unezinye zezi mpawu, qiniseka ukuba ubona ugqirha ukuze ufumane ukuxilongwa ngokuchanekileyo kunye neengcebiso ezifunekayo.
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