Tsɔe be dzamezã alo dɔgbo nɔ veve sem ŋkeke ʋɛ aɖewoe nye esi va yi eye wò lãme sẽ vie fifia. Gake kasia nèsena le ɖokuiwò me be yeƒe ŋkuwo me mekɔ vie o, èkpɔa nuwo le akpa eve me. Èsena le ɖokuiwò me be yemeli ke o ne èle zɔzɔm, wò afɔwo xaxana. Ne nane si le abe esia ene dzɔ la, ame sia ame avɔ̃ ŋutɔ, alo? Egbea míele nu ƒom tso nɔnɔme aɖe si hea dzesiwo abe esia ene vɛ, si ame geɖe mese kpɔ o, gake ele vevie ŋutɔ be woanya. Emae nye Miller Fisher Dɔléle.
Kpuie ko la, nukae nye Miller Fisher Dɔlélea?
Miller Fisher ƒe dɔlélea nye ahɔhɔ̃mekawo ƒe dɔléle si mebɔ kura o. Ðewohĩ èse Guillain-Barré ƒe dɔléle (GBS) ŋu nya kpɔ. Enye dɔléle si me míaƒe dɔlélenutsiŋutete dzea mía ŋutɔwo ƒe lãmekawo dzi le hã. Miller Fisher ƒe dɔlélea nye GBS ƒe tɔtrɔ aɖe. Ƒã ale gbegbe be wòdzea GBS dɔnɔ siwo le Ɣetoɖoƒedukɔwo me ƒe 1% va ɖo 5% dzi. Gake le Asia-dukɔ aɖewo abe Taiwan kple Japan ene me la, xexlẽmea sɔ gbɔ vie wu. Eyata àte ŋu ase egɔme be menye gbesiagbedɔlélee nye esia o. Gake ele vevie ŋutɔ be nànya esia.
Nukatae esia dzɔna ɖo? Nukawoe nye susu siwo tae?
Esiae nye nu vevitɔ kekeake. Miller Fisher ƒe dɔlélea kple GBS siaa dzɔna le dɔlékui aɖe si gena ɖe míaƒe ŋutilã me ta.
Kpuie ko la, mía ŋutɔwo ƒe ametakpɔnu, si nye dɔlélenutsiŋutete, ‘tɔtɔna’ vie eye le esi teƒe be wòawɔ avu kple dɔlékuia la, edzea mía ŋutɔwo ƒe lãmekawo dzi dzedze gɔme vodadatɔe. Ðɔktawo menya nusi tututu hea esia vɛ haɖe o. Zi geɖe la, dzesi siawo dzena le ŋkeke ʋee aɖewo va ɖo kwasiɖa 4 me le dɔléle aɖe megbe, vevietɔ dɔgbo ƒe vevesese abe aɖuɖɔtoe, alo gbɔgbɔtsixetsixe (vuvɔ, asrã). Dɔlékui vevitɔ si ateŋu ahe nɔnɔme sia vɛ enye `Campylobacter jejuni`. Esiae nye nusi hea dɔgbo ƒe ʋuʋu kple aɖuɖɔtoe vɛ zi geɖe. Tsɔ kpe ɖe eŋu la, dɔlékui aɖewo hã li siwo ate ŋu ahe nɔnɔme sia vɛ:
- Zika dɔlékui aɖe
- Amegbetɔ ƒe Dɔlélenutsiŋutete ƒe Dɔlékui ( HIV ) .
- Epstein-Barr dɔlékui, si hea dɔléle si le abe asrã ene si nye mononucleosis vɛ.
Nukawoe nye dzesiawo? Aleke nèwɔ de dzesi esia?
Ame geɖe yia ɖɔkta gbɔ
elabena woƒe ŋku dzi ɖena kpɔtɔna kabakaba le ŋkeke ʋɛ aɖewo ko me eye
azɔlizɔzɔ sesẽna na wo . Miller Fisher ƒe dɔlélea ƒe dzesi vevi etɔ̃e li. Mina míase esiawo gɔme le kplɔ̃ dzi.
| Dzesi vevitɔ | Kpuie ko la, nukae dzɔna? |
|---|
| Ŋku ƒe lãmekawo ƒe gbɔdzɔgbɔdzɔ (Ophthalmoplegia) . | Nukpɔkpɔ eve dzɔna, eye eva sesẽna be woaɖu ŋkuawo dzi ahafia mɔ wo ɖe mɔ si wodi nu. |
| Dadasɔ ƒe bu (Ataxia) . | Meklia nu ne mele zɔzɔm, mesena le ɖokuinye me be nyemeda sɔ o. Esesẽna nam be mawɔ ɖeka kple nye abɔwo kple afɔwo. |
| Areflexia ƒe dɔléle | Nuwo abe ne ɖɔktaa tsɔ akplɔ sue aɖe ƒo wò klo la, wò afɔ maʋuʋu o. Ŋutilãa ƒe nuŋububu ƒe ŋutetewo bu. |
Tsɔ kpe ɖe dzesi vevi etɔ̃ siawo ŋu la, ame aɖewo ate ŋu aɖe dzesi bubuwo afia:
Vevietɔ: Ne gbɔdzɔgbɔdzɔ kpe ɖe dzesi siawo ŋu le wò abɔwo kple gbɔgbɔ ƒe lãmekawo me la, ate ŋu anye nɔnɔme si woyɔna be GBS-MFS overlap syndrome. GBS ƒe dzesi vevitɔe nye gbɔdzɔgbɔdzɔ si dzea egɔme tso afɔwo me eye wòkakana ɖe ŋutilã bliboa me.
Aleke ɖɔkta awɔ anya esia?
Esesẽ vie be woanya dɔléle sia pɛpɛpɛ. Elabena ahɔhɔ̃medɔléle bubu geɖewo li siwo ƒe dzesiwo sɔ kple wo nɔewo. Le kpɔɖeŋu me, dɔlélewo abe `Basal meningitis`, `Botulism`, `Ahɔhɔ̃ ƒe ʋusɔgbɔdɔ`, `Myasthenia Gravis`. Eyata ɖɔkta la ado wò kpɔ nyuie, abia wò dzesiwo kple dɔléle siwo nèdze nyitsɔ laa. Emegbe, awɔ dodokpɔ geɖe atsɔ aɖo kpe dɔlélea dzi.
| Dodokpɔ | Kpuie ko la, nukae nèwɔna/kpɔnɛ kplii? |
|---|
| Akɔta ƒe ʋuʋu | Woxɔa tsi si ƒo xlã wò aklã (ahɔhɔ̃ me tsi) ƒe agbɔsɔsɔ sue aɖe eye wokpɔa egbɔ be protein sɔ gbɔ ɖe eme hã. Zi geɖe la, esia dzina ɖe edzi le Miller Fisher dɔnɔwo me. |
| Ʋudodokpɔ | Wodoa ʋua kpɔna be dɔlékuiwutike aɖe si woyɔna be `anti-GQ1b`, si nye dɔléle sia koŋ le eme hã. Woateŋu akpɔ dɔlékuiwutike sia le dɔnɔ 95% me. |
| Lãmetsiŋusẽ ƒe Ʋuʋu Ŋuti Numekuku (EMG) . | Wozãa elektrikŋusẽ sue aɖe ŋutɔ si me vevesese mele o tsɔ dzidzea alesi wò lãmekawo kple lãmekawo le dɔ wɔm nyuie. Dɔléle sia ɖea nusiwo mesɔ o aɖewo fiana le lãmekawo me. |
| MRI Scan ƒe Dɔwɔɖoɖo | Wowɔa dodokpɔ sia be woatsɔ aɖe nɔnɔme bubuwo, abe ʋusɔgbɔdɔ ene, ɖa. Le Miller Fisher gome la, zi geɖe la, MRI ɖea emetsonu siwo sɔ fiana. |
Nukawoe nye atike siwo wozãna na esia? Ɣeyiɣi didi kae wòxɔna hafi wòhayana?
Gbã la, ‘atike’ aɖeke koŋ meli si ate ŋu ada dɔléle sia keŋkeŋ o.
Gake atikewɔmɔnu siwo wɔa dɔ ŋutɔ li siwo ate ŋu akpe ɖe ŋuwò nàɖu dzesiawo dzi eye wòakpe ɖe ŋuwò nàhaya kaba. Zi geɖe la, woxɔa ame si ŋu dzesi siawo le la ɖe kɔdzi. Esia nye be woalé ŋku ɖe GBS dɔléle sesẽwo ŋu nyuie. Elabena GBS ate ŋu ade ame ƒe agbe afɔku me ɣeaɖewoɣi. Wozãa mɔnu vevi eve abe atikewɔwɔ ene: 1.
Intravenous Immunoglobulin (IVIg): Esia nye atike si nye tsi si le abe dze ene si wotsɔ dea ʋuka me. Dɔlékuiwutike siwo ŋu wokɔ siwo woɖe ɖe vovo tso ame akpe geɖe siwo le lãmesẽ me ƒe ʋumenugbagbeviɣi me la le eme. Wotsɔa esia naa ame madzudzɔmadzudzɔe abe ŋkeke 5 ene. 2.
Plasma Exchange (Plasmapheresis): Esia nye nusi sesẽ vie. Kpuie ko la, woɖea ʋu sue aɖe le wò ŋutilã me, mɔ̃ tɔxɛ aɖe ɖea ʋumenugbagbevi dzĩ si ŋu kuxi le (akpa si me dɔlékuiwutike siwo dzea lãmekawo dzi le) ɖa eye wòtsɔa wò ŋutɔ wò ʋumenugbagbeviwo tsɔ kpe ɖe ʋumenugbagbevi dzĩwo ɖɔliɖɔli ŋu. Wowɔa esia abe zi 5 ene le kwasiɖa eve ƒe ɣeyiɣi aɖe me. Ne wò lãmekawo gbɔdzɔ ŋutɔ le atikewɔwɔ siawo megbe la, ɖewohĩ
ahiã be woawɔ kamedede be nàgado ŋusẽ wo ake.Ehiã. Le hayahaya gome la, zi geɖe la, exɔa kwasiɖa 8 va ɖo 12 hafi wòhaya nyuie.
Ame akpa gãtɔ hayana keŋkeŋ le ɣleti 6 me. Alesi wògadzɔna ake la mede 3% o. Eyata dɔlélea didi kaba kple edadae nye nu vevitɔ kekeake.
Gbedasi si Wotsɔ Yi Aƒeme
- Miller Fisher ƒe dɔlélea nye dɔléle si mebɔ o si dzɔna ne mía ŋutɔwo ƒe dɔlélenutsiŋutete dze míaƒe lãmekawo dzi le dɔléle aɖe si míexɔ nyitsɔ laa ta.
- Dzesi vevitɔwoe nye ŋku ƒe lãmekawo ƒe gbɔdzɔgbɔdzɔ ( nukpɔkpɔ zi eve ), dadasɔ ƒe anyimanɔmanɔ (azɔlizɔzɔ sesẽna), kple ŋku ƒe lãmekawo ƒe gbɔdzɔgbɔdzɔ.
- Ne dzesi siawo dze wò alo ame aɖe si nènya la dzi kpata la, yi ɖɔkta gbɔ enumake. Mègatsi dzodzodzoe o, gake mègahe ɖe megbe hã o.
- Esia nye nɔnɔme si woate ŋu ada to kɔdziyiyi kple kamedede , eye ame akpa gãtɔ hayana bliboe.
Miller Fisher Dɔléle, Guillain-Barré ƒe dɔléle, Ahɔhɔ̃mekawo ƒe dɔlélewo, Nukpɔkpɔ ƒe bu, Azɔlizɔzɔ sesẽ, GBS, Dɔlélenutsiŋutete ƒe dɔlélewo
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