Wake waphawula into efana neqhubu elincane emzimbeni wakho, noma enganeni yakho? Kuvamile ukuzizwa wesaba kancane uma ubona into efana naleyo, akunjalo? "Kuyini lokhu? Kungani lokhu kwenzeka?" Ucabanga into ngokulandelana. Esikhathini esiningi, lezi kungaba izinto ezincane nje. Kodwa-ke, ngezinye izikhathi kudingeka sikhathazeke kancane futhi sibheke izimo ezidinga ukuphenywa. Namuhla, sizokhuluma ngeqhubu elingavamile kancane, okungukuthi, akuwona wonke umuntu olikhulisayo, kodwa kufanelekile ukulazi. Lokhu kubizwa ngokuthi i-Angiomatoid Fibrous Histiocytoma , noma i-AFH ngamafuphi. Nakuba igama lingase libonakale lide kancane, masiliqonde kalula.
Iyini ngempela i-Angiomatoid Fibrous Histiocytoma?
Kalula nje, lesi isimila esingavamile esakheka ezicutshini ezithambile zomzimba wakho, njengesikhumba nemisipha. Lokhu kuvame ukwakheka ezingalweni zakho, emilenzeni, futhi ngezinye izikhathi ezintendeni nasezinyaweni zakho.
Manje, ake sichaze incazelo yaleli gama elide kancane. Khona-ke kuzocaca.
Asho ukuthini la magama?
- I-Histiocytoma: Lesi yisigaxa esakheka lapho ama-histiocyte, uhlobo lweseli lokuzivikela elivamile emzimbeni wakho, ehlangana ndawonye. Lawa maseli avame ukutholakala ezingxenyeni ezahlukene zomzimba wethu futhi asisize ekusivikeleni ezifweni.
- I-Angiomatoid: Leli gama libhekisela ekubukekeni kweqhubu. Okusho ukuthi, uma ubheka leli qhubu, libukeka njengemithambo yegazi emincane. Kufana nemithambo yegazi eminingi ehlangene.
- I-Fibrous: Lokhu kubhekisela esimweni sefindo. Okusho ukuthi, lingaba nomuzwa we-fib, ropey, ne-sinewy kancane.
Ngakho-ke, uma uhlanganisa la magama amathathu, i-Angiomatoid Fibrous Histiocytoma isho inqwaba yamaseli abizwa ngokuthi ama-histiocytes anokubukeka okune-fibrous futhi abukeka njengemithambo yegazi. Uyaqonda?
Ubani othinteka kakhulu yilesi simo? Sivelaphi?
Lesi simo, esibizwa ngokuthi i-AFH, sivame kakhulu ezinganeni , intsha kanye nabantu abadala abasebasha . Eqinisweni, abantu abangu-88% abatholakale benalesi sifo bangaphansi kweminyaka engu-30. Isilinganiso seminyaka yokuxilongwa sicishe sibe yiminyaka eyi-14.
Lawa maqhuqhuva avame ukuvela esikhumbeni (i-dermis ), ungqimba olungaphansi kwesikhumba, ezingalweni nasemilenzeni yakho. Kodwa-ke, akuvamile kakhulu, ezimweni ezingavamile kakhulu, la maqhuqhuva e-AFH angavela nasezicutshini ezithambile emzimbeni wakho (izicubu ezithambile zomzimba). Isibonelo, angavela ebuchosheni, emaphashini, endaweni ephakathi kwesifuba sakho lapho inhliziyo yakho ikhona khona (i-mediastinum) , noma esicutshini esixhumanisa isisu sakho nezinye izitho zakho zesisu (i-omentum) . Kodwa-ke, lawa angavamile kakhulu.
Ingabe lo mdlavuza? Ingabe kufanele ngikhathazeke?
Lena yinkinga enkulu kubantu abaningi. Amaqhubu e -Angiomatoid Fibrous Histiocytoma avame ukutholakala njengamaqhubu ezicubu ezithambile angenabungozi . Lokhu kusho ukuthi awabangeli umonakalo omkhulu futhi awasabalali emzimbeni wonke.
Kodwa-ke, kwezinye izimo, lokhu kungaba yingozi . Kuleso simo, kubizwa ngokuthi i-soft tissue sarcoma .
Kodwa, nansi into ebalulekile. Nakuba i-AFH ingumdlavuza, ivame ukubhekwa njengesimila esibi esisezingeni eliphansi . Lokho kusho ukuthi inamathuba amancane kakhulu okusabalala kwezinye izingxenye zomzimba. Ngakho-ke, akukho okufanele ukhathazeke ngakho uma uzwa igama.
Sivame kangakanani lesi simo?
I-AFH iyisimo esingavamile kakhulu . Kuzo zonke izimila ezithambile zezicubu, i-AFH ibalwa ngamaphesenti amancane kakhulu, cishe angu-0.3%. Lokho kusho ukuthi ithinta cishe abantu abathathu kwabayinkulungwane. Ngakho-ke, akuwona wonke umuntu oke wezwa ngayo.
Ziyini izimpawu zalokhu? Ingabe kwenzeka kuwo wonke umuntu?
Ingxenye engcono kakhulu ukuthi, abantu abaningi abane-AFH ababonisi zimpawu futhi bangase bangazi nokuthi banalo iqhubu.
Kodwa-ke, abanye abantu bangase babe nezimpawu. Uma bezithola, zingase zihlanganise:
- Imfiva
- I-anemia, okusho ukuntuleka kwegazi
- Ukwehlisa isisindo
Lezi yizimpawu ezivame ukubonakala. Ubuhlungu nokuzwela akuvamile kakhulu . Lokhu kwenzeka kubantu abambalwa kakhulu abanalesi simo.
Kungani lolu hlobo lwefindo lwakheka? Iyini imbangela?
I-Histiocytoma ikhula lapho amangqamuzana omzimba okukhulunywe ngawo ngaphambili abizwa ngokuthi ama-histiocytes ekhula ngokushesha futhi ekhiqiza amangqamuzana amaningi e-histiocyte. Lokhu kusho ukuthi amangqamuzana ahlukana kancane kakhulu.
Imbangela eqondile ye-AFH ayikacaci okwamanje . Kodwa-ke, ezinye izifundo ziphakamise ukuthi kungenzeka ukuthi ihlotshaniswa nezici ezifana nezakhi zofuzo , izimo ezizuzwe njengefa , kanye nokuchayeka ekwelashweni ngemisebe . Kodwa-ke, lezi yizinto ezidinga ukuhlolisiswa kabanzi.
Ingabe leli qhubu lingasakazeka kwezinye izingxenye zomzimba?
Lokhu futhi kuyinto abantu abaningi abayesabayo. Kungenzeka ukuthi isimila se-AFH sisakazeke (sisakazeke) kwezinye izingxenye zomzimba, kodwa akuvamile kakhulu. Lokhu kwenzeka ngaphansi kwe-1% yamacala. Lokho kusho ukuthi abantu abangaphansi koyedwa kwabayikhulu bazosabalala. Ngakho-ke, asikho isidingo sokukhathazeka kakhulu ngaso.
Odokotela bakuthola kanjani lokhu? (Ukuxilongwa)
Ngenxa yemvelo yamaqhubu e-AFH, ngezinye izikhathi angadidaniswa nezinye izimo. Isibonelo, i-hematoma, okuyiqoqo legazi elingaphandle komthambo wegazi.Kungase kudidaniswe ne -hemangioma, uphawu olubomvu olukhona lapho kuzalwa.
Ngakho-ke, uma udokotela wakho esola ukuthi i-AFH ikhona, cishe uzosusa ingxenye noma lonke iqhubu bese elihlola ngaphansi kwe-microscope. Lokhu kubizwa ngokuthi i-biopsy .
Le biopsy ibheka izici eziningana eziqondene ne-AFH, okuhlanganisa:
- Izidleke eziqinile zamaseli afana ne-histiocyte
- Izikhala ezifana ne-cyst ezigcwele uketshezi
- Ukuqongelela kwamaseli okuvuvukala okungapheli
Uma lezi zici zikhona kusampula, odokotela bazoqinisekisa isimo njenge-AFH.
Yiziphi izindlela zokwelapha?
Ukwelashwa okuyinhloko kwe-AFH ukususa iqhubu ngokuhlinzwa . Udokotela wakho ohlinzayo ngeke asuse iqhubu kuphela, kodwa futhi nezinye izicubu ezinempilo ezizungezile. Lokhu kunganciphisa ingozi yokuthi iqhubu libuyele endaweni efanayo (ukuphindaphinda).
Ukuhlinzwa
Ezimweni eziningi, lokhu kuhlinzwa kuyindlela eyinhloko yokwelapha. Le ndlela iyaphumelela, ikakhulukazi uma isimila singakasabalali.
Ukwelashwa ngamakhemikhali kanye nokwelashwa ngemisebe
Kodwa-ke, ngezinye izikhathi ukuhlinzwa kungaba nzima kuye ngokuthi isimila sitholakala kuphi. Isibonelo, uma sisendaweni eyinkimbinkimbi njengekhanda noma intamo. Noma, ngokungajwayelekile, uma isimila sisakazekele ezingxenyeni ezikude zomzimba, ukwelashwa ngamakhemikhali noma ngemisebe kunganconywa.
- Ukwelashwa ngamakhemikhali kuyindlela yokwelapha ebhubhisa amangqamuzana omdlavuza.
- Ukwelashwa ngemisebe kuyindlela yokubhubhisa amangqamuzana omdlavuza kusetshenziswa imisebe enamandla aphezulu.
Zombili lezi zindlela zokwelapha zenziwa ngaphansi kokuqondisa kodokotela abangochwepheshe.
Yiziphi izinkinga ezingaba khona ngesikhathi sokwelashwa?
Njenganoma yikuphi ukuhlinzwa, kuneminye imiphumela emibi engenzeka ngesikhathi sokuhlinzwa ukuze kususwe lesi simila. Lokhu kufaka phakathi:
- Kukhona ingozi yokutheleleka .
- Ngezinye izikhathi umonakalo wezinzwa ungenzeka.
- Ubuhlungu bungase buvele.
- Kungase kube nokopha .
Lezi yizinto ezingalawulwa ngokuvamile.
Abantu abathola ukwelashwa ngamakhemikhali noma ngemisebe bangase babe nemiphumela emibi ehlukahlukene. Eminye yale miphumela ihlanganisa:
- I-anemia isho inani eliphansi legazi.
- Ukulahlekelwa izinwele .
- Ukukhathala .
- Isicanucanu nokuhlanza.
Udokotela wakho uzokuchazela ngokuningiliziwe ukuthi hlobo luni lokwelashwa ozolunikwa nokuthi yini ongayilindela kukho.
Ingabe ikhona indlela yokuvimbela lokhu ukuthi kungenzeki?
Eqinisweni, okwamanje ayikho indlela eyaziwayo yokuvimbela ukuthuthukiswa kwe -Angiomatoid Fibrous Histiocytoma . Ngenxa yokuthi imbangela eqondile ayikakaziwa, kunzima ukusho ukuthi ingavinjelwa kanjani.
Yini okufanele ngiyenze uma mina noma ingane yami sinalesi simo? Yini engingayilindela?
Uma udokotela wakho ethola ukuthi wena noma ingane yakho ine-AFH, uzoxoxa ngezinketho zakho ngokuningiliziwe.
- Uma iqhubu lingasakazekelanga kwezinye izindawo, cishe kuyanconywa ukuhlinzwa ukuze lisuswe . Ezimweni eziningi, iqhubu aliphinde libuye ngemva kokuhlinzwa.
- Kodwa-ke, uma isimila sesisakazekele ezingxenyeni ezikude zomzimba kusukela lapho saqala khona ukubonakala, khona-ke ukwelashwa ngamakhemikhali noma ngemisebe kunganconywa. Ezimweni ezinjalo, kuzodingeka uqhubeke nokubona udokotela wakho ukuze akulandelele futhi akuhlole ukuze aqaphe impilo yakho.
Ingabe lokhu kungelapheka ngokuphelele?
Ezimweni eziningi, yebo! I-AFH ingelapheka ngokuphelele ngokuhlinzwa.
Kodwa-ke, njengoba kushiwo ngaphambili, ezimweni ezingavamile kakhulu, lesi sifo singasakazekela kwezinye izingxenye zomzimba. Uma lokho kwenzeka, kungaba kubi kakhulu, kuze kube yingozi empilweni. Kodwa khumbula, lokhu akuvamile kakhulu.
Ngingayibona nini udokotela?
Uma ubona ushintsho olusheshayo ekubukekeni kwesikhumba sakho, njengeqhubu elisha noma ibala, ungalishayi indiva bese ubona udokotela ngokushesha . Udokotela angase alihlole bese enza ezinye izivivinyo uma kudingeka. Uma litholakala ngokushesha, kuba lula ukulilapha.
Yimiphi imibuzo ebalulekile okufanele uyibuze udokotela?
Uma uthola ukuthi unalesi simo, kubalulekile ukufunda okuningi ngangokunokwenzeka ngaso. Lokhu kuzokusiza ukuthi wenze izinqumo ezinolwazi mayelana nempilo yakho. Nansi eminye imibuzo ongayibuza udokotela wakho:
- Liphi ifindo lami?
- Ingakanani ifindo lami?
- Ingabe iqhubu lami alinabungozi noma liyingozi?
- Ingabe isimila sami sisakazekele kwezinye izindawo?
- Yiziphi izindlela zokwelapha enginazo?
- Angakanani amathuba okuba ukuhlinzwa kuphumelele?
- Ingabe kufanele ngicabangele ukwelashwa nge-chemotherapy noma ngemisebe?
- Ngingakufunda kuphi okwengeziwe ngalesi sifo? (isib. izincwadi, amawebhusayithi)
Ungesabi ukubuza le mibuzo. Kubalulekile ukususa noma yikuphi ukungabaza onakho.
Ekugcineni, umyalezo okufanele uwuthathe uye nawo ekhaya
Kulungile, ngakho-ke, kusukela kulokho esikhulume ngakho, lezi yizinto ezibaluleke kakhulu okudingeka uzikhumbule:
I-Angiomatoid fibrous histiocytoma iyisimila esithambile esingavamile.
Esikhathini esiningi, lezi azinawo umdlavuza futhi zingelapheka ngokuhlinzwa .
Lokhu kuvame kakhulu ezinganeni nakubantu abasha .
Abantu abaningi ababonisi izimpawu.
Akuvamile, lokhu kungaba umdlavuza futhi kusakazekele kwezinye izindawo. Uma lokhu kwenzeka , kungadingeka ukwelashwa ngamakhemikhali noma ngemisebe .
Uma ubona iqhubu elisha emzimbeni wakho, bona udokotela ngokushesha .
Ngiyethemba ukuthi lolu lwazi luzokusiza. Khumbula, uma unemibuzo noma ukungabaza, ungalokothi unqikaze ukukhuluma nodokotela wakho. Ungumuntu ongcono kakhulu ongakweluleka.
I- Angiomatoid fibrous histiocytoma, i-AFH, umdlavuza wezicubu ezithambile, amaqhubu esikhumba, izingane, ukwelashwa komdlavuza, ukuhlinzwa











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