Wetin yu kin tink we yu si nyu lump ɔ tumbu na yu bɔdi, mɔ na yu leg ɔ yu an? Bɔku tɛm, wi kin tink se na nɔmal tin ɛn wi nɔ kin pe atɛnshɔn to am. Bɔt sɔntɛnde, ivin sɔntin we smɔl lɛk dat kin bi sɔntin we wi nid fɔ pe atɛnshɔn to. Tide, wi go tɔk bɔt wan kansa we nɔ kin bɔku ɛn we kin apin lɛk lump. Dɛn kɔl dis fibrosarkoma.
Fɔ tɔk am simpul wan, wetin na fibrosarcoma?
Fibrosarcoma na wan kayn kansa we nɔ kin bɔku ɛn we kin apin na di sɔft tisu dɛm. Insay mɛrɛsin, wi kin kɔl dis sarkoma. Naw yu go de wɔnda wetin na sɔft tisu. I rili simpul. na di tisu we de kכnekt εn ol difrεn pat dεm na wi bכdi. fכ bi prεsis, tin dεm lεk tεndon dεm εn ligament dεm we de kכnεkt tin dεm lεk bon dεm εn mכsul dεm na wi bכdi na dεn kכnektiv tisu dεm ya.
Bɔku tɛm, fibrosarkoma kansa kin kam na di sɔft tisu dɛn we de dip insay di bɔdi. I kin mɔs bi na di leg (arawnd di hip ɔ di shɔl bon), di ɔp an, di ni, ɔ di trɔnk. I nɔ kin rili kam bak na di ed ɔ nɛk. sכmtεm, dis kεnsar kin kam bak insay di bon dεm כ insay di fayv kכnektiv tisu we de kכba di bon dεm.
If yu ɔ yu pikin gɛt dis sik, wetin go apin nɛks kin dipen pan bɔku tin dɛn. Yu ej, di sayz fɔ di kansa, ɛn usay i de, ɔl go ɛp yu. Yu dɔktɔ go ɛksplen ɔltin bay wetin yu dɔn no bɔt yu sik.
Tu men kayn dis de.
Fibrosarcoma kin sheb to tu men kayn. Dɛn tu kayn ya rili difrɛn frɔm dɛnsɛf.
| Di kayn kansa we yu gɛt | Tɔk bɔt |
|---|---|
| Infantil/Kɔnjɛnital Fibrosarkoma | Dɛn kin si dis kayn we we dɛn bɔn am ɔ jɔs afta dɛn bɔn am. Pan ɔl we dis tumbu kin gro kwik kwik wan, i nɔ kin izi fɔ mek i go ɔda pat dɛn na di bɔdi. So, na wan sik we dɛn kin mɛn ɔltogɛda . |
| Faybrosarkoma we gɛt fɔ du wit big pipul dɛn | Dis kayn tin kin mɔs si pan big pipul dɛm wae ol bitwin 20 ɛn 60. Bɔt sɔmtɛm i kin kam pan big pikin dɛm ɛn yɔŋ pipul dɛm. Nɔ lɛk di kayn pikin, i kin bi mɔ agresiv ɛn i kin at fɔ trit. |
Fibrosarcoma na wan sik we nɔ kin apin so ɔltɛm. I nɔ kin bɔku pan big pipul ɛn pikin dɛn. So nɔr frayd se ɛvri lump we de divɛlɔp na di bɔdi na kansa. Bɔt i fayn fɔ sho dɔktɔ bɔt ɛni nyu lump we de kam.
Wetin na di sayn dɛm fɔ dis sik?
Bɔrku tɛm, i kin tek sɔm tɛm fɔ mek di sayn dɛm fɔ fibrosarcoma sho. Bikɔs dɛn tumbu ya de divɛlɔp na sɔft tisu dɛn we de dip insay di bɔdi, yu nɔ go notis ɛnitin te di tumbu dɔn big fɔ prɛs pan wan nɛv ɔ blɔd vesel we de nia yu.
Dis na di sayn dɛm wae pɔrsin kin si:
- Sɔft lump we nɔ de pen ɔ we nɔ de pen smɔl: Dis kin apin na di leg, an, ɔ di trɔnk.
- Wan tingling senseshɔn ɔ shap, stab pen: Sɔntɛnde wi kin se "pin ɛn nidul." dis kin bi bikoz fכ prεshכn pan wan nεv nia di tכmכro.
- abnכmal swel: Dis kayn swel kin apin we di tכmכro kכmprεs di bכdi vεsul dεm.
Dɛn sayn ya kin tan lɛk ɔda kayn sik dɛm wae nɔr kin siriɔs, so na dɔktɔ nɔmɔ kin no fɔ tru if dɛn chenj ya na bikɔs ɔf fibrosarcoma ɔr ɔda kɔmɔn, nɔr gɛt kansa (benign) kɔndishɔn.
Wetin na di tin dɛn we kin mek pɔsin gɛt fibrosarcoma ɛn di tin dɛn we kin mek pɔsin gɛt prɔblɛm?
Risach pipul dɛn nɔ shɔ yet wetin rili de mek pɔsin gɛt fibrosarcoma. Bɔt dɛn biliv se di chenj we di jɛnɛtiks kin chenj na di sɛl dɛn kin du sɔntin. Fɔ tɔk am simpul wan, chenj dɛn kin apin na di DNA we de na wi sɛl dɛn. Dɛn chenj ya kin mek di sɛl dɛn sheb kwik kwik wan ɛn dɛn nɔ kin ebul fɔ kɔntrol dɛn, ɛn dɛn kin mek tɔŋ dɛn we gɛt kansa.
wan kכmכn jεnεtik mכtεshכn dεn dכn no insay pikin fכ fibrosarkoma, spεshal wan. bכt 90% pan dεn ya de riliyt to prכblεm dεm na di NTRK jin famili. We dɛn jin ya nɔ de wok fayn, kansa tumbu kin kam.
Factor dɛm wae de mek di risk bɔku
Risach pipul dɛn dɔn si se sɔm tin dɛn we pɔsin kin gɛt frɔm in mama ɛn papa kin mek i gɛt fibrosarcoma.
- Famili adenomatous polyposis we de mek pɔsin gɛt sik
- Li-Fraumeni sindrom we gɛt di sik
- Nyurofibromatosis tayp 1 `(Nyurofibromatosis tayp 1)`
- Nevoid basal sel kansa sindrom
- Retinoblastoma we gɛt di sik
- Tuberous sclerosis we gɛt di sik
- Werner sindrom `(Werner sindrom)`
Apat frɔm dat, sɔm ɔda mɛrɛsin dɛn kin gɛt fɔ du wit dis:
- bon infarkshכn (di bon sεl dεm we de day bikoz fכ di bכdi we de fכlכ di bon dεm dכn dכn) .
- Infεkshכn na di bon dεm we de te (Krכnik כstiomyelitis) .
- Displasia we gɛt fayv
- Paget in sik we de na di bon
Sɔm tin dɛn de bak we gɛt fɔ du wit di envayrɔmɛnt ɛn yu past mɛdikal histri:
- Fɔ dɔn gɛt redyushɔn tɛrapi to di eria usay di kansa de.
- Bɔn bad bad wan usay di kansa de.
- If yu gɛt sɔm kemikal dɛn lɛk tɔriɔm dayɔgzayd, vaynil klorayd, ɔ asɛnik.
- εksposhכn to mεtal pat dεm (e.g. kromiכm, kכbalt, nikel) we dεn put insay di bכdi tru כpεrayshכn.
Aw dɔktɔ kin no bɔt dis? (Diagnosis) .
Dɔktɔ dɛn kin du bɔku tɛst dɛn fɔ no if pɔsin gɛt fibrosarcoma. Di infɔmeshɔn we dɛn kin gɛt frɔm dɛn tɛst ya kin sho di stej ɛn di gred we di kansa gɛt.
- MRI skan (Magnetic Resonance Imaging): Dis na di kɔmɔn imej tɛst we dɛn kin yuz fɔ no if pɔsin gɛt fibrosarkoma. I kin sho klia wan di sayz ɛn usay di tumbu de, ɛn if i de afɛkt di blɔd vesel ɔ di nerv dɛn.
- CT scan (Computed Tomography scan): Dis kin yuz sɔm X-ray ɛn kɔmpyuta fɔ mek tri-dimɛnshɔnal (3D) pikchɔ dɛn fɔ yu sɔft tisu ɛn bon dɛn.
- bayopsi: dis involv fכ pul wan sכm pat pan di tכmכro (kor nidul bayopsi) כ di כl tכmכro (excisional biopsy) fכ egzamin. Wan dɔktɔ we de stɔdi bɔt sik dɛn kin chɛk di tisu na lɛbɔtri fɔ si if i gɛt kansa sɛl dɛn.
- Immunohistochemistry (IHC): Dis na spɛshal laboratory test we de yuz protin dεm we dεn kכl antibodies fכ kכnfכm if di tumor na fibrosarcoma כ כda kayn sכft tisu kεnsar.
Aw dɛn kin no di stej dɛm we pɔsin kin gɛt kansa?
Dɔktɔ dɛn kin sheb kansa to difrɛn stej dɛn fɔ no aw fa i dɔn skata ɛn aw i siriɔs. Dis kin tek tɛm tink bɔt di sayz we di tumbu gɛt, usay i de, ɛn if i dɔn skata. Dɛn kin luk bak pan di "grɛd" fɔ di kansa. Dis na aw di kansa sɛl dɛn kin luk abnɔmal we dɛn si am ɔnda maykroskɔp. di sεl dεm we de luk abnכmal dεn kin tek dεm as "high-grade" kεnsar, we kin bi mכr agresiv.
| Stej | Tɔk bɔt |
|---|---|
| Faz I we yu de du | Dis na low-grade fibrosarcomas. if di tכmכro big pas 5 sεntimita, dεn kin kכnsidr am as mכr advans stej. |
| Faz II | Mid-grɛd ɔ ay-grɛd fibrosarkoma. i de go bifo if di tכmכro big pas 5 sεntimita. |
| Stej III | Fibrosarkoma we gɛt ay gred. di tכmכro big pas 5 sεntimita εn i kin dכn spre to di limf no dεm we de nia. |
| Stej IV | Fibrosarcoma we gɛt ɛni gred ɔ saiz dɔn spre (mɛtastas) to ɔgan ɔ tisu dɛn we de fa na di bɔdi. |
Yu dɔktɔ go ɛksplen to yu wetin go apin afta yu dɔn trit yu, i go dipen pan di stej we yu kansa gɛt.
Wetin na di tritmɛnt dɛm fɔ dis?
Di tritmɛnt fɔ fibrosarcoma dipen pan bɔku tin, lɛk yu ɔl yu wɛl bɔdi, wetin yu lɛk, ɛn di kayn kansa.
Tritmɛnt fɔ big pipul-tayp fibrosarkoma
- Ɔpreshɔn: Insay dis we dɛn de du dis, dɔktɔ dɛn kin pul di kansa tɔŋ ɛn smɔl wɛlbɔdi tisu we de rawnd am fɔ mek shɔ se nɔ kansa sɛl nɔ lɛf.
- Radieshɔn Tɛrapi: Dɛn kin gi redyushɔn tɛrapi bifo dɛn du di ɔpreshɔn fɔ mek di tumbu smɔl ɔ fɔ pwɛl ɛni kansa sɛl we lɛf afta dɛn du di ɔpreshɔn.
- Kimotɛrapi: .Pan ɔl we sɔm dɔktɔ dɛn kin gi dɛn dis tritmɛnt, i nɔ bin rili fayn fɔ gɛt fibrosarcoma we kin bigin fɔ big pipul dɛn. Bɔku tɛm, dis kayn kansa nɔ kin ansa fayn we dɛn tek kimotɛrapi.
Tritmɛnt fɔ pikin dɛn we gɛt fibrosarkoma
- Ɔpreshɔn: Insay pikin dɛn, bɔku tɛm if dɛn du ɔpreshɔn fɔ pul di tumbu, i kin mɛn di sik kpatakpata.
- Radieshɔn ɛn/ɔ kemotɛrapi: Dɛn kin yuz dɛn tritmɛnt ya fɔ mek di tumbu dɛn smɔl bifo dɛn du di ɔpreshɔn ɔ fɔ pwɛl di sɛl dɛn we lɛf afta dɛn du am. difrεnt frכm di fכm we big pipul dεn kin gεt, bכku pan di fibrosarkoma dεm we pikin kin gεt kin rεspכnd bכku bכku wan we dεn de gi kεmothεrapi.
- Targeted Therapy: Dis tritmεnt kin stכp di sεl dεm fכ divayd kwik kwik wan bikoz fכ prכblεm wit di `NTRK` jin. Dis kin mek di tumbu dɛn smɔl ɛn mek i izi fɔ du ɔpreshɔn.
Aw de sik kin bi afta dɛn dɔn trit am? (Prɔgnosis) .
Di autkam fɔ infantil fibrosarcoma rili gud. Bɔku pan dɛn tin ya kin wɛl ɔl if dɛn yuz ɔpreshɔn, raytin, kemotɛrapi, ɔ tritmɛnt we dɛn want. di 10 ia sכvayv rεt na bכt 90%. If ɔpreshɔn ebul fɔ pul ɔl di trays dɛm fɔ di kansa fayn fayn wan, da nɔmba de go nia 100%.
di kכndyushכn fכ big pipul dεm we de bigin fכ fibrosarkoma na mכr komplikεt. Bɔku tɛm, dɛn kin no dɛn tumbu ya afta dɛn dɔn big fɔ afɛkt di nerv dɛn ɔ di blɔd flɔ. Jɔs lɛk ɛni kansa, if yu no am kwik, dat kin mek yu gɛt bɛtɛ tin fɔ du. We di kansa dɔn go bifo, i kin at fɔ trit am. Na lɛk af pan di sik pipul dɛn kin gɛt dis sik bak afta dɛn dɔn trit dɛn.
If yu gɛt dis sik, aw yu kin kia fɔ yusɛf?
Bɔku pipul dɛn kin fil se dɛn nɔ ebul fɔ du natin we dɛn kam fɔ no se dɛn gɛt kansa. Wan pan de bɛst we fɔ dil wit dɛn filin ya na fɔ kia fɔ yusɛf we yu de trit yu ɛn afta yu dɔn trit yu. Na sɔm tin dɛn we yu kin du:
- Ɔndastand yu fɔlɔp plan: Aks yu dɔktɔ wetin fɔ ɛkspɛkt we yu de wɛl ɛn we yu de fala di apɔntinmɛnt.
- Manage Anxiety: Fɔ chɛk-ap ɔltɛm afta tritmɛnt impɔtant fɔ no kwik kwik wan se kansa de kam bak. Bɔt i kin mek pɔsin wɔri bak. Tɔk to pɔsin we de gi advays bɔt am.
- Aks fɔ ɛp: Yu go mɔs nid ɛp we yu de du yu tritmɛnt. Sɔntɛm di wan dɛn we yu lɛk de wet fɔ ɛp yu. Tɛl dɛn aw yu go ɛp.
- Fokus pan gud wɛlbɔdi abit dɛn: Fɔ it tin dɛn we gɛt fayn fayn tin dɛn fɔ du, fɔ du ɛksɛsayz, ɛn fɔ slip fayn rili impɔtant.
- Rilaks:Kansa ɛn kansa tritmɛnt kin mek yu fil taya bad bad wan. Plan fɔ rɛst bɔku tɛm we yu de trit yu.
- Fɛt strɛs: Tin dɛn lɛk fɔ tink gud wan, fɔ rilaks, ɛn fɔ blo dip dip wan kin ɛp fɔ mek yu nɔ strɛs.
Ustɛm yu nid fɔ go to dɔktɔ?
Afta yu dɔn gɛt tritmɛnt, yu go ɔltɛm go to yu dɔktɔ ɛvri tri mɔnt fɔ di fɔs tu ia ɛn afta dat yu go go to yu dɔktɔ fɔ 4 to 5 ia. If fibrosarcoma kin kam bak, we kin apin insay di fɔs fayv ia, dis schedule go ɛp fɔ no if i kam bak kwik kwik wan.
Yu fɔ kɔntak yu dɔktɔ ɛni tɛm we yu gɛt nyu lumps ɔ nyu pen.
Ustɛm yu nid fɔ go na di Imejɛnsi Tritmɛnt Yunit (ETU)?
Bɔku tritmɛnt dɛn fɔ kansa kin afɛkt yu imyun sistɛm, we kin mek yu gɛt mɔ sik. Na sɔm sayn dɛm wae kin mek yu go na di Imejɛnsi Dipatmɛnt (ETU) we yu de trit yu:
- Fiva we kin rich 38.3 digri sɛlshiɔs (100.4 Fahrenheit) ɔ pas dat.
- Fɔ fil kol ɛn shek shek.
- Kɔf wit mɔkus.
- Bɛlɛ de pen.
- Dayarɛa we de kɔntinyu fɔ de.
- Nɔs ɛn vɔmit we de kɔntinyu fɔ de.
Mɛsej we dɛn kin kɛr go na os
- Fibrosarcoma na wan kayn kansa we nɔ kin bɔku ɛn we kin kam na di bɔdi in kɔnektiv tisu dɛm.
- tu men kayn dεm de fכ dis: di tכp we dεn kin bכn pikin (bכku tεm dεn kin kכl am) εn di big wan (we kin agresiv mכr).
- Nɔ ignore nyu lump, numbness, ɔ unusual swelling na yu bɔdi. Si yu dɔktɔ wantɛm wantɛm.
- Di tritmɛnt we dɛn kin pik (ɔpareshɔn, raytin, kemotɛrapi) kin dipen pan di kayn kansa, di stej we i gɛt, ɛn aw yu gɛt wɛlbɔdi.
- Fɔ no di sik kwik kwik wan rili impɔtant fɔ mek i go fayn.











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