Wake wambona umntwana wakho egxumagxuma ngokuzumayo, sengathi ushaywe umbani? Izingalo nemilenze yakhe ivele igoqeke, noma iziphonsa emuva. Ngisho noma lokhu kuqhubeka imizuzwana embalwa kuphela, uma kwenzeka izikhathi eziningana zilandelana, kungaba yinto eyesabekayo kunoma yimuphi umzali oyibonayo. Sizokhuluma ngesimo esesabekayo kakhulu, kodwa kubaluleke kakhulu ukusiqaphela ngokushesha. Leso yi-West Syndrome.
Kalula nje, iyini i-West Syndrome?
I-West Syndrome uhlobo olungavamile lwesifo sokuwa oluthinta izingane ezincane, ikakhulukazi ezingaphansi konyaka owodwa ubudala . Iqanjwe ngodokotela owasithola okokuqala.
Lokhu kunamagama amaningana phakathi kodokotela. Ungase uzwe igama elithi `Infantile Spasms (IS)`. Lokho kusho ukuthi ``baby spasms.'' Kubizwa nangokuthi ``Epileptic Spasms.'' Nakuba kunamagama amaningi, wonke abhekisela esimweni sezokwelapha esifanayo.
Ziyini izimpawu zalesi simo?
Isici esiyinhloko salokhu ukugxumagxuma okukhulunywe ngakho ngaphambilini. Lokhu kubizwa ngokuthi 'ama-spasms'. La ma-jerk anezici eziningana ezikhethekile:
- Indlela okufika ngayo ukuminyana: Ingane ivele igobe phambili ngokuzumayo (njengalapho ihlushwa yisisu) noma ijikijele emuva. Izingalo nemilenze kuyaqina futhi kudikize ngokuzumayo.
- Isikhathi: Ukushaya okukodwa kuthatha imizuzwana embalwa kuphela.
- Amaqoqo: Lokhu kufinyela akufiki kanye bese kuyama. Kuza ngendlela eqhubekayo, ehlanganisiwe . Ukufinyela okukodwa kulandelwa okunye, bese kuba okunye, bese kuba okunye, kuze kube yi-150 eqoqweni. Kukhona izingane ezineziqoqo ezinjalo ezingafika ku-60 ngosuku.
- Isikhathi: Ngokuvamile ungabona lokhu kunyakaza ngokushesha nje lapho umntwana evuka ebuthongweni.
Ngaphezu kwalokhu kuthuthumela, ezinye izimpawu zingase zibonakale.
| Isibonakaliso | Incazelo |
|---|---|
| Ukukhala/ukuthukuthela njalo (Ukucasuka) | Ingane ikhala njalo ngaphandle kwesizathu futhi kunzima ukuyiduduza. |
| Ukulahlekelwa yisifiso sokudla | Nciphisa noma wenqabe ukuphuza ubisi. |
| Izinguquko zokulala | Ukulala kancane ebusuku, ukulala kakhulu emini. |
| Ukuma noma ukuhlehla kokukhula | Lesi yisici esibaluleke kakhulu. Umntwana, owayevame ukwenza izinto ezifana nokumomotheka, ukudlala, nokuqaphela unina, kancane kancane uyeka ukwenza lezo zinto. Uyakhohlwa izinto azifunda ngaphambilini. |
Kungani lokhu kwenzeka ezinganeni?
I-West Syndrome iyisimo esingavamile kakhulu. Sithinta cishe izingane ezingu-6 kwezingu-10,000. Sivame ukuthinta izingane eziphakathi kwezinyanga ezingu-4 nezingu-8. Nakuba imbangela eqondile ingaziwa ngaso sonke isikhathi, kuye kwatholakala izimbangela eziningana eziyinhloko.
- Izinkinga zobuchopho eziphathelene nokwakheka: Noma yikuphi ukukhubazeka okwenzeka ngesikhathi sokuthuthukiswa noma ukwakheka kobuchopho.
- Izinguquko zofuzo: Lesi simo singabangelwa izinguquko ezithile ezizakhini zofuzo zomntwana.
- Ukulimala kobuchopho: Ngenxa yokuntuleka komoya-mpilo ebuchosheni ngesikhathi sokuzalwa noma ngesinye isikhathi, njengengozi.
- Ukuphazamiseka kwe-Metabolic: Ngenxa yezinkinga ezithile ngezinqubo zamakhemikhali zomzimba.
- Ukutheleleka kobuchopho: Izimo ezithelelanayo ezithinta ubuchopho.
- I-Tuberous Sclerosis Complex: Isimo sofuzo lapho kuvela khona izimila ezingezona umdlavuza emzimbeni nasebuchosheni.
Kwenziwa kanjani ukuxilongwa?
Uma ubona ingane yakho inalolu hlobo lokuxhuzula, kufanele ubonane nodokotela wezingane ngokushesha okukhulu .
Kubaluleke kakhulu: Ngaphambi kokuthi uye kudokotela wakho, kuyasiza kakhulu uma ungaqopha ngevidiyo ukuminyana kwengane yakho. Lokhu kungavame ukuphambaniswa ne-colic, ngakho-ke kuyasiza kakhulu kudokotela ukubona ividiyo ukusiza ekuxilongeni lesi simo.
Udokotela ubhekisela kakhulu kulezi zivivinyo:
- I-EEG (i-Electroencephalogram): Lolu vivinyo olubaluleke kakhulu. Kalula nje, luqopha umsebenzi kagesi ebuchosheni njengephethini. Ingane ene-West Syndrome izobonisa iphethini engajwayelekile kakhulu ebizwa ngokuthi 'i-Hypsarrhythmia' ku-EEG. Lena yinkomba eyinhloko yokuxilongwa kwalesi simo.
- I-MRI noma i-CT scan:Lezi zindlela zokuskena zisiza ukubona ukuthi kukhona yini izinkinga, umonakalo, noma ukukhubazeka esakhiweni sobuchopho.
- Ukuhlolwa kwegazi, umchamo, kanye noketshezi lomgogodla (i-CSF): Lokhu kuhlolwa kusiza ekunqumeni ukuthi imbangela yokuthuthumela iyinkinga yofuzo noma ye-metabolic.
Yiziphi izindlela zokwelapha lokhu?
Kubaluleke kakhulu ukuqala ukwelashwa ngokushesha ngangokunokwenzeka ngemva kokuba i-West Syndrome isitholakale, ngoba ukulawula ukuxhuzula kusiza ekunciphiseni umonakalo ekukhuleni kobuchopho bengane.
Imithi
Ukwelashwa okuvame ukusetshenziswa kakhulu kulokhu imithi.
- I-ACTH: Lena yi-hormone. Inikezwa njengomjovo. Isebenza kahle kakhulu ekulawuleni ukushaya kwenhliziyo.
- I-Vigabatrin (Sabril): Lona futhi umuthi wesifo sokuwa. Usebenza kahle kakhulu ezinganeni ezine-West Syndrome, isimo esibangelwa yi-Tuberous Sclerosis.
- Ama-Steroids: Ama-Steroids afana ne-'Prednisone' nawo ayasetshenziswa.
Le mithi ingaba nemiphumela emibi njengokuncipha kokuzivikela komzimba, ukwanda komfutho wegazi, kanye nezinkinga zokubona. Ngakho-ke, udokotela uhlala ehlola ingane futhi ayiphathe ngokusekelwe ezinzuzweni nasezingozini zayo.
Ukudla kwe-Ketogenic
Kwabanye abantwana, uma imithi inganele ukulawula uhudo lwabo, udokotela angase asikisele lokhu kudla okukhethekile. Lokhu ukudla okunamafutha amaningi, okunama-carbohydrate amancane kakhulu .
Isexwayiso: Ungalokothi uzame ukukwenza lokhu ekhaya wedwa. Lokhu kuvame ukuqaliswa esibhedlela, ngosizo lukadokotela kanye nochwepheshe wezokudla/uchwepheshe wezokudla.
Ukuhlinzwa
Uma i-MRI scan ikhombisa ngokusobala ukuthi isifo sohlangothi sibangelwa yinxeba elithile ebuchosheni, udokotela angase asikisele ukususwa kwaleyo ndawo ngokuhlinzwa. Lokhu akuyona into wonke umuntu angayenza. Kunqunywa yithimba lezokwelapha.
Ungathini ngekusasa? (I-Outlook)
Nakuba lo mbuzo unzima ukuwubuza, kubalulekile ukwazi iqiniso. Ikusasa le-West Syndrome lizonqunywa yizici eziningana ezibalulekile.
- Imbangela: Iyini imbangela yokuquleka? Uma kubangelwa ukulimala okukhulu kobuchopho, imiphumela ingaba mibi. Uma kubangelwa ngaphandle kwembangela esobala (idiopathic), imiphumela iba mihle kakhulu.
- Isikhathi sokuqala ukwelashwa: Uma ukwelashwa kungaqalwa phakathi nenyanga ngemuva kokuxilongwa, ukukhula komntwana kungenzeka kakhulu ukuthi kubuyele esimweni esijwayelekile.
- Impendulo yokwelashwa: Indlela ukuxhuzula okungalawulwa ngayo ngokushesha.
Lokhu kukhuluma kuvame ukuphela cishe eminyakeni engu-4. Kodwa-ke,Izingane eziningi zingase zibe nezinye izinhlobo zesifo sokuwa kamuva.
Izingane eziningi zinezinga elithile lokukhubazeka ekufundeni noma izinkinga zokukhula kwengqondo. Kodwa-ke, ngokwelashwa okungcono kakhulu okutholakala kusenesikhathi, cishe u-20%-25% wezingane angaphila impilo evamile ngokuhlakanipha okuvamile. Ngakho-ke, ukuthatha isinyathelo kusenesikhathi kubalulekile.
Umlayezo Wokuya Nawe Ekhaya
- Uma ubona ukudikiza okungazelelwe, okuhlangene engane yakho encane (ikakhulukazi phakathi kwezinyanga ezingu-3-12), ungakushayi indiva.
- Uma kungenzeka, qopha ngevidiyo ukufinyela kwamathumbu. Kuzoba usizo kakhulu kudokotela.
- Bona udokotela wezingane ngokushesha. Ukuchitha isikhathi kungandisa umonakalo ebuchosheni bengane.
- I-West Syndrome iyisimo esingelapheka. Ukwelashwa kusenesikhathi kungalawula lesi simo futhi kunikeze ingane ithuba elihle kakhulu lokukhula esikhathini esizayo.
- Lolu hambo lunzima, kodwa awuwedwa. Khuluma nodokotela wakho njalo futhi uthole ukwesekwa okudingayo.
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