Ua luhi paha ʻoe no kekahi manawa, me ka ʻū a me ka ihu wai? Ua ʻike paha ʻoe i nā puʻupuʻu liʻiliʻi ma kou ʻili. ʻO ka hapa nui o kēia mau hōʻailona pili ʻole e hiki ke hana ʻia e kahi maʻi āu e noʻonoʻo ʻole ai, i kapa ʻia ʻo 'Sarcoidosis.' ʻOiai ke kani iki nei ka inoa, e kamaʻilio maʻalahi a maopopo e pili ana i ke ʻano maoli, ke kumu e hana ʻia ai, a me nā mea hiki iā ʻoe ke hana e pili ana.
He aha ka Sarcoidosis maʻalahi?
ʻAe, e hoʻomaopopo kākou i kēia ma kēia ʻano. He ʻōnaehana pale ko ko kākou kino. Ua like ia me kahi pūʻali koa pale i loko o ko kākou kino. ʻO ka hana a kēia pūʻali koa, ʻo ia ke pale iā kākou mai nā ʻenemi e like me nā germs , bacteria , a me nā virus e hele mai ana mai waho.
ʻO ka mea e hana ʻia ana ma ka sarcoidosis, ʻo ia ka lilo ʻana o kā mākou ʻōnaehana pale i ʻoi aku ka ikaika ma mua o ka mea e pono ai. ʻO ia hoʻi, ʻoiai ʻaʻohe ʻenemi maoli, hōʻuluʻulu nā pūnaewele o ka ʻōnaehana pale (ʻoi aku hoʻi nā keʻena koko keʻokeʻo ) a hana i nā kahua liʻiliʻi ma nā wahi like ʻole o ke kino. ʻO kēia mau kahua liʻiliʻi ka mea a mākou e kapa nei he mau puʻupuʻu a i ʻole granulomas .
Hiki i kēia mau puʻupuʻu (granulomas) ke hana ʻia ma nā wahi āpau o ke kino. Eia nō naʻe, ʻike pinepine ʻia lākou ma nā māmā a me nā lymph node . Hiki iā lākou ke hana ʻia ma ka ʻili, nā maka, ka puʻuwai , a me ka lolo.
ʻO ka mea nui, ʻaʻole kēia granuloma he hōʻiliʻili o nā hunaola kanesa . ʻAʻole kēia he kanesa. He hana nui wale nō kēia o ka ʻōnaehana pale.
I kekahi manawa, ʻaʻole hōʻike kēia mau nodules i kekahi mau hōʻailona. Akā i kekahi manawa, ma muli o kahi a lākou e hana ai a me ko lākou nui, hiki iā lākou ke hana i nā hōʻailona like ʻole. I ka hihia ʻino loa, hiki ke hana ʻia nā ʻōpala mau loa i ka hala ʻana o ka manawa ma nā wahi i loaʻa ai kēia mau nodules. Kāhea mākou i kēia he fibrosis . E like me ke koena o kahi ʻōpala ma hope o ka ho'ōla ʻana o kahi ʻeha. Inā hana kēia i loko o nā māmā, hiki iā ia ke loaʻa nā hopena lōʻihi i ke kaʻina hana hanu.
ʻO wai ka mea i hoʻopilikia nui ʻia e kēia kūlana?
He maʻi ʻo Sarcoidosis e hiki ke hoʻopilikia i kekahi. Eia nō naʻe, aia kekahi mau kumu e hoʻopilikia ai iā ʻoe:
- Makahiki:ʻIke pinepine ʻia kēia maʻi i nā kānaka ma waena o 25 a me 40 mau makahiki.
- Kāne: ʻOi aku ka nui o ka pilikia o nā wahine ma mua o nā kāne.
- Moʻolelo ʻohana: ʻAʻole kēia he maʻi i hoʻoilina pololei ʻia. Eia nō naʻe, inā loaʻa kēia maʻi i kekahi o kou ʻohana pili (makuahine, makuakāne, kaikunāne a kaikuahine paha), ʻoi aku ka kiʻekiʻe o kou pilikia o ka loaʻa ʻana ma mua o ke kanaka maʻamau.
Ua manaʻo ʻia kēia he maʻi laha ʻole. No laila, ʻaʻohe pono e hopohopo nui e pili ana i ia mea, akā he mea nui e makaʻala.
He aha nā hōʻailona o ka Sarcoidosis?
ʻO kēia kahi e huikau ai ka poʻe he nui. No ka mea, he ʻokoʻa loa nā hōʻailona o ka sarcoidosis. ʻOkoʻa loa nā hōʻailona ma muli o kahi e hana ʻia ai nā puʻupuʻu (granulomas). ʻAʻole paha i loaʻa i kekahi poʻe kekahi mau hōʻailona, a hiki ke ʻike ʻia ma kahi hanana i ka wā o kahi X-ray i hana ʻia no kekahi kumu ʻē aʻe.
E nānā kākou i nā hōʻailona nui.
| ʻĀpana kino i hoʻopilikia ʻia | Nā hōʻailona e ʻike ʻia |
|---|---|
| Nā Hōʻailona Laulā | |
| Kino holoʻokoʻa |
|
| Ke hoʻopilikia ʻia nā māmā (Nā Hōʻailona o ka Māmā) | |
| ʻŌnaehana hanu |
|
| I ka wā e hoʻopilikia ai i ka ʻili (Nā Hōʻailona ʻIli) | |
| ʻIli |
|
| Ke pilikia nā maka (Nā Hōʻailona Maka) | |
| Nā maka |
|
| Ke hoʻopilikia ʻia ka puʻuwai (Nā hōʻailona o ka puʻuwai) | |
| Puʻuwai |
|
| Ke hoʻopilikia ʻia ka ʻōnaehana nerve (Nā hōʻailona o ka ʻōnaehana nerve) | |
| ʻO ka lolo a me nā aʻalolo |
|
Ua māhele ʻia ka Sarcoidosis o nā māmā i nā pae?
ʻAe, ʻo Sarcoidosis (Pulmonary Sarcoidosis), kahi maʻi e hoʻopilikia ai i nā māmā, ua māhele ʻia i nā pae e pili ana i ke ʻano o nā māmā ma kahi X-ray umauma. Akā, ʻaʻole ia he pae e holomua ana mai kekahi pae a i kekahi e like me ke kanesa. Pili wale ia i kahi o nā granulomas. Hiki i ke kanaka ke neʻe mai kekahi pae a i kekahi, hoʻi i ke kahua kahiko, a i ʻole e nalowale loa nā granulomas.
- Pae 0: ʻAʻohe loli i ʻike ʻia ma ke kiʻi X. He maʻamau nā māmā a me nā lymph node.
- Pae 1: Aia nā ʻōpū i loko o nā lymph nodes o ka umauma wale nō.
- Pae 2: Hiki ke ʻike ʻia nā nodules ma nā lymph nodes o ka umauma a me nā māmā.
- Pae 3: Aia nā puʻupuʻu i loko o nā māmā wale nō. ʻAʻole lākou i loko o nā lymph nodes.
- Pae 4: Ua loaʻa ka ʻeha mau loa o nā māmā (pulmonary fibrosis). He paʻakikī ke hoʻohuli i kēia pae.
No ke aha e ulu ai ʻo Sarcoidosis? He aha ke kumu?
ʻAʻole maopopo i nā kauka ke kumu maoli o kēia, akā ʻo ke kumumanaʻo i ʻae ʻia i kēia manawa, ʻo ia ka wā e hōʻike ʻia ai ka poʻe me kahi predisposition genetic i kahi mea kikoʻī i ke kaiapuni (e like me ka bacteria, virus, a i ʻole ka lepo), pane nui kā lākou ʻōnaehana pale .
I ka ʻōlelo maʻalahi, ua manaʻo ʻia ua hoʻokumu ʻia e ka hui pū ʻana o nā kumu genetic a me ke kaiapuni. ʻOiai he maʻi ia e pili ana i ka ʻōnaehana pale, ʻaʻole ia i hoʻokaʻawale ʻia he maʻi 'autoimmune'.
Pehea e ʻike ʻia ai ka Sarcoidosis?
Hiki ke paʻakikī iki ka ʻike ʻana i ka sarcoidosis, ʻoiai hiki ke ʻike ʻia nā hōʻailona a mākou i kūkākūkā ai ma luna i nā maʻi ʻē aʻe he nui. No laila, e kāpae kāu kauka i nā kūlana ʻē aʻe ma mua o ka hoʻoholo ʻana he hiki ke loaʻa ka sarcoidosis.
Hoʻohana ʻia kekahi mau hoʻokolohua no kēia:
- Hoʻokolokolo kino: E hoʻolohe pono ke kauka i kāu mau hōʻailona a nānā i nā mea e like me kou ʻili, maka, a me nā lymph node.
- Nā hoʻāʻo kiʻi: ʻO ka X-ray umauma ka mea mua āu e hana ai. Hiki iā ia ke nānā i ke kūlana o kou mau māmā a me nā lymph node. Eia kekahi, pono paha kahi CT scan a i ʻole MRI scan .
- Biopsy: ʻO kēia ke ala maikaʻi loa e hōʻoia i ka maʻi 100%. Lawe ʻia kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai kahi wahi i manaʻo ʻia (e.g. ʻili, lymph node) a nānā ʻia ma lalo o kahi microscope.
- Nā hoʻāʻo hana pulmonary: Ke ana kēia i ka maikaʻi o ka hana ʻana o nā māmā.
- Nā hoʻāʻo koko a me ka mimi:Nānā ʻia nā mea e like me ka hana o nā ʻōkana e like me ke akepaʻa a me nā puʻupaʻa a me ka nui o ka calcium i loko o ke koko.
- EKG (Electrocardiogram): Hana ʻia kēia hoʻāʻo e ʻike inā he hopena ma ka puʻuwai.
- Hoʻāʻo TB: ʻOiai ua like nā hōʻailona o ka maʻi puʻupuʻu me kēia, hana ʻia kahi hoʻāʻo ʻili maʻalahi e hōʻoia ʻaʻole ia ka hihia.
He aha nā lāʻau lapaʻau no kēia?
ʻO ka nūhou maikaʻi, ʻaʻole pono ka lāʻau lapaʻau i nā kānaka a pau me ka sarcoidosis. No kahi o ʻelua hapakolu o ka poʻe, e hoʻomaikaʻi ke ʻano iā ia iho i loko o ʻelua a ʻekolu mau makahiki, me ka ʻole o kekahi lāʻau lapaʻau.
ʻO ka hoʻomaka ʻana a i ʻole ka hoʻomaka ʻana i ka lāʻau lapaʻau e pili ana i ke koʻikoʻi o kāu mau hōʻailona a me kahi o nā puʻupuʻu. No ka laʻana, inā pilikia nā maka, ka puʻuwai, a i ʻole ka ʻōnaehana nerve, e hoʻomaka koke ka lāʻau lapaʻau e hoʻōki i ka hōʻino ʻana o nā kino.
ʻO nā pahuhopu nui o ka mālama ʻana:
1. Ke kāohi ʻana i nā hōʻailona.
2. Hoʻemi i ka mumū i loko o ke kino.
3. Ke pale ʻana i ka hōʻino mau loa (fibrosis) i nā ʻōpū.
ʻO nā ʻano lāʻau lapaʻau nui i hāʻawi ʻia no kēia:
- ʻO Corticosteroids: ʻO kēia ke ʻano lāʻau lapaʻau i hoʻohana nui ʻia (e.g., Prednisone). Hana kēia mau mea ma ke kāohi ʻana i ka ʻōnaehana pale a me ka hōʻemi koke ʻana i ka mumū i loko o ke kino. Loaʻa lākou ma ke ʻano o nā pila, nā mea hoʻoheheʻe, a i ʻole nā kirimi i hoʻopili ʻia i ka ʻili.
- Nā Immunosuppressants: Ma waho aʻe o nā corticosteroids a i ʻole e hōʻemi i kā lākou dosage, hāʻawi ʻia nā lāʻau ʻē aʻe e kaohi ana i ka ʻōnaehana pale (e laʻa, Methotrexate).
- Nā antibodies Anti-TNF-alpha: He ʻano lāʻau lapaʻau intravenous (infusion) kēia e pili ana i kahi kemika kikoʻī i loko o ka ʻōnaehana pale.
- Nā NSAID (nā lāʻau hoʻopau ʻeha): Hiki ke hāʻawi ʻia kēia mau mea e kāohi i nā hōʻailona pōkole e like me ka ʻeha o nā hono.
He mea nui: ʻO ka hoʻohana lōʻihi ʻana i nā lāʻau lapaʻau e like me corticosteroids hiki ke hana i nā hopena ʻaoʻao e like me ka piʻi ʻana o ke kaumaha, ka maʻi diabetes, a me ke koko kiʻekiʻe. No laila, e noʻonoʻo mau kāu kauka inā ʻoi aku ka maikaʻi o ka lāʻau lapaʻau ma mua o nā pilikia. Mai hoʻomaka a hoʻōki paha i ka lawe ʻana i kēia mau lāʻau me ka ʻole o ka ʻōlelo aʻoaʻo a kāu kauka.
Nā mea e pono ai ʻoe e ʻike i ka wā e noho ai me ka sarcoidosis
Hiki i ke kanaka e noho ana me ka sarcoidosis ke hana i nā mea he nui e mālama ai i ko lākou kūlana.
- E hahai i nā ʻōlelo a kāu kauka: e lawe i kāu lāʻau lapaʻau e like me ke kauoha, e hele i nā keʻena lapaʻau i nā lā i hoʻonohonoho ʻia, a e hoʻomaopopo i kāu kauka inā he mau loli i kāu mau hōʻailona.
- Ka nohona olakino:He mea nui e ʻai i ka meaʻai kaulike, e pale loa i ka puhipaka (ʻoi aku hoʻi inā ua hoʻopilikia i nā māmā), a e hoʻoikaika kino mālie e like me ke kuhikuhi a kāu kauka.
- ʻAi: Manaʻo kekahi mau noiʻi e hiki i ka hōʻemi ʻana i nā meaʻai kō a me nā mea ʻai starchy a me ka ʻai ʻana i nā mea kanu, nā huaʻai, a me nā meaʻai waiwai i ka omega-3s (e.g., iʻa liʻiliʻi) ke kōkua i ka hōʻemi ʻana i ka mumū. Eia nō naʻe, e kamaʻilio me kāu kauka ma mua o ka hana ʻana i nā hoʻololi nui i ka ʻai.
Hiki i ka hapa nui o nā kānaka ke ola i kahi ola maʻamau a hauʻoli me ka sarcoidosis. Kākaʻikahi ia e hoʻopōkole i ka manaʻolana ola (1%-5%). ʻO ka mea nui loa, ʻaʻole e makaʻu i ka maʻi, akā e hoʻomaopopo pono iā ia a hana pū me kāu kauka e hoʻomohala i ka hoʻolālā hoʻokele maikaʻi loa e pono ai nāu.
Leka Lawe-Home
- ʻO Sarcoidosis kahi kūlana kahi e pane nui ai ka ʻōnaehana pale a hoʻoulu ai i nā puʻupuʻu pehu (granulomas) ma nā ʻāpana like ʻole o ke kino.
- ʻAʻole kēia he maʻi lele a ʻaʻole hoʻi he maʻi kanesa.
- ʻOkoʻa loa nā hōʻailona, ma muli o kahi e kū ai nā puʻupuʻu. ʻO nā māmā ka mea i hoʻopilikia pinepine ʻia.
- No ka hapa nui o nā kānaka, e hoʻomaikaʻi wale kēia i kona iho i ka hala ʻana o ka manawa me ka ʻole o ka lāʻau lapaʻau. Pono kekahi poʻe i ka lāʻau lapaʻau e kāohi i nā hōʻailona a pale i ka hōʻino ʻana o nā kino.
- Inā he kānalua kou no kēia, a inā he mau hōʻailona i wehewehe ʻole ʻia, e ʻike pono i ke kauka no ka ʻōlelo aʻo.











💬 Comments (0)
ʻAʻohe manaʻo i kau ʻia. Hoʻohui i kāu manaʻo ma ʻaneʻi no ka manawa mua.
Hoʻohui i kāu manaʻo