Ingabe ngezinye izikhathi uzizwa sengathi amhlophe amehlo akho aphuzi kancane? Noma umngane wakho wake wakubuza ukuthi, "Kungani amehlo ami ephuzi?"? Uma lokho kwenzeka, uzizwa wesaba ngokuzumayo, "O, ingabe nami nginesifo se-jaundice?" Ngoba sonke siyazi ukuthi ukuphuzi kwamehlo kungaba uphawu lwenkinga ethile esibindini. Kodwa akuzona zonke izifo ze-jaundice ezibangelwa yisifo sesibindi esibi. Namuhla sizokhuluma ngesimo abantu abaningi abanaso, kodwa lokho akuyona into okufanele uyesabe kakhulu. Leyo yi-Gilbert Syndrome.
Kalula nje, iyini i-Gilbert Syndrome?
I-Gilbert Syndrome ayisona isifo esibi kakhulu. Yisimo esivamile kakhulu sezakhi zofuzo esidluliselwa ezizukulwaneni ngezizukulwane. Cabanga ukuthi amangqamuzana abomvu egazi emzimbeni wethu ayafa ngokuhamba kwesikhathi. Bese kuthi lapho ephuka, kukhiqizwe umkhiqizo wemfucuza ophuzi obizwa ngokuthi i-bilirubin . Kubukeka sengathi imfucuza eluhlaza ebolayo. Omunye wemisebenzi eyinhloko yesibindi sethu ukususa lo mkhiqizo wemfucuza obizwa ngokuthi i-bilirubin emzimbeni.
Abantu abane-Gilbert's Syndrome banenqubo ecothayo yokususa i-bilirubin. Lokhu kungenxa yokuthi isibindi sabo sinezinga eliphansi le-enzyme esiza kule nqubo. I-gene ethinta lokhu ibizwa ngokuthi 'UGT1A1'. Ukuze ube nalesi simo, kumele ukuthi uthole amakhophi amabili alesi gene esishintshiwe, elilodwa kumama wakho nelinye kuyihlo.
Kalula nje, kufana nefektri esibindini, lapho i-bilirubin yomkhiqizo ongcolile isebenza kancane. Ngakho-ke ngezinye izikhathi le nto ephuzi ebizwa ngokuthi i-bilirubin iqoqana egazini. Yilapho amehlo nesikhumba kubukeka kuphuzi. Lokhu sikubiza nangokuthi i-jaundice . Kodwa khumbula, i-Gilbert's Syndrome akuyona isifo esilimaza isibindi futhi akuyona into okufanele uyesabe.
Ziyini izimpawu? Kungani zivele ngokuzumayo?
Esikhathini esiningi, abantu abane-Gilbert's Syndrome ababonisi zimpawu. Le enzyme yanele ukulawula amazinga e-bilirubin emizimbeni yabo.
Kodwa kwezinye izimo ezikhethekile, izinga le-bilirubin egazini likhuphuka kancane. Yilapho-ke amhlophe amehlo nesikhumba kuba phuzi. Lokhu sikubiza ngokuthi i-jaundice. Uma ubona lolu hlobo lokuphuzi, kufanele nakanjani ubone udokotela ukuze uthole ukuthi kukhona yini esinye isizathu esingathi sína.
Ngezinye izikhathi, lokhu kuphuzi kungahambisana nekhanda elibuhlungu, ukukhathala, kanye nokungakhululeki esiswini.
Pho kungani leli zinga le-bilirubin likhuphuka ngokuzumayo? Kunezizathu eziningana eziqondile ezithinta lokhu. Ake sibone ukuthi ziyini.
| Izimbangela ezikhulisa amazinga e-bilirubin | Kwenzekani? |
|---|---|
| Ukucindezeleka | Izinto ezifana nokuhlolwa nezinkinga zomsebenzi zingashintsha izinqubo zomzimba. |
| Ukuphelelwa amanzi emzimbeni | Uma ungaphuzi amanzi anele. |
| Ukweqa ukudla | Uma uzila ukudla noma weqa ukudla ngenxa yokuba matasa. |
| Izifo | Uma uthola isifo esinjengomkhuhlane noma umkhuhlane, umzimba wakho uyalwa naso. |
| Ukuzivocavoca okunzima | Uma umzimba wakho ukhathele kakhulu ukuba ungamelana nawo. |
| Utshwala | Utshwala bubangela ukucindezeleka okwengeziwe esibindini. |
| Ukuya esikhathini kwabesifazane | Lesi simo singase sibangelwe ukushintsha kwama-hormone. |
Udokotela ukuthola kanjani lokhu?
Ngokuvamile, othile utholakala ene-Gilbert's Syndrome ngengozi. Mhlawumbe uma uhlolwa igazi lesinye isimo, udokotela wakho uqaphela ukuthi izinga lakho le-bilirubin liphakeme kancane kunejwayelekile. Yilapho-ke besola khona.
Lezi zinyathelo zivame ukulandelwa ukuze kutholakale isifo:
- Ukuhlolwa kwegazi:Amazinga e-Bilirubin ayahlolwa. Ukuhlolwa kokusebenza kwesibindi kwenziwa futhi ukuhlola ukusebenza kwesibindi. Lokhu kungavimbela ezinye izifo zesibindi ezingathi sína.
- Ukuskena nge-Ultrasound: Ngezinye izikhathi ukuskena kungenziwa ukuqinisekisa ukuthi azikho ezinye izinkinga ngesibindi (njengamatshe noma ukugcinwa kwamafutha).
- Ukuhlolwa Kwezakhi Zofuzo: Lokhu kuhlolwa kungenziwa ukuqinisekisa ukuthi kukhona yini ukuguquka kwezakhi zofuzo ze-`UGT1A1`. Kodwa-ke, lokhu akwenziwa njalo.
- Ukuhlolwa Kwesibindi: Lokhu akuvamile ukwenziwa ukuhlola i-Gilbert Syndrome. Kwenziwa kuphela uma kukhona okusolakala ukuthi kunesinye isifo esibi kakhulu.
Ingabe ikhona indlela yokwelapha i-Gilbert Syndrome? Yini okufanele siyenze?
Nazi izindaba ezinhle. I-Gilbert's Syndrome akuyona isifo esidinga ukwelashwa. Ukuphuzi (i-jaundice) ekubangelwe yiyo ngeke kubangele noma yimuphi umonakalo wesikhathi eside emzimbeni wakho.
Ngakho-ke okudingeka sikwenze ukuhlala kude ngangokunokwenzeka nezinto ezibangela ukwanda kwamazinga e-bilirubin esikhulume ngawo ngaphambili.
- Ungayeki ukudla. Yidla ngesikhathi.
- Phuza amanzi amaningi. Kubaluleke kakhulu ukuphuza okungenani amalitha angu-2-3 amanzi ngosuku.
- Nciphisa ukucindezeleka. Khulula ingqondo yakho ngokuzindla, ukulalela umculo, noma ukuzibandakanya entweni oyithandayo.
- Lala kahle. Lala okungenani amahora angu-7-8 ngosuku.
- Nciphisa noma uyeke ngokuphelele ukuphuza utshwala .
- Gwema ukuvivinya umzimba okucindezela umzimba kakhulu. Izinto ezifana nokuhamba njalo kanye ne-yoga zinhle.
Indaba ekhathazayo kakhulu!
Yilapho okudingeka ugxile khona kakhulu. I-enzyme efanayo ephula i-bilirubin esibindini sethu iyasiza nasekususeni eminye imithi emzimbeni. Ngenxa yokuthi leyo enzyme isebenza kancane kancane kumuntu one-Gilbert's Syndrome, leyo mithi ihlala emzimbeni isikhathi eside futhi ingase ibangele imiphumela emibi.
Njengomuntu one-Gilbert's Syndrome, kubalulekile ukukhuluma nodokotela wakho nganoma yimiphi imithi emisha oyithathayo.
Isibonelo, imithi evame ukusetshenziswa njenge -acetaminophen (i-Panadol, i-Paracetamol) iwela kulesi sigaba. Kufakwe nemithi efana ne-'Irinotecan', esetshenziselwa umdlavuza, kanye ne-'Protease inhibitor', esetshenziselwa i-HIV kanye ne-Hepatitis C.
Ngakho-ke, uma uya kudokotela, kubaluleke kakhulu ukuthi, "Ngine-Gilbert Syndrome." Khona-ke udokotela uzokucabangela lokho lapho ekunikeza imithi.
Umlayezo Wokuya Nawe Ekhaya
- I-Gilbert Syndrome akuyona isifo okufanele sesatshwe. Yisimo esingenangozi, esinofuzo esidluliselwa ezizukulwaneni ngezizukulwane.
- Uphawu oluyinhloko ukuphuzi kwamehlo nesikhumba (i-jaundice) ngezikhathi zokucindezeleka, ukugula, noma ukuzila ukudla.
- Lesi simo asidingi ukwelashwa. Okudingeka ukwenze ukugwema izinto ezibangela ukwanda kwamazinga e-bilirubin.
- Uma amehlo noma isikhumba sakho siphenduka sibe phuzi, qiniseka ukuthi ufuna iseluleko sezokwelapha ukuqinisekisa ukuthi akuyona enye inkinga enkulu.
- Uma wazi ukuthi unesifo sikaGilbert, kubaluleke kakhulu ukwazisa udokotela wakho ngaphambi kokuthatha noma yimuphi umuthi omusha.











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