Ðe nèsea wò ŋutɔ wò gbɔgbɔ ƒe ɖiɖi, wò ŋkuwo ƒe ʋuʋu ƒe ɖiɖi, alo wò ŋutɔ wò gbe ƒe ɖiɖi si le ɖiɖim sesĩe le to me ne èle nu ƒom ɣeaɖewoɣia? Alo ɖe nèsena le ɖokuiwò me zi ɖeka be yeƒe ta le ƒoƒom le susu aɖeke manɔmee, alo ɖe nusiwo ƒo xlã wò le tsatsam abe ta si le tsatsam enea? Mègabu nusiawo be wonye ŋutilã me ɖeɖiteameŋu ko o. Elabena esiawo ate ŋu anye dɔléle aɖe si mebɔ o gake woate ŋu adae ƒe dzesiwo ne wokpɔe nyuie. Egbea, míaƒo nu tso nɔnɔme sia si woyɔna be `Superior Canal Dehiscence Syndrome`, alo `(SCDS)` kpuie ŋu.
Nukae nye `Superior Canal Dehiscence Syndrome (SCDS)`? Mina míase egɔme bɔbɔe ŋutɔ.
Kpuie ko la, SCDS nye
dɔléle si mebɔ o si gblẽa nu le wò to ememetɔ ŋu . Ate ŋu akpɔ ŋusẽ ɖe wò dadasɔ kple nusese dzi. Tsɔe be le wò to me, abe maze sue aɖe ene la, mɔ̃ etɔ̃ siwo le nyuie ŋutɔ siwo me tsi yɔ fũu la le eme. Woyɔa esiawo be tɔdzisasrã siwo le gota afã. Le mɔ̃ siawo dome, le etame, si te ɖe ahɔhɔ̃a ŋu vie la, nye tɔdzisasrã si le gota afã si le etame. Ne míeʋuʋu míaƒe ta alo le míaƒe ŋutilã ʋuʋum la, tsi si le mɔ̃ siawo me hã ʋãna kpli wo. Lãmetsi ma ƒe ʋuʋu ɖoa dzesiwo ɖe míaƒe ahɔhɔ̃ be "míaƒe ŋutilã ƒe nɔnɔme le tɔtrɔm." Ahɔhɔ̃a zãa nyatakaka siawo tsɔ kpɔa míaƒe
dadasɔ dzi . Fifia, le `SCDS` gome la,
do sue aɖe alo (dehiscence) si le sue ŋutɔ la dona le ƒu si kpɔa ame ta si ƒo xlã tɔdzisasrãa le etame (`superior semicircular canal`), si fia be, le gli sesẽ ma me. Ele abe do sue aɖe si le tsido me ene. Do sia ate ŋu ahe kuxi aɖewo vɛ le dzesiɖoɖo ma me. Azɔ hã, gbeɖiɖi siwo sɔ siwo dona le to me (le kpɔɖeŋu me, gbɔgbɔ ƒe ɖiɖi, ŋkumeʋuʋu ƒe ɖiɖi) ate ŋu ato do sia me ayi ahɔhɔ̃a me, si ana wòadze abe ɖe wole sesẽm wu ene, eye tosese ƒe kuxi bubuwo ate ŋu ado mo ɖa. Wotsɔ ŋkɔ bubu geɖewo yɔa nɔnɔme sia si woyɔna be `SCDS`, gake ŋkɔ si wozãna wu enye `SCDS`.
Aleke gbegbee `SCDS` nɔnɔme sia bɔe?
Esia nye
nɔnɔme si mebɔ kura o . Wobu akɔnta be amehawo ƒe 1% va ɖo 2% ate ŋu axɔ dɔléle sia. Ame aɖewo ateŋu akpɔ nɔnɔme sia le to eveawo me (`bilateral superior semicircular canal dehiscence`). Gake ɣemaɣi gɔ̃ hã la, zi geɖe la, wosea dzesiawo le to ɖeka me wu.
Dzesi kawoe ame si ŋu `SCDS` le ate ŋu akpɔ?
Esiae nye nu vevitɔ kekeake. Menye amesiamee ŋu dzesiawo katã dzena le o. Eyata ɣeaɖewoɣi la, ate ŋu asesẽ vie be woade dzesii pɛpɛpɛ. Nu bubue nye be ame aɖewo mate ŋu aɖe dzesi aɖeke afia o ne ƒua le sue alo do sue aɖe le eŋu gɔ̃ hã. Azɔ hã, amesiwo ƒe ƒu me do ŋutɔŋutɔ mele o, gake wole tsɛ ko la, ate ŋu akpɔ dzesi siwo sɔ kple amesiwo ŋu do le. Gake ne dzesiwo dze ƒã la, ate ŋu akpɔ ŋusẽ ɖe wò gbesiagbegbenɔnɔ dzi. Nusiwo koŋ wògblẽna le ame ŋue nye
tosese kple dadasɔ . Esia ate ŋu ahe susu me nuteɖeamedzi aɖewo hã vɛ.
Tosese ƒe kuxiwo:
- ` Autophony` : Esia nye ne èse wò ŋutɔ wò gbe, wò gbɔgbɔ ƒe ɖiɖi, wò nuɖuɖu ɖuɖu ƒe ɖiɖi, kple ɣeaɖewoɣi wò ŋkuwo ƒe ʋuʋu gɔ̃ hã ƒe ɖiɖi, sesĩe ŋutɔ eye wòdze ƒã le wò to me. Ate ŋu ase le ɖokuiwò me abe ɖe nètrɔ nuƒomɔ̃ ɖe ta me ene.
- `Hyperacusis` (hyperacusis): Nɔnɔme si me nèsea gbeɖiɖi siwo míesena zi geɖe be wosẽna ŋutɔ, wodoa dziku, eye ɣeaɖewoɣi wosea veve . Gbeɖiɖi sue aɖe gɔ̃ hã ate ŋu anye nusi dzi womate ŋu ado dzi le o.
- Pulsatile tinnitus : Gbeɖiɖi si le ɖiɖim le wò ta alo to me si wɔ ɖeka kple wò dzi ƒe tsotso (pulse) .
- Tosese ƒe Dɔmawɔmawɔ : Tosese ƒe kuxi ate ŋu adzɔ, vevietɔ ne eƒe tosese mebɔ o .
Kuxi siwo ku ɖe ŋutilã ƒe dadasɔ ŋu:
- ` Vertigo `: Seselelãme be nuwo le tsatsam, alo be èle tsatsam, ne èle tsitre ɖe teƒe ɖeka gɔ̃ hã . Esia ate ŋu anye nuteƒekpɔkpɔ si me dziɖeleameƒo le ŋutɔ eye wòdoa vɔvɔ̃ na ame.
- `Oscillopsia` (visual oscillation): Seselelãme si nye be nane si kpɔm nèle la le ʋuʋum, le dzi yim kple anyime, alo le ʋuʋum tso axa ɖeka yi axa ke, ne ele kpoo gɔ̃ hã. Ele abe fotoɖemɔ̃ aɖe si woʋuʋu esime wole video aɖe lém ene.
Vevietɔ la, `Vertigo` (taɖuame) kple `Oscillopsia` (nukpɔkpɔ ƒe ʋuʋu) ƒe nɔnɔme siawo ateŋu adzi ɖe edzi ne wole nusiwo trɔa nyaƒoɖeamenu le ta alo to me (le kpɔɖeŋu me, kɔdzidɔ sesẽ, aɖuɖɔɖɔɖɔ, nu kpekpewo kɔkɔ, nugododeƒe ƒe tsilele, kple bubuawo) kple ne wodo go toɣliɖeɖe sesẽwo . Bu eŋu kpɔ, èsusɔ vie nàkɔ agba sue aɖe eye kasia wò ta dze ƒoƒo gɔme!
Ŋusẽ si wòkpɔna ɖe susu ƒe lãmesẽ dzi:
Ne dzesi sesẽwo abe esiawo ene gakpɔtɔ li la, ate ŋu akpɔ ŋusẽ gbegblẽ ɖe wò susu ƒe lãmesẽ hã dzi.
- Taɖuame .
- `Ahɔhɔ̃ ƒe afu`:Esesẽna be nàbu tame nyuie, eye nèsena le ɖokuiwò me be yeƒe ta me mekɔ o.
- Ŋkuɖodzinyawo ƒe kuxiwo.
Ne èdze agbagba be yeanɔ adzɔge tso hadomegbenɔnɔ gbɔ eye yeanɔ aƒeme be yeasi le gbeɖiɖi kple taɖuame siawo siwo meɖea dzi ɖi o nu la,
nɔnɔmewo abe akogotsitsi, dzimaɖitsitsi, kple blanuiléle gɔ̃ hã ate ŋu ado mo ɖa.
Nukatae `SCDS` sia dzɔna? Nukawoe gbɔ wòtsona?
Le nyateƒe me la,
womenya nusi tututu gbɔ SCDS tsona haɖe o. Ate ŋu anye nusi wodzina. Eyae nye be le fugboe ƒe agbenɔɣi la, ƒu si ƒo xlã tɔdzisasrã si le etame la mekɔna nyuie o. Numekula bubuwo gblɔ be dɔléle sia ate ŋu atso
dɔlékui aɖewo alo ta ƒe abi hã gbɔ . Anɔ eme godoo be nusiwo gbɔ wòtso la wu ɖeka. Le kpɔɖeŋu me, ne wodzi wò la, teƒe tsɛ aɖe nɔa ƒua me, eye emegbe la, afɔku alo dɔlékui bubu aɖe ate ŋu ana wòatsi eye do ate ŋu ado. Alo, ƒua ate ŋu aɖiɖi vivivi ne èle tsitsim eye nɔnɔme sia va le dzɔdzɔm.
Aleke wowɔa dea dzesi SCDS nyuie?
Ne dzesi siawo le ŋuwò la, nu gbãtɔ si wòle be nàwɔe nye be nàyi ɖɔkta bibi aɖe gbɔ. Eŋutinunyala bibiwo li na nɔnɔme siawo. Zi geɖe la
, ele be nàkpɔ ahɔhɔ̃ŋutinunyala. Abia nya wò tso wò dzesiawo, alesi wodze egɔmee, kple zi nenie wova gagblẽ ɖe edzi ŋu. Emegbe aɖe gbe be woawɔ dodokpɔ geɖe atsɔ aɖe dɔléle bubu siwo bɔ siwo ƒe dzesiwo sɔ kple SCDS tɔ ɖa eye woatsɔ aɖo kpe SCDS ƒe dzesi dzi. Dodokpɔ vevi siwo wowɔnae nye:
- CT scan (Computed Tomography scan) si woɖena le ƒu siwo ƒo xlã to ŋu: Esia nye CT scan si ƒe nɔnɔme deŋgɔ. Ate ŋu akpɔe nyuie ne do alo ƒu si le ƒuƒlu ƒo xlã tɔdzisasrã si le gota afã si le etame la me.
- Tosese dodokpɔ: Toŋutinunyalae wɔa esia. Esia doa wò tosese kpɔna, vevietɔ gbeɖiɖi siwo mebɔ o.
- `VEMP` (Vestibular-Evoked Myogenic Potential) dodokpɔ: Esia ateŋu ana nyatakaka tso alesi wò to ememetɔ ƒe akpa vovovo siwo kpɔa gome le dadasɔ me le dɔ wɔm ŋu. Esia nye dodokpɔ si me vevesese aɖeke mele o. Nusi nàwɔ koe nye be nàlé ŋku ɖe miame, ɖusime, alo dziƒo esime nèle ŋku lém ɖe nusi nèdi be yeaɖo taɖodzinu na ŋu alo le to ɖom gbeɖiɖi aɖewo. Ame siwo ŋu `SCDS` le ateŋu akpɔ ŋuɖoɖo ƒe ɖoɖo tɔxɛ aɖe le `VEMP` dodokpɔ sia me.
Nukae nye atikewɔwɔ na `SCDS`?
Le ame geɖe gome la,
tɔtrɔ suesuesuewo wɔwɔ le woƒe agbenɔnɔ meÀte ŋu anɔ agbe kple nɔnɔmea ne èƒo asa na nusiwo nana nèsena le ɖokuiwò me be taɖuame kple taɖuame (oscillopsia) ye, le kpɔɖeŋu me, ne èƒo asa na nuwɔna siwo naa taɖuame kple nuwo ƒe ʋuʋu ƒe seselelãme (abe nu kpekpewo kɔklɔ, aɖuɖɔɖɔɖɔ alo kɔdzidede ene), kple ne èle adzɔge tso teƒe siwo toɣliɖeɖe le. Ame aɖewo zãa
tomeka alo tomeka tsɔ ɖea toɣliɖeɖe si wosena dzi kpɔtɔna. Azɔ hã,
kamededeŋutinunyala si wona hehee le dadasɔ me yiyi (vestibular ŋutilãmedɔdala) ate ŋu akpe ɖe ŋuwò nàkpɔ wò dzesiwo gbɔ. Woate ŋu afia kamedede wò be nàda asɔ nyuie wu eye wòaɖe afɔku si le asiwò be nàdze anyi dzi akpɔtɔ. Gake ne nu siawo mekpɔ ŋusẽ ɖe dzesiawo dzi o, alo ne dzesiawo le ŋusẽ kpɔm ɖe wò agbenɔnɔ dzi vevie la, ekema
ahiã be woawɔ dɔ na doa alo agbugbɔe ado ɖe edzi .
Amekoko na `SCDS` (`SCDS amekoko`) .
Amekoko ƒomevi vevi geɖewo li siwo wowɔna na SCDS:
- Plugging the dehiscence - Middle Cranial Fossa Mɔnu: Esia bia be woatu do si le ƒua me keŋkeŋ. Esia bia be woaɖe to sue aɖe ɖe taɖua ƒe axadzi be woate ŋu age ɖe to ememetɔ me. Zi geɖe la, to , ŋɔti, kple ŋɔti ŋuti nunyala bibi ( ENT specialist) kple ahɔhɔ̃ŋutinunyalae wɔa dɔ sia.
- Plugging the dehiscence - Transmastoid approach: Le mɔnu sia me la, wogena ɖe to ememetɔ me to ʋuƒo sue aɖe wɔwɔ le to megbe me.
- Gbugbɔgadze: Esia bia be woatsyɔ doa dzi evɔ womatue keŋkeŋ o. Esia mebɔ abe plugging ene o.
Ɣeaɖewoɣi la, ɖɔktawo ateŋu azã `plugging` kple `resurfacing` mɔnuwo siaa le amekoko me.
Kuxi kawoe ate ŋu ado tso amekoko me?
Afɔku si le kuxi gãwo me le SCDS dɔwɔwɔ vɔ megbe la le sue ŋutɔ. Abe alesi wòle le amekoko ɖesiaɖe gome ene la, afɔku sue aɖe koe li be woaxɔ dɔlékuiwo. Kuxi sue aɖewo ate ŋu anɔ dadasɔ me le kwasiɖa gbãtɔ alo esi wu nenema le amekokoa megbe, esime ŋutilãa le tɔtrɔm ɖe nɔnɔme yeyea ŋu. Gake zi geɖe la, esia nyona ɖe edzi le ŋkeke ʋɛ aɖewo megbe.
Ðe `SCDS` ƒe nɔnɔmea anyo ɖe edzi le eɖokui sia?
Ao,
SCDS medaa gbe le eɖokui si amekoko manɔmee o. To vovo na ƒu bubu siwo le míaƒe ŋutilã me la, ƒu si ƒo xlã tɔdzisasrã si le gota afã si le etame la medaa gbe le eɖokui si o. Ne èle mɔ siwo dzi nàto akpɔ wò dzesiwo gbɔ srɔ̃m la, àte ŋu akpɔ gbɔdzɔe aɖe. Gake SCDS madzo keŋkeŋ ne womewɔ atike nɛ o.
Aleke gbegbee `SCDS` ƒe amekokoa kpɔ dzidzedzee?
Ame geɖewo ƒe dzesiwo dzi ɖena kpɔtɔna alo woɖea wo ɖa keŋkeŋ to `SCDS` amekoko me.Numekuku aɖewo ɖee fia be dzesi aɖewo nyona ɖe edzi kabakaba le amekoko megbe wu bubuwo. Le kpɔɖeŋu me, tosese, autophone, pulsatile tinnitus, kple vertigo ate ŋu anyo ɖe edzi kabakaba. Gake taɖuame kple ahɔhɔ̃ me kuɖiɖi ate ŋu axɔ ɣeyiɣi didi hafi wòanyo ɖe edzi. Ƒo nu tso amekokoa me tsonu ŋu na wò ɖɔkta, le wò dzesiwo kple doa ƒe lolome nu.
Aleke mawɔ akpɔ ɖokuinye dzi kple nɔnɔme sia?
Ne wokpɔe be SCDS le ŋuwò la, ele vevie be nàwɔ ɖe wò ɖɔkta ƒe mɔfiamewo dzi. Le go geɖe me la, woate ŋu akpɔ dzesiawo gbɔ to tɔtrɔwɔwɔ le agbenɔnɔ me. Nu siwo nàte ŋu awɔ dometɔ aɖewoe nye esi:
- Tomekawo zazã .
- Ƒo asa na nuto siwo me toɣliɖeɖe le ɣesiaɣi si wòanya wɔ.
- Ne wò gbe ɖi vevesese na wò la, ƒo nu blewu (`ɣlidodo`).
- Ƒo asa na nuwɔna siwo gblẽa nu le dadasɔ ŋu, abe kpekpeme kɔkɔ ene.
- Ƒo asa na dɔwɔna siwo ate ŋu atrɔ to ƒe nyaƒoɖeamenu (e.g., yameʋuɖoɖo) alesi nàte ŋui.
- Le dɔwɔƒe la, ne anya wɔ la, bia be woana teƒe si tomefafa le, si me ame aɖeke mele o tsɔ wu be nànɔ teƒe si amewo katã anɔ .
Ðo ŋku edzi be menye wò ɖeka koe o. Enye nusi sɔ be nàse seselelãme ƒe fuɖename aɖewo ne èle agbe kple nɔnɔme sia tɔgbe. Ne ehiã la, ƒo nu tso eŋu na wò ɖɔkta.
Mlɔeba la, nusiwo dzi wòle be woaɖo ŋkui (Take-Home Message) .
Ne wokpɔ dɔléle si nye Superior Canal Dehiscence Syndrome (SCDS) le ŋuwò la, mègatsi dzodzodzoe o.
Ame geɖe kpɔa woƒe dzesiwo gbɔ to tɔtrɔ le agbenɔnɔ me. Wò ɖɔkta aɖo aɖaŋu na wò be mɔ siwo dzi nàto akpe ɖe ŋuwò nàxe mɔ ɖe dzesi siwo gblẽa nu le wò dadasɔ kple/alo tosese ŋu be woagagblẽ ɖe edzi o. Le go aɖewo me la, ne wò dzesiawo nu sẽ la,
amekoko ate ŋu axe do si le ƒua me eye wòaɖe dzesiawo dzi akpɔtɔ alo aɖe wo ɖa. Ðo dze kple wò ɖɔkta tso atikewɔmɔnu nyuitɔ kekeake si nàte ŋu azã ŋu.
Ðo ŋku edzi be ne èkpɔ dɔlélea nyuie eye nèdae nyuie la, ate ŋu akpe ɖe ŋuwò nàkpɔ gbɔdzɔe.
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