Anemia, akā nui loa ka hao i loko o ke kino? E kamaʻilio kākou e pili ana i ka Anemia Sideroblastic

Ke lohe ka hapa nui o ka poʻe i ka huaʻōlelo 'anemia ' , manaʻo koke lākou i ka nele i ka hao . ʻO ia ke kumu e luhi mau ai lākou, palaualelo, poniuniu, a i kekahi manawa hiki ʻole ke hiamoe. Akā ua ʻike anei ʻoe i kekahi mau hihia o ka anemia, ʻo ka mea ʻē aʻe ka mea e hana maoli ai? Ma kahi o ka nele i ka hao, ʻo ka hao i loko o nā hunaola koko 'e hoʻonui'. ʻAʻole anei kēia he mea kupanaha iki? I kēia lā ke kamaʻilio nei mākou e pili ana i kekahi ʻano anemia kūikawā, akā ʻaʻole maʻamau loa, i kapa ʻia ʻo sideroblastic anemia.

I ka ʻōlelo maʻalahi, he aha ka Sideroblastic Anemia?

I mea e hoʻomaopopo ai i kēia, e nānā mua kākou i ko kākou koko. Aia i loko o nā hunaola koko ʻulaʻula i loko o ko kākou koko kahi protein i kapa ʻia ʻo hemoglobin . ʻO kāna hana nui ka hopu ʻana i ka oxygen e komo mai ana i loko o nā māmā i ka wā e hanu ai kākou a lawe iā ia ma ke kino holoʻokoʻa. No laila, he mea nui kēia oxygen no kēlā me kēia cell i loko o ko kākou kino e ola ai.

I kēia manawa, no ka hana ʻana i kēia hemoglobin, pono maoli ko mākou kino i ka mineral 'hao'. Ma keʻano laulā, loaʻa ka anemia ke nele ke kino i ka hao. No laila, ʻaʻole hiki iā ia ke hana i ka hemoglobin.

E noʻonoʻo i kahi lumi kuke me ka laiki, ka wai, a me ka paʻakai e kuke ai i ka laiki, akā ua haki ka mea kuke laiki. A laila, ʻaʻole hiki iā ʻoe ke kuke i ka laiki. Pēlā nō ia. I loko o kēia maʻi, nui ka hao, kahi mea e pono ai no ka hana ʻana i ka hemoglobin. Akā, ʻaʻole hana pono ka hale hana e hoʻohana ana i kēlā hao e hana i ka hemoglobin, ʻo ko kākou mau ʻulaʻula koko, no laila, hoʻomaka ka hao i hoʻohana ʻole ʻia e hōʻiliʻili i loko o kēia mau ʻulaʻula koko kīnā. Kāhea mākou i kēia mau ʻano ʻē i hōʻiliʻili i ka hao ma kēia ʻano he `(Sideroblasts)`.

He aha nā hōʻailona o kēia maʻi?

Ua like loa nā hōʻailona o kēia maʻi me nā kūlana anemia ʻē aʻe, no laila hiki ke huikau maʻalahi i kekahi manawa. A no ka mea e ulu mālie ana ka maʻi, ʻaʻole paha ʻoe e ʻike ua loaʻa iā ʻoe. ʻO kēia nā hōʻailona nui āu e ʻike ai.

He aha nā ʻano nui o ka Anemia Sideroblastic?

Hiki ke puʻunaue nui ʻia kēia maʻi i ʻelua ʻano.

1. Anemia Sideroblastic i hoʻoilina ʻia

He maʻi laha ʻole kēia, he maʻi hoʻoilina. ʻO ia hoʻi, ua hoʻoili ʻia i kahi keiki ma o nā genes mai kekahi o nā mākua. ʻO ke ʻano maʻamau o kēia ʻo ia ka X-linked Sideroblastic Anemia . Hoʻokumu ʻia kēia e kahi mutation i loko o kahi gene e hoʻopilikia ai i ka hana hemoglobin. ʻO ka hopena, hoʻāʻo ke kino e omo i ka hao hou aku mai ka meaʻai e hoʻopiha ai i ka nele o ka hemoglobin. I nā hihia koʻikoʻi, hiki iā ia ke hōʻino i nā ʻōpū e like me ke akepaʻa . ʻIke pinepine ʻia kēia ʻano hānau ma mua o 30 mau makahiki.

2. ʻAno hoʻomaka ma hope (Acquired Sideroblastic Anemia)

ʻO kēia ke ʻano maʻamau. ʻO ka mea maikaʻi loa, hiki ke ho'ōla pinepine ʻia . ʻOiai ʻaʻole ʻike nā kauka i ke kumu pololei i kekahi manawa, aia kekahi mau kumu nui e kōkua ai i kēia maʻi:

• Kekahi mau lāʻau lapaʻau: ʻOi aku kekahi mau lāʻau lapaʻau i hāʻawi ʻia no ka maʻi puʻupuʻu.
• ʻO ka inu nui ʻana i ka waiʻona: ʻO ka inu nui ʻana i ka waiʻona i ka wā lōʻihi he kumu nui ia o ka pilikia.
• Nā kemika ʻawahia : ʻO ka hoʻopili lōʻihi ʻana i kekahi mau kemika ʻawahia, e like me ke kēpau.
• Nā maʻi ʻē aʻe: Hiki ke hana ʻia kēia ʻano e nā maʻi ʻē aʻe e like me nā maʻi pale, nā ʻōpū, a i ʻole nā ​​​​maʻi metabolic.

Eia kekahi, hiki i nā ʻano ʻelua ke hoʻomohala i kahi kūlana i kapa ʻia ʻo hemochromatosis , kahi e hōʻiliʻili ai ka hao keu i loko o ke kino.

Pehea e ʻike pono ai i kēia maʻi?

Ma muli o ke ʻano like o nā hōʻailona me nā maʻi anemia ʻē aʻe, hiki ke paʻakikī iki ke ʻike. No laila he mea nui e hoʻolohe i kou kino. Inā loaʻa iā ʻoe kekahi a ʻoi aku paha o nā hōʻailona i helu ʻia ma luna, e ʻoluʻolu e ʻike i kāu kauka.

E nīnau pono ke kauka iā ʻoe e pili ana i kāu mau hōʻailona, ​​​​e nānā iā ʻoe, a laila e kauoha i kekahi mau hoʻokolohua e hōʻoia inā loaʻa iā ʻoe kēia maʻi.

• Nā hoʻāʻo koko: He mea nui ka helu koko piha a me nā haʻawina hao.
• ʻO ka Smear Koko Peripheral: Maanei, ua nānā ʻia kahi hāpana koko ma lalo o kahi microscope e ʻike inā he mau hunaola hao ʻē aʻe (Sideroblasts) a mākou i kamaʻilio ai ma mua.
• Biopsy o ka iwi iwi: I kekahi mau hihia, pono e lawe ʻia kahi hāpana liʻiliʻi o ka iwi iwi a hoʻāʻo ʻia e hōʻoia i ka maʻi.
• Nā hoʻokolohua ʻē aʻe: Inā pono, hiki i ke kauka ke ʻōlelo aku i kahi MRI scan a i ʻole ka hoʻāʻo genetic.

Pehea e mālama ʻia ai?

ʻO nā koho lapaʻau e pili ana i ka loaʻa ʻana o ke ʻano congenital a i loaʻa paha.

• Ke mālama ʻana i ke kumu: Inā loaʻa iā ʻoe ke ʻano i loaʻa, ʻo ka hana mua e wehe i ke kumu. No ka laʻana, inā he lāʻau lapaʻau ke kumu o ke kūlana, e hoʻōki kāu kauka i kēlā lāʻau lapaʻau a kuhikuhi i kekahi. Inā he mea inu nui ʻoe, pono ʻoe e hoʻōki loa i ka inu ʻana i ka waiʻona.
• Wikamina B6: Ua hōʻike ʻia nā noiʻi he kōkua paha ka wikamina B6, a i ʻole pyridoxine, i ka mālama ʻana i nā ʻano ʻelua o ke ʻano. Hiki i kāu kauka ke kuhikuhi i kēia wikamina ma ke ʻano he mea hoʻohui.
• Ke wehe ʻana i ka hao keu: Aia nā lāʻau lapaʻau e hiki ke hāʻawi ʻia e wehe i ka hao keu mai ke kino. Hāʻawi ʻia ʻo Deferoxamine ma ke ʻano he inikini ma lalo o ka ʻili, a hāʻawi ʻia ʻo Deferasirox ma ke ʻano he pila. Eia nō naʻe, hiki i kēia mau lāʻau lapaʻau ke hoʻopilikia i nā puʻupaʻa, no laila pono e hoʻohana ʻia ma lalo o ka nānā pono ʻana o ke kauka.
• Ka Hoʻoili Koko: Inā ʻaʻole pane kou kino i ka lāʻau lapaʻau vitamin B6, hiki i kāu kauka ke ʻōlelo aku i ka hoʻoili koko. Eia nō naʻe, he hemahema kēia. Me ka hoʻomau ʻana o ka hoʻoili koko, e piʻi aʻe ka nui o ka hao o kou kino, e hoʻonui ana i ka pilikia o ka hōʻino ʻia o ke akepaʻa.
• Hoʻoili Iwi ʻŌpū: ʻO kēia ka lāʻau lapaʻau o ka hopena hope loa. Manaʻo ʻia ia i nā hihia koʻikoʻi kahi i loaʻa ʻole ai kahi lāʻau ʻē aʻe i kahi lāʻau lapaʻau.