Miiri k’a filɛ, farigan walima kɔnɔdimi tun bɛ aw la a tile damadɔw tɛmɛnen kɔ, wa sisan aw bɛ ka kɛnɛya dɔɔni. Nka yɔrɔnin kelen i b’a ye ko i ka yeli bɛ ka jɛya dɔɔnin, i bɛ fɛnw ye yɔrɔ fila la. I b’a ye ko i tɛ sabati ni i bɛ taama, i senw bɛ siri. Ni nin ɲɔgɔnna ko dɔ kɛra, bɛɛ tun bɛna siran kosɛbɛ, tiɲɛ tɛ? Bi an bɛ kuma bana dɔ kan min bɛ nin taamasiɲɛ suguw bila mɔgɔ la, mɔgɔ caman ma min mɛn, nka a nafa ka bon kosɛbɛ k’a dɔn. O ye Miller Fisher ka bana ye.
N’an y’a fɔ cogo nɔgɔman na, Miller Fisher ka bana ye mun ye?
Miller Fisher ka bana ye hakiliɲagami bana ye min man ca kosɛbɛ. N’a sɔrɔ aw ye Guillain-Barré syndrome (GBS) ko mɛn. O fana ye bana ye min na an farikolo tangalanw bɛ bin an yɛrɛ ka nɛrɛw kan. Miller Fisher ka bana ye GBS suguya dɔ ye. A man ca fo a bɛ GBS banabagatɔ 1% ni 5% cɛ Tlebi jamanaw na. Nka, Azi jamana dɔw la i n’a fɔ Tayiwani ani Zapɔn, o hakɛ ka ca dɔɔnin. O la aw bɛ se k’a faamu ko nin tɛ don o don bana ye. Nka a nafa ka bon kosɛbɛ ka o dɔn.
Mun na o bɛ kɛ? O kunw ye mun ye?
O de ye ko ye min nafa ka bon kosɛbɛ. Miller Fisher ka bana ni GBS fila bɛɛ bɛ sɔrɔ banakisɛ dɔ jaabi la min bɛ don an farikolo la.
N’an y’a fɔ cogo nɔgɔman na, an yɛrɛ ka lafasalitɔn, n’o ye farikolo tangalan ye, o bɛ ‘jatigɛ’ dɔɔnin wa sanni a ka banakisɛ kɛlɛ, a bɛ daminɛ ka bin an yɛrɛ ka nɛrɛw kan fili la. Dɔgɔtɔrɔw t’a dɔn hali bi fɛn min bɛ nin ko in sababuya tigitigi. A ka ca a la nin taamasiɲɛ ninnu bɛ ye tile damadɔ fo dɔgɔkun 4 kɔnɔ bana dɔ kɔfɛ, kɛrɛnkɛrɛnnenya la kɔnɔdimi i n’a fɔ kɔnɔboli, walima ninakilidegun (farigan, mura). Banakisɛba min bɛ se ka nin bana in bila mɔgɔ la, o ye `Campylobacter jejuni` ye. A ka ca a la, o de bɛ kɔnɔboli ni kɔnɔboli bila mɔgɔ la. Ka fara o kan, banakisɛ dɔw fana bɛ yen minnu bɛ se ka nin bana in bila mɔgɔ la:
- Zika banakisɛ
- Hadamadenw ka farikolo tangalanw ( sida ) .
- Epstein-Barr banakisɛ, o bɛ kɛ sababu ye ka bana in sɔrɔ min bɛ i n’a fɔ sumaya, mononucleosis.
A taamasiɲɛw ye mun ye? I b’o dɔn cogo di?
mɔgɔ caman bɛ taa dɔgɔtɔrɔso la
barisa u ka yeli bɛ dɔgɔya joona tile damadɔ kɔnɔ , wa
taama ka gɛlɛn u ma . Miller Fisher ka bana taamasiɲɛba saba bɛ yen. An ka ninnu faamuya tabali dɔ kɔnɔ.
| Taamaʃyɛnba min bɛ a la | N’an y’a fɔ cogo nɔgɔman na, mun bɛ kɛ? |
|---|
| Ɲɛkisɛw fanga dɔgɔyali (Ophthalmoplegie) . | Yeli fila bɛ kɛ, wa a bɛ gɛlɛya ka ɲɛw kunbɛn ani k’u ɲɛsin sira ɲininen ma. |
| Balan bɔnɛ (Ataxia) . | N bɛ senna tiɲɛ ni n bɛ taama, n b’a ye ko n tɛ balansi la. A ka gɛlɛn ne ma ka n farikolo yɔrɔw labɛn ɲɔgɔn fɛ. |
| Areflexia (Areflexia) ye | Fɛn minnu bɛ i n’a fɔ ni dɔgɔtɔrɔ ye i gɛnɛgɛnɛ gosi ni marifa fitinin ye, i sen tɛna lamaga. Farikolo ka fɛnɲɛnamafagalanw bɛ tunun. |
Ka fara nin taamasiɲɛba saba ninnu kan, mɔgɔ dɔw bɛ se ka taamasiɲɛ wɛrɛw jira:
- Ɲɛkisɛ minnu bɛ bonya .
- Ɲɛda farikolo fanga dɔgɔyali
- Galaka fasa fanga dɔgɔyali (gag reflexe dɔgɔyali) .
Nafama : Ni nin taamasiɲɛ ninnu bɛ fara aw senkɔniw ni aw ninakili fasaw fanga dɔgɔyali kan, o bɛ se ka kɛ bana ye min bɛ wele ko GBS-MFS overlap syndrome. GBS taamasiɲɛ fɔlɔ ye barikantanya ye min bɛ daminɛ senw na ka jɛnsɛn farikolo fan bɛɛ la.
Dɔgɔtɔrɔ bɛ o bana sɛgɛsɛgɛ cogo di?
A ka gɛlɛn dɔɔni ka nin bana in sɛgɛsɛgɛ tigitigi. Sabula hakilibana caman wɛrɛw bɛ yen minnu taamasiɲɛw bɛ ɲɔgɔn ta. Misali la, banaw i n’a fɔ `Basal meningitis`, `Botulism`, `Brainstem stroke`, `Myasthenia Gravis`. O la, dɔgɔtɔrɔ bɛna aw sɛgɛsɛgɛ ka ɲɛ, ka aw ɲininka aw ka bana taamasiɲɛw ni bana minnu kɛra kɔsa in na. O kɔ, a bɛna sɛgɛsɛgɛli caman kɛ walasa ka bana in dɔn.
| Kɔrɔbɔli | N’an y’a fɔ cogo nɔgɔman na, i bɛ mun kɛ/ka mun ye n’a ye? |
|---|
| Kɔnɔbara basigilen | Aw bɛ aw kɔkolo lamini ji dɔɔni ta ka a lajɛ ni farikolojɔli dumuni caman bɛ a la. O bɛ wuli tuma caman na Miller Fisher banabagatɔw la. |
| Joli Sɛgɛsɛgɛli | Joli bɛ sɛgɛsɛgɛ ni banakisɛfagalan dɔ bɛ a la min bɛ wele ko `anti-GQ1b`, o ye bana in kɛrɛnkɛrɛnnen ye. Nin banakisɛfagalan in bɛ se ka ye banabagatɔ 95% la. |
| Nɛrɛmuguma sɛgɛsɛgɛli (EMG) . | Kuran min ka dɔgɔn kosɛbɛ, dimi tɛ min na, o bɛ kɛ ka aw farikolo ni aw farikolo yɔrɔw baara ka ɲɛ cogo min na, o jateminɛ. Nin bana in bɛ fɛn dɔw jira farikolo la. |
| MRI Scan (MRI Scan) ye | Nin sɛgɛsɛgɛli in bɛ kɛ walasa ka bana wɛrɛw bɔ kɛnɛ kan, i n’a fɔ kirinni. Miller Fisher la, a ka ca a la, MRI bɛ a jira ko a bɛ kɛ cogo bɛnnen na. |
O furakɛcogo jumɛnw bɛ yen? A bɛ waati joli ta walasa ka kɛnɛya?
A fɔlɔ, ‘fura’ kɛrɛnkɛrɛnnen tɛ yen min bɛ se ka nin bana in furakɛ pewu.
Nka, furakɛli nafamaba dɔw bɛ yen minnu bɛ se ka dɛmɛ don ka bana taamasiɲɛw kunbɛn ani ka aw dɛmɛ ka kɛnɛya joona. A ka ca a la nin taamasiɲɛ ninnu bɛ mɔgɔ min na, o tigi bɛ don dɔgɔtɔrɔso la. O ye ka GBS bana jugumanba kɔlɔsi kosɛbɛ. Sabula GBS bɛ se ka mɔgɔ ka ɲɛnamaya bila farati la tuma dɔw la. Fɛɛrɛba fila de bɛ kɛ furakɛli la: 1.
Immunoglobuline intravenous (IVIg): Nin ye fura jilama ye min bɛ i n’a fɔ kɔgɔ, a bɛ di jolisira dɔ kɔnɔ. Banakisɛfagalan saniyalenw bɛ a la minnu farala ɲɔgɔn kan ka bɔ mɔgɔ kɛnɛman ba caman joli la. O bɛ kɛ ka ban fo tile 5 ɲɔgɔn. 2.
Plasma Exchange (Plasmapheresis): Nin ye wale ye min ka gɛlɛn dɔɔni. N’an y’a fɔ cogo nɔgɔman na, joli dɔɔni bɛ bɔ i fari la, masin kɛrɛnkɛrɛnnen dɔ bɛ joli-sira-funu gɛlɛyalen bɔ (yɔrɔ min na farikolo tangalanw bɛ bin nɛrɛmuguma kan) ka o bila i yɛrɛ ka joli-sira-funu nɔ na ka fara joli-sira-funu nɔnabila kan. O bɛ kɛ siɲɛ 5 ɲɔgɔn dɔgɔkun fila kɔnɔ. Ni aw farikolo fanga dɔgɔyara kosɛbɛ nin furakɛli ninnu kɔfɛ, aw bɛ se
ka farikoloɲɛnajɛ furakɛli kɛ walasa ka fanga di u ma kokura.Wajibi don. Kɛnɛyako ta fan fɛ, a ka ca a la a bɛ dɔgɔkun 8 ni dɔgɔkun 12 cɛ walasa ka kɛnɛya ka ɲɛ.
Mɔgɔ fanba bɛ kɛnɛya pewu kalo 6 kɔnɔ. A seginni hakɛ bɛ dɔgɔya ni 3% ye. O la, bana sɛgɛsɛgɛli ni a furakɛli joona de ye fɛnw ye minnu nafa ka bon kosɛbɛ.
Take-Home cikan
- Miller Fisher ka bana ye bana ye min man teli ka sɔrɔ ni an yɛrɛ farikolo tangalanw ye an ka nɛrɛw bin ka a sababu kɛ banakisɛ dɔ ye min sɔrɔla kɔsa in na.
- A taamasiɲɛ kunbabaw ye ɲɛkisɛw fanga dɔgɔyali ye ( yelikɛcogo fila ), balansi bɔnɛni (taama gɛlɛya), ani hakilijagabɔbaliya.
- Ni aw walima aw dɔnbaga dɔ barila ka nin taamasiɲɛ ninnu sɔrɔ, aw bɛ taa dɔgɔtɔrɔso la joona. Aw kana siran, nka aw kana mɛn fana.
- Nin ye bana ye min bɛ se ka furakɛ ni dɔgɔtɔrɔso ladonni ni farikoloɲɛnajɛ ye , wa mɔgɔ fanba bɛ kɛnɛya pewu.
Miller Fisher ka bana, Guillain-Barré ka bana, Farikolo banaw, Yelibaliya, Taama gɛlɛya, GBS, farikolo tangalanw ka banaw
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