Ke luhi mau nei ʻoe, a luhi loa paha? I kekahi manawa, ke manaʻo nei ʻoe he paʻakikī iki kou hanu ʻana, a ke kuʻi wikiwiki nei paha kou umauma? Ua haʻi aku anei kekahi iā ʻoe ua melemele iki ke kala o kou ʻili a me ke keʻokeʻo o kou mau maka? Hiki i kēia mau mea ke lilo i mau hōʻailona o kahi maʻi i kapa ʻia ʻo Hemolytic Anemia, a mākou e kamaʻilio nei i kēia lā. Mai hopohopo, e kamaʻilio mākou e pili ana i kēia i kēia lā ma ke ʻano pololei a maʻalahi. No ka mea, he mea nui loa ka ʻike ʻana i kēia maʻi no ʻoe a me kou ʻohana.
He aha ka Anemia Hemolytic? I ka ʻōlelo maʻalahi...
Aia i loko o ko kākou koko kekahi ʻano o nā ʻāpana i kapa ʻia he mau ʻāpana koko ʻulaʻula. ʻO kēia ka mea a kākou e kapa aku nei he `(Nā ʻĀpana Koko ʻUlaʻula)`. Lawe kēia mau ʻāpana koko ʻulaʻula i ka oxygen ma loko o ko kākou kino. E noʻonoʻo, ua like lākou me nā kalaka liʻiliʻi e hāʻawi ana i ka oxygen i nā ʻāpana a pau o ko kākou kino. ʻO ka maʻamau, ola kahi ʻāpana koko ʻulaʻula i loko o ke kino o ke kanaka olakino no kahi o 120 mau lā. Ma hope o kēlā, make lākou, a hoʻokumu ʻia nā ʻāpana hou ma ko lākou wahi. ʻO kēia ke kaʻina hana maʻamau.
Eia nō naʻe, i loko o ke kūlana i kapa ʻia ʻo Hemolytic Anemia, haki kēia mau hunaola koko ʻulaʻula a luku ʻia paha ma mua o ko lākou manawa kūpono, ʻo ia hoʻi, ma mua o 120 mau lā. He aha ka mea e hana ai? ʻAʻole hiki i ko kākou iwi iwi (kahi i loko o nā iwi e hana ai i kēia mau hunaola) ke hana i nā hunaola koko ʻulaʻula hou e hoʻopiha ai i ka hemahema, ʻo ia hoʻi, ua luku koke ʻia nā hunaola ma mua o ka hana ʻia ʻana. ʻO ia ka manawa e emi ai ka helu o nā hunaola koko ʻulaʻula i loko o ke kino, a loaʻa ka anemia, ʻo ia hoʻi ka nele o ke koko i loko o ke kino. ʻO ka anemia hemolytic kahi ʻano anemia e kū mai ana ma muli o ka haki wikiwiki ʻana o nā hunaola koko ʻulaʻula.
Aia kekahi mau ʻano ʻē aʻe o ka anemia?
ʻAe, aia kekahi mau kumu o ka anemia, a i ʻole ka mea a mākou e kapa nei he "helu koko haʻahaʻa."
- I kekahi manawa, ke nalowale ke koko nui o ke kino ma muli o kahi ʻeha a maʻi paha, hiki ke emi nā hunaola koko ʻulaʻula.
- I nā manawa ʻē aʻe, hiki ke hana ʻia ka anemia ma muli o ka emi ʻana o ka hana ʻana o nā cell koko ʻulaʻula a i ʻole ke kūkulu kūpono ʻole ʻia, e like me ka nele o ka hao.
ʻOi aku ka liʻiliʻi o ka maʻamau o ka anemia hemolytic ma mua o nā anemia i hoʻokumu ʻia e kēia mau kumu ʻē aʻe, akā he kūlana nō hoʻi ia e pono ai mākou e hopohopo.
He aha ka mea e hana inā ʻaʻole mālama ʻia ka anemia hemolytic?
He mea nui loa kēia. Manaʻo paha kekahi poʻe, "Auē, he aha ka mea e hana inā emi iki ke koko i loko o kou kino?" Eia nō naʻe, inā lilo ka anemia hemolytic i mea koʻikoʻi a ʻaʻole mālama pono ʻia, hiki iā ia ke hana i nā pilikia puʻuwai koʻikoʻi.
ʻO ke ʻano kēia, hiki i kēia kūlana ke koʻikoʻi, a hiki ke alakaʻi i ka hāʻule ʻana o ka puʻuwai, e like me ka arrhythmia, cardiomyopathy, a me ka hāʻule ʻana o ka puʻuwai. ʻO ia ke kumu ʻaʻole ia he manaʻo maikaʻi e lawe māmā i kēia.
ʻO wai ka mea hiki ke hoʻomohala i kēia maʻi?
Aia kekahi mau ʻano o ka anemia hemolytic. Hiki i kekahi o kēia mau ʻano ke hoʻopilikia i kekahi, i kēlā me kēia makahiki, o kēlā me kēia lāhui, a me ka nānā ʻole i ke kāne.No laila, mai manaʻo ʻoe, "ʻAʻole ia e hiki mai iaʻu." He mea maikaʻi no kākou a pau e ʻike i kēia.
He aha ka ʻokoʻa ma waena o ka Anemia Hemolytic a me ka Anemia Hemolytic Autoimmune (AIHA)?
E wehewehe iki kākou i kēia. ʻO ka Autoimmune Hemolytic Anemia (AIHA) kahi kūlana kahi e kuhi hewa ai ko kākou ʻōnaehana pale ponoʻī (ka ʻōnaehana e pale aku iā kākou mai ka maʻi) i ko kākou mau hunaola koko ʻulaʻula ponoʻī he "ʻenemi". A laila hana ia i nā antibodies e luku i kēlā mau hunaola. ʻO kēia ke kumu o ka haki ʻana o nā hunaola koko ʻulaʻula a hoʻoulu i ka anemia.
I ka wā e pili ana i ka anemia hemolytic laulā, hiki ke hana ʻia e nā kumu like ʻole, me nā genetics, nā maʻi, a me kekahi mau lāʻau lapaʻau. ʻO ka `AIHA` kahi ʻano kikoʻī o ka anemia hemolytic.
He aha nā kumu o ka Anemia Hemolytic?
Aia kekahi mau kumu nui e kōkua ana i kēia kūlana. E nānā kākou iā lākou pākahi.
1. Nā Kūlana Hoʻoilina
I kekahi manawa hiki ke lilo kēia i mea hoʻoilina, ʻo ia hoʻi he mea ia e hele mai ana mai kēlā hanauna a i kēia hanauna.
- ʻO ka Anemia Kelepona Sickle: He ʻano kēia kahi i ʻole poepoe ai nā hunaola koko ʻulaʻula, akā, e like me ke ʻano sickle me ke ʻano ʻē. Hoʻopaʻa ʻia kēia mau hunaola ʻē i loko o nā kīʻaha koko liʻiliʻi o ka spleen a haki maʻalahi.
- Thalassemia: He maʻi koko hoʻoilina nō hoʻi kēia. I kēia hihia, hana pū ke kino i nā hunaola koko ʻulaʻula ʻē. Hoʻopau koke ʻia lākou. Ua ʻike paha ʻoe aia kekahi poʻe maʻi thalassemia ma ko mākou ʻāina.
- Ka hemahema o ka G6PD: He kūlana hoʻoilina kēia. ʻO ka G6PD kahi enzyme e pale ana i nā hunaola koko ʻulaʻula. Ke haʻahaʻa kēia enzyme, e haki maʻalahi nā hunaola koko ʻulaʻula ke hōʻike ʻia i kekahi mau maʻi a i ʻole nā lāʻau lapaʻau.
2. Nā maʻi
Hiki ke hana ʻia ka anemia hemolytic e kekahi mau maʻi, e like me nā maʻi.
- Malaria: I loko o kēia maʻi i lawe ʻia e nā makika, komo nā parasites malaria i loko o ko kākou koko. Inā ʻaʻole mālama pono ʻia, hiki i ka malaria ke hana i ka anemia hemolytic.
- ʻO ka maʻi kuni mauna pōhaku: He maʻi bacteria kēia i lawe ʻia e nā ʻuku (Rickettsia rickettsii).
- ʻO ka maʻi Haemophilus influenzae: He maʻi kēia i hoʻokumu ʻia e ka bacteria H. influenzae.
- HIV (Human Immunodeficiency Virus): Hoʻoulu kēia maʻi i kahi maʻi i kapa ʻia ʻo AIDS (Acquired Immune Deficiency Syndrome). ʻO ka poʻe i loaʻa i ka maʻi HIV, aia pū kekahi i ka pilikia o ka loaʻa ʻana o ka anemia hemolytic.
3. Kekahi mau lāʻau lapaʻau
Hiki ke loaʻa ka anemia hemolytic ma ke ʻano he hopena ʻaoʻao o kekahi mau lāʻau lapaʻau. Eia naʻe, ʻaʻole nā mea āpau e lawe i kēia mau lāʻau lapaʻau e loaʻa i kēia maʻi. E nānā kāu kauka i kāu mōʻaukala olakino a hoʻoholo inā kūpono kēia lāʻau lapaʻau iā ʻoe.
ʻO kekahi mau laʻana:
- ʻO ka Penicillin (he lāʻau antibiotic)
- ʻO Quinine (he lāʻau lapaʻau no ka malaria)
- Methyldopa (he lāʻau lapaʻau no ke koko kiʻekiʻe)
- Sulfonamides (nā lāʻau antibacterial)
4. Nā kumu ʻē aʻe
Eia kekahi, i kekahi manawa hiki ke haki nā ʻāpana koko ʻulaʻula, e like me ka loaʻa ʻana o kahi hoʻoili koko mai kahi ʻano koko kūlike ʻole.
He aha nā hōʻailona o ka Anemia Hemolytic?
Hiki i kēia mau hōʻailona ke akahai loa no kekahi poʻe, a ʻoi aku ka ʻino no kekahi. Hiki iā lākou ke ʻike koke ʻia a ulu mālie paha i ka hala ʻana o ka manawa. ʻO nā hōʻailona nui e ʻike ʻia:
- Jaundice: He melemele kēia o ka ʻili, sclera, a me nā membrane mucous (e like me loko o ka waha). Hana ʻia kēia i ka wā e piʻi ai ke koko o kahi mea i kapa ʻia ʻo bilirubin, ka mea i hana ʻia i ka wā e haki ai nā hunaola koko ʻulaʻula.
- ʻO Dyspnea: Ke emi iho nā hunaola koko ʻulaʻula e lawe ana i ka oxygen ma ke kino holoʻokoʻa, hiki iā ʻoe ke manaʻo i ka hanu ʻole a manaʻo e like me ʻoe e hanu ana no ka ea.
- Luhi: Manaʻo luhi mau a hiki ʻole ke hana i kekahi mea. Hiki iā ʻoe ke manaʻo ua luhi loa ʻoe a hiki ʻole iā ʻoe ke hana i nā hana o kēlā me kēia lā.
- Tachycardia: He manaʻo e kuʻi wikiwiki ana ka puʻuwai. Ke kuʻi wikiwiki ka puʻuwai, ʻaʻohe ona manawa e hoʻopiha pono ai i ke koko, a ʻaʻole hiki ke hāʻawi i ke kino i ka oxygen e pono ai.
- Hypotension: Ke koko haʻahaʻa loa ma mua o ka mea i manaʻo ʻia.
- Hematuria: Koko i loko o ka mimi . He mea maʻamau kēia i nā poʻe me ka anemia cell sickle.
- Ka Hoʻonui ʻia ʻana o ka Spleen a i ʻole ke Ake: ʻO ka spleen a me ke akepaʻa ke kuleana no ka kānana ʻana a me ka luku ʻana i nā hunaola koko ʻulaʻula i haki a kahiko i loko o ko kākou kino. Ke wāwahi nui ʻia nā hunaola koko ʻulaʻula, hiki i kēia mau ʻōkana ke pehu a hoʻonui ʻia no ka mea pono lākou e hana ikaika.
Hiki i ka anemia ke lilo i pilikia olakino?
ʻAe, i kekahi manawa hiki i ka anemia ke lilo i pilikia. Kāhea mākou iā ia he anemia koʻikoʻi. Hana ʻia kēia ke nalowale koke ʻoe i ka nui o ke koko, a i ʻole ke hoʻomaka koke kāu mau hunaola koko ʻulaʻula e haki. ʻO kēia no ka poʻe e like me:
- E nāwaliwali loa paha ʻoe.
- Hiki i ka puʻuwai ke manaʻo e kuʻi nui ana a wikiwiki hoʻi .
- He mea paʻakikī paha ke hanu .
Inā hiki koke mai kēia mau hōʻailona, hiki ke lilo i pilikia. I kēlā hihia, ʻo ka mea maikaʻi loa e hana ai, ʻo ia ke ʻimi koke i ke kōkua lapaʻau.
Pehea ʻoe e ʻike ai inā loaʻa iā ʻoe ka anemia hemolytic?
Inā loaʻa iā ʻoe kēia mau hōʻailona, ke ʻike ʻoe i ke kauka, e hana ʻo ia i kēia mau mea:
- Kou mōʻaukala lapaʻau pihaE nīnau e pili ana i ia mea. ʻOi aku hoʻi, e nīnau inā ua loaʻa kekahi o ka ʻohana i ka anemia.
- E nīnau lākou inā ua loaʻa iā ʻoe kekahi mau maʻi i hala koke aku nei a i ʻole nā lāʻau lapaʻau āu e lawe nei , no ka mea hiki i kēia ke hana i ka anemia hemolytic.
- E hana ʻia kahi hoʻokolohua kino , kahi e nānā ai i nā hōʻailona o ka anemia, jaundice, a me ka spleen a me ke akepaʻa.
He aha nā hoʻokolohua diagnostics?
Hana pinepine nā kauka i kekahi mau hoʻāʻo koko e ʻike ai i ka anemia hemolytic. Hiki iā lākou ke hoʻāʻo no nā māka genetic e ʻike inā he hoʻoilina.
Nā Hoʻāʻo Koko Mua:
ʻO ka mea mua e hana ai, ʻo ia ke nānā inā he anemia maoli kāu mau hōʻailona.
- Helu Koko Piha (CBC): Nānā kēia i ka helu o nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a me nā platelets i loko o kou koko, ka nui o kou mau hunaola koko ʻulaʻula, ke kiʻekiʻe o ka hemoglobin, ka protein e lawe ana i ka oxygen, a me ka hematocrit, e ana ana i ka nui o ka hakahaka o kou mau hunaola koko ʻulaʻula i loko o kou koko.
Nā Hoʻāʻo Kūikawā ʻē aʻe:
Inā hōʻoia ka CBC i ka anemia, hana ʻia nā hoʻokolohua hou aʻe e hoʻoholo pono i ke ʻano o ka anemia, inā he anemia hemolytic.
- Hoʻāʻo Coombs (Hoʻāʻo Antiglobulin Kūlike): Nānā kēia no ka anemia hemolytic autoimmune (AIHA).
- Helu Reticulocyte: He mau hunaola koko ʻulaʻula ʻōpiopio nā Reticulocytes. Nānā kēia hoʻāʻo inā e hana ana ka iwi iwi i nā hunaola koko ʻulaʻula olakino.
- Hoʻāʻo Haptoglobin: ʻO ka Haptoglobin kahi protein i wehe ʻia mai nā hunaola koko ʻulaʻula i haki. ʻO nā pae haʻahaʻa o kēia protein e hōʻike ana e wāwahi ʻia ana nā hunaola koko ʻulaʻula.
- ʻO Lactate Dehydrogenase (LDH): ʻO LDH kahi enzyme i loaʻa i loko o nā hunaola koko ʻulaʻula. ʻO nā pae kiʻekiʻe o LDH e hōʻike ana ua luku ʻia nā hunaola koko ʻulaʻula hou aʻe.
- ʻO Bilirubin i hoʻohui ʻole ʻia: Hana ʻia ʻo Bilirubin ke wāwahi ʻia nā hunaola koko ʻulaʻula. Ana kēia hoʻāʻo i ka nui o ka bilirubin i hoʻohui ʻole ʻia i hana ʻia e ke akepaʻa. ʻO nā pae kiʻekiʻe o kēia he hōʻailona ia e wāwahi ʻia ana nā hunaola koko ʻulaʻula he nui loa.
- ʻO ka hoʻāʻo ʻana i ke koko peripheral: Pili kēia i ka lawe ʻana i kahi hāpana koko a nānā iā ia ma lalo o kahi microscope e ʻike ai inā he ʻano ʻē ke ʻano a me ka nui o nā keena koko ʻulaʻula.
- Hemoglobin Electrophoresis: Hoʻopili kēia i ka protein hemoglobin. Kōkua ia i ka ʻike ʻana i nā kūlana e like me ka thalassemia a me ka sickle cell.
Pehea e mālama ʻia ai ka Anemia Hemolytic?
Ua hoʻoholo ʻia nā ʻano lapaʻauAia nō ia i ke kumu o ka maʻi a me ke koʻikoʻi o kou mau hōʻailona.
Eia kekahi laʻana, inā manaʻo kāu kauka he anemia koʻikoʻi kou, hiki iā ia ke hāʻawi mua iā ʻoe i nā hoʻoili koko e hoʻopaʻa i kāu helu koko ʻulaʻula. A laila, e ʻimi a mālama lākou i ke kumu kumu o ka anemia (e.g., kahi maʻi, kahi hopena ʻaoʻao o ka lāʻau lapaʻau, kahi maʻi hoʻoilina).
Pehea e hōʻemi ai i ka pilikia o ka hoʻomohala ʻana i ka anemia hemolytic?
Nui nā kumu e hiki ai ke hoʻoulu i ka anemia hemolytic ʻaʻole hiki iā mākou ke kaohi. Eia kekahi laʻana, hiki ke hana ʻia e kahi ʻeha a i ʻole kahi maʻi hoʻoilina.
Eia nō naʻe, ʻo ka mea nui loa hiki iā ʻoe ke hana, ʻo ia ke kamaʻilio koke me ke kauka e pili ana i ia mea inā ʻike ʻoe i nā hōʻailona o ka anemia. Hiki i kēia ke kōkua iā ʻoe e ʻike i ke kūlana a hoʻomaka koke i ka mālama ʻana, e hōʻemi ana i ka pilikia o ka loaʻa ʻana o nā kūlana koʻikoʻi.
He aha kaʻu e manaʻo ai inā loaʻa iaʻu ka Anemia Hemolytic?
Hiki ke ʻokoʻa kēia mai kēlā kanaka a kēia kanaka. I kekahi manawa hiki i ka anemia hemolytic ke lilo i hōʻailona o kahi maʻi koʻikoʻi e pono ai ka mālama ʻana i ka wā lōʻihi.
I kekahi manawa, hiki ke lilo i hopena i kahi maʻi a lāʻau lapaʻau paha. I ia mau hihia, hiki i ka mālama ʻana i ka maʻi a i ʻole ka hoʻololi ʻana i ka lāʻau lapaʻau ke ho'ōla loa i ke kūlana.
Pehea wau e mālama ai iaʻu iho? / Pehea wau e mālama ai i koʻu olakino?
Hiki i nā kauka ke mālama i kou anemia hemolytic. Ma hope o kou ho'ōla ʻana, hiki i kēia mau mea ke kōkua iā ʻoe e noho olakino a pale i ke ʻano mai ka hoʻi hou ʻana mai:
- E ʻai i ka meaʻai olakino i waiwai i nā wikamina B12, C, a me B9 (waikawa folic). Hiki iā ʻoe ke kamaʻilio me kahi meaʻai meaʻai e aʻo hou e pili ana i nā meaʻai e kōkua ai e hoʻoikaika i kou mau hunaola koko ʻulaʻula.
- E inu i ka wai e like me ka mea e pono ai kou kino.
- E hoʻoikaika kino mau. Eia nō naʻe, e kūkākūkā me kāu kauka e pili ana i ka pehea e hoʻoikaika kino ai me ka palekana.
- E pale i nā maʻi. E holoi pinepine i kou mau lima a e noho mamao aku mai ka poʻe maʻi.
- E mālama i kahi moʻolelo o kāu mau hōʻailona. Inā he loli i kāu mau hōʻailona, e haʻi i kāu kauka.
I ka hōʻuluʻulu manaʻo, nā mea e pono ai mākou e hoʻomanaʻo (Leka Lawe-Home)
ʻO ka anemia hemolytic kahi maʻi e kū mai ana i ka wā e luku ʻia ai kāu mau hunaola koko ʻulaʻula. Hiki ke hana ʻia e nā kumu hoʻoilina, nā maʻi, a i ʻole kekahi mau lāʻau lapaʻau. ʻOiai ke kumu, e ʻike kāu kauka i ke kumu kumu a mālama iā ia. ʻO ka hoʻomaka mua ʻana i ka mālama ʻana hiki ke hana i ka ʻokoʻa ma waena o ka maikaʻi a i ʻole ka ʻino.
Hiki i nā hōʻailona o ka anemia hemolytic ke like me ka maʻi maʻamau, ʻaʻole koʻikoʻi loa. Akā, ʻike maikaʻi ʻoe i kou kino.Inā lōʻihi ka manawa e ho'ōla ai kahi maʻi maʻamau ma mua o ka maʻamau, a inā paha e loaʻa iā ʻoe nā hōʻailona hou a ʻano ʻē, ʻaʻole loa e lohi ke kamaʻilio me ke kauka. Hiki i ka lāʻau lapaʻau koke ke kōkua iā ʻoe e hoʻōla wikiwiki!
ʻO ka anemia hemolytic, anemia, nā hunaola koko ʻulaʻula, ke koko, nā hōʻailona, ka lāʻau lapaʻau, nā kumu











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