Ingabe ingane yakho inenkinga ngemithambo ye-lymph emathunjini ayo? (I-Primary Intestinal Lymphangiectasia) Ake sixoxe ngalokhu!

Wake waphawula ukuthi imilenze nezingalo zengane yakho ziyavuvukala ngezinye izikhathi? Noma ingabe ivame ukukhononda ngobuhlungu besisu? Ingabe yehlisa isisindo ngaphandle kokwandisa isisindo? Ungase ucabange ukuthi lezi yizimpawu ezivamile esingazinaki kakhulu. Kodwa-ke, ngemuva kwalezi, kungase kube nesimo esingavamile kodwa esikhathazayo esibizwa ngokuthi 'i-Primary Intestinal Lymphangiectasia' (PIL) . Leli gama lizwakala liyesabeka kancane, akunjalo? Kodwa ungakhathazeki. Ake sixoxe ngalokhu ngokuningiliziwe nangokulula kakhulu namuhla.

Kuyini 'i-Primary Intestinal Lymphangiectasia'?

Kalula nje, lesi yisifo esingavamile esenzeka ohlelweni lokugaya ukudla lwezingane zethu, ikakhulukazi emathunjini amancane. Uyazi, ukudla okuningi esikudlayo kuyagaywa futhi izakhamzimba ezikuwo zimuncwa emzimbeni kuleli thumbu elincane.

Manje, kulesi simo (i-PIL), uhlelo lwepayipi elincane elibizwa ngokuthi 'imithambo ye-lymph' emathunjini amancane engane yakho lonakele futhi azisebenzi kahle. Le mithambo ye-lymph iyinethiwekhi enhle kakhulu yeziteshi ezisakazeke kuwo wonke umzimba wethu. Kufana nolunye 'uhlelo lwepayipi' emzimbeni wethu. Umsebenzi wazo oyinhloko ukuqoqa uketshezi namaprotheni aqoqana ezicutshini zethu (esilubiza ngokuthi 'i-lymph') bese siwabuyisela ohlelweni lokujikeleza kwegazi.

Kodwa enganeni ene-PIL, le mithambo ye-lymph iyavuvukala futhi 'ivuza'. Okwenzekayo ukuthi esikhundleni sokumunca izakhamzimba namaprotheni avela kule mithambo ye-lymph angene emzimbeni, avuza abuyele emathunjini. Kufana namanzi avuzayo avela epayipini elivuzayo.

Uma izinto zivuza kanje, kuvela izinkinga ezimbili ezinkulu:

1. Amazinga aphansi amaprotheni: Amaprotheni ayinto eyenza umsebenzi obaluleke kakhulu emzimbeni. Ngakho-ke uma lokhu kuvuza emathunjini, umzimba awutholi amaprotheni anele. Lokhu kungabangela ukuthi umzimba wonke uvuvuke. Siphinde sibize lesi simo ngokuthi 'i-protein-losing enteropathy' ngokwezokwelapha.

2. Ukushoda kokudla okunempilo: Kanye nalolo ketshezi oluvuzayo, amavithamini namaminerali abalulekile nawo ayalahleka. Uma lokhu kunganakekelwa kahle, ingane ingase ibe nokushoda kokudla okuhlukahlukene.

(PIL) ivame kakhulu ukuhlasela izingane ezincane kanye nentsha. Ivame ukuxilongwa ngaphambi kweminyaka emi-3. Kodwa-ke, ngezinye izikhathi ingathinta abantu abadala ngisho nezingane ezisakhula esibelethweni. Akukho ukwelashwa kwayo okwamanje. Kodwa-ke, odokotela bangalawula izimpawu futhi banciphise ukuvuza nokuvuvukala ngokusebenzisa uhlelo lokudla olukhethekile kanye nemithi. Bangaphinde banike umzimba amavithamini namaminerali owadingayo.

Lesi simo (i-PIL) sibizwa ngamanye amagama amaningana:

• I-lymphangiectasia yamathumbu
• I-Lymphangiectasia
• Isifo saseWaldmann

Yiziphi izimpawu zalesi simo (i-PIL)?

Uphawu oluyinhloko noluvame kakhulu lwe-PIL ukuvuvukala okubangelwa ukugcinwa koketshezi. Odokotela bakubiza lokhu ngokuthi i-lymphedema . Ungase ukubone lokhu emilenzeni nasezinyaweni zengane yakho. Njengoba lolu ketshezi luqoqana, ubuso bengane yakho, izandla, ngisho nendawo yangasese kungase kuqale ukuvuvukala.

Cabanga nje, lapho ingane yakho ivuka ekuseni, izinyawo zayo sezijwayelekile, kodwa njengoba usuku luqhubeka, kusihlwa, izinyawo zayo sezivuvukele kangangokuthi ayikwazi ngisho nokugqoka izicathulo. Yilokho okwenzekayo kulokhu.

Ngaphezu kwalokho, ingane ingase ibe noketshezi oluzungeze inhliziyo (olubizwa ngokuthi i-pericarditis ), uketshezi esifubeni (olubizwa ngokuthi i-pleural effusion ), noma uketshezi esiswini (olubizwa ngokuthi i-ascites noma i-abdominal effusion) .

Nazi ezinye izimpawu:

• Ubuhlungu besisu
• Isicanucanu nokuhlanza
• Uhudo (ubuhlungu besisu )
• Ukuzizwa ukhathele ngaso sonke isikhathi (Ukukhathala)
• Ukwehlisa isisindo
• Ukungakhuluphali kungakhathaliseki ukuthi udla ukudla okungakanani (lokhu kungenxa yokuthi umzimba awumunci kahle izakhamzimba, okubizwa ngokuthi 'i-malabsorption' )

Uma ingane yakho inesinye noma ngaphezulu salezi zimpawu, kungcono ukufuna iseluleko sezokwelapha.

Ingabe zikhona izinkinga ezinkulu zesimo (se-PIL)?

Yebo, nakuba kungavamile kakhulu, (i-PIL) ingabangela ukuthi umzimba wonke wengane uvuvuke ngokweqile. Lokhu kubizwa ngokuthi 'i-anasarca' . Lesi yisimo esibi esingaba yingozi ngisho nokuphila. Ngakho-ke, kubaluleke kakhulu ukuqaphela izimpawu.

Iyini imbangela yalesi simo (i-PIL)?

Lesi simo (i-PIL) sibangelwa ukungajwayelekile kweziteshi ze-lymphatic zomntwana. Lezi ziteshi ze-lymphatic, njengoba kushiwo ngaphambili, ziyisimiso samapayipi athwala izinto ezifana namafutha avela emathunjini amancane omntwana aye esibindini nakwezinye izingxenye zomzimba.

Lokhu kungavamile kubangela ukuthi imithambo ye-lymph ivaleke. Bese igcwala uketshezi lwe-lymph, imithambo ivuvuke, bese ekugcineni iqhuma, bese okuqukethwe yileyo mithambo kuqongelela emathunjini amakhulu engane (ikholoni).

Kodwa-ke, ochwepheshe bezokwelapha abakakazi kahle ukuthi kungani lesi simo senzeka. Yileyo inkinga.

Ingabe lokhu kuyizakhi zofuzo? (Ingabe i-intestinal lymphangiectasia iyizakhi zofuzo?)

Akuvamile kakhulu ukuthi kube nemibiko yamalungu amaningana omndeni ofanayo athintekile yilesi simo. Kodwa-ke, abacwaningi abakaqiniseki ukuthi lesi yisimo sofuzo yini. Ucwaningo olwengeziwe luyenziwa ngalokhu.

Sitholakala kanjani lesi sifo (i-PIL)? (Ukuxilongwa)

Esikhathini esiningi, into yokuqala udokotela angayenza ukuhlola ingane yakho ngokomzimba bese ekubuza ngezimpawu zengane yakho. Ngezinye izikhathi, i-ultrasound yokukhulelwa , eyenziwa ngesikhathi ingane isesesibelethweni, ingabonisa izimpawu zokuvuvukala (i-edema) emilenzeni yengane, okungakunikeza umbono wokuthi kwenzekani.

Ngemva kokuzalwa komntwana, udokotela uzohlola i-PIL ngokusebenzisa ithuluzi elikhethekile elibizwa ngokuthi i-endoscope ukuze abheke ngaphakathi kwamathumbu omntwana. Leli yipayipi eliguquguqukayo elinekhamera elinamathiselwe kulo. Umntwana uzolaliswa ngaphansi kwe-anesthesia phakathi nalolu vivinyo, ukuze angazizwa ubuhlungu. Ngakho ungakhathazeki.

Ngesikhathi sale endoscopy, udokotela uthatha izingcezu ezincane zezicubu (ezibizwa ngokuthi i-biopsy ) ezindaweni eziningana zamathumbu engane. Ngemuva kwalokho, isazi sezifo , udokotela ogxile ekuhloleni izicubu, ubheka lawa masampula ezicubu ngaphansi kwe-microscope ukuze ahlole noma yikuphi ukuvuvukala okungajwayelekile kwama-lymph node.

Ngaphezu kwalokho, ukuhlolwa kwegazi kunganquma ukuthi ingakanani iphrotheni emzimbeni. Isampula yendle ingathathwa futhi ukuze kubonakale ukuthi uketshezi luyavuza yini luvela kuma-lymph node luye emathunjini amancane.

Yiziphi izindlela zokwelapha ezingcono kakhulu (i-PIL)?

Uma welapha i-PIL, into ebaluleke kakhulu ukushintsha ukudla. Lesi yisikhali esiyinhloko ngokumelene ne-PIL. Cabanga ngakho njengokufaka 'ipulaki' emseleni wokudonsa amanzi ukuze umise ukuvuza kwezakhamzimba.

Odokotela abaningi banikeza ukudla okunamafutha aphansi namaprotheni amaningi.

Amafutha kunzima ukuwagaya. Ngakho-ke kunzima ukuthi isisu sengane yakho sivuvuke ukuze simunce amafutha kahle. Ngakho-ke ukudla kwakho okusha kungafaka uhlobo olukhethekile lwamafutha olubizwa ngokuthi 'ama-triglycerides aphakathi nendawo (ama-MCT).' Lawa (ama-MCT) uhlobo lwamafutha olumuncwa kalula ngumzimba. Futhi, ukwengeza amaprotheni amaningi ekudleni kwakho kungandisa inani lezakhamzimba umzimba wakho ozimuncayo.

Njengoba ezinye izakhamzimba zilahleka, udokotela angase futhi ancome izithako zamavithamini namaminerali ukuqinisekisa ukuthi umzimba wengane uthola lokho ekudingayo.

Ngaphezu kwalokho, udokotela angase futhi anikeze imithi efana nale ukusiza ngezici ezahlukene zesimo (i-PIL):

• Ama-diuretics (abizwa nangokuthi amaphilisi amanzi): Lawa asebenza ngokunciphisa inani loketshezi olwengeziwe oluqongelela emzimbeni ngenxa yokuvuza kwamaprotheni.
• Ama-Somatostatin analogues (njenge-octreotide): Le mithi isiza ekunciphiseni ukuvuza kwezinto ezivela ohlelweni lwe-lymphatic.

Ezinye izinketho zokwelapha:

• Ukuhlinzwa: Uma ezinye izindlela zokwelapha zingasizi, futhi zingavamile, odokotela bangase batuse ukuhlinzwa ukuze kususwe ingxenye egulayo yamathumbu engane yakho.
• Ezinye izindlela zokwelapha ezingaba khona: Ucwaningo ngalokhu luyaqhubeka. Imithi emisha eminingana, njenge -sirolimus, iyahlolwa i-PIL. Lokhu kungaba usizo kwezinye izimo, kodwa ayikasetshenziswa kabanzi.

Iyini iphrojekthi yesimo (se-PIL)?

Njengoba kushiwo ngaphambili, i-(PIL) ayisona isifo esingelapheki ngokuphelele. Kodwa-ke, amazinga amaprotheni egazini lengane kufanele akhuphuke zingakapheli amasonto ambalwa kusukela iqalile ukwelashwa. Kodwa-ke, ingane kuzodingeka idle ukudla okunamafutha amancane futhi ithathe izithasiselo zokudla okunempilo impilo yayo yonke.

Nakuba lokhu kuyinselele, uma kuphathwa kahle, ingane ingaphila impilo evamile. Into ebaluleke kakhulu ukulandela imiyalelo kadokotela nokunakekela ukudla kwengane.

Ingabe isimo (se-PIL) singavinjelwa?

Njengoba abacwaningi bengakazi ukuthi yini ebangela lesi simo (i-PIL), okwamanje ayikho indlela yokuvimbela lesi simo.

Ingane yami kufanele ibone nini udokotela?

Uma ubona ukuvuvukala emilenzeni, ezinyaweni zengane yakho, noma kunoma yiziphi izimpawu ze-PIL ezishiwo ngenhla, kungcono ukuyisa ingane yakho kudokotela ngokushesha. Uma isheshe yatholakala, ukwelashwa kungasheshe kuqale.

Yimiphi imibuzo okufanele ngiyibuze udokotela wengane yami?

Uma ingane yakho ine-PIL, ungase ube nemibuzo eminingi okufanele uyibuze udokotela wakho. Nazi ezinye zazo:

• Yikuphi ukudla okufanelekela kangcono lesi simo (i-PIL)?
• Yiziphi izithasiselo okufanele ngizinike ingane yami?
• Yini enye engingayenza ukuze ngiphathe kangcono izimpawu zengane yami?
• Ingabe lesi simo (se-PIL) sibucayi?
• Yiziphi izinkinga okufanele ngiziqaphele?

Ungesabi ukubuza le mibuzo. Xoxa nodokotela wakho nganoma yiziphi izinkinga onazo.

Okokugcina, izinto okufanele uzikhumbule (Umyalezo Wokuya Ekhaya)

Uma uqala ukuzwa izimpawu ze-Primary Intestinal Lymphangiectasia, kungaba nzima ngawe nodokotela bakho ukuqonda ukuthi kwenzekani. Kungaba yinto edidayo kakhulu futhi edidayo. Kodwa-ke, odokotela bakho bangasebenzisana nawe ukukusiza ukuthi uthole ukuthi yini ebangela lokhu.

Ngenhlanhla, ngokudla okunamafutha aphansi kanye nezithako zokudla okunempilo, izimpawu zengane yakho zingalawulwa ngokuhamba kwesikhathi. Buza udokotela wengane yakho ukuthi yini enye ongayenza ukusiza ingane yakho ilawule lesi simo. Uthando lwakho, ukwesekwa, kanye nokunaka kwakho kubaluleke kakhulu enganeni yakho phakathi nalolu hambo.

'I-lymphangiectasia yamathumbu eyinhloko, i-PIL, ukuvinjelwa kwe-lymphatic, izifo zesisu ezinganeni, ukuvuvukala kwemilenze, ukuntuleka kwamaprotheni, izifo zesistimu yokugaya ukudla