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Ingabe unethusi eliningi emzimbeni wakho? Ake sifunde kahle ngeSifo sikaWilson!

Ingabe unethusi eliningi emzimbeni wakho? Ake sifunde kahle ngeSifo sikaWilson!

Ingabe ngezinye izikhathi uzizwa ukhathele nje? Noma uhlangabezana nezinto ezifana nomuzwa wobuthakathaka, ukungakhululeki esiswini, nokudideka kwengqondo ngaphandle kwesizathu? Kunezifo ezithile ezingavamile ezithinta umzimba ngezindlela esingenakuzicabanga. Namuhla sizokhuluma ngesifo esingavamile, kodwa uma unolwazi olufanele, ungasibona kusenesikhathi futhi unciphise umonakalo esingawubangela empilweni yakho. Lokhu kubizwa ngokuthi i-Wilson Disease .

Iyini i-Wilson Disease?

Kalula nje, i-Wilson's Disease yisimo esingavamile sofuzo esibangela imizimba yethu ukuthi iqoqe ithusi eliningi kunalokho ekudingayo. Le thusi iqongelela esibindini nasebuchosheni bethu. Imizimba yethu empeleni idinga inani elincane lethusi ekudleni ukuze ihlale iphilile. Kodwa-ke, uma umuntu onesifo sikaWilson engelashwa kahle, amazinga ethusi emzimbeni angaba phezulu kakhulu, okubangela ukulimala kwezitho ezisongela ukuphila.

Ubani othinteka kakhulu yisifo sikaWilson?

Isifo sikaWilson siyisifo esidluliselwa kubazali ezinganeni . Ukuze sikhule, ingane kumele ithole isakhi esisodwa esingavamile kumzali ngamunye. Lokhu kubizwa ngokuthi ifa eliyi-autosomal recessive. Kunzima kakhulu ukusho ukuthi ubani ozokhula naso. Lokhu kungenxa yokuthi isikhathi esiningi, abazali ababonisi zimpawu zokuba nalesi sakhi esingavamile emzimbeni wabo. Ngakho-ke, abazi ukuthi 'bangumthwali' walesi sakhi. Kodwa-ke, uma isihlobo esiseduze emndenini wakho sinalesi sifo, nawe ungaba sengozini.

Sivame kangakanani isifo sikaWilson?

Lesi yisifo esingavamile kakhulu . Kulinganiselwa ukuthi cishe umuntu oyedwa kwabangu-30,000 uba nalesi sifo. Kodwa-ke, uma othile emndenini enalesi sifo, amathuba okuba abanye basithole aphezulu. Abantu abaningi kakhulu banezakhi zofuzo ezinephutha elilodwa kuphela, elibizwa ngokuthi abathwali. Ngokuvamile abanazo izimpawu, kodwa bangadlulisela lesi sifo ezinganeni zabo. Njengoba abathwali bengenazo izimpawu, kunzima ukusho ukuthi bangaki abantu emphakathini jikelele abanezakhi zofuzo ezinephutha.

Isifo sikaWilson sithinta kanjani umzimba wami?

Isifo sikaWilson, uma singaqashelwa futhi selashwe kusenesikhathi, singaholela ezinkingeni ezisongela ukuphila . Ithusi liyanqwabelana emzimbeni liye emazingeni anobuthi, ikakhulukazi esibindini nasebuchosheni. Lokhu kungabangela umonakalo kulezi zitho zomzimba. Lapho amazinga ethusi emzimbeni ekhuphuka, indlela ozizwa ngayo ingashintsha. Ungase uzizwe ukhathele kakhulu, ubuthakathaka, futhi ube nezinhlungu nezinhlungu. Uma unobuthakathaka obuqhubekayo, ukukhathala, noma ubuhlungu, kungcono ukufuna iseluleko sezokwelapha.

Ziyini izimpawu zesifo sikaWilson?

Izimpawu zesifo sikaWilson zingahluka kakhulu kumuntu nomuntu.Nakuba lesi kuyisimo sokuzalwa, izimpawu ziqala ukuvela ngemva kokuba ithusi liqongeleleke esibindini, ebuchosheni, emehlweni, noma kwezinye izitho zomzimba. Abantu abanesifo sikaWilson bavame ukuba nezimpawu phakathi kweminyaka emi-5 nengama-40. Kodwa-ke, abanye abantu bangase babe nezimpawu besebancane noma bebadala.

Khumbula, ngezinye izikhathi lezi zimpawu zifana nezinye izifo zesibindi noma izinkinga zempilo yengqondo, ngakho abantu bangacabanga ngephutha ukuthi kuyinto ehlukile. Kungaba nzima ukusho ngokuqinisekile ukuthi yisifo sikaWilson yini uze uhlolwe amazinga akho ethusi.

Izimpawu ezihlobene nesibindi

Abantu abaningi abanesifo sikaWilson bangase babe nezimpawu ze-hepatitis. Bangase futhi babe nokwehluleka kwesibindi okungazelelwe. Izimpawu zifaka:

  • Ngihlala ngikhathele.
  • Isicanucanu nokuhlanza.
  • Ukudla akunambitheki.
  • Ubuhlungu ohlangothini lwesokudla lwesisu, phezu kwesibindi.
  • Umchamo omnyama.
  • Izitulo ezinombala okhanyayo.
  • Ukuphuzi kwamhlophe kwamehlo nesikhumba (i-jaundice).

Abanye abantu bangase babe nezimpawu kuphela uma isifo sikaWilson siqhubekela ezinkingeni ezifana nesifo sesibindi esingamahlalakhona kanye ne-cirrhosis. Lokhu kufaka phakathi:

  • Ukukhathala nobuthakathaka obuhlala njalo.
  • Ukwehlisa isisindo okungenakucatshangwa.
  • Ukuvuvukala kwesisu (ama-ascites).
  • Ukuvuvukala kwemilenze engezansi, amaqakala, nezinyawo (i-edema).
  • Isikhumba esilumayo.
  • I-jaundice enzima.

Izimpawu ezihlobene nesistimu yezinzwa ephakathi

Uma ithusi linqwabelana emzimbeni, abantu abanesifo sikaWilson bangaba nezimpawu ezithinta uhlelo lwezinzwa oluphakathi, ezingathinta impilo yengqondo. Nakuba lezi zivame kakhulu kubantu abadala, zingavela nasezinganeni.

Izimpawu ezihlobene nesimiso sezinzwa zingafaka:

  • Izinkinga ngokukhuluma, ukugwinya, noma ukuhlangana komzimba.
  • Ukuqina kwemisipha.
  • Ukuthuthumela noma ukunyakaza okungalawuleki (ukungaphumuli).

Izimpawu zesifo sikaWilson ezithinta impilo yengqondo:

  • Ukukhathazeka.
  • Izinguquko esimweni sengqondo, ubuntu, noma ukuziphatha.
  • Ukucindezeleka.
  • Isimo lapho imicabango nemizwa kuphazamiseka khona futhi kunzima ukuhlukanisa phakathi kweqiniso namanga (i-psychosis).

Izimpawu ezihlobene namehlo

Abantu abaningi abanesifo sikaWilson banezindandatho eziluhlaza, ezigolide, noma ezinsundu (izindandatho zikaKayser-Fleischer) ezizungeze unqenqema lwe-cornea (ingxenye emnyama yeso). Lezi "zindandatho zikaKayser-Fleischer" zibangelwa ukunqwabelana kwethusi esweni. Udokotela wakho angazibona lezi zindandatho ngesikhathi sokuhlolwa kwamehlo okukhethekile (ukuhlolwa kwesibani esiqhekekile).

Abantu abaningi abanezimpawu ezithinta uhlelo lwezinzwa futhi abatholakale benesifo sikaWilson banalezi "zindandatho zikaKayser-Fleischer." Cishe ingxenye yabantu abanezimpawu ezithinta isibindi kuphela abangabona lezi zindandatho.

Ezinye izimpawu zesifo sikaWilson

Isifo sikaWilson singathinta nezinye izingxenye zomzimba wakho, okubangela izimpawu ezifana nalezi:

  • I-hemolytic anemia ibangelwa ukuwohloka kwamaseli egazi.
  • Izinkinga zamathambo namalunga (i-arthritis noma i-osteoporosis).
  • Isifo semisipha yenhliziyo `(cardiomyopathy)`.
  • Izinkinga zezinso (i-renal tubular acidosis noma amatshe ezinso).

Yini ebangela isifo sikaWilson?

Imbangela eyinhloko yesifo sikaWilson ukuguquka kwezakhi zofuzo okubizwa ngokuthi i-ATP7B . Le zakhi zofuzo zinomthwalo wokususa ithusi eliningi emzimbeni wethu.

Ngokuvamile, isibindi sikhipha ithusi elengeziwe libe uketshezi (i-bile). Le bili igcinwa enyongweni. Isiza ekugayeni ukudla. I-Bile isusa ithusi, kanye nobunye ubuthi kanye nemikhiqizo engcolile, emzimbeni ngomgudu wokugaya ukudla. Uma unesifo sikaWilson, isibindi sakho sikhipha ithusi elincane enyongweni. Lokhu kubangela ukuthi ithusi elengeziwe lihlale emzimbeni wakho.

Ngingayithola yini ifa lesifo sikaWilson?

Yebo, ungazuza ifa lokuguquka kwezakhi zofuzo ze-ATP7B okubangela isifo sikaWilson. Lokhu kusho ukuthi ukuguqulwa kwezakhi zofuzo kudluliselwa kusuka komunye umzali kuya komunye. Ukuze umuntu abe nesifo sikaWilson, kufanele azuze izakhi zofuzo ezimbili ezinephutha - elilodwa kunina kanye nelinye kuyise (i-autosomal recessive) .

Abantu abanezakhi zofuzo ze-ATP7B ezingenayo i-mutation kanti enye ine-mutation ababi nesifo sikaWilson. Kodwa bangabathwali balesi sifo. Lokhu kusho ukuthi, kuye ngesimo sofuzo somlingani wabo, bangadlulisela izakhi zofuzo ezinempilo, isimo somthwali, noma lesi sifo ezinganeni zabo.

Isifo sikaWilson sitholakala kanjani? (Ukuxilongwa)

Ukuze ahlole isifo sikaWilson, udokotela wakho uzobuza ngomlando wezokwelapha womndeni wakho kanye nomlando wakho wezokwelapha ukuze azame ukuthola ukuthi izimpawu zakho zingabangelwa yini yilesi simo.

Odokotela bazokuhlola ukuze babone ukuthi zikhona yini ezinye izimpawu ezibonisa izinkinga ngesibindi sakho, ubuchopho, noma amehlo. Ngesikhathi sokuhlolwa kwamehlo, udokotela uzokwenza "ukuhlolwa kwesibani esivulekile." Lokhu ukuhlolwa okusebenzisa isibani esikhethekile ukubheka "izindandatho zikaKayser-Fleischer."

Uma kusolwa ukuthi une-Wilson's disease, udokotela wakho uzoyala ukuhlolwa kwegazi nomchamo.

Yiziphi izivivinyo ezisetshenziswa ukuxilonga isifo sikaWilson?

Isifo sikaWilson sitholakala ngokuhlolwa kwegazi, ukuhlolwa komchamo, ukuhlolwa kofuzo, noma ukuhlolwa kwesibindi.

Ukuhlolwa kwegazi

Ukuhlolwa kwegazi kungahlola izinto eziningi egazini lakho:

  • I-Ceruloplasmin: I-Ceruloplasmin iyiprotheni ethwala ithusi egazini. Abantu abanesifo sikaWilson banamazinga aphansi e-ceruloplasmin.
  • Ithusi: Abantu abanesifo sikaWilson bangase babe namazinga aphezulu noma aphansi ethusi egazini labo.
  • I-Alanine transaminase (ALT) kanye ne-aspartate transaminase (AST): I-ALT kanye ne-AST ama-enzyme esibindi ayanda lapho isibindi sonakele.
  • Amangqamuzana abomvu egazi: Abantu abanesifo sikaWilson bangase babe nenani eliphansi lamangqamuzana abomvu egazi (i-anemia).

Uma ezinye izivivinyo zezokwelapha zingakwazi ukuqinisekisa noma ukuqeda isifo sikaWilson, udokotela wakho angase akucele ukuhlolwa kwegazi ukuze kuhlolwe ukuguquka kwezakhi zofuzo okubangela isifo sikaWilson.

Ukuhlolwa kokuqoqwa komchamo kwamahora angama-24

Esikhathini samahora angama-24, uzoqoqa umchamo wakho ekhaya, esitsheni esikhethekile esingenathusi esinikezwe udokotela wakho. Ilabhorethri izohlola inani lethusi emchameni wakho. Abantu abanesifo sikaWilson banezinga eliphezulu lethusi emchameni wabo.

Ukuhlolwa kwesibindi

Uma ukuhlolwa kwegazi nomchamo kungakwazi ukuqinisekisa noma ukuqeda isifo sikaWilson, udokotela wakho angase akucele ukuthi kwenziwe i-biopsy yesibindi. Kule nqubo, udokotela wakho uthatha isampula encane yezicubu esibindini sakho. Udokotela wezifo uhlola izicubu ngaphansi kwe-microscope ukuze abheke izimpawu zezifo ezithile zesibindi ezifana nesifo sikaWilson, ukulimala kwesibindi, kanye ne-cirrhosis. Ucezu lwezicubu zesibindi luthunyelwa elabhorethri ukuze luhlolwe ithusi.

Ukuhlolwa kwezithombe

Uma unezimpawu ezihlobene nohlelo lwakho lwezinzwa, udokotela wakho angase asebenzise izivivinyo zezithombe ukuze abheke izimpawu zesifo sikaWilson noma ezinye izimo ebuchosheni. Lokhu kungafaka:

  • I-MRI (Umfanekiso Wokuqabulana Kwamagnetic)
  • `I-X-ray`
  • `I-CT scan` (I-Computerized Tomography Scan)

Isifo sikaWilson selashwa kanjani?

Umgomo oyinhloko wokwelashwa kwesifo sikaWilson ukunciphisa amazinga ethusi elinobuthi emzimbeni wakho, ukuvimbela ukulimala kwezitho zomzimba, nokuvimbela izimpawu ezenzeka lapho izitho zomzimba zingasebenzi kahle . Ukwelashwa kuhlanganisa:

  • Ukuthatha imithi esusa ithusi emzimbeni (ama-chelating agents - isibonelo i-D-penicillamine, i-Trientine, i-Tetrathiomolybdate).
  • Ukuthatha i-zinc ukuvimbela ukumuncwa kwethusi emathunjini.
  • Ukudla ukudla okune-copper eningi.

Abantu abanesifo sikaWilson badinga ukwelashwa impilo yonke. Uma ukwelashwa kuyekwa, ukwehluleka kwesibindi okukhulu kungenzeka. Udokotela wakho uzokwenza ukuhlolwa kwegazi nomchamo njalo ukuze ahlole ukuthi ukwelashwa kusebenza kahle kangakanani.

Yimiphi imithi yesifo sikaWilson?

Udokotela wakho angase asikisele imithi ehlukahlukene yokunciphisa inani lethusi emzimbeni wakho.

Ama-ejenti okuchela

Izinto ezibulala amagciwane zisebenza ngokukhipha ithusi emzimbeni wakho. Izibonelo zalokhu zifaka:

  • I-Penicillamine
  • I-Trientine

Uma ukwelashwa kuqala, odokotela bandisa kancane kancane umthamo wezinto ezibangela ukubola. Kudingeka imithamo ephezulu kuze kube yilapho ithusi eliningi emzimbeni lisusiwe. Uma izimpawu zesifo sikaWilson seziphelile futhi ukuhlolwa kuqinisekisa ukuthi ithusi lisezingeni eliphephile, udokotela angase anikeze imithamo ephansi yezinto ezibangela ukubola njengokwelashwa kokunakekelwa. Ukwelashwa kokunakekelwa impilo yonke kuvimbela ithusi ukuthi lingaphinde liqongelelane futhi.

Le mithi ingaba nemiphumela emibi, ngakho-ke kubalulekile ukubuza udokotela wakho uma udinga ukuthatha noma yiziphi izithasiselo, njengamavithamini, noma ukuthatha noma yiziphi izinyathelo zokuphepha ngaphambi kokuhlinzwa.

I-Zinc

I-Zinc ivimbela ukumuncwa kwethusi emathunjini. Udokotela wakho angase akunike i-zinc njengokwelashwa kokunakekela ngemva kokususa ithusi eliningi ngama-chelating agents. Uma unesifo sikaWilson kodwa ungenazo izimpawu, udokotela wakho angase akunike i-zinc.

Isifo sikaWilson siphathwa kanjani ngesikhathi sokukhulelwa?

Uma ukhulelwe, kufanele ubuze udokotela wakho ukuthi ungasiphatha kanjani isifo sikaWilson phakathi nokukhulelwa kwakho. Ngenxa yokuthi ingane esanda kuzalwa idinga inani elincane lethusi, udokotela wakho angase akunike imithi yokwehlisa ukukhulelwa ephansi. Kungaba usizo ukuba nodokotela wezifo zokubeletha ojwayelene nesifo sikaWilson.

Futhi, buza udokotela wakho ukuthi kuphephile yini ukuncelisa ngenkathi welashwa isifo sikaWilson.

Yikuphi ukudla okufanele ukugweme uma unesifo sikaWilson?

Uma unesifo sikaWilson, udokotela wakho angase akucebise ukuthi ugweme ukudla okuthile okune-copper eningi. Ikakhulukazi, kufanele ugweme:

  • Izinhlanzi ezibizwa ngokuthi amagobolondo, njengezinhlanzi ezibizwa ngokuthi ama-clams nama-oyster
  • Isibindi

Okunye ukudla okunethusi eliningi:

  • Ushokoledi
  • Izithelo ezomisiwe
  • Ubhontshisi nobhontshisi obomisiwe
  • Amakhowe
  • Amantongomane (njenge-cashews, amantongomane)

Ngemva kokuba amazinga akho ethusi esehlile ngokwelashwa futhi ukwelashwa kokulungisa sekuqalile, khuluma nodokotela wakho mayelana nokuthi ungakudla yini okunye kwalokhu kudla ngokulinganisela.

Uma amanzi akho empompini evela emthonjeni noma ngamapayipi ethusi, hlola izinga lethusi emanzini akho. Ungase ufune futhi ukusebenzisa isihlungi samanzi ukususa ithusi emanzini akho empompini.

Uma ucabanga ukuthatha izithasiselo, njengamavithamini, khuluma nodokotela wakho ngaphambi kokuzithatha. Ezinye izithasiselo zingase zibe nethusi.

Ingabe kukhona izinkinga ekwelashweni?

Isifo sikaWilson singadala izinkinga, kodwa ukutholakala kusenesikhathi kanye nokwelashwa kunganciphisa ingozi yemiphumela emibi. Imithi esetshenziswa ukwelapha isifo sikaWilson ingaba nemiphumela emibi, ngakho buza udokotela wakho ukuthi yini okufanele uyiqaphele.

Ukwehluleka kwesibindi okukhulu

Isifo sikaWilson singabangela ukwehluleka kwesibindi okukhulu. Yilapho isibindi silahlekelwa ukusebenza ngokuzumayo ngaphandle kwesixwayiso. Cishe abantu abangu-5% abanesifo sikaWilson banenkinga yokwehluleka kwesibindi okukhulu ngesikhathi sokuxilongwa. Lesi simo singadinga ukufakelwa isibindi.

Abantu abanesifo sesibindi esibi kakhulu ngenxa yesifo sikaWilson bavame ukuba nokukhubazeka kwezinso okubi kakhulu kanye nohlobo lwe-anemia olubizwa ngokuthi i-hemolytic anemia.

I-Cirrhosis

I-cirrhosis yisimo lapho izicubu zesibindi ezinempilo zithathelwa indawo yizicubu zesibazi, okwenza isibindi singakwazi ukusebenza kahle. Izicubu zesibazi zivimba nokugeleza kwegazi esibindini ngezinga elithile. Njengoba i-cirrhosis iqhubeka, isibindi siqala ukwehluleka.

Abantu abaphakathi kuka-35% no-45% abatholakale benesifo sikaWilson banesifo sokuqina kwesibindi ngesikhathi sokuxilongwa.

I-cirrhosis yandisa ingozi yokuba nomdlavuza wesibindi. Kodwa-ke, odokotela bathole ukuthi abantu abathola i-cirrhosis ngenxa yesifo sikaWilson banamathuba amancane okuthola umdlavuza wesibindi kunalabo abathola i-cirrhosis ngenxa yezinye izimbangela.

Ukwehluleka kwesibindi

I-cirrhosis ingagcina iholele ekuhlulekeni kwesibindi. Ukwehluleka kwesibindi kwenzeka lapho isibindi sakho sonakala kakhulu kangangokuthi siyeka ukusebenza. Lokhu kubizwa nangokuthi isifo sesibindi sesigaba sokugcina. Lesi simo singadinga ukufakelwa isibindi.

Ziphathwa kanjani izinkinga zesifo sikaWilson?

Uma isifo sikaWilson sibangela i-cirrhosis, udokotela wakho angase akwazi ukwelapha izinkinga zakho ngemithi noma ngokuhlinzwa.

Uma isifo sikaWilson sibangela ukwehluleka kwesibindi okukhulu noma ukwehluleka kwesibindi okungapheli ngenxa yesifo sokuqina kwesibindi, ungase udinge ukufakelwa isibindi. Abanye abantu abafakelwe isibindi balulama ngokuphelele esifweni sikaWilson. Kodwa udokotela wakho uzokuqapha eduze ukuqinisekisa ukuthi ukufakelwa kuphumelele.

Ngizozizwa ngingcono ngokushesha kangakanani ngemva kokwelashwa?

Ukwelashwa kwesifo sikaWilson kuyinqubo ethatha impilo yonke . Isikhathi esithathayo ukuze uzizwe ungcono sincike ebunzimeni bezimpawu zakho. Kodwa-ke, ngemva kwezinyanga ezine kuya kweziyisithupha zokwelashwa, kulandelwa ukwelashwa okuvamile, izimpawu zakho zingancishiswa kakhulu. Udokotela wakho uzokwenza izivivinyo ezivamile ukuhlola ukuthi ukwelashwa kwesifo sikaWilson kusebenza kahle kangakanani. Uzophinde alungise umthamo wemithi yakho ukuze uvumelane nezidingo zomzimba wakho.

Uma nginesifo sikaWilson, yini okufanele ngiyilindele?

Kuye ngokuthi uxilongiwe yini, ungase ube nezimpawu ezihlobene nesifo sikaWilson noma ungabi nazo. Uma unezimpawu, zingaba yingozi empilweni uma ungatholi ukwelashwa. Into ebaluleke kakhulu ukulandela uhlelo lokwelashwa lukadokotela wakho ngqo ukuze ususe ithusi elinobuthi emzimbeni wakho futhi uvimbele ukulimala kwezitho zomzimba.

Isifo sikaWilson siyisimo sokuphila konke, futhi asikho ikhambi. Isifo sikaWilson esingelashwanga sinobude besikhathi sokuphila obufushane. Abantu abatholakala benesifo sikaWilson futhi bafakelwe isibindi ngempumelelo banesikhathi sokuphila esihle. Kodwa-ke, ngisho nangemva kokufakelwa, kuzodingeka babe ngaphansi kokuqashwa kwezokwelapha impilo yabo yonke.

Ingabe isifo sikaWilson singavinjelwa?

Isifo sikaWilson siwumphumela wokuguqulwa kwezakhi zofuzo okuzuzwe njengefa, ngakho-ke asinakuvinjelwa. Uma unomlando womndeni wesifo sikaWilson, khuluma nodokotela wakho mayelana nokuhlolwa kwezakhi zofuzo ukuze uqonde ingozi yakho yokuthola isifo sikaWilson noma ukuba nengane enalesi simo sezakhi zofuzo.

Ngingazinakekela kanjani?

Uma unesifo sikaWilson, ungazinakekela ngokuthatha imithi yakho njengoba uyalelwe udokotela wakho futhi ususe ukudla okunethusi eliningi ekudleni kwakho. Ngokwelashwa, unganciphisa izimpawu zakho futhi uvimbele izinkinga ezisongela ukuphila.

Kufanele ngimbone nini udokotela wami?

Uma izimpawu zesifo sakho sikaWilson ziba zimbi kakhulu, ikakhulukazi uma sezithuthuke ngaphambilini, kufanele ubonane nodokotela wakho. Lokhu kungasho ukuthi umthamo wemithi yakho udinga ukushintshwa.

Uma izimpawu zesifo sakho sikaWilson zikuvimbela ekwenzeni imisebenzi yakho yansuku zonke evamile, ikakhulukazi uma ungakwazi ukudla, ukuhlanza njalo, uba nesifo sengqondo, isikhumba sakho siphenduka siphuzi (i-jaundice), noma unezinhlungu zesisu ezinzima, iya ekamelweni eliphuthumayo ngokushesha noma ushayele u-911.

Yimiphi imibuzo okufanele ngiyibuze udokotela wami?

  • Ingabe ngizodinga ukufakelwa isibindi?
  • Yimiphi imiphumela emibi yemithi enikezwe ukwelapha isifo sikaWilson?
  • Uma ngikhulelwa, ingabe ingane yami izoyithola isifo sikaWilson?
  • Ngingawuthatha yini umuthi wami uma ngikhulelwa?
  • Kudingeka ngithathe isikhathi esingakanani umuthi onginike wona?

Okokugcina, khumbula (Umyalezo Wokuya Ekhaya)

Ukuxilongwa kusenesikhathi kanye nokwelashwa kwesifo sikaWilson kuyindlela engcono kakhulu yokwelapha lesi simo sofuzo sokuphila konke. Kungase kudingeke wenze izinguquko endleleni yokuphila ukuze unciphise ithusi ekudleni kwakho. Qiniseka ukuthi ubona udokotela wakho ukuqinisekisa ukuthi ukwelashwa kwakho kuyasebenza ukunciphisa inani lethusi emzimbeni wakho. Ukwelashwa okufanele kungakusiza ukuthi ube ngcono futhi uvimbele izinkinga ezisongela ukuphila. Ungesabi, into ebaluleke kakhulu ukuqaphela nokulandela iseluleko sikadokotela wakho.


Isifo sikaWilson , ithusi, isibindi, ubuchopho, izifo zofuzo, i-cirrhosis, izindandatho zikaKeiser-Fleischer

Frequently Asked Questions (FAQ)

Yiziphi izivivinyo ezisetshenziswa ukuxilonga isifo sikaWilson?

Isifo sikaWilson sitholakala ngokuhlolwa kwegazi, ukuhlolwa komchamo, ukuhlolwa kofuzo, noma ukuhlolwa kwesibindi.

Yimiphi imithi yesifo sikaWilson?

Udokotela wakho angase asikisele imithi ehlukahlukene yokunciphisa inani lethusi emzimbeni wakho.

Isifo sikaWilson siphathwa kanjani ngesikhathi sokukhulelwa?

Uma ukhulelwe, kufanele ubuze udokotela wakho ukuthi ungasiphatha kanjani isifo sikaWilson phakathi nokukhulelwa kwakho. Ngenxa yokuthi ingane esanda kuzalwa idinga inani elincane lethusi, udokotela wakho angase akunike imithi yokwehlisa ukukhulelwa ephansi. Kungaba usizo ukuba nodokotela wezifo zokubeletha ojwayelene nesifo sikaWilson.

Yikuphi ukudla okufanele ukugweme uma unesifo sikaWilson?

Uma unesifo sikaWilson, udokotela wakho angase akucebise ukuthi ugweme ukudla okuthile okune-copper eningi. Ikakhulukazi, kufanele ugweme:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Ingabe unethusi eliningi emzimbeni wakho? Ake sifunde kahle ngeSifo sikaWilson!

Ingabe unethusi eliningi emzimbeni wakho? Ake sifunde kahle ngeSifo sikaWilson!

Ingabe ngezinye izikhathi uzizwa ukhathele nje? Noma uhlangabezana nezinto ezifana nomuzwa wobuthakathaka, ukungakhululeki esiswini, nokudideka kwengqondo ngaphandle kwesizathu? Kunezifo ezithile ezingavamile ezithinta umzimba ngezindlela esingenakuzicabanga. Namuhla sizokhuluma ngesifo esingavamile, kodwa uma unolwazi olufanele, ungasibona kusenesikhathi futhi unciphise umonakalo esingawubangela empilweni yakho. Lokhu kubizwa ngokuthi i-Wilson Disease .

Iyini i-Wilson Disease?

Kalula nje, i-Wilson's Disease yisimo esingavamile sofuzo esibangela imizimba yethu ukuthi iqoqe ithusi eliningi kunalokho ekudingayo. Le thusi iqongelela esibindini nasebuchosheni bethu. Imizimba yethu empeleni idinga inani elincane lethusi ekudleni ukuze ihlale iphilile. Kodwa-ke, uma umuntu onesifo sikaWilson engelashwa kahle, amazinga ethusi emzimbeni angaba phezulu kakhulu, okubangela ukulimala kwezitho ezisongela ukuphila.

Ubani othinteka kakhulu yisifo sikaWilson?

Isifo sikaWilson siyisifo esidluliselwa kubazali ezinganeni . Ukuze sikhule, ingane kumele ithole isakhi esisodwa esingavamile kumzali ngamunye. Lokhu kubizwa ngokuthi ifa eliyi-autosomal recessive. Kunzima kakhulu ukusho ukuthi ubani ozokhula naso. Lokhu kungenxa yokuthi isikhathi esiningi, abazali ababonisi zimpawu zokuba nalesi sakhi esingavamile emzimbeni wabo. Ngakho-ke, abazi ukuthi 'bangumthwali' walesi sakhi. Kodwa-ke, uma isihlobo esiseduze emndenini wakho sinalesi sifo, nawe ungaba sengozini.

Sivame kangakanani isifo sikaWilson?

Lesi yisifo esingavamile kakhulu . Kulinganiselwa ukuthi cishe umuntu oyedwa kwabangu-30,000 uba nalesi sifo. Kodwa-ke, uma othile emndenini enalesi sifo, amathuba okuba abanye basithole aphezulu. Abantu abaningi kakhulu banezakhi zofuzo ezinephutha elilodwa kuphela, elibizwa ngokuthi abathwali. Ngokuvamile abanazo izimpawu, kodwa bangadlulisela lesi sifo ezinganeni zabo. Njengoba abathwali bengenazo izimpawu, kunzima ukusho ukuthi bangaki abantu emphakathini jikelele abanezakhi zofuzo ezinephutha.

Isifo sikaWilson sithinta kanjani umzimba wami?

Isifo sikaWilson, uma singaqashelwa futhi selashwe kusenesikhathi, singaholela ezinkingeni ezisongela ukuphila . Ithusi liyanqwabelana emzimbeni liye emazingeni anobuthi, ikakhulukazi esibindini nasebuchosheni. Lokhu kungabangela umonakalo kulezi zitho zomzimba. Lapho amazinga ethusi emzimbeni ekhuphuka, indlela ozizwa ngayo ingashintsha. Ungase uzizwe ukhathele kakhulu, ubuthakathaka, futhi ube nezinhlungu nezinhlungu. Uma unobuthakathaka obuqhubekayo, ukukhathala, noma ubuhlungu, kungcono ukufuna iseluleko sezokwelapha.

Ziyini izimpawu zesifo sikaWilson?

Izimpawu zesifo sikaWilson zingahluka kakhulu kumuntu nomuntu.Nakuba lesi kuyisimo sokuzalwa, izimpawu ziqala ukuvela ngemva kokuba ithusi liqongeleleke esibindini, ebuchosheni, emehlweni, noma kwezinye izitho zomzimba. Abantu abanesifo sikaWilson bavame ukuba nezimpawu phakathi kweminyaka emi-5 nengama-40. Kodwa-ke, abanye abantu bangase babe nezimpawu besebancane noma bebadala.

Khumbula, ngezinye izikhathi lezi zimpawu zifana nezinye izifo zesibindi noma izinkinga zempilo yengqondo, ngakho abantu bangacabanga ngephutha ukuthi kuyinto ehlukile. Kungaba nzima ukusho ngokuqinisekile ukuthi yisifo sikaWilson yini uze uhlolwe amazinga akho ethusi.

Izimpawu ezihlobene nesibindi

Abantu abaningi abanesifo sikaWilson bangase babe nezimpawu ze-hepatitis. Bangase futhi babe nokwehluleka kwesibindi okungazelelwe. Izimpawu zifaka:

  • Ngihlala ngikhathele.
  • Isicanucanu nokuhlanza.
  • Ukudla akunambitheki.
  • Ubuhlungu ohlangothini lwesokudla lwesisu, phezu kwesibindi.
  • Umchamo omnyama.
  • Izitulo ezinombala okhanyayo.
  • Ukuphuzi kwamhlophe kwamehlo nesikhumba (i-jaundice).

Abanye abantu bangase babe nezimpawu kuphela uma isifo sikaWilson siqhubekela ezinkingeni ezifana nesifo sesibindi esingamahlalakhona kanye ne-cirrhosis. Lokhu kufaka phakathi:

  • Ukukhathala nobuthakathaka obuhlala njalo.
  • Ukwehlisa isisindo okungenakucatshangwa.
  • Ukuvuvukala kwesisu (ama-ascites).
  • Ukuvuvukala kwemilenze engezansi, amaqakala, nezinyawo (i-edema).
  • Isikhumba esilumayo.
  • I-jaundice enzima.

Izimpawu ezihlobene nesistimu yezinzwa ephakathi

Uma ithusi linqwabelana emzimbeni, abantu abanesifo sikaWilson bangaba nezimpawu ezithinta uhlelo lwezinzwa oluphakathi, ezingathinta impilo yengqondo. Nakuba lezi zivame kakhulu kubantu abadala, zingavela nasezinganeni.

Izimpawu ezihlobene nesimiso sezinzwa zingafaka:

  • Izinkinga ngokukhuluma, ukugwinya, noma ukuhlangana komzimba.
  • Ukuqina kwemisipha.
  • Ukuthuthumela noma ukunyakaza okungalawuleki (ukungaphumuli).

Izimpawu zesifo sikaWilson ezithinta impilo yengqondo:

  • Ukukhathazeka.
  • Izinguquko esimweni sengqondo, ubuntu, noma ukuziphatha.
  • Ukucindezeleka.
  • Isimo lapho imicabango nemizwa kuphazamiseka khona futhi kunzima ukuhlukanisa phakathi kweqiniso namanga (i-psychosis).

Izimpawu ezihlobene namehlo

Abantu abaningi abanesifo sikaWilson banezindandatho eziluhlaza, ezigolide, noma ezinsundu (izindandatho zikaKayser-Fleischer) ezizungeze unqenqema lwe-cornea (ingxenye emnyama yeso). Lezi "zindandatho zikaKayser-Fleischer" zibangelwa ukunqwabelana kwethusi esweni. Udokotela wakho angazibona lezi zindandatho ngesikhathi sokuhlolwa kwamehlo okukhethekile (ukuhlolwa kwesibani esiqhekekile).

Abantu abaningi abanezimpawu ezithinta uhlelo lwezinzwa futhi abatholakale benesifo sikaWilson banalezi "zindandatho zikaKayser-Fleischer." Cishe ingxenye yabantu abanezimpawu ezithinta isibindi kuphela abangabona lezi zindandatho.

Ezinye izimpawu zesifo sikaWilson

Isifo sikaWilson singathinta nezinye izingxenye zomzimba wakho, okubangela izimpawu ezifana nalezi:

  • I-hemolytic anemia ibangelwa ukuwohloka kwamaseli egazi.
  • Izinkinga zamathambo namalunga (i-arthritis noma i-osteoporosis).
  • Isifo semisipha yenhliziyo `(cardiomyopathy)`.
  • Izinkinga zezinso (i-renal tubular acidosis noma amatshe ezinso).

Yini ebangela isifo sikaWilson?

Imbangela eyinhloko yesifo sikaWilson ukuguquka kwezakhi zofuzo okubizwa ngokuthi i-ATP7B . Le zakhi zofuzo zinomthwalo wokususa ithusi eliningi emzimbeni wethu.

Ngokuvamile, isibindi sikhipha ithusi elengeziwe libe uketshezi (i-bile). Le bili igcinwa enyongweni. Isiza ekugayeni ukudla. I-Bile isusa ithusi, kanye nobunye ubuthi kanye nemikhiqizo engcolile, emzimbeni ngomgudu wokugaya ukudla. Uma unesifo sikaWilson, isibindi sakho sikhipha ithusi elincane enyongweni. Lokhu kubangela ukuthi ithusi elengeziwe lihlale emzimbeni wakho.

Ngingayithola yini ifa lesifo sikaWilson?

Yebo, ungazuza ifa lokuguquka kwezakhi zofuzo ze-ATP7B okubangela isifo sikaWilson. Lokhu kusho ukuthi ukuguqulwa kwezakhi zofuzo kudluliselwa kusuka komunye umzali kuya komunye. Ukuze umuntu abe nesifo sikaWilson, kufanele azuze izakhi zofuzo ezimbili ezinephutha - elilodwa kunina kanye nelinye kuyise (i-autosomal recessive) .

Abantu abanezakhi zofuzo ze-ATP7B ezingenayo i-mutation kanti enye ine-mutation ababi nesifo sikaWilson. Kodwa bangabathwali balesi sifo. Lokhu kusho ukuthi, kuye ngesimo sofuzo somlingani wabo, bangadlulisela izakhi zofuzo ezinempilo, isimo somthwali, noma lesi sifo ezinganeni zabo.

Isifo sikaWilson sitholakala kanjani? (Ukuxilongwa)

Ukuze ahlole isifo sikaWilson, udokotela wakho uzobuza ngomlando wezokwelapha womndeni wakho kanye nomlando wakho wezokwelapha ukuze azame ukuthola ukuthi izimpawu zakho zingabangelwa yini yilesi simo.

Odokotela bazokuhlola ukuze babone ukuthi zikhona yini ezinye izimpawu ezibonisa izinkinga ngesibindi sakho, ubuchopho, noma amehlo. Ngesikhathi sokuhlolwa kwamehlo, udokotela uzokwenza "ukuhlolwa kwesibani esivulekile." Lokhu ukuhlolwa okusebenzisa isibani esikhethekile ukubheka "izindandatho zikaKayser-Fleischer."

Uma kusolwa ukuthi une-Wilson's disease, udokotela wakho uzoyala ukuhlolwa kwegazi nomchamo.

Yiziphi izivivinyo ezisetshenziswa ukuxilonga isifo sikaWilson?

Isifo sikaWilson sitholakala ngokuhlolwa kwegazi, ukuhlolwa komchamo, ukuhlolwa kofuzo, noma ukuhlolwa kwesibindi.

Ukuhlolwa kwegazi

Ukuhlolwa kwegazi kungahlola izinto eziningi egazini lakho:

  • I-Ceruloplasmin: I-Ceruloplasmin iyiprotheni ethwala ithusi egazini. Abantu abanesifo sikaWilson banamazinga aphansi e-ceruloplasmin.
  • Ithusi: Abantu abanesifo sikaWilson bangase babe namazinga aphezulu noma aphansi ethusi egazini labo.
  • I-Alanine transaminase (ALT) kanye ne-aspartate transaminase (AST): I-ALT kanye ne-AST ama-enzyme esibindi ayanda lapho isibindi sonakele.
  • Amangqamuzana abomvu egazi: Abantu abanesifo sikaWilson bangase babe nenani eliphansi lamangqamuzana abomvu egazi (i-anemia).

Uma ezinye izivivinyo zezokwelapha zingakwazi ukuqinisekisa noma ukuqeda isifo sikaWilson, udokotela wakho angase akucele ukuhlolwa kwegazi ukuze kuhlolwe ukuguquka kwezakhi zofuzo okubangela isifo sikaWilson.

Ukuhlolwa kokuqoqwa komchamo kwamahora angama-24

Esikhathini samahora angama-24, uzoqoqa umchamo wakho ekhaya, esitsheni esikhethekile esingenathusi esinikezwe udokotela wakho. Ilabhorethri izohlola inani lethusi emchameni wakho. Abantu abanesifo sikaWilson banezinga eliphezulu lethusi emchameni wabo.

Ukuhlolwa kwesibindi

Uma ukuhlolwa kwegazi nomchamo kungakwazi ukuqinisekisa noma ukuqeda isifo sikaWilson, udokotela wakho angase akucele ukuthi kwenziwe i-biopsy yesibindi. Kule nqubo, udokotela wakho uthatha isampula encane yezicubu esibindini sakho. Udokotela wezifo uhlola izicubu ngaphansi kwe-microscope ukuze abheke izimpawu zezifo ezithile zesibindi ezifana nesifo sikaWilson, ukulimala kwesibindi, kanye ne-cirrhosis. Ucezu lwezicubu zesibindi luthunyelwa elabhorethri ukuze luhlolwe ithusi.

Ukuhlolwa kwezithombe

Uma unezimpawu ezihlobene nohlelo lwakho lwezinzwa, udokotela wakho angase asebenzise izivivinyo zezithombe ukuze abheke izimpawu zesifo sikaWilson noma ezinye izimo ebuchosheni. Lokhu kungafaka:

  • I-MRI (Umfanekiso Wokuqabulana Kwamagnetic)
  • `I-X-ray`
  • `I-CT scan` (I-Computerized Tomography Scan)

Isifo sikaWilson selashwa kanjani?

Umgomo oyinhloko wokwelashwa kwesifo sikaWilson ukunciphisa amazinga ethusi elinobuthi emzimbeni wakho, ukuvimbela ukulimala kwezitho zomzimba, nokuvimbela izimpawu ezenzeka lapho izitho zomzimba zingasebenzi kahle . Ukwelashwa kuhlanganisa:

  • Ukuthatha imithi esusa ithusi emzimbeni (ama-chelating agents - isibonelo i-D-penicillamine, i-Trientine, i-Tetrathiomolybdate).
  • Ukuthatha i-zinc ukuvimbela ukumuncwa kwethusi emathunjini.
  • Ukudla ukudla okune-copper eningi.

Abantu abanesifo sikaWilson badinga ukwelashwa impilo yonke. Uma ukwelashwa kuyekwa, ukwehluleka kwesibindi okukhulu kungenzeka. Udokotela wakho uzokwenza ukuhlolwa kwegazi nomchamo njalo ukuze ahlole ukuthi ukwelashwa kusebenza kahle kangakanani.

Yimiphi imithi yesifo sikaWilson?

Udokotela wakho angase asikisele imithi ehlukahlukene yokunciphisa inani lethusi emzimbeni wakho.

Ama-ejenti okuchela

Izinto ezibulala amagciwane zisebenza ngokukhipha ithusi emzimbeni wakho. Izibonelo zalokhu zifaka:

  • I-Penicillamine
  • I-Trientine

Uma ukwelashwa kuqala, odokotela bandisa kancane kancane umthamo wezinto ezibangela ukubola. Kudingeka imithamo ephezulu kuze kube yilapho ithusi eliningi emzimbeni lisusiwe. Uma izimpawu zesifo sikaWilson seziphelile futhi ukuhlolwa kuqinisekisa ukuthi ithusi lisezingeni eliphephile, udokotela angase anikeze imithamo ephansi yezinto ezibangela ukubola njengokwelashwa kokunakekelwa. Ukwelashwa kokunakekelwa impilo yonke kuvimbela ithusi ukuthi lingaphinde liqongelelane futhi.

Le mithi ingaba nemiphumela emibi, ngakho-ke kubalulekile ukubuza udokotela wakho uma udinga ukuthatha noma yiziphi izithasiselo, njengamavithamini, noma ukuthatha noma yiziphi izinyathelo zokuphepha ngaphambi kokuhlinzwa.

I-Zinc

I-Zinc ivimbela ukumuncwa kwethusi emathunjini. Udokotela wakho angase akunike i-zinc njengokwelashwa kokunakekela ngemva kokususa ithusi eliningi ngama-chelating agents. Uma unesifo sikaWilson kodwa ungenazo izimpawu, udokotela wakho angase akunike i-zinc.

Isifo sikaWilson siphathwa kanjani ngesikhathi sokukhulelwa?

Uma ukhulelwe, kufanele ubuze udokotela wakho ukuthi ungasiphatha kanjani isifo sikaWilson phakathi nokukhulelwa kwakho. Ngenxa yokuthi ingane esanda kuzalwa idinga inani elincane lethusi, udokotela wakho angase akunike imithi yokwehlisa ukukhulelwa ephansi. Kungaba usizo ukuba nodokotela wezifo zokubeletha ojwayelene nesifo sikaWilson.

Futhi, buza udokotela wakho ukuthi kuphephile yini ukuncelisa ngenkathi welashwa isifo sikaWilson.

Yikuphi ukudla okufanele ukugweme uma unesifo sikaWilson?

Uma unesifo sikaWilson, udokotela wakho angase akucebise ukuthi ugweme ukudla okuthile okune-copper eningi. Ikakhulukazi, kufanele ugweme:

  • Izinhlanzi ezibizwa ngokuthi amagobolondo, njengezinhlanzi ezibizwa ngokuthi ama-clams nama-oyster
  • Isibindi

Okunye ukudla okunethusi eliningi:

  • Ushokoledi
  • Izithelo ezomisiwe
  • Ubhontshisi nobhontshisi obomisiwe
  • Amakhowe
  • Amantongomane (njenge-cashews, amantongomane)

Ngemva kokuba amazinga akho ethusi esehlile ngokwelashwa futhi ukwelashwa kokulungisa sekuqalile, khuluma nodokotela wakho mayelana nokuthi ungakudla yini okunye kwalokhu kudla ngokulinganisela.

Uma amanzi akho empompini evela emthonjeni noma ngamapayipi ethusi, hlola izinga lethusi emanzini akho. Ungase ufune futhi ukusebenzisa isihlungi samanzi ukususa ithusi emanzini akho empompini.

Uma ucabanga ukuthatha izithasiselo, njengamavithamini, khuluma nodokotela wakho ngaphambi kokuzithatha. Ezinye izithasiselo zingase zibe nethusi.

Ingabe kukhona izinkinga ekwelashweni?

Isifo sikaWilson singadala izinkinga, kodwa ukutholakala kusenesikhathi kanye nokwelashwa kunganciphisa ingozi yemiphumela emibi. Imithi esetshenziswa ukwelapha isifo sikaWilson ingaba nemiphumela emibi, ngakho buza udokotela wakho ukuthi yini okufanele uyiqaphele.

Ukwehluleka kwesibindi okukhulu

Isifo sikaWilson singabangela ukwehluleka kwesibindi okukhulu. Yilapho isibindi silahlekelwa ukusebenza ngokuzumayo ngaphandle kwesixwayiso. Cishe abantu abangu-5% abanesifo sikaWilson banenkinga yokwehluleka kwesibindi okukhulu ngesikhathi sokuxilongwa. Lesi simo singadinga ukufakelwa isibindi.

Abantu abanesifo sesibindi esibi kakhulu ngenxa yesifo sikaWilson bavame ukuba nokukhubazeka kwezinso okubi kakhulu kanye nohlobo lwe-anemia olubizwa ngokuthi i-hemolytic anemia.

I-Cirrhosis

I-cirrhosis yisimo lapho izicubu zesibindi ezinempilo zithathelwa indawo yizicubu zesibazi, okwenza isibindi singakwazi ukusebenza kahle. Izicubu zesibazi zivimba nokugeleza kwegazi esibindini ngezinga elithile. Njengoba i-cirrhosis iqhubeka, isibindi siqala ukwehluleka.

Abantu abaphakathi kuka-35% no-45% abatholakale benesifo sikaWilson banesifo sokuqina kwesibindi ngesikhathi sokuxilongwa.

I-cirrhosis yandisa ingozi yokuba nomdlavuza wesibindi. Kodwa-ke, odokotela bathole ukuthi abantu abathola i-cirrhosis ngenxa yesifo sikaWilson banamathuba amancane okuthola umdlavuza wesibindi kunalabo abathola i-cirrhosis ngenxa yezinye izimbangela.

Ukwehluleka kwesibindi

I-cirrhosis ingagcina iholele ekuhlulekeni kwesibindi. Ukwehluleka kwesibindi kwenzeka lapho isibindi sakho sonakala kakhulu kangangokuthi siyeka ukusebenza. Lokhu kubizwa nangokuthi isifo sesibindi sesigaba sokugcina. Lesi simo singadinga ukufakelwa isibindi.

Ziphathwa kanjani izinkinga zesifo sikaWilson?

Uma isifo sikaWilson sibangela i-cirrhosis, udokotela wakho angase akwazi ukwelapha izinkinga zakho ngemithi noma ngokuhlinzwa.

Uma isifo sikaWilson sibangela ukwehluleka kwesibindi okukhulu noma ukwehluleka kwesibindi okungapheli ngenxa yesifo sokuqina kwesibindi, ungase udinge ukufakelwa isibindi. Abanye abantu abafakelwe isibindi balulama ngokuphelele esifweni sikaWilson. Kodwa udokotela wakho uzokuqapha eduze ukuqinisekisa ukuthi ukufakelwa kuphumelele.

Ngizozizwa ngingcono ngokushesha kangakanani ngemva kokwelashwa?

Ukwelashwa kwesifo sikaWilson kuyinqubo ethatha impilo yonke . Isikhathi esithathayo ukuze uzizwe ungcono sincike ebunzimeni bezimpawu zakho. Kodwa-ke, ngemva kwezinyanga ezine kuya kweziyisithupha zokwelashwa, kulandelwa ukwelashwa okuvamile, izimpawu zakho zingancishiswa kakhulu. Udokotela wakho uzokwenza izivivinyo ezivamile ukuhlola ukuthi ukwelashwa kwesifo sikaWilson kusebenza kahle kangakanani. Uzophinde alungise umthamo wemithi yakho ukuze uvumelane nezidingo zomzimba wakho.

Uma nginesifo sikaWilson, yini okufanele ngiyilindele?

Kuye ngokuthi uxilongiwe yini, ungase ube nezimpawu ezihlobene nesifo sikaWilson noma ungabi nazo. Uma unezimpawu, zingaba yingozi empilweni uma ungatholi ukwelashwa. Into ebaluleke kakhulu ukulandela uhlelo lokwelashwa lukadokotela wakho ngqo ukuze ususe ithusi elinobuthi emzimbeni wakho futhi uvimbele ukulimala kwezitho zomzimba.

Isifo sikaWilson siyisimo sokuphila konke, futhi asikho ikhambi. Isifo sikaWilson esingelashwanga sinobude besikhathi sokuphila obufushane. Abantu abatholakala benesifo sikaWilson futhi bafakelwe isibindi ngempumelelo banesikhathi sokuphila esihle. Kodwa-ke, ngisho nangemva kokufakelwa, kuzodingeka babe ngaphansi kokuqashwa kwezokwelapha impilo yabo yonke.

Ingabe isifo sikaWilson singavinjelwa?

Isifo sikaWilson siwumphumela wokuguqulwa kwezakhi zofuzo okuzuzwe njengefa, ngakho-ke asinakuvinjelwa. Uma unomlando womndeni wesifo sikaWilson, khuluma nodokotela wakho mayelana nokuhlolwa kwezakhi zofuzo ukuze uqonde ingozi yakho yokuthola isifo sikaWilson noma ukuba nengane enalesi simo sezakhi zofuzo.

Ngingazinakekela kanjani?

Uma unesifo sikaWilson, ungazinakekela ngokuthatha imithi yakho njengoba uyalelwe udokotela wakho futhi ususe ukudla okunethusi eliningi ekudleni kwakho. Ngokwelashwa, unganciphisa izimpawu zakho futhi uvimbele izinkinga ezisongela ukuphila.

Kufanele ngimbone nini udokotela wami?

Uma izimpawu zesifo sakho sikaWilson ziba zimbi kakhulu, ikakhulukazi uma sezithuthuke ngaphambilini, kufanele ubonane nodokotela wakho. Lokhu kungasho ukuthi umthamo wemithi yakho udinga ukushintshwa.

Uma izimpawu zesifo sakho sikaWilson zikuvimbela ekwenzeni imisebenzi yakho yansuku zonke evamile, ikakhulukazi uma ungakwazi ukudla, ukuhlanza njalo, uba nesifo sengqondo, isikhumba sakho siphenduka siphuzi (i-jaundice), noma unezinhlungu zesisu ezinzima, iya ekamelweni eliphuthumayo ngokushesha noma ushayele u-911.

Yimiphi imibuzo okufanele ngiyibuze udokotela wami?

  • Ingabe ngizodinga ukufakelwa isibindi?
  • Yimiphi imiphumela emibi yemithi enikezwe ukwelapha isifo sikaWilson?
  • Uma ngikhulelwa, ingabe ingane yami izoyithola isifo sikaWilson?
  • Ngingawuthatha yini umuthi wami uma ngikhulelwa?
  • Kudingeka ngithathe isikhathi esingakanani umuthi onginike wona?

Okokugcina, khumbula (Umyalezo Wokuya Ekhaya)

Ukuxilongwa kusenesikhathi kanye nokwelashwa kwesifo sikaWilson kuyindlela engcono kakhulu yokwelapha lesi simo sofuzo sokuphila konke. Kungase kudingeke wenze izinguquko endleleni yokuphila ukuze unciphise ithusi ekudleni kwakho. Qiniseka ukuthi ubona udokotela wakho ukuqinisekisa ukuthi ukwelashwa kwakho kuyasebenza ukunciphisa inani lethusi emzimbeni wakho. Ukwelashwa okufanele kungakusiza ukuthi ube ngcono futhi uvimbele izinkinga ezisongela ukuphila. Ungesabi, into ebaluleke kakhulu ukuqaphela nokulandela iseluleko sikadokotela wakho.


Isifo sikaWilson , ithusi, isibindi, ubuchopho, izifo zofuzo, i-cirrhosis, izindandatho zikaKeiser-Fleischer

Frequently Asked Questions (FAQ)

Yiziphi izivivinyo ezisetshenziswa ukuxilonga isifo sikaWilson?

Isifo sikaWilson sitholakala ngokuhlolwa kwegazi, ukuhlolwa komchamo, ukuhlolwa kofuzo, noma ukuhlolwa kwesibindi.

Yimiphi imithi yesifo sikaWilson?

Udokotela wakho angase asikisele imithi ehlukahlukene yokunciphisa inani lethusi emzimbeni wakho.

Isifo sikaWilson siphathwa kanjani ngesikhathi sokukhulelwa?

Uma ukhulelwe, kufanele ubuze udokotela wakho ukuthi ungasiphatha kanjani isifo sikaWilson phakathi nokukhulelwa kwakho. Ngenxa yokuthi ingane esanda kuzalwa idinga inani elincane lethusi, udokotela wakho angase akunike imithi yokwehlisa ukukhulelwa ephansi. Kungaba usizo ukuba nodokotela wezifo zokubeletha ojwayelene nesifo sikaWilson.

Yikuphi ukudla okufanele ukugweme uma unesifo sikaWilson?

Uma unesifo sikaWilson, udokotela wakho angase akucebise ukuthi ugweme ukudla okuthile okune-copper eningi. Ikakhulukazi, kufanele ugweme:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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