Sɔntɛnde, yu kin fil se yu nɔ ebul fɔ blo fayn? Ɔ yu kin gɛt dray kɔf we nɔ de dɔn? Ɔ yu kin fil fɔdɔm we yu de tray tranga wan? Sɔntɛm dɛn tin ya nɔto jɔs we pɔsin taya. Dɛn kin bi sayn bak fɔ wan sik we wi go tɔk bɔt tide we dɛn kɔl ``Interstitial Lung Disease`` (``ILD``). Nɔ wɔri, wi go tɔk bɔt dis simpul wan, di we we yu go ɔndastand.
Wetin na Interstitial Lung Disease?
Fɔ tɔk am simpul wan, intastitial lɔng sik (ILD) nɔto wan sik. Na wan grup we gɛt sik dɛn. Infakt, i pas 200 kayn dɛn. Dɛn sik ya kin mek di dilik tisu we de insay yu lɔng ( di interstitium ) inflam, wund, ɛn gɛt skata. Naw yu kin de aks, "Wetin na dis intastitium?" Tink bɔt am lɛk se wi lɔng dɛn mek wit wan bɔnch smɔl smɔl balyɔn dɛn (we dɛn kɔl alveoli ). di intastitium na di dilik tisu bitwin dεn ay sak dεm ya εn di bכdi vεsul dεm we de rawnd dεm. We wi de blo, dɛn kin tek ɔksijɛn ɛn kɔmɔt insay di blɔd tru dɛn ay sak dɛn ya. So, insay ILD, dɛn impɔtant tisu ya kin pwɛl, so ɔksijɛn nɔ kin pas to di bɔdi fayn fayn wan.
`ILD` dεn kכl am bak `Diffuse Parenchymal Lung Disease (DPLD).` כltu, `ILD` na di nem we dεn kin yus mכst.
Wetin kin apin to di bɔdi we `ILD` de divɛlɔp?
If yu gɛt ILD, di pat dɛn na yu lɔng we de gɛda ɔksijɛn frɔm yu blɔd ɛn sɛn am to di ɔda pat dɛn na yu bɔdi kin pwɛl. Dis tisu kin gɛt skata (dɛn kin kɔl am bak fibrosis ), we kin mek i nɔ izi fɔ blo. Yu kin gɛt bak wan kɔf we nɔ de dɔn ɛn we de dray. Yu kin fil taya ɔltɛm bikɔs yu bɔdi nɔ de gɛt bɛtɛ ɔksijɛn.
If dis damej kɔntinyu fɔ bɔku, i kin mek pɔsin gɛt prɔblɛm dɛn we kin mek pɔsin in layf de pan denja sɔntɛnde. fכ egzampl, infεkshכn na di lכng εn di we aw di bכdi nכ de gεt inof כksijεn כ i de gεt tu mכch kabכn dayכksayd).
Us kayn `ILD` de?
As wi bin dɔn tɔk, i pas 200 kayn `ILD`. wan pan di wan dεm we kכmכn pas כl na `Idiopathic Pulmonary Fibrosis` . pan tap dat, `ILD` kin kכz bak bay tin dεm na wi wok envayroment (occupational exposure) כ kכnektiv tisu dizכrd. Sɔm ɔda ɛgzampul dɛn na:
- Asbestosis we pɔsin kin gɛt
- Silikɔsis we de mek pɔsin gɛt sik
- Nyumonitis we gɛt raytin
- Nɔn spɛsifi k Intɛrstitial Nyumonia
Wetin na di difrɛns bitwin `Interstitial Lung Disease` (ILD) ɛn `Pulmonary Fibrosis`?
Dis na sɔntin we kin mek bɔku pipul dɛn kɔnfyus. Pɔlmonari fibrosis we de na di bɔdiPulmonary Fibrosis (Pulmonary Fibrosis) na wan kayn ILD. Dat min se nɔto ɔl di ILD dɛn na pulmonary fibrosis. di pulmonary fibrosis na di fכmeshכn fכ ska dεm na di lכng dεm. Pan ɔl we dis skata na wan men tin we sɔm ILD dɛn gɛt, inflamɛns kin bi di men tin we ɔda ILD dɛn gɛt.
Udat de pan denja fɔ gɛt `ILD`?
Yu kin gɛt ILD mɔ if yu:
- If yu dɔn pas 70 ia.
- If yu na man. (Uman dɛn kin gɛt am bak, bɔt i kin bɔku pan man dɛn)
- If yu de smok ɔ yu dɔn smok trade.
- If yu dɔn gɛt sɔm sik dɛn bifo, fɔ ɛgzampul, Epataytis C, Tubakulosis, Nyumonia, COPD, ɔ Kɔnɛktiv Tisu Disease.
- If yu blo tin dɛn we de ambɔg yu lɔng bikɔs ɔf di wok we yu de du ɔ di say we yu de . Ɛgzampul dɛn: asbest, silika, mold, fɛns, ɔ baktri dɛm.
- If yu dɔn gɛt redyushɔn tritmɛnt to yu chɛst eria .
Aw siriɔs `ILD` de?
Bikɔs bɔku kayn `ILD` de, di kayn bad bad `ILD` we ɛnibɔdi kin gɛt kin difrɛn. Sɔm kin nɔ at fɔ du, bɔt ɔda wan dɛn kin rili siriɔs. di imכtant tin na di damej we di lכng dεm we plεnti kayn `ILD` de mek na `irrεvεrsibl`. Dis min se i nɔ kin izi fɔ mek di tisu we dɔn pwɛl. Sɔm siriɔs kayn `ILD` kin wɔs as tɛm de go (`progressive`).
Wetin na di sayn dɛm fɔ `ILD`?
Di sayn dɛm wae kin kam pan ILD na:
- I nɔ kin izi fɔ yu fɔ blo (dyspnea): Dis kin wɔs, mɔ we yu de du ɛksɛsayz ɔ we yu de du tin tranga wan.
- Wan dray kɔf (kɔf we nɔ gɛt blɔd).
- Fɔ fil taya bad bad wan (taya).
- Chɛst nɔ kin fil fayn ɔ i kin fil pen.
Dɛn sayn ya nɔr kin tranga fɔs, bɔt dɛn kin wɔs smɔl smɔl fɔ sɔm mɔnt ɔr ia. Ɔda sayn dɛm kin kam bak, i kin dipen pan di ɔndalayn kɔz fɔ di ILD.
Wetin na di tin dɛn we kin mek pɔsin gɛt `ILD`?
Dɛn kin sheb di tin dɛn we kin mek pɔsin gɛt ILD to tu men grup dɛn: di tin dɛn we dɛn dɔn no bɔt di tin dɛn we kin mek pɔsin gɛt ILD ɛn di tin dɛn we dɛn nɔ no bɔt .
Di Tin dɛn we Dɛn No bɔt di Kɔz
Dis min se ILD kin kam bikɔs ɔf ɔda sik we yu dɔn gɛt, ɔ bikɔs ɔf sɔm mɛrɛsin dɛn we yu de tek, redyushɔn tɛrapi, ɔ we yu de gɛt tin dɛn we de ambɔg yu na di say we yu de.
Sɔm pan di men rizin dɛn we dɛn dɔn no:
- Kɔnɛktiv Tisu Sik: Sɔm ɛgzampul dɛn na sik dɛn lɛk Rimatɔyd Atraytis (RA), Lupus, ɛn Sklerodama.
- Granulomatous Disease: Wan ɛgzampul na sarcoidosis.
- We yu blo sɔm tin dɛn: tin dɛn lɛk asbest, silika, tabak, ɛn bɛriliɔm.
- Inhalant allergy (Hypersensitivity Pneumonitis): Dis sik kin kam bay we yu inhal tin lɛk mold, fɛns, baktri, bɔd dɛn fɛda, ɔ smɔl smɔl tin dɛn we de na bɔd dɛn dɔti.
- Sɔm mɛrɛsin ɔ tritmɛnt dɛn: Fɔ ɛgzampul, mɛrɛsin dɛn lɛk amiodarone, nitrofurantoin, methotrexate, ɛn redyushɔn tɛrapi.
Di Kɔz dɛm we dɛn nɔ no (`Kɔz dɛm we wi nɔ no` ɔ `Idiopathic`)
Sɔntɛnde, dɔktɔ dɛn nɔ kin ebul fɔ fɛn di rayt tin we kin mek pɔsin gɛt ILD. Dis min se yu gɛt ILD we yu nɔ gɛt ɛni ɔda mɛrɛsin ɔ yu nɔ gɛt ɛnitin we go ambɔg yu. Wi kin kɔl dis idiopatik intastitial nyumonia . Bɔku kayn ILD dɛn de. Di kayn ILD we kin bɔku pas ɔl, usay dɛn nɔ kin fɛn ɛni kɔz, na idiopathic pulmonary fibrosis .
Aw fɔ no if pɔsin gɛt ILD? (Diagnosis) .
Yu dɔktɔ go fala sɔm step fɔ no if yu gɛt ILD. Fɔs, dɛn go chɛk yu, lisin to yu lɔng ɛn chɛk fɔ ɛni sawnd we nɔ kɔmɔn (lɛk krak krak). Dɔn dɛn go aks yu kwɛstyɔn dɛn lɛk:
- Yu kɔmplit mɛdikal istri ɛn ɛni ɔda mɛdikal kɔndishɔn we de naw.
- Bɔt di mɛrɛsin dɛn we yu de yuz naw ɔ we yu dɔn yuz trade .
- Ɛnibɔdi na yu famili gɛt ɛni wan pan dɛn sik ya ɔ kɔnektiv tisu sik?
- If yu wok ɔ yu ɔbi de mek yu gɛt tin dɛn we kin mek yu gɛt `ILD` .
Us tɛst dɛn kin yuz fɔ no if pɔsin gɛt `ILD`?
If di dɔktɔ saspek ILD, dɛn kin du dɛn tɛst ya:
- Pulmonary Function Tests (PFT): Dɛn kin du dis na tɛst fɔ brith, bɔt sɔntɛnde dɛn kin gɛt blɔd tɛst ɔ ɛksesaiz tɛst bak. Dɛn tin ya de chɛk aw yu lɔng dɛn de wok fayn fayn wan.
- Imej Tɛst: Dɛn kin tek ɛkstrem rayt na di chɛst ɔ ay-rɛzolushɔn CT skan (HRCT) fɔ luk aw di lɔng dɛn de. Wan HRCT kin si fayn fayn tin dɛn.
- Blɔd Tɛst: Dɛn kin tɛst blɔd sɛmpul we dɛn tek frɔm yu an fɔ si if ɛnitin de we dɛn no se kin mek pɔsin gɛt sik (e.g., kɔnɛktiv tisu sik) we kin mek pɔsin gɛt ILD.
- Brɔnkoskɔpi: .dis involv fכ pas wan tint tכb we gεt kεmεra (wan `bronchoscope`) tru yu nos כ mכt insay yu lכng fכ egzamin yu aywe dεm. sכmtεm dεn kin tek sεmpl sεl dεm (`lavage`) bak frכm yu lכng dεm.
- Bayopsi: Sɔntɛnde, dɛn kin pul wan smɔl tisu na di lɔng ɛn chɛk am wit maykroskɔp. Dis kin ɛp fɔ no di rayt kayn ILD. di bayopsi kin bi tru brכnkoskopi כ tru sכm כpεrayshכn (sכjεkכl lכng bayopsi).
Wetin na di tritmɛnt dɛm fɔ `ILD`?
I sɔri fɔ no se, no tritmɛnt stil nɔ de we go ebul fɔ mɛn `ILD` ɔltogɛda.
Bɔt nɔ giv ɔp fɔ gɛt op. Di tritmɛnt na fɔ trit di ɔndalayn kɔndishɔn we mek ILD, kɔntrol di sayn dɛm, ɛn slo di sik fɔ go bifo. Yu dɔktɔ kin gi yu fyzikal tritmɛnt, ɔda ɔksijɛn, ɔ mɛrɛsin fɔ mek yu nɔ swel na yu lɔng ɔ fɔ kɔntrol skata.
Wetin na di mɛrɛsin ɛn tritmɛnt dɛn we dɛn kin yuz fɔ `ILD`?
- Kɔtikosterɔyd: Mɛrɛsin lɛk prɛdnisɔn kin ɛp fɔ ridyus di swɛlin na di lɔng dɛn.
- Anti-fibrotic ɛn Cytotoxic Drugs: Dɛn drɔgs ya kin slo di rεt fɔ skata na di lכng. Ɛgzampul dɛn: Azathioprine, Sayklofosfamid, Pirfenidone, Nintedanib.
- Bayolojikal Drug: Dɛn kin yuz drɔgs lɛk Rituximab fɔ trit sɔm ɔtoimyun sik dɛn ɛn ɔda kɔndishɔn dɛn we kin mek pɔsin gɛt ILD.
- Tritmɛnt fɔ GERD: If yu gɛt gastroesophageal reflux disease (GERD), i kin mek ILD wɔs. So, dɛn kin gi yu mɛrɛsin fɔ kɔntrol di asid we de na yu bɛlɛ.
- Pulmonary Rehabilitation: Dis na spɛshal ɛksɛsayz ɛn ɛdyukeshɔn program. We yu de du ɛksasaiz fɔ blo ɛn ɛksesaiz fɔ yu bɔdi kin ɛp fɔ mek yu lɔng dɛn strɔng ɛn mek i izi fɔ yu fɔ blo.
- Ɔksijɛn Tɛrapi: If yu blɔd ɔ di tisu dɛn nɔ de gɛt bɛtɛ ɔksijɛn, yu dɔktɔ kin gi yu ɔda ɔksijɛn. Dɛn kin gi dis tru wan kanula na di nos ɔ wan fes mask.
- Lɔng Transplant: Fɔ pipul dɛn we gɛt ILD we rili bad, fɔ transplant lɔng kin bi las tin fɔ du.
Di sayd ɛfɛkt dɛn we di tritmɛnt kin gɛt
Sɔm tritmɛnt fɔ ILD (espɛshali kɔtikosterɔyd ɛn saytotoksik drɔgs) kin mek yu imyun sistɛm wik. So, yu dɔktɔ go de wach yu ɔltɛm ɛn wach fɔ di prɔblɛm dɛn we kin apin.
Yu tink se dɛn kin mek dɛn nɔ gɛt ILD?
I nɔ kin izi fɔ mek dɛn nɔ gɛt bɔku kayn ILD. Bɔt yu kin du dɛn tin ya fɔ ridyus yu risk fɔ gɛt ILD:
- Manej eni mεdikal kכndyushכn wae yu כlrεdi gεt (e.g., kכnektiv tisu sik dεm).
- Nɔ inhal tin dɛn we de ambɔg di lɔng dɛn.
- If yu de wok na say dɛn usay asbest, mɛtal dɔst, ɔ kemikal de, wɛr fayn mashin fɔ blo (mask we de filta di tin dɛn we de na di briz).
- Alɛji fɔ lɔng tɛm kin kam bikɔs ɔf tin dɛm lɛk hay, gren, bɔd dɔti ɔ fɛda, ɛn di we aw dɛn kin ɔt ɛn kol. Wear respirator we yu de wok wit dɛn tin ya.
- If yu gɛt wan sik lɛk kɔnɛktiv tisu sik ɔr sarkoidosis, tɔk to yu dɔktɔ bɔt aw fɔ mek yu nɔ gɛt ILD.
- If yu de smok, yu fɔ stɔp fɔ smok. If yu nɔ de smok, nɔ bigin.
Wetin di fiuja de hol fɔ pɔsin we gɛt `ILD`?
If yu gɛt ILD, yu ɛn yu dɔktɔ go wok togɛda fɔ no aw fɔ mɛn yu sik, i go dipen pan wetin mek yu gɛt di ILD. Fɔ ɛgzampul, if yu ILD na yu wok ɔ yu gɛt alɛji (hypersensitivity pneumonitis), yu kin nid fɔ stɔp fɔ wok wit di tin we de mek yu gɛt di ILD ɔ tek spɛshal tin fɔ tek tɛm wit.
Pan ɔl we mɛrɛsin kin ridyus di swɛlin, di skata we kin apin na di lɔng dɛn bikɔs ɔf ILD kin de sote go. Dis min se dɛn nɔ go ebul fɔ chenj di damej. If yu gɛt wan sik we de ɔnda yu, if yu manej am fayn fayn wan, dat kin ɛp fɔ mek yu nɔ pwɛl mɔ. If yu gɛt ILD we dɛn nɔ go ebul fɔ fɛn ɛni kɔz fɔ (idiopathic), yu dɔktɔ go trit yu sik dɛn ɛn tray fɔ mek yu nɔ pwɛl mɔ.
Wetin na di poshubul komplikashɔn dɛm fɔ `ILD`?
If ILD kam tranga, prɔblɛm dɛn kin apin we kin mek pɔsin in layf de pan denja, lɛk:
- Pulmonari Haypatɛnshɔn
- Lɔng we dɔn kol (Nyumotɔraks) .
- Infεkshכn dεm na di Lכng
- Di we aw pɔsin de blo fayn
- Kansa na di Lɔng
Wetin na di layf we pɔsin we gɛt `ILD` de liv?
Dis na kwɛstyɔn we bɔku pipul dɛn kin aks. Di layf we pɔsin we gɛt `ILD` de liv, de dipen pan wetin mek di `ILD` de ɛn aw i siriɔs. Sɔm pipul kin liv nɔrmal layf wae nɔr gɛt tritmɛnt ɔr wit smɔl tritmɛnt if dɛn `ILD` nɔr siriɔs. If yu sik nɔr de wɔs (dat na if i `stebul`), di lukin-grɔn (`prognosis`) kin rili fayn.
Bɔt fɔ di wan dɛn we gɛt di kayn `ILD` we kin rili bad ɛn we kin wɔs kwik kwik wan, di layf we dɛn kin liv afta dɛn dɔn no di sik kin shɔt lɛk 3-5 ia. Nɔ mek yu fred wit dɛn statystik ya. Dis kin difrɛn fɔ ɛnibɔdi.
Aw a go tek kia ɔf misɛf if a gɛt `ILD`?
If dɛn dɔn no se yu gɛt ILD, di bɛst we fɔ tek kia ɔf yusɛf na fɔ wok wit yu dɔktɔ fɔ mek wan plan fɔ manej yu sik dɛn ɛn fɔ mek yu nɔ pwɛl mɔ.
- Trit ɛni ɔndalayn kɔndishɔn we kin de kɔz di ILD.
- Kɔntrol tin dɛm wae kin mek ILD wɔs (e.g., GERD).
- If yu de wok wit tin dɛn we de pwɛl yu lɔng ɔ we de mek yu gɛt alɛji fɔ lɔng tɛm, yu nid fɔ tek spɛshal tin dɛn fɔ mek yu nɔ gɛt prɔblɛm.
Ustɛm a fɔ go to dɔktɔ?
Si dɔktɔ wantɛm wantɛm if yu gɛt dɛn sayn ya:
- Smɔl smɔl i de mek i nɔ izi fɔ blo.
- I nɔ kin izi fɔ yu fɔ blo we yu de du ɛksɛsayz.
- Wan dray kɔf we nɔ de dɔn.
Di kwik we dɛn de trit ILD, na di mɔ i go bɛtɛ.
Us kwɛstyɔn dɛn a fɔ aks mi dɔktɔ?
Nɔ fɔgɛt fɔ aks dɛn kwɛstyɔn ya we yu go si yu dɔktɔ:
- Wetin mek a gɛt dis sik?
- Us tritmɛnt opshɔn dɛn a gɛt?
- Yu tink se dis tin go wɔs?
- Yu tink se di damej we de na di lɔng dɛn kin ridyus?
- Us chenj dɛn a go mek fɔ mek mi layf bɛtɛ?
Dɔzin kayn ILD de. Sɔm nɔ kin vɛks, sɔm kin rili siriɔs. Yu kin si sɔm statystik dɛn we de mek yu fred na di Intanɛt, bɔt na yu dɔktɔ nɔmɔ go ebul fɔ tɛl yu di rayt tin bɔt yu patikyula sik. Tɔk ɔnɛs wit yu dɔktɔ ɛn ɔndastand klia wan wetin yu de op fɔ. Yu ɛn yu dɔktɔ kin mek wan plan fɔ kɔntrol yu sik dɛn ɛn liv di bɛst kwaliti layf.
Lɛ wi mɛmba di tin dɛn we impɔtant pas ɔl (Take-Home Message)
- `ILD` na grup fכ sik dεm we de pwεl di dilik tisu dεm na di lכng, we de mek i at fכ brith.
- Dray kɔf, i nɔ kin izi fɔ blo, ɛn taya na di men sayn dɛm.
- Bɔku rizin dɛn kin de, ɛn sɔntɛnde dɛn nɔ kin fɛn ɛni rizin.
- Pan ɔl we dɛn nɔ gɛt kɔmplit mɛrɛsin, tritmɛnt dɛn de fɔ kɔntrol di sayn dɛm ɛn fɔ mek di sik nɔ wɔs.
- I impɔtant fɔ avɔyd fɔ smok, nɔ fɔ blo tin dɛn we de ambɔg yu, ɛn kɔntrol di prɔblɛm dɛn we de mek yu sik.
- If yu gɛt sɔm sayn dɛm, nɔr panik ɛn go to dɔktɔ. Fɔ no di sik kwik kwik wan ɛn fɔ trit am rili impɔtant.
Wi op se yu go si se dis infɔmeshɔn go ɛp yu. Stay wit wɛlbɔdi!
` intastitial lכng sik, ILD, lכng sik, rεspiretכri distres, dray kכf, pulmonary fibrosis, lכng ska, rεspiretכri simptom dεm











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