Kungani inani legazi lehla ngokuzumayo? Ake sixoxe nge-Aplastic Crisis

Kungani inani legazi lehla ngokuzumayo? Ake sixoxe nge-Aplastic Crisis - Nirogi Lanka

Physician Reviewed — Not Medical Advice

Wake wezwa noma wabona isimo lapho othile—ikakhulukazi ingane encane—ngokuzumayo ehlangabezana nokwehla okukhulu kwenani legazi, okumenza azizwe ekhathele futhi, kwezinye izimo, ebhekene nesimo esiphuthumayo esisongela ukuphila? Yilokho kanye esizokuxoxa ngakho lapha: i -Aplastic Crisis . Nakuba igama lingase lizwakale liyesabisa, ukuqonda lesi simo kuyisinyathelo sakho sokuqala ekusiphatheni ngempumelelo nokuqinisekisa ukunakekelwa ngesikhathi. Kwa-Nirogi Lanka, silapha ukukuqondisa kulokho okudingeka ukwazi ukuze uhlale ulungele.

Iyini ngempela i-Aplastic Crisis?

Kalula nje, i -Aplastic Crisis yenzeka lapho umongo wakho wethambo uphela ngokuzumayo ukukhiqiza amangqamuzana amasha egazi abomvu . Ungase uzibuze, “Kungani lokhu kubalulekile?” Nokho, amangqamuzana abomvu egazi ayizinto ezibalulekile zokuthutha umoya-mpilo emzimbeni wakho wonke. Lapho ukukhiqizwa kwawo kuma, inani lamangqamuzana abomvu egazi lakho liyehla, okuholela ekulahlekelweni kwegazi okukhulu . Lesi yisimo esibucayi esingaba yingozi empilweni.

Ngokuvamile, inkinga yokungapheleli kwegazi ithinta kakhulu abantu abanezinkinga zegazi eziyisisekelo, njenge- Sickle Cell Anemia . Ivame ukubangelwa yi -Parvovirus B19 , ukutheleleka okuvamile kwegciwane. Nakuba abantu abaningi bathola leli gciwane ngaphandle kwezinkinga ezinkulu, libeka ingozi enkulu kulabo abanezinkinga zegazi ezikhona kakade. Livame ukubonakala ezinganeni, ikakhulukazi izinsana. Kodwa-ke, kunezindaba ezinhle: ukwelashwa okusebenzayo, okuhlanganisa ukumpontshelwa igazi kanye nokwelashwa nge-Intravenous Immunoglobulin (IVIG) , kuyatholakala eNirogi Lanka nakwezinye izikhungo zezokwelapha.

Ingabe lesi yisimo esivamile kuwo wonke umuntu?

Lutho neze. Njengoba kushiwo, i-Parvovirus B19 ivame kakhulu, kodwa ayibangeli inkinga yokungapheleli kubantu abaningi. Ithinta cishe kuphela labo asebevele bephila nesifo segazi esingamahlalakhona.

Izinsana nezingane ezine- Sickle Cell Anemia zisengozini enkulu kakhulu. Ngaphezu kwalokho, uma unezinye izimo ezibangela i-hemolytic anemia (lapho amangqamuzana abomvu egazi ebhujiswa ngaphambi kwesikhathi), usengozini enkulu uma ubhekene ne-Parvovirus B19. Lokhu kufaka phakathi:

  • I-Spherocytosis Yefa
  • Isifo se-Hemoglobin C
  • I-Thalassemia
  • I-G6PD deficiency syndrome
  • Ukuntuleka kwe-Pyruvate Kinase
  • I-Autoimmune Hemolytic Anemia
  • I-Paroxysmal Nocturnal Hemoglobinuria
  • I-Elliptocytosis Yefa

Uma wena noma ingane yakho ninayo noma iyiphi yalezi zinkinga zegazi, kubalulekile ukuhlala niqaphile mayelana nalezi zimpawu.

Yiziphi izimpawu ze-Aplastic Crisis?

Kubantu abadala kanye nezingane, inkinga yokungapheleli ibonakala ngezimpawu ezihlobene nokuntuleka kwegazi okukhulu. Izinsana nezingane ezincane zingase zibonakale zithukuthele noma zithukuthele ngendlela engavamile . Uma ubona ingane yakho ikhala ngokungaduduzeki noma ibonakala ithukuthele ngendlela engavamile, kungaba uphawu lwesixwayiso kusenesikhathi.

Izimpawu ezibalulekile zifaka:

  • Ukukhathala: Ukuzizwa ukhathele futhi ungenawo amandla okwenza imisebenzi yansuku zonke.
  • Umkhuhlane: Izinga lokushisa lomzimba likhuphukela ku-38°C (101°F) noma ngaphezulu.
  • Ukuzungeza: Ukuzizwa unekhanda elibuthakathaka noma uzwa ubuhlungu bekhanda.
  • Ukuphelelwa umoya (ukuphelelwa umoya): Ukuzizwa uphelelwa umoya ngesikhathi somsebenzi olula noma ngenkathi ukhuphuka izitebhisi.
  • Ukushaya kwenhliziyo okungajwayelekile noma okusheshayo: Inhliziyo yakho ingase izwakale sengathi iyagijima noma iyagxumagxuma.
  • Umbala okhanyayo: Isikhumba sakho, izindebe, izinsini, noma imibhede yezinzipho ibonakala iphaphathekile ngendlela engavamile.

Uma wena noma ingane yakho nibonisa noma yiziphi zalezi zimpawu—ikakhulukazi uma ninesifo segazi esaziwayo— sicela nifune usizo lwezokwelapha ngokushesha emnyangweni wezimo eziphuthumayo oseduze.

Kungani kwenzeka i-Aplastic Crisis?

Igama elithi “aplastic” lisho ukuyeka ukukhula noma ukukhiqizwa. Ngesikhathi senkinga ye-aplastic, umongo wakho wethambo awusakwazi ukukhiqiza amangqamuzana abomvu egazi anempilo. Umbangela, i-Parvovirus B19 , ihlasela futhi ilimaze amangqamuzana abomvu egazi angakavuthwa. Njengoba umongo wakho wethambo unesibopho sokukhiqizwa okuqhubekayo kwamangqamuzana abomvu egazi, lokhu kuphazamiseka kwegciwane kuvala ngempumelelo “ifektri” yegazi lomzimba wakho, okuholela ekulahlekelweni kwegazi okukhulu .

Yiziphi izinkinga ezingaba khona ngenxa yalesi simo?

Inkinga yokungapheleli kwezicubu ingadala izinkinga ezinkulu ezahlukahlukene, ikakhulukazi kubantu abane- Sickle Cell Anemia . Lezi zinkinga zinzima futhi zidinga ukungenelela kwezokwelapha ngokushesha.

  • Inkinga Ehlala Isikhathi Eside Yokugoba Kwemithambo Yegazi (i-VOC): I-VOC iyisihlava sobuhlungu obungazelelwe, obukhulu obuvame ukutholwa abantu abane-sickle cell anemia. Inkinga engapheli ingandisa kakhulu lobu buhlungu.
  • I-Myocarditis: Lokhu kubhekisela ekuvuvukeni kwemisipha yenhliziyo, okungaholela ekuvuvukeni nasekuphazamisekeni kokusebenza.
  • Ukususwa kwe-splenic: Lokhu kwenzeka lapho amangqamuzana abomvu egazi angajwayelekile ebhajwa ngaphakathi kwe-spleen, okwenza ikhule ngokushesha.
  • I-Glomerulonephritis: Lesi yisimo esithinta izinso. Uma singalashwa, singaholela esifweni sezinso esingamahlalakhona noma ekuhlulekeni kwezinso.

Yingakho sigcizelela ukuthi ukuhlala uqaphile nokuqapha impilo yakho eduze kubalulekile.

Odokotela bakuthola kanjani lesi simo?

Uma wena noma ingane yakho nibonisa izimpawu eziphathelene nalesi sifo, udokotela wakho uzoqala ngokuthatha umlando wezokwelapha onemininingwane bese enza ukuhlolwa ngokomzimba. Ukuze aqinisekise ukuxilongwa, angayala ukuhlolwa okuningana:

  • Ukubalwa Kwegazi Okuphelele (i-CBC): Lokhu kulinganisa amazinga akho amangqamuzana abomvu egazi, amangqamuzana amhlophe egazi, nama-platelet. Esimweni esibucayi, inani lamangqamuzana abomvu egazi livame ukuba phansi kakhulu.
  • Inani lama-reticulocyte: Ama-reticulocyte angamaseli abomvu egazi angakavuthwa. Lokhu kuhlolwa kwembula ukuthi umongo wakho wethambo ukhiqiza kanjani amaseli amasha abomvu egazi ngempumelelo. Ngesikhathi senkinga ye-aplastic, leli nani liphansi kakhulu.
  • Ukuhlolwa kwe-Parvovirus B19: Lokhu kuhlolwa kwegazi kuqinisekisa ukuthi unesifo se-Parvovirus B19 samanje noma sakamuva.

Ngale miphumela, udokotela wakho anganquma ngokuqinisekile ukuthi ubhekene ne-Aplastic Crisis noma enye inkinga yezokwelapha.

Yiziphi izindlela zokwelapha?

Ukwelashwa okuyinhloko kwe-Aplastic Crisis ukumpontshelwa igazi . Lokhu kunikeza amangqamuzana egazi abomvu asheshayo nanempilo ukuze athathe indawo yalokho umzimba wakho ongakwazi ukukukhiqiza njengamanje. Ngaphezu kwalokho, ukwelashwa nge -Intravenous Immunoglobulin (IVIG) kunganikezwa ngqo ngemithambo yegazi.

Iningi leziguli liyalulama zingakapheli izinsuku eziyi-10 kuya kweziyi-14 ngemva kokuqala ukwelashwa. Isici esihle ukuthi uma usuthole i-Parvovirus B19, umzimba wakho uvame ukuba nokuzivikela komzimba impilo yonke, okunciphisa kakhulu ingozi yezinkinga zesikhathi esizayo ezibangelwa yileli gciwane elithile.

Ingabe iNhlekelele ye-Aplastic ingavinjelwa?

Kunzima ukuvimbela ngokuphelele, njengoba inkinga yokungapheleli kwegazi iqala lapho umuntu onesifo segazi esikhona etheleleke nge -Parvovirus B19 . Leli yigciwane elivame kakhulu, futhi ngeshwa, akukho muthi wokugomela okwamanje.

Kodwa-ke, uma wena noma ingane yakho nine- Sickle Cell Anemia noma isifo segazi esifanayo, xhumana nodokotela wakho mayelana namasu okuzivikela. Izinyathelo ezilula njengokugwema izindawo ezinabantu abaningi ngesikhathi sokuqubuka kwezifo nokugcina inhlanzeko yezandla enhle kungasiza ekunciphiseni ingozi yakho yokuchayeka iyonke.

Iyini i-prognosis ngemva kwalesi simo?

Isibikezelo sibhekisela endleleni okungenzeka isimo sakho siqhubeke ngayo. Abantu ababhekene ne-Aplastic Crisis bavame ukululama kahle zingakapheli izinsuku eziyi-10 kuya kweziyi-14 uma kuqala ukungenelela kwezokwelapha. Nakuba abanye abantu bengase bathambekele ezigamekweni eziphindaphindayo, ukuhlala uqaphela izimpawu zakho nokulandela uhlelo lokunakekelwa kwesikhathi eside lukadokotela wakho eNirogi Lanka kubalulekile enhlalakahleni yakho eqhubekayo.

Ngingazinakekela kanjani mina noma ingane yami?

Inkinga Ebangelwa I-Aplastic ingenye yezinkinga eziningi ezingase zihlotshaniswe nezinkinga zegazi njenge- Sickle Cell Anemia . Nakuba ungase ungakwazi ukuvimbela igciwane njalo, ungasekela impilo yakho iyonke:

  • Gcina ukuhlolwa kwezokwelapha njalo: Ukugcina ama-aphoyintimenti njalo nethimba lakho lezokunakekelwa kwempilo eNirogi Lanka kusiza ekubambeni izinkinga ezingaba khona kusenesikhathi.
  • Nciphisa ingozi yokutheleleka: Xoxa nadokotela wakho ngamasu okuzivikela ezifweni ezivamile ezifana nomkhuhlane noma umkhuhlane ovamile.
  • Yidla ukudla okunempilo nokulinganiselayo: Beka phambili ukudla okunempilo futhi uqinisekise ukuthi uhlala unamanzi ngokuphuza izingilazi zamanzi ezingu-8-10 nsuku zonke.
  • Zivocavoce kancane: Ukuzivocavoca njalo kuthuthukisa isimo sengqondo kanye nempilo iyonke. Lalela umzimba wakho, phumula uma uzizwa ukhathele, futhi uhlale unamanzi anele.

Le mikhuba iqinisa amasosha omzimba wakho futhi inegalelo empilweni yakho iyonke.

Kufanele ngimbone nini udokotela?

Inkinga ye-Aplastic iyisimo esiphuthumayo sezokwelapha.

Uma wena noma ingane yakho nine- Sickle Cell Anemia , sicela nifune usizo lwezokwelapha ngokushesha uma nizwa ukukhathala okungazelelwe, ubuthakathaka obukhulu, noma ezinye izimpawu ezesabekayo. Ungalibali; ukwelashwa okusheshayo kubalulekile ukuze ululame ngokuphephile. Uma kudingeka, iya ekamelweni eliphuthumayo eliseduze noma ushayele u-911.

Yimiphi imibuzo okufanele ngiyibuze udokotela wami?

Uma wena noma ingane yakho nibhekene ne-Aplastic Crisis, kubalulekile ukuxhumana ngokukhululekile nethimba lakho lezokunakekelwa kwempilo. Nazi ezinye zemibuzo ebalulekile ongase ufune ukuyibuza:

  • Mina/ingane yami ngingalindela nini ukululama?
  • Amathuba okuthi lokhu kwenzeke futhi angakanani?
  • Ingabe kukhona izinyathelo zokuphepha ezithile okufanele ngizithathe lapho ngiphatha lesi simo?

Ukubuza le mibuzo kuyisinyathelo esibalulekile ekunciphiseni ukukhathazeka kwakho nokuhlala unolwazi ngohlelo lwakho lokunakekelwa.

Ingabe i-Aplastic Crisis kanye ne-Aplastic Anemia ziyinto efanayo?

Nakuba zombili lezi zimo zihilela ukwehla kwenani lamaseli abomvu egazi, ziyizinkinga zezokwelapha ezihlukile.

I-Aplastic Crisis ibhekisela ekumisweni okungazelelwe nokwesikhashana kokukhiqizwa kwamangqamuzana abomvu egazi.

I-Aplastic Anemia yisimo esingamahlalakhona esikhula ngokuhamba kwesikhathi, esivame ukuthinta zonke izinhlobo zamaseli egazi—kufaka phakathi amaseli amhlophe egazi nama-platelet—hhayi amaseli abomvu egazi kuphela.

Kalula nje, i-Aplastic Crisis iyisimo esiphuthumayo esiphuthumayo, sesikhathi esifushane, kanti i-Aplastic Anemia iyisimo sesikhathi eside esiqala ngaphakathi komnkantsha.

Izinto Ezibalulekile Ongazithatha

Sithemba ukuthi lokhu kubuka konke kukunikeza ukuqonda okucacile nge-Aplastic Crisis. Lokhu kuyinkinga enkulu engathinta abantu abanezinkinga zegazi ezifana ne -Sickle Cell Anemia . Kwenzeka lapho umongo wethambo uyeka ukukhiqizwa kwamangqamuzana abomvu egazi ngokuzumayo, okuholela ekulahlekelweni kwegazi okukhulu, okungase kusongela ukuphila.

Ngenxa yokuthi izimpawu zivela ngokushesha, kungaba yinto exakile. Kodwa-ke, ochwepheshe bezokwelapha bangakuphatha lokhu ngempumelelo ngokumpontshelwa igazi nokunakekelwa okuqondiwe.

Uma wena noma ingane yakho nisengozini, xoxani ngezibonakaliso zesixwayiso nodokotela wakho. Nakuba ungase ungakwazi njalo ukuvimbela iNhlekelele ye-Aplastic, ukwazi kahle ukuthi yini okufanele uyenze nokuthi nini lapho kufanele ufune usizo oluphuthumayo (911) kubalulekile. Ukulungiselela okunolwazi kuyindlela yakho engcono kakhulu yokuzivikela.

👩🏽‍⚕️ Imibuzo Evame Ukubuzwa (Imibuzo Evame Ukubuzwa)

💬 Iyini i-Aplastic Crisis?

Umnkantsha wethu unesibopho sokukhiqiza amangqamuzana abomvu egazi. Inkinga ye-Aplastic yenzeka lapho, ngokuvamile ibangelwa ukutheleleka ngegciwane (njenge-Parvovirus B19), umnkantsha umisa ukukhiqizwa ngokuzumayo izinsuku eziningana.

💬 Kwenzekani esigulini phakathi nalokhu kwehla okungazelelwe?

Njengoba amangqamuzana abomvu egazi ethwala umoya-mpilo emzimbeni wakho wonke, ukwehla okungazelelwe kuholela ekulahlekelweni kwegazi okukhulu. Ungase uqaphele isikhumba esikhanyayo, izindebe, kanye nemibhede yezinzipho, ukushaya kwenhliziyo okwandayo, ubunzima bokuphefumula, noma ngisho nokuquleka.

💬 Lokhu kuphathwa kanjani, ikakhulukazi ezinganeni?

Lokhu kubaluleke kakhulu ezinganeni ezineSickle Cell Disease. Uma zilaliswa esibhedlela, odokotela bazonikeza igazi ukuze kuqiniswe isiguli. Ngokuvamile, umnkantsha uqala ukuqala kabusha ukukhiqizwa okuvamile zingakapheli izinsuku eziyi-10 kuya kweziyi-14 ngemva kokwelashwa.


Inkinga Ye-Aplastic YaseNirogi Lanka , Amaseli Egazi Abomvu, Umnkantsha Wamathambo, I-Anemia, I-Parvovirus B19, I-Anemia Yamaseli E-Sickle