Ke manaʻo nei hoʻi ʻoe i ka luhi a me ka luhi loa i ka lā a pau me ke kumu ʻole? Ke manaʻo nei ʻoe ʻaʻohe ou ikaika? A i ʻole ke emi nei kou kaumaha me ka nalowale o ka makemake? ʻOiai ke manaʻo pinepine nei mākou i kēia mau mea he luhi maʻamau, i kekahi manawa hiki i kēia ke lilo i hōʻailona o kahi mea ʻoi aku ka koʻikoʻi. ʻO ia ke kūlana a mākou e kamaʻilio nei i kēia lā, ʻo ka maʻi ʻo Addison. Mai hopohopo, e kamaʻilio mākou e pili ana i nā mea āpau ma nā ʻōlelo maʻalahi.
I ka ʻōlelo maʻalahi, he aha ka maʻi ʻo Addison?
E noʻonoʻo he hale hana paʻakikī a kupaianaha ko kākou kino. Ma kēia hale hana, aia kahi hui o nā ʻelele kemika e mālama i nā mea āpau i ke kaulike a me ka holo pono. Kāhea mākou iā lākou
he mau hormones . Ma luna pono o ko mākou mau puʻupaʻa, aia ʻelua mau kelepa liʻiliʻi, kapa mākou iā lākou
he mau kelepa adrenal . Hoʻopuka kēia mau kelepa liʻiliʻi ʻelua i kekahi mau ʻano hormones e pono ai no ko mākou ola. No laila, inā no kekahi kumu ʻaʻole hiki i kēia mau kelepa adrenal ke hana i ka nui o nā hormones e pono ai, ʻo ia ka mea a mākou e kapa nei he Maʻi Addison a i ʻole ka Adrenal Insufficiency mua. He ʻano kakaikahi loa kēia. Hoʻopilikia ia i hoʻokahi i loko o hoʻokahi miliona mau kānaka. Akā ʻo ka mea maikaʻi loa,
inā ua ʻike pololei ʻia ʻoe a lawe i ka lāʻau lapaʻau i kuhikuhi ʻia e ke kauka, hiki iā ʻoe ke ola i ke ola maʻamau me ka ʻole o nā pilikia. E aʻo kākou e pili ana i ʻelua o nā hormones koʻikoʻi loa.
ʻElua ʻano nui o nā hormones i hoʻemi ʻia i loko o ke kino i ka maʻi ʻo Addison. 1.
Cortisol: Ua kapa ʻia hoʻi kēia ʻo ka 'hormone stress'. Hoʻohana ʻia kēia hormone e hoʻomākaukau i ke kino e hana me ke kaumaha, inā noʻonoʻo a kino paha. Eia kekahi, kōkua ia i ka hoʻomalu ʻana
i ke koko a pehea e hoʻohana ai ke kino i ka protein, nā carbohydrates, a me ka momona. 2.
Aldosterone: Hoʻomalu kēia hormone i ka paʻakai (sodium) a me ka potassium i loko o ke kino ma o ko mākou mau puʻupaʻa. Inā ʻaʻole hana pono ʻia kēia, e emi ana nā pae paʻakai i loko o ke kino a hoʻomaka ke koko e hāʻule.
He aha nā hōʻailona o ka maʻi ʻo Addison?
ʻIke mālie ʻia nā hōʻailona o kēia maʻi, lohi loa. No laila, i kekahi manawa he manawa ka manawa e ʻike ai i ka maʻi. ʻOiai ua like ka nui o kēia mau hōʻailona me nā maʻi ʻē aʻe, he mea nui loa ke ʻike ʻana i ke kauka e hana i kahi
hōʻailona pololei.
| Hōʻailona | He wehewehe maʻalahi o ka mea e hana nei |
|---|
| Luhi mau a me ka nāwaliwali o nā ʻiʻo | Ka luhi nui a me ka manaʻo o ke ola ʻole ʻoiai me ka hana ʻole ʻana i kekahi mea. |
| Ka nalowale o ka makemake a me ka pohō kaumaha | Ka nalowale o ka makemake e ʻai, e hopena ana i ka emi mālie o ke kaumaha. |
| ʻEleʻele o ka ʻili (Hyperpigmentation) | ʻO ke kala ʻeleʻele/ʻeleʻele o ka ʻili ma nā wahi i hōʻike ʻia i ka lā a me nā mea i hōʻike ʻole ʻia. Hiki ke ʻike ʻia kēia loli ma ka lae, nā kuli, nā kuʻekuʻe lima, nā ʻōpala, nā laina lahilahi, a me nā ʻāʻī. |
| Ke koko haʻahaʻa (Hypotension) | Ke koko haʻahaʻa. Hiki i kēia ke hoʻoulu i ka poniuniu a me ka māʻule ʻana, ʻoiai ke kū i luna. |
| Makemake nui i ka paʻakai | I ka lawe ʻia ʻana o ka paʻakai mai ke kino aku, aia ka makemake mau e ʻai i nā meaʻai paʻakai. |
| Nā hiʻohiʻona ʻē aʻe | Haʻahaʻa ke kō koko (Hypoglycemia), nausea, luaʻi, ʻeha o ka ʻōpū, diarrhea, hiki ʻole ke hoʻomanawanui i ke kaumaha, ka huhū, ka maloʻo o ka wai, a me ka ʻeha o nā hono. |
He mea nui: Hiki ke hana ʻia kēia mau hōʻailona e nā maʻi ʻē aʻe. No laila, inā loaʻa iā ʻoe kekahi mea e like me kēia, e ʻike pono i kāu kauka ʻohana no ka ʻōlelo aʻo.
He aha nā kumu o ka maʻi ʻo Addison?
ʻO ke kumu nui a maʻamau o kēia,
he maʻi autoimmune . I ka ʻōlelo maʻalahi, hoʻouka hewa ka ʻōnaehana pale o ko mākou kino (ʻōnaehana pale) a luku i kā mākou mau kelepa adrenal ponoʻī. ʻO kēia ke kumu o kahi 70% o nā hihia. Eia kekahi, aia paha nā kumu ʻē aʻe.
- Nā maʻi: Tuberculosis ,ʻO nā maʻi koʻikoʻi a lōʻihi, e like me ka maʻi HIV a me kekahi mau maʻi fungal, hiki ke hōʻino i nā kelepa adrenal .
- Kanesa: Hiki i nā hunaola kanesa mai kahi ʻē aʻe ke laha i nā kelepa adrenal (he mea kākaʻikahi loa kēia).
- Ke kahe koko kūloko: Ke kahe koko ʻana i loko o nā kelepa adrenal.
- Nā kumu hoʻoilina: Aia kekahi pilikia o ka hoʻomohala ʻana i kēia maʻi ma muli o kekahi mau kūlana hoʻoilina.
- ʻOki kino: Nā mea e like me ke ʻoki kino e wehe ai i nā kelepa adrenal.
Pehea e ʻike ai ke kauka i kēia maʻi?
Ke hele ʻoe e ʻike i ke kauka, e hoʻolohe pono ʻo ia i kāu mau hōʻailona a nānā i kou kino, e ʻimi pono ana i nā ʻano ʻeleʻele ma kou ʻili a me kou ʻāʻī. A laila, e hana lākou i kekahi mau hoʻokolohua e hōʻoia i ka hōʻailona.
- Nā hoʻāʻo koko: Nānā kēia i nā pae o ka sodium (paʻakai), potassium, a me nā hormones cortisol i loko o ke kino. I ka maʻi ʻo Addison, haʻahaʻa paha nā pae sodium a kiʻekiʻe paha nā pae potassium.
- Hoʻāʻo hoʻoulu ACTH: ʻO kēia ka hoʻāʻo nui i hoʻohana ʻia e ʻike i ka maʻi. Ma kēia hoʻāʻo, hāʻawi ʻia kahi hormone i kapa ʻia ʻo ACTH, kahi i hoʻokuʻu ʻia mai ka lolo, ma ke ʻano he inikini, a laila ana ʻia ka pae cortisol i loko o ke koko. I ke kanaka olakino, kiʻekiʻe nā pae cortisol. Eia nō naʻe, i loko o ke kanaka me ka maʻi ʻo Addison, ʻaʻole hana nā kelepa adrenal, no laila e haʻahaʻa mau ana nā pae cortisol.
- Nā hoʻokolohua ʻē aʻe: I kekahi manawa, hiki ke hana ʻia kahi CT scan e nānā no ka maʻi, ke kanesa, a i ʻole ke kahe koko ʻana i loko o nā kelepa adrenal.
Ka mālama ʻana a me ka hoʻokele ʻana
ʻO ka maʻi ʻo Addison kahi hemahema o ka hormone i loko o ke kino, a ʻo ka lāʻau lapaʻau, ʻo ia ka hāʻawi ʻana i nā hormones hemahema i waho. He mea kēia e pono e hana ʻia i ke ola holoʻokoʻa.
- Nā papa Hydrocortisone: Pono e lawe ʻia kēia i kēlā me kēia lā e pani i ka hormone cortisol.
- Nā papa Fludrocortisone: Pono e lawe ʻia kēia mau mea i kēlā me kēia lā e pani i ka hormone aldosterone.
ʻO ka mea nui loa, ʻo ia ka lawe ʻana i ka lāʻau i kuhikuhi ʻia e kāu kauka, i ka manawa kūpono, me ka ʻole o ka hala ʻana i hoʻokahi lā. Hiki ke hoʻoweliweli ka hala ʻana o hoʻokahi lāʻau.
Inā ʻoe ma lalo o ke kaumaha, e like me ka maʻi, ke ʻoki kino, a i ʻole kahi ulia, pono paha e hoʻonui ʻia kāu nui o kēia lāʻau. E hoʻomaopopo kāu kauka iā ʻoe e pili ana i kēia.
ʻO ka pilikia weliweli loa: ʻO ka pilikia Addisonian
ʻO kēia
ka pilikia koʻikoʻi loa a hoʻoweliweli hoʻi i ke ola e hiki ke hana ma ka maʻi ʻo Addison.Ke kaumaha nui ke kino (e.g., kahi maʻi nui, kahi ulia, ʻoki kino), ʻaʻole hiki i ke kino ke hoʻomanawanui ma muli o nā pae hormone haʻahaʻa. A laila lilo koke nā hōʻailona i mea koʻikoʻi.
Nā hōʻailona o kahi pilikia Addisonian:- ʻEha koke a koʻikoʻi hoʻi ma ke kua, ka ʻōpū, a i ʻole nā wāwae
- ka luaʻi nui a me ka maʻi pahū, e hopena ana i ka dehydration
- ʻO ka haʻalulu i hoʻokumu ʻia e ke koko haʻahaʻa loa
- Nalowale o ka ʻike
- Ke kuni nui a me ka nāwaliwali
Inā loaʻa kekahi o kēia mau hōʻailona, he pilikia olakino ia. Pono e lawe koke ʻia ka mea maʻi i ka Emergency Treatment Unit (ETU) o ka haukapila kokoke loa. Leka Lawe-Home
- ʻOiai he maʻi ola ke ʻano o ka maʻi ʻo Addison, me ka mālama kūpono, hiki ke ola i kahi ola maʻamau a olakino hoʻi .
- Mai hoʻowahāwahā i nā hōʻailona e like me ka luhi mau, ka ʻili ʻeleʻele, ka nalowale o ka makemake, a me ka pohō kaumaha. E kamaʻilio me kāu kauka e pili ana i ia mea.
- Mai poina i kahi mahele lāʻau i kuhikuhi ʻia e kāu kauka. E mālama mau i nā lāʻau keu me ʻoe.
- E kau mau i kahi kāleka ID lapaʻau a kūpeʻe lima paha e hōʻike ana he maʻi ʻo Addison kou. Hiki iā ia ke kōkua i ka hoʻopakele ʻana i kou ola i ka wā pilikia.
- E hoʻomaopopo he pilikia olakino ka pilikia Addisonian . He mea nui iā ʻoe a me kou ʻohana e makaʻala i kona mau hōʻailona.
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