Wake waphawula ibala elibomvu-nsundu emzimbeni wengane yakho noma wakho? Mhlawumbe umane wayithinta kancane ibala ngomunwe wakho, kwathi kungazelelwe ibala laphenduka laba bomvu, laqala ukulunywa, kwavela iqhubu elincane phezulu. Uma lokhu kujwayelekile kuwe, kubaluleke kakhulu ukuqaphela lesi simo esikhuluma ngaso namuhla.
Kalula nje, iyini i-Urticaria Pigmentosa?
I-Urticaria Pigmentosa uhlobo lwezikhumba ezenzeka esikhumbeni. Ivame ukubonakala ezinganeni ezincane nakubantu abadala abasebasha. Empeleni uhlobo lwesimo esibizwa ngokuthi 'i-mastocytosis'.
Manje ungase uzibuze ukuthi iyini i-'mastocytosis'. Kulula kakhulu. "amaseli e-mast" awuhlobo olukhethekile lweseli ohlelweni lokuzivikela lomzimba wethu. Afana nonogada bomzimba. Uma ngesizathu esithile lawa maseli e-mast eqoqana ngokweqile endaweni eyodwa yesikhumba, siwabiza ngokuthi i-Urticaria Pigmentosa. Kodwa-ke, lawa maseli e-mast angaqoqana hhayi esikhumbeni kuphela, kodwa ngezinye izikhathi nakwezinye izitho ezifana namathambo namathumbu. Bese kuba yisimo esibizwa ngokuthi i-"systemic mastocytosis". Kodwa ungakhathazeki, isikhathi esiningi, i-Urticaria Pigmentosa ezinganeni ikhawulelwe esikhumbeni.
Kulesi sifo, uma kuvela ibala elinsundu esikhumbeni, liba bomvu, livuvuke, lilume, futhi liphakame sengathi lishayiswe yimoto. Ngokwezokwelapha, lesi sibonakaliso sibizwa ngokuthi "uphawu lukaDarier."
Kungani kwenzeka into efana nale?
Isizathu esiyinhloko salokhu "amaseli e-mast" esikhulume ngawo ngaphambili. Lawa uhlobo lwamaseli amhlophe egazi akhiqizwa emnkantsheni wethu wamathambo. Lawa maseli atholakala kuyo yonke imizimba yethu, ikakhulukazi lapho sihlangana khona nomhlaba wangaphandle, njengesikhumba, amaphaphu, namathumbu. Uma into efana negciwane ingena emzimbeni, lawa maseli e-mast akhipha ikhemikhali ebizwa ngokuthi "i-histamine" ukusiza ekuvikeleni umzimba.
I-Urticaria Pigmentosa ibangelwa ukuguquka kwezakhi zofuzo okubangela ukuthi la maseli e-mast aqoqeke ngokweqile esikhumbeni. Lolu shintsho lwezakhi zofuzo luvame ukwenzeka ingane isesesibelethweni. Kodwa-ke, akuyona into ezuzwa ngabazali ezinganeni . Imbangela eqondile yalolu guquko ayikatholakali.
Uma abantu abadala bethola lesi simo, singaba sibi kakhulu. Sibizwa ngokuthi 'indolent systemic mastocytosis'. Kulesi simo, amaseli e-mast aqoqana ezindaweni ezifana nomnkantsha wethambo ngaphezu kwesikhumba. Akuvamile kakhulu, lesi simo singaba yisimo somdlavuza esibizwa ngokuthi 'i-mast cell leukemia'. Kodwa futhi, lezi yizinto ezingavamile kakhulu . Ama-99% e-Urticaria Pigmentosa ayenzeka ezinganeni awabi mabi kangako.
Ziyini izimpawu zalesi sifo?
Uphawu oluyinhloko nolusobala kakhulu `uphawu lukaDarier' esikhulume ngalo. Okusho ukuthi, amabala ansundu aba bomvu futhi alume uma ehlikihlwa. Ngaphezu kwalokho, abanye abantu bangase babe nalezi zimpawu ezilandelayo.
| Isibonakaliso | Incazelo elula |
|---|---|
| Ukushaya kwenhliziyo | Isilinganiso senhliziyo siyanda njengokungathi uzizwa wesaba. |
| Uhudo (ubuhlungu besisu) | Kungase kubangelwe ukusebenza kweseli le-mast ohlelweni lokugaya ukudla. |
| Ukuhlanza | Ukubomvu okungazelelwe kobuso nomzimba ongaphezulu. |
| Ubunzima bokuphefumula (Ukuphefumula kanzima) | Umsindo 'woshizi-ushizi' lapho uphefumula, ofana nowabantu abane-asthma. |
| Ukuquleka | Ukulahlekelwa ukwazi ngenxa yokwehla ngokuzumayo komfutho wegazi. |
| Ikhanda elibuhlungu | Ikhanda elibuhlungu. |
Iziguli ezingaphezu kuka-75% ze-Urticaria Pigmentosa ziyizingane ezingaphansi kweminyaka eyi-10. Ezinganeni eziningi, lesi simo sikhawulelwe esikhumbeni futhi siyathuthuka njengoba zikhula.
Udokotela uhlonza kanjani lokhu?
Ezimweni eziningi, udokotela wakho angasithola kalula lesi simo ngokubheka amabala esikhumbeni sakho nokuhlola uphawu lukaDarier. Azikho ezinye izivivinyo ezidingekayo.
Kodwa-ke, uma kukhona ukungabaza ngokuthi lesi simo asigcini nje esikhumbeni kodwa sithinte nezinye izingxenye zomzimba, udokotela angase ancome ukuhlolwa okulandelayo.
- Ukuhlolwa kwegazi (`Inani legazi`): Funda ngezinhlobo ezahlukene kanye namanani amaseli egazini.
- Ukuhlolwa kwe-serum tryptase: Kuhlola ukuba khona kwe-enzyme egazini ekhishwa amaseli e-mast.
- Ukuskena kobuningi bamathambo: Bona ukuthi aqine kangakanani amathambo akho.
- Ukuhlolwa komnkantsha: Kuhlola ukuthi umnkantsha uyawakhiqiza yini amaseli anempilo.
Izindlela zokwelapha kanye nendlela yokulawula lesi sifo
Izindaba ezinhle ukuthi ezinganeni eziningi, i-Urticaria Pigmentosa izozixazulula yodwa njengoba zikhula . Akukho ukwelashwa okuqondile kokuvimbela ukwakheka kwamabala amasha. Amabala akhona angathatha iminyaka ukuthi aphele.
Uma nje lesi simo sikhawulelwe esikhumbeni, ngokuvamile akukho ukwelashwa okukhulu okudingekayo. Udokotela wakho angase ancome okulandelayo ukusiza ekulawuleni izimpawu zakho:
- Ama-antihistamine omlomo: Lawula ukulunywa nokuvuvukala.
- Okhilimu be-corticosteroid: Faka ezindaweni ezilumayo.
- I-Cromolyn sodium: Umuthi onikezwa ukwelapha izimpawu ezifana nokuhlanza kanye nohudo.
- I-EpiPen: Idivayisi enikezwa abantu abanokusabela okukhulu kokungezwani komzimba (ukusabela kwe-anaphylactic) ukuze bayisebenzise esimweni esiphuthumayo. Akuwona wonke umuntu oyidingayo.
Izinto okufanele uzigweme ngokukhethekile
Into ebaluleke kakhulu kulesi sifo ukugwema izinto ezibangela izimpawu zibe zimbi kakhulu, okungukuthi, izinto ezibangela ukuba amabala alume futhi abe bomvu.
| Imithi okufanele uyigweme | Ezinye izinto okufanele uzigweme |
|---|---|
| I-aspirini | Ukuzivocavoca (ikakhulukazi okunzima) |
| Utshwala | Ukuhlikihla isikhumba ngamandla ngamathawula |
| Izibulala-zinhlungu ezifana ne-morphine ne-codeine (`Ama-Opiates`) | Ukugeza emanzini ashisayo |
| I-Thiamine (i-Vitamin B1) | Iziphuzo ezishisayo |
| I-Quinine (`i-Quinine` - umuthi kamalaleveva) | Ukuchayeka elangeni ngokweqile |
| I-Dextromethorphan (umuthi wokukhwehlela) | Ukuchayeka emakhazeni amakhulu |
| Eminye imithi yokubulala izinzwa kanye nodayi be-X-ray | Ukudla okubabayo, okushisayo |
Okubalulekile: Uma wena noma ingane yakho kudingeka nithathe imithi yesinye isimo, qiniseka ukuthi wazisa udokotela wakho nge-Urticaria Pigmentosa.
Ingabe izinkinga zingaba khona?
Akuvamile kakhulu, lesi simo singaqhubekela ku-'systemic mastocytosis'. Abantu abanjalo basengozini enkulu yokusabela okukhulu kwe-allergy okubizwa ngokuthi 'i-anaphylactic shock', okungaba yingozi empilweni. Uma uhlangabezana nezimpawu ezifana nobunzima bokuphefumula nokulahlekelwa ukwazi , kufanele uye ngokushesha emnyangweni wezimo eziphuthumayo wesibhedlela (ETU) .
Ezinye izinkinga ze-mastocytosis yesistimu zifaka:
- I-Osteoporosis: Ubuthakathaka bamathambo.
- I-Cytopenia: Ukwehla kokukhiqizwa kwamaseli egazi emzimbeni.
- Izinkinga zesibindi.
- Umdlavuza (ongavamile kakhulu).
Futhi, lezi yizinkinga ezingavamile kakhulu. Zingavamile kakhulu ezinganeni ezine-Urticaria Pigmentosa.
Umlayezo Wokuya Nawe Ekhaya
- I-Urticaria Pigmentosa yisifo sesikhumba esithinta kakhulu izingane. Asithelelani noma asizuzwe njengefa kubazali.
- Uphawu oluyinhloko ukuthi uma ibala elinsundu lihlikihlwa, liba bomvu, livuvuke, futhi lilume (`uphawu lukaDarier`).
- Ungesabi ngokungadingekile, njengoba lesi simo sizoba ngcono ngokwaso ezinganeni eziningi njengoba zikhula.
- Indlela engcono kakhulu yokuphatha ukuyeka ukudla, imithi, kanye nemisebenzi ekhulisa izimpawu.
- Uma wena noma ingane yakho ninayo noma iyiphi yalezi zimpawu, qiniseka ukuthi ubona udokotela ukuze uthole ukuxilongwa okunembile kanye neseluleko esidingekayo.
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