Cabanga nje, usempilweni enhle futhi ngokuzumayo enye yezingalo noma imilenze yakho iba ndikindiki bese uquleka. Noma umzimba wakho wonke uba buthakathaka kangangokuthi awukwazi ukunyakaza. Kuvamile ukuzizwa wesaba kakhulu lapho kwenzeka into efana nale. Abantu abaningi bacabanga ukuthi lokhu kungenxa yokukhathala noma okunye. Kodwa-ke, ngezinye izikhathi kungase kube nesizathu sezokwelapha ngemuva kwalokhu okudingeka sixoxwe ngokujulile. Namuhla sikhuluma ngesimo sezokwelapha esingavamile kodwa esibaluleke kakhulu okufanele siqashelwe.
Kalula nje, kuyini i-Primary Periodic Paralysis (PPP)?
I-Primary Periodic Paralysis, noma i-PPP ngamafuphi, iyiqembu lezimo ezingavamile ezithinta imisipha yethu ngokuzumayo. Okwenzekayo ukuthi, ngaphandle kwesixwayiso , imisipha yakho iba buthakathaka, iqine, noma ikhubazeke ngokuphelele. Lesi simo singahlala imizuzu embalwa kwabanye abantu, kanti kwabanye singahlala izinsuku eziningi.
Isizathu esiyinhloko salokhu sisezingqamuzaneni zethu zemisipha. Cabanga ukuthi amangqamuzana ethu emisipha aneziteshi ezincane. Lezi ziteshi yilapho amaminerali abalulekile njenge- potassium, i-sodium, ne-calcium angena khona futhi aphume emangqamuzaneni. Ukuze imisipha isebenze kahle, inani lala maminerali ngaphakathi nangaphandle kweseli kumele libe selinganisweni eliphelele. Okwenzekayo kumuntu one-PPP ukuthi leli bhalansi liyalahleka ngenxa yephutha kulezi ziteshi. Khona-ke imisipha ayikwazi ukusebenza kahle.
Esikhathini esiningi, lezi zimpawu ziqala ebuntwaneni noma ebusheni, kodwa abanye abantu bangase bangakhombisi zimpawu baze babe neminyaka engu-60 noma engu-70 ubudala.
Yiziphi izinhlobo eziyinhloko zalesi sifo?
I-PPP ihlukaniswe ngezinhlobo eziningana eziyinhloko. Lokhu kuhlukaniswa kuthonywa kakhulu ukuthi yikuphi ukukhubazeka kwesiteshi samaminerali okukhona kumaseli akho emisipha.
| Uhlobo lwesimo sezokwelapha | Kwenzekani (ngamagama alula) |
|---|---|
| Ukukhubazeka Kwesikhathi Esivamile Kwe-Hypokalemic (hypoKPP) | Okwenzekayo kulokhu ukuthi izinga le-potassium egazini lehla ngokuzumayo kakhulu. |
| Ukukhubazeka Kwesikhathi Esivamile Kwe-Hyperkalemic (hyperKPP) | Okwenzekayo kulokhu ukuthi izinga le-potassium egazini likhuphuka kakhulu ngokuzumayo. |
| I-Paramyotonia Congenita | Lapha, ibhalansi ye-sodium ne-potassium emaseli emisipha iyaphazamiseka. |
| I-Andersen-Tawil Syndrome (ATS) | Kulesi simo, inqubo yokungena nokuphuma kwe-potassium emangqamuzaneni ayenzeki kahle. Izinga le-potassium egazini lingase libe phezulu, libe phansi, noma libe lijwayelekile. |
Ngezinye izikhathi, ubuthakathaka bemisipha bungabangelwa ezinye izimo. Isibonelo yi -Thyrotoxic Periodic Paralysis (TPP) . Lesi yisimo lapho i-thyroid gland ikhiqiza khona i-thyroid hormone eningi kakhulu. Lokhu kuhambisana namazinga aphansi e-potassium egazini, okungabangela izimpawu ezifana ne-HypoKPP.
Yiziphi izimbangela kanye nezici "ezibangela" lesi simo?
I-PPP ibangelwa ukukhubazeka kwezakhi zofuzo . Kalula nje, ibangelwa ukukhubazeka kwezakhi zofuzo ezilawula iziteshi emangqamuzaneni emisipha esikhulume ngakho ngaphambili. Esikhathini esiningi, ingane izuza leli gciwane elinokukhubazeka komunye wabazali bayo. Kodwa-ke, akuvamile kakhulu ukuthi ingane ibe nalesi sifo ngisho noma abazali bengenalo leli gciwane.
Manje ake sibheke ukuthi yini engabangela lobu buthakathaka bemisipha. Lokhu kungahluka kumuntu nomuntu.
- Ukudla: Ukudla ukudla okucebile nge-potassium (ku-hyperKPP) noma i-potassium ephansi (ku-hypoKPP). Futhi, ukudla ukudla okunama-carbohydrate amaningi (isitashi/ushukela).
- Ukuzivocavoca : Uma uphumule ngemva kokuzivocavoca okunzima.
- Ukuphumula: Ukuhlala endaweni efanayo isikhathi eside, lapho uvuka ekuseni, noma ngemva kokulala.
- Ezinye izimbangela: Ukucindezeleka, ukuchayeka emakhazeni amakhulu, ukuphuza utshwala, kanye nemithi ethile (isib., imithi yokuphumula imisipha, eminye imithi ye-asthma, imithi yobuhlungu).
Yiziphi izimpawu eziyinhloko?
Uphawu oluyinhloko ubuthakathaka bemisipha obungazelelwe noma ukukhubazeka okuphelele. Lokhu kungathinta ingalo noma umlenze owodwa ngesikhathi, noma wonke umzimba ngezinye izikhathi.
Ngaphezu kwalesi sibonakaliso esiyinhloko, abanye abantu bangase babe nezinye izimpawu uma bebona lobu buthakathaka:
- Ubuthakathaka bemisipha yobuso
- Ubuhlungu bemisipha nokuqina kwayo
- Ukushaya kwenhliziyo okungajwayelekile
- Ubunzima bokuphefumula noma ukugwinya
I-HypoKPP (uhlobo lwe-potassium ephansi)
Izimpawu zingavela kaningi kanye ngosuku, noma kaningi kanye ngonyaka. Zingahlala ihora elilodwa noma amabili, noma zingahlala izinsuku ezimbili noma ezintathu. Ngokuhamba kwesikhathi, imisipha ingase ibe buthaka unomphela.
I-HyperKPP (uhlobo lwe-potassium ekhuphukile)
Ubuthakathaka bungaba bufushane, kodwa bungenzeka njalo. Izimpawu zingavela ngokuzumayo, futhi ngezinye izikhathi zihlale imizuzu embalwa. Ngisho noma kungekho buthakathaka, ungase uzizwe ukuqaqamba kwemisipha noma ukuqina.
I-Andersen-Tawil Syndrome (ATS)
Ngaphezu kobuthakathaka bemisipha, nezinye izimpawu zomzimba nazo ziyabonwa.
- Ukushaya kwenhliziyo okusheshayo noma okungajwayelekile
- I-Scoliosis
- Iminwe enezintambo
- Zincane kunezandla nezinyawo ezijwayelekile
- Izinguquko ezithile zobuso (isib., ibunzi elibanzi, izindlebe eziphansi)
Ungasithola kanjani lesi sifo ngokunembile?
Ngenxa yokuthi i-PPP iyisimo esingavamile futhi izimpawu zayo zifana nezinye izifo ezivamile, kungathatha isikhathi ukuxilonga lesi sifo ngokunembile. Ngakho-ke, uma unalezi zimpawu, kungcono ukubona udokotela ochwepheshe bezifo ezihlobene nesimiso sezinzwa (i-Neurologist) .
Udokotela wakho angase akubuze imibuzo efana nale ukuze ahlole lesi simo:
- Lezi zimpawu zaqala nini?
- Ingabe ukhona omunye emndenini onesifo esifanayo?
- Kwenzekani uma kwenzeka ubuthakathaka?
- Wake wazizwa sengathi ukudla noma isenzo esithile sibangele lokhu?
Ngaphezu kwalokho, kungenziwa izivivinyo eziningana ukuqinisekisa lesi sifo:
- Ukuhlolwa kwegazi: Hlola amazinga e-potassium, ama-hormone e-thyroid, nezinye izinto.
- I-Electromyography (EMG): Ukuhlola ukusebenza kwemisipha kanye nezinzwa.
- I-Electrocardiogram (EKG): Ukuhlola ukuhambisana kokushaya kwenhliziyo.
- Ukuhlolwa Kwemisipha: Ukuthatha ingxenye encane yomsipha bese uyihlola.
Indlela yokwelapha nokuphatha?
Ukwelashwa okuyinhloko kwalokhu ukuhlonza nokugwema izinto ezibangela lokhu. Lokhu kusho ukwenza izinguquko ezithile ekudleni kwakho kanye nokuzivocavoca umzimba.
Ngaphezu kwalokho, kunemithi yokulawula amazinga e-potassium emzimbeni.
- Umuthi i-Dichlorphenamide (Keveyis) uvunyelwe ukwelapha kokubili i-hypoKPP kanye ne-hyperKPP.
- Odokotela ngezinye izikhathi batusa nomuthi obizwa ngokuthi i-Acetazolamide (Diamox) .
- Izithasiselo ze-potassium zinikezwa labo abane-HypoKPP.
- Umuntu one-HyperKPP ngezinye izikhathi angalawula ubuthakathaka bakhe ngokuphuza isiphuzo esinoshukela (isb., i-soda) ngokushesha nje lapho siqala.
Into ebaluleke kakhulu ukuthi, ungalokothi uyeke ukuthatha noma ukuyeka imithi wedwa. Yenza konke kuphela ngokweseluleko sikadokotela wakho. Uma uzwa ubuthakathaka obukhulu obungazelelwe, ubunzima bokuphefumula, noma ubuhlungu besifuba, iya eMnyangweni Wezimo Eziphuthumayo (ETU) wesibhedlela esiseduze ngokushesha.
Ungasilawula lesi simo ngezinga elikhulu ngokwenza izinguquko ezincane endleleni yakho yokuphila.
- Ukudla: Uma une-hyperKPP (i-potassium ephezulu), kuzodingeka unciphise ukudla okune-potassium eningi njengobhanana, amadethi, i-broccoli, namakinati. Uma une-hypoKPP (i-potassium ephansi), kuzodingeka unciphise ukudla okune-carbohydrate eningi njengesinkwa, i-pasta, ilayisi, namaswidi. Thola iseluleko esifanele kudokotela wakho ngalokhu.
- Ukuzivocavoca: Njengokuzivocavoca ngokweqile, ukungazivocavoci nakho kubi. Khuluma nodokotela wakho ngezinga lokuzivocavoca elikufanele.
Umlayezo Wokuya Nawe Ekhaya
- Ukukhubazeka Okuyinhloko Kwezikhathi Ezivamile (i-PPP) akuyona nje ukukhubazeka ngokomzimba, kuyiphutha lofuzo elivela eziteshini ze-ion zamaseli emisipha.
- Kunezimbangela ezingase zibangele lesi simo. Qaphela izinto ezifana nokudla, ukuzivocavoca umzimba, kanye nokucindezeleka, bese ubona futhi ugweme izinto ezikuthintayo.
- Uma kuvela izimpawu, kubaluleke kakhulu ukubona uchwepheshe ukuze ahlole kahle lesi sifo.
- Abantu abaningi bangalawula lesi simo ngempumelelo futhi baphile impilo esebenzayo ngokushintsha indlela yokuphila kanye nemithi enikezwe udokotela wabo.
- Landela njalo iseluleko sikadokotela wakho. Ungenzi izinqumo ngokwakho, njengokuthatha imithi noma ukushintsha ukudla kwakho.
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