Wake wazibuza ukuthi kuzokwenzekani uma amakamelo amancane angaphakathi kwenhliziyo yakho eyeka ukusebenza kahle? Ngezinye izikhathi, imisipha yenhliziyo yethu iyaqina kancane futhi ayikwazi ukugcwala igazi kahle. Yilapho-ke lapho singathuthukisa khona lokho esizokhuluma ngakho, i-cardiomyopathy evimbelayo. Ungakhathazeki, masikwenze kube lula.
Kuyini i-Restrictive Cardiomyopathy?
Kalula nje, lesi yisimo esihilela imisipha yenhliziyo. Imisipha emakamelweni amabili angaphansi kwenhliziyo yethu, abizwa ngokuthi ama-ventricles , iyaqina. Akufani nebhande lerabha elibuyela endaweni yalo uma ulinweba, kodwa imisipha ayiguquguquki kahle. Lokhu kusho ukuthi la makamelo awanandawo eyanele yokugcwala igazi kahle. Uma lokhu kwenzeka, ukugeleza kwegazi enhliziyweni kuyaphazamiseka.
Kunezinye amagama alokhu, futhi ngezinye izikhathi odokotela bangasebenzisa la magama:
- `I-cardiomyopathy evimbelayo ye-Idiopathic`
- I-cardiomyopathy engene ngaphakathi (isifo semisipha yenhliziyo esibangelwa ukungena kwezinye izinto emisipheni)
Ubani onamathuba amaningi okuthola lesi sifo? Sivame kangakanani?
Nakuba noma ubani angaba nalesi simo, `(Restrictive Cardiomyopathy)`, sivame kakhulu kwabanye abantu ngenxa yezimo ezithile eziyisisekelo. Isibonelo, `(Sarcoidosis)` (engabangela futhi `(Restrictive Cardiomyopathy)`) sivame kakhulu kwabesifazane bezinhlanga ezithile.
I-cardiomyopathy yisifo esivame kakhulu. Sithinta cishe umuntu oyedwa kwabangu-500. Kodwa-ke, lolu hlobo lwe-cardiomyopathy luyivelakancane kakhulu . Lubangela cishe u-5% wazo zonke izimo ze-cardiomyopathy. Ngakho-ke, lokhu kuyinto engavamile ukuzwakala ngayo, kodwa kufanelekile ukuyazi.
I-cardiomyopathy ekhawulelwe iyithinta kanjani inhliziyo?
Inhliziyo yethu iyisitho esimangalisayo. Inamakamelo amane, akhiwe kakhulu ngemisipha. La makamelo aphompa igazi ngokufinyela. Amakamelo amabili aphezulu abizwa ngokuthi i-'Atria' , kanti amakamelo amabili aphansi abizwa ngokuthi i-'Ventricles' .
Okwenzekayo kulesi simo `(Restrictive Cardiomyopathy)` ukuthi imisipha yamagumbi angaphansi (`Ventricles`) iyaqina futhi ilahlekelwe ukunwebeka kwayo. Khona-ke lawo magumbi awakwazi ukugcwala igazi ngokuphelele. Cabanga ngakho njengokufutha ibhaluni, uma ibhaluni lingafuthwanga kahle, lizobamba umoya omncane kuphela. Yilokho okwenzekayo nalapha. Lokhu kubangela ukuvinjelwa kuyo yonke inqubo yokugeleza kwegazi enhliziyweni.
Ziyini izimpawu? Ingabe zingatholakala kusenesikhathi?
Ngezinye izikhathi kungase kungabi khona zimpawu , ikakhulukazi ezigabeni zokuqala. Kodwa njengoba lesi sifo siqhubeka, ukwehluleka kwenhliziyo kungenzeka.Izimpawu ezifana nezomkhuhlane ziqala ukuvela. Nazi ezinye zalezo zimpawu:
- Ukugcwala kwesisu noma isicanucanu.
- Ubuhlungu besifuba (obungenzeka lapho uphumule noma ngesikhathi sokuzivocavoca).
- Ukuzizwa unesizungu noma ukuphelelwa yithemba.
- Ukuvuvukala kwemilenze nezinyawo (`Edema`).
- Ukuzizwa ukhathele ngaso sonke isikhathi (`Ukukhathala`).
- Ukuzwa ukushaya kwenhliziyo okungavamile (`Ukushaya kwenhliziyo okungavamile`).
- Ubunzima bokuphefumula (i-Dyspnea), ngezinye izikhathi ngisho nangomzamo omncane.
- Ukukhuluphala okungazelelwe.
Okubalulekile: Uma unesinye noma ngaphezulu salezi zimpawu, ungacabangi ukuthi 'kuyi-Restrictive Cardiomyopathy'. Kodwa-ke, kungcono ukubona udokotela ukuze uthole iseluleko.
Kungani lesi simo senzeka? Yiziphi izizathu?
Kunezimbangela eziningana eziyinhloko ze-cardiomyopathy ekhawulelwe. Okusho ukuthi, ingabangelwa ezinye izimo zezokwelapha.
- `I-Amyloidosis` : Lokhu kwenzeka lapho iphrotheni ifakwa emisipheni yenhliziyo.
- Izifo zezicubu ezixhumeneyo : Izifo ezithinta izicubu ezahlukene zomzimba.
- I-Hemochromatosis (ukugcwala kwensimbi) : Ukuqongelela insimbi ngokweqile emzimbeni.
- I-Sarcoidosis : Ukwakheka kwamaqoqo amancane amaseli abizwa ngokuthi ama-granuloma ezithweni ezahlukene zomzimba.
Ngaphezu kwalokho, kungenzeka ukuthi lesi simo singenzeka ngemva kokwelashwa komdlavuza:
- Ukwelashwa ngamakhemikhali
- Ukwelashwa ngemisebe
Odokotela basithola kanjani lesi sifo ngokunembile? (Ukuxilongwa)
Uma uya kudokotela, uzoqala ngokukubuza ngezimpawu zakho, ahlole umzimba, alalele ukushaya kwenhliziyo yakho, futhi ahlole umfutho wegazi lakho.
Ngemuva kwalokho, ukuqinisekisa ukuxilongwa nokuhlola ukuthi amakamelo enhliziyo (ama-ventricle) asebenza kahle yini, kwenziwa i- echocardiogram (ukuskena kwenhliziyo). Lokhu kungahlola izinto ezifana nokusebenza kwenhliziyo kanye nobukhulu bemisipha.
Udokotela wakho angase futhi ancome ezinye izivivinyo eziningana ukuze ahlole ezinye izimo eziyisisekelo ezingase zibangele i-Restrictive Cardiomyopathy. Lezi zifaka:
- Ukuhlolwa kwegazi nomchamo.
- I-X-ray yesifuba.
- Ukuskena kwenhliziyo okubizwa ngokuthi ‘CT’ (‘Cardiac CT scan’).
- Ukuhlolwa kokucindezeleka kokuzivocavoca.
- I-MRI yenhliziyo.
- Ukuskena kwe-PET yenhliziyo.
- Ukufakwa kwe-catheter kwenhliziyo kwesokudla.
- I-biopsy ye-myocardial - Lokhu kuhilela ukuthatha isampula encane yemisipha yenhliziyo bese uyihlola.
- Ukuhlolwa kofuzo.
Ingabe kukhona ukwelashwa? Kuphathwa kanjani?
Ngeshwa, lesi simo, esibizwa ngokuthi 'i-Restrictive Cardiomyopathy', sithinta lesi simo ngqo.Akukho ikhambi okwamanje. Kodwa-ke, odokotela bangakwazi ukwelapha imbangela eyinhloko nokulawula izimpawu.
Uma unezimpawu ezihlobene nokwehluleka kwenhliziyo, udokotela wakho angase ancome izindlela zokwelapha ezilandelayo:
- Ama-Corticosteroids (imithi yohlobo lwe-steroid) uma une-sarcoidosis.
- Imithi yokwehlisa uketshezi emzimbeni (i- diuretics ) ebangela ukwanda kokuchama.
- Imithi yokwelapha ukungalingani kwe-cardiogram yenhliziyo (isib. `Ama-Antiarrhythmics`, `ama-Beta-blockers` noma `ama-Calcium channel blockers`).
- I-phlebotomy yokwelapha iyindlela yokwelapha abantu abane-hemochromatosis (ukugcwala kwensimbi).
- Imithi ethile yezinhlobo ezithile ze-`(Amyloidosis)`.
Abanye abantu bangagcina bedinga ukuhlinzwa kokufakelwa inhliziyo uma isifo siba sibi kakhulu. Bangathunyelwa futhi ukuze bathole ukunakekelwa kokunciphisa ubuhlungu ukuze balawule izimpawu futhi balondoloze izinga lempilo elihle.
Yiziphi izinkinga ezingaba khona ngenxa yalesi sifo?
Ezinye izinkinga eziningana zingavela ngenxa ye-'Restrictive Cardiomyopathy'. Lezi yizi:
- Ukushaya kwenhliziyo okungajwayelekile : Ukushaya kwenhliziyo okungajwayelekile.
- Ukwehluleka kwenhliziyo : Inhliziyo ayikwazi ukupompa igazi elanele emzimbeni.
- Amahlule egazi kanye nesifo sohlangothi (`Thromboembolism` noma `Stroke`) : Amahlule egazi angabangela isifo sohlangothi.
Yini esingayenza ukuze sinciphise ingozi?
Lesi simo, esithi "Restrictive Cardiomyopathy," sisho ukuthi inhliziyo yakho kufanele isebenze kanzima ukupompa igazi. Ngakho-ke, kubalulekile ukukhuluma nodokotela wakho ngalokho ongakwenza ukuze unciphise umthwalo womsebenzi enhliziyweni yakho.
Nakuba kunzima ukuvimbela izimo zezokwelapha eziyisisekelo ezibangela i-Restrictive Cardiomyopathy, ungenza okulandelayo ukuze ugcine inhliziyo yakho iphilile:
- Lawula umfutho wegazi lakho .
- Gcina isisindo esinempilo .
- Nciphisa ukucindezeleka .
Yini okufanele uyilindele uma uphila nalesi sifo?
I-Restrictive Cardiomyopathy iyisimo esiyinkimbinkimbi, ngakho-ke kubalulekile ukukhuluma nodokotela wakho njalo ngezinyathelo ongazithatha ukuze ugcine inhliziyo yakho iphilile.
Isikhathi ongasiphila nalesi sifo siyahlukahluka kuye ngomuntu nomuntu. Udokotela wakho uzochazela wena nomndeni wakho ukuthi lesi sifo sizoqhubeka kanjani nokuthi yini ongayilindela.
Kufanele ngizinakekele kanjani? (Ukuzinakekela)
Into ebaluleke kakhulu ukulandela imiyalelo kadokotela wakho ngqo futhi uphuze yonke imithi oyinikezwe udokotela ngesikhathi. Ngaphezu kwalokho, udokotela wakho angakutshela nokuthi wenze izinguquko endleleni yokuphila ezifana nalezi:
- Ukudla okunempilo okunosawoti omncane (okulawulwa yi-sodium)Okuzo thathwa.
- Ukuzivocavoca umzimba (kuphela njengoba kuqondiswe udokotela wakho).
Kunini lapho kufanele ufune khona iseluleko sezokwelapha ngokushesha?
Uma uzizwa sengathi izimpawu zakho zokwehluleka kwenhliziyo ziya ziba zimbi kakhulu, noma uma uba nezimpawu ezintsha, shayela udokotela wakho ngokushesha .
Futhi, uma kwenzeka isimo esiphuthumayo esinjengalesi, iya esibhedlela ngokushesha (uma useSri Lanka, shayela inombolo ephuthumayo efana no-1990):
- Uma unezinhlungu zesifuba ezinzima .
- Uma uquleka .
- Uma ngokuzumayo uba nobunzima obukhulu bokuphefumula .
Khumbula: Inhliziyo iyisitho esibaluleke kakhulu empilweni yethu, ngakho-ke kubaluleke kakhulu ukuyinakekela.
Umlayezo Wokuya Nawe Ekhaya
Kulungile, nansi izinto ezilula okufanele uzikhumbule mayelana ne-`(Restrictive Cardiomyopathy)` esikhulume ngayo:
- Okwenzekayo kulokhu ukuthi imisipha emakamelweni angaphansi (ama-ventricle) enhliziyo iyaqina futhi ilahlekelwe ukuguquguquka kwayo .
- Ngakho-ke, lawo maseli awakwazi ukugcwala igazi kahle .
- Ngemuva kwalokho inhliziyo kufanele isebenze kanzima ukupompa igazi liye emzimbeni, okungabangela "ukwehluleka kwenhliziyo".
- Nakuba kungekho ikhambi eliqondile lalokhu, kulawulwa ngokwelapha imbangela eyinhloko nokulawula izimpawu .
- Uma unemibuzo noma ukungabaza ngalokhu, ungesabi ukukhuluma nodokotela wakho .
Ngikufisela impilo enhle!
I- Cardiomyopathy Evinjelwe, isifo senhliziyo, isifo semisipha yenhliziyo, ukuphelelwa umoya, ubuhlungu besifuba, ukuhlaselwa yinhliziyo, ukwelashwa kwezokwelapha











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