O, ngezinye izikhathi sizwa izinto ezinjengokuthi, 'isimila sobuchopho', 'Ngiphethwe yikhanda futhi ngizolihlola'. Kungenza inhliziyo yami iqhaqhazele uma ngizwa into efana naleyo. Kodwa ubuwazi, akuzona zonke izimila ezakha ebuchosheni eziwuhlobo olufanayo lomdlavuza oluyingozi. Kunezinye izimila ezikhula kancane, ezingenabungozi, okungukuthi, ezingezona umdlavuza. Namuhla sizokhuluma ngezinhlobo ezimbili ezinjalo, ezingavamile, kodwa ezifanele ukuzazi, zezimila zobuchopho. Lezi yi-gangliocytoma kanye ne-pineocytoma.
Yini i-Gangliocytoma ne-Pineocytoma?
Kalula nje, lezi zombili ziyizinhlobo zezimila zobuchopho ezingavamile kakhulu, ezingeyona ingozi (okungukuthi ezingezona ezomdlavuza - `ezingenobungozi`).
I-Gangliocytoma uhlobo lwesimila esithinta izingxenye zesimiso sakho sezinzwa esiyinhloko (esaziwa nangokuthi i-CNS).
Olunye uhlobo, i-pineocytoma, lukhula endlaleni ye-pineal, indlala encane etholakala ngaphakathi ebuchosheni bakho. Indlala ye-pineal yindlala esiza ukulawula ubuthongo bethu. Cabanga nje, le ndlala encane ibaluleke kakhulu ezintweni ezifana nokulala ebusuku nokuvuka ekuseni.
Zombili izinhlobo zezimila zikhula kancane . Yingakho ngezinye izikhathi kuthatha isikhathi ukuthi izimpawu zivele. Odokotela bavame ukuzelapha ngokuhlinzwa futhi ngezinye izikhathi ngokwelashwa ngemisebe.
Ubani onamathuba amaningi okuthuthukisa lezi zinhlobo zezimila zobuchopho?
Eqinisweni, uhlobo lwesimila esibizwa ngokuthi i-gangliocytoma lungakhula kubantu banoma yimuphi ubudala. Lokhu kusho ukuthi ngisho nengane encane noma umuntu omdala angaba sengozini. Kodwa-ke, sivame ukubonakala kakhulu kubantu abasha abaneminyaka ephakathi kweyi-10 nengama-30 .
Izimila ze-pineocytoma zivame ukuthinta abantu abadala, okusho abantu abaneminyaka ephakathi kuka-20 no-64. Isilinganiso seminyaka yokuxilongwa singaba yiminyaka engu-38.
Kukuziphi izingxenye zesimiso sethu sezinzwa esiyinhloko (i-CNS) lapho kuvela khona izimila ze-gangliocytoma?
Ama-gangliocytomas avame ukukhula ezingxenyeni zobuchopho bakho ezibizwa ngokuthi ama-temporal lobes . Lawa atholakala ngemuva kwezindlebe zakho. Lawa ma-temporal lobes asiza ukulawula izinto ezifana nenkumbulo yakho, ukuzwa, kanye nemizwa. Cabanga nje, ukhumbula isenzakalo esidala, ulalele ingoma bese uyijabulela, bese uzizwa ujabule noma udangele ngenxa yomsebenzi walezi zingxenye.
Akukhona lokho kuphela, lesi simila singakhula nasezindaweni ezilandelayo emzimbeni wakho:
- I-Brainstem: Lena yingxenye yobuchopho bakho efana nebhuloho exhumanisa ingxenye ephezulu yobuchopho bakho (ubuchopho), intambo yomgogodla, kanye ne-cerebellum. Ithumela izimpawu ezilawula imisebenzi ebalulekile njengokuphefumula kwakho kanye nokushaya kwenhliziyo.
- I-Cerebellum:Le ngxenye yobuchopho bakho, engemuva kwekhanda lakho, ilawula ibhalansi yakho, ukunyakaza, kanye nokubona. Cabanga ngakho, le ngxenye yobuchopho bakho yiyo ekugcina uqonde lapho uhamba, ikuvimbele ekuweni, futhi ikusize welule isandla sakho ukuze ubambe ibhola.
- Isitezi se-ventricle yesithathu: Lesi yisikhala esincane ngaphambili kobuchopho. Sivikela ubuchopho ekulimaleni futhi sisize ukuhambisa izakhamzimba kanye nemikhiqizo engcolile.
- Umgogodla: Lena yindlela eyinhloko ethwala izimpawu zemizwa zisuka ebuchosheni bakho ziye emzimbeni wakho futhi zisuka emzimbeni wakho ziye ebuchosheni bakho. Lezi zimpawu zemizwa yizo ezikwenza uzizwe izinto (ukushisa, ukubanda, ubuhlungu) futhi zinyakazise umzimba wakho.
Uyini umehluko phakathi kwe-pineal cyst ne-pineocytoma?
Lokhu futhi kuyinto engadida abantu abaningi. Cabanga ngakho, i-pineal cyst iyisikhwama esigcwele uketshezi noma umoya . Kufana ne-water blister. Lokhu kuvame ukutholakala ngengozi ngesikhathi sokuskena. Kodwa-ke, i-pineocytoma iyisimila esakhiwa yiqoqo elikhulu lamaseli angajwayelekile .
Ama-cyst e-pineal avame ukungakhuli, okusho ukuthi awavamile ukushintsha ngobukhulu. Nokho, ama-pineocytomas akhula kancane. Kodwa-ke, womabili ayizimo ezingengozi (ezingezona ezomdlavuza). Lokhu kusho ukuthi awawona umdlavuza.
Yiziphi izimpawu ezibangelwa yilezi zimo?
Esikhathini esiningi, ungase ungabi nazimpawu noma ngabe une-gangliocytoma. Ngezinye izikhathi, odokotela bathola lezi zimila ngengozi lapho benza izivivinyo zezithombe (njenge-MRI noma i-CT scan) zenkinga ethile.
Kodwa-ke, zombili izinhlobo zezimila, i-gangliocytoma kanye ne-pineocytoma, zingabangela izimo ezithile ezinezimpawu ezahlukene.
Izimpawu ezivamile ze-gangliocytoma
Lesi simila singabangela ukuthi ube nezimpawu ezifana nalezi:
- Izinguquko ekunyakazeni: Njengokulahlekelwa ukulawula imisipha. Isibonelo, ukuthuthumela, ukukhubazeka, ubuthakathaka. Cabanga nje, ngokuzumayo uthola kunzima ukubamba indebe, noma imilenze yakho izwa sengathi iyakhubeka lapho uhamba.
- Izinguquko ekuzweni: Umuzwa wokuba ndikindiki kwezinye izindawo, njengokuzwa okubuhlungu emlenzeni.
- Ubunzima bokukhuluma: Inkulumo engacacile, cishe njengokungathi awukwazi ukukhuluma. Awukwazi ukusho lokho ofuna ukukusho ngokucacile.
- Ukushintsha kombono: Umbono ungase ungabonakali, ubonakale sengathi ubona izingxenye ezimbili, futhi ngezinye izikhathi kungase kuzwakale sengathi ulahlekelwa ingxenye yombono wakho.
Ingabe i-gangliocytoma ingabangela izimo zezokwelapha ezingathi sína?
Yebo, lesi simila singabangela ezinye izimo zezokwelapha ezimbi kakhulu. Isibonelo:
- Izinkinga zesistimu ye-endocrine:Lezi yizimo ezenzeka lapho inani lama-hormone akhiqizwa yizindlala emzimbeni wakho landa noma lehla. Lokhu kungaphazamisa imisebenzi eminingi yomzimba wakho.
- Ukuquleka: Kungenzeka ukuthi uke wezwa ngalokhu, ukulahlekelwa yingqondo ngokuzumayo kanye nokuquleka. Lawa mathumba angabangela lesi simo ngokuvuselela ubuchopho.
- Ukwanda kwengcindezi ngaphakathi kobuchopho: Lokhu kungabangela ikhanda elibuhlungu, isicanucanu, ukuhlanza, kanye nokudideka. Kungase kuzwakale sengathi ikhanda lakho licindezelwa ngaphakathi.
- Isifo i-Lhermitte-Duclos (LDD): Lesi isimila esingavamile kakhulu, esingenangozi. Sikhula ku-cerebellum yakho. Ngezinye izikhathi sibizwa ngokuthi i-dysplastic gangliocytoma ye-cerebellum. Umuntu one-LDD angase abe nekhanda elibuhlungu, isicanucanu, uketshezi ebuchosheni (i-hydrocephalus), ubunzima bokuhamba nokulahlekelwa ibhalansi (i-ataxia), kanye nezinkinga zokubona. Abantu abane-LDD bangase babe nesimo sofuzo esibizwa ngokuthi i-Cowden syndrome, esibangela izimila zesikhumba kanye nengozi eyengeziwe yomdlavuza.
Izimpawu ezivamile zePineocytoma
I-Pineocytoma ingabangela uketshezi ukuqoqana ngaphakathi kobuchopho bakho, okubangela ukucindezeleka okukhulu. Lokhu kubizwa ngokuthi i-hydrocephalus . Uma une-hydrocephalus, ungase ube nezimpawu ezifana nalezi:
- Izinkinga zokulinganisela: Ukulahlekelwa ibhalansi ngenkathi uhamba, uzizwa sengathi uzowa.
- Izinkinga zokunyakaza kwamehlo (`i-Parinaud syndrome`): Ubunzima bokubheka phezulu, ikakhulukazi uma ubheka phambili. Ungase ungakwazi ukuhambisa amehlo womabili ngesikhathi esisodwa.
- Ikhanda elibuhlungu: Ungase ube nekhanda elibuhlungu elibi nelihlala njalo. Ngezinye izikhathi lobu buhlungu buba bubi nakakhulu uma uvuka ekuseni.
- Izinkinga zenkumbulo: Ukukhohlwa izinto, ukuba nobunzima bokukhumbula izinto ezintsha.
- Isicanucanu nokuhlanza: Lokhu kungaba kubi kakhulu, ikakhulukazi ekuseni.
- Izinkinga zokulala: Ukungakwazi ukulala, noma ukulala kakhulu. Lokhu kungenxa yokuthi i-pineal gland ihilelekile ekulaleni.
- Ubunzima bokuhamba: Kuzwakala sengathi awukwazi ukuhamba, imilenze yakho iyaxega.
Iyini imbangela yangempela yalezi zimila zobuchopho?
Njengezinye izimila eziningi, ama-gangliocytoma nama-pineocytoma akhula lapho kuba noshintsho emiyalweni yezakhi zofuzo zamaseli ethu. Cabanga ngale ndlela: amaseli emzimbeni wethu afana nezimboni ezincane. Athola imiyalelo yokusebenza. Lapho le miyalelo ishintsha, amaseli aqala ukuhlukana ngokungalawuleki. Yilapho-ke akha khona isimila.
Kodwa-ke, abacwaningi abakakazi kahle ukuthi yini "i-trigger" eqondile ebangela lezi zinguquko. Okusho ukuthi, ayikho impendulo ecacile yokuthi kungani la maseli eqala ukuziphatha ngale ndlela ngokuzumayo.
Kodwa-ke, bathole ukuthi i-Cowden syndrome, ehlotshaniswa nesifo se-Lhermitte-Duclos, ibangelwa ukuguquka kwezakhi zofuzo okuthiwa i-PTEN. Le zakhi zofuzo ze-PTEN yenza iphrotheni esiza ukulawula indlela amangqamuzana akhula futhi ahlukana ngayo. Ngakho-ke, lapho izakhi zofuzo ze-PTEN ziguquguquka, ukukhiqizwa kwaleyo phrotheni kuyayeka, futhi amangqamuzana aqala ukukhula ngendlela engalawuleki.
Odokotela bawaxilonga kanjani la mathumba? (Ukuxilongwa)
Uma unalezi zimpawu, udokotela uzoqala akubuze ngezimpawu zakho nokuthi ngabe kukhona yini emndenini wakho oke waba nalezi zimo ('umlando wezempilo yomndeni'). Bese, bazokuhlola. Bazokwenza 'ukuhlolwa kwe-neurologic', ikakhulukazi ukuhlolwa kwesistimu yakho yezinzwa . Lokhu kuzobheka okulandelayo:
- Indlela amehlo akho nomlomo wakho ohamba ngayo.
- Amandla emisipha.
- Ukuzindla (njengokuthi umlenze uzogxuma yini uma ushaywa edolweni ngesando esincane)
Ngaphezu kwalokho, udokotela angenza nalezi zivivinyo:
- I-Magnetic Resonance Imaging (MRI): Lokhu kuhlolwa okungenabuhlungu. Kusebenzisa i-magnet enkulu, amaza omsakazo, kanye nekhompyutha ukwenza izithombe ezicacile zezitho nezakhiwo ezingaphakathi komzimba wakho. Kusetshenziselwa ukubona ukuthi kukhona yini izimila, ukuthi zikhulu kangakanani, nokuthi zikuphi.
- Iskeni se-CT (computed tomography): Lokhu kusebenzisa uchungechunge lwe-X-ray kanye nekhompyutha ukudala izithombe ezinezici ezintathu zezicubu zakho ezithambile namathambo. Njenge-MRI, isetshenziselwa ukuthola nokuhlola izimila.
- Ukuhlolwa kwegazi: Lokhu kungenziwa ukuze kubonakale ukuthi unamazinga angavamile yini e-melatonin egazini lakho (ikakhulukazi ezimweni ze-pineocytoma, njengoba ihlobene ne-pineal gland).
- Ukubhoboza umgogodla (ukubhoboza i-lumbar): Lokhu kuhilela ukuthatha isampula yoketshezi lwe-cerebrospinal (CSF) oluzungeze ubuchopho bakho kanye nomgogodla bese uluhlola ukuthi alunawo yini amaseli esimila.
- I-Biopsy: Lokhu kuhilela ukuthatha isampula encane yamaseli avela ku-tumor bese uwahlola elabhorethri ukuze kutholakale ukuthi uhlobo luni lwe-tumor. Odokotela bavame ukusebenzisa amasu angangenisi kakhulu njenge-endoscopy noma i-stereotactic needle biopsy.
Iphathwa kanjani i-gangliocytoma?
Cabanga ukuthi une-gangliocytoma, kodwa awunazo izimpawu. Ngaleso sikhathi, udokotela wakho uzokutshela ukuthi, "Ake sibheke." Okusho ukuthi, uzokutshela ukuthi uze uzohlolwa njalo ukuze abone ukuthi unezimpawu ezintsha, noma ukuthi isimila sishintshile noma sikhule kangakanani. Angase futhi enze izinto ezifana nokuhlolwa kwezithombe nokuhlolwa kwegazi.
Kodwa,Uma udinga ukwelashwa, odokotela bavame ukwenza ukuhlinzwa kobuchopho ukuze kususwe isimila. Ngenhlanhla, ama-gangliocytomas cishe awaphinde abuye ngemva kwalolu hlobo lokususwa.
Iphathwa kanjani i-Pineocytoma?
Kwezinye izimo ze-pineocytoma, odokotela bangase benze ukuhlinzwa kobuchopho ukuze kususwe yonke noma ingxenye yesimila. Bangase futhi basebenzise ukwelashwa okubizwa ngokuthi ukwelashwa ngemisebe .
Ngesikhathi sokuhlinzwa, uma une-hydrocephalus (isimo lapho ubuchopho bugcwele uketshezi futhi bunomfutho ophezulu), odokotela bangafaka ipayipi elincane lepulasitiki elibizwa ngokuthi i-shunt ebuchosheni bakho. Le shunt isusa uketshezi lwe-cerebrospinal olungeziwe ebuchosheni bakho, inciphise umfutho ngaphakathi kwekhanda lakho. Lokhu kunganciphisa kakhulu izimpawu zakho.
Ingabe ikhona indlela esingavimbela ngayo ukwakheka kwalezi zimila zobuchopho?
Nokho, akukho lutho ongakwenza ukuvimbela la mathumba ukuthi akheke . Njengoba kushiwo ngaphambili, akhiwa lapho amangqamuzana eshintshashintsha futhi eqala ukuhlukana ngokungalawuleki. Ngaphandle kokuthi kuhlobene ne-Cowden syndrome, abacwaningi abasazi kahle ukuthi yini ebangela lokhu kuguquka. I-Cowden syndrome ibangelwa ushintsho ku-gene elawula ukukhula kwamangqamuzana. Ngakho-ke, lokhu akuyona into esingayilawula.
Kwenzekani uma unesimila esinjengalesi? Yini ongayilindela?
Ezimweni eziningi, ngemva kokuhlinzwa ukuze kususwe lesi simila, amathuba okuthi sibuye aphansi kakhulu . Lokho kuyaduduza ngempela, akunjalo? Lokho kusho ukuthi ungaphila impilo evamile ngemva kokwelashwa. Kodwa-ke, njengoba udokotela esho, kubalulekile ukuya kokuhlolwa 'kokulandelela'.
Kufanele ngimbone nini udokotela?
Kuye ngesimo sakho, udokotela wakho angase ahlele ama-aphoyintimenti okulandelela njalo ukuze aqaphe impilo yakho iyonke. Uma uhlinzwe ukuze kususwe isimila, bangase batuse nokuhlolwa kwezithombe ukuze kuhlolwe ukuthi isimila sesibuyile yini noma ukuthi isimila esisha sesivele sakhiwe.
Into ebaluleke kakhulu ukubona udokotela nganoma yisiphi isikhathi uma uzwa izimpawu zesimila sangaphambilini, noma uma ubona noma yiziphi izinguquko ezintsha nezisolisayo emzimbeni wakho . Ungakuhlehlisi, kulungile? Ngoba uma usheshe uqaphele lesi simo, kuba lula ukwelapha.
Izinto ezibaluleke kakhulu okufanele uzikhumbule kulokho esixoxe ngakho (Umyalezo Wokuya Ekhaya)
I-Gangliocytoma kanye ne-pineocytoma yizimila ezimbili zobuchopho ezingavamile kakhulu, ezikhula kancane, ezingenabungozi ezikhula ohlelweni lwakho lwezinzwa oluphakathi (i-CNS) kanye ne-pineal gland.
Nakuba lezi zingewona umdlavuza, zingadala izimo zezokwelapha ezahlukahlukene ezingathinta impilo yakho. Kuye ngohlobo lwesimila onaso, odokotela bangase baselaphe ngokuhlinzwa noma ngokwelashwa ngemisebe. Lawa mathumba cishe awakwazi ukubuya ngemva kokususwa ngokuhlinzwa.
Uma unesimila esingesihle njengalesi, khuluma nodokotela wakho mayelana nezinketho zakho zokwelashwa, ukuthi yini ongayilindela ngemva kokwelashwa, nokuthi yini okudingeka ukwazi ngokuphila nalolu hlobo lwesimila. Ungagodli lutho, lalela konke . Kuzokunika amandla. Ungesabi, into ebaluleke kakhulu ukuqaphela lezi zinto nokulandela imiyalelo kadokotela wakho.
Izimila zobuchopho, i-gangliocytoma, i-pineocytoma, i-CNS, i-pineal gland, izimpawu, ukwelashwa











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