Yu kin fil taya ɔl di de ɛn yu nɔ gɛt trɛnk fɔ du ɛnitin? Bɔku tɛm wi kin tink se na bikɔs wi de wok tumɔs, wi nɔ de it fayn, ɔ wi nɔ de slip fayn. Bɔt, yu no se sɔntɛm dip rizin de fɔ ɔl dis insay wi bɔdi? Yu dɔn yɛri bɔt di smɔl smɔl ɛnaji faktri dɛn we de na wi bɔdi? Na dεn tin ya wi kin kכl maytochכndria. If dɛn tin ya nɔ de wok fayn, big prɔblɛm kin kam we wi nɔ kin ivin tink bɔt. So lɛ wi tɔk bɔt dis ditayli ɛn rili simpul wan tide.
Wetin na dɛn maytokɔndria ya?
Fɔ tɔk am simpul wan,
di maytochondria dɛn tan lɛk smɔl smɔl injin ɔ pawa plant dɛn we de na ɔlmost ɔl di sɛl dɛn na wi bɔdi. Imajin, if wi bɔdi na bin big siti, dɛn maytokɔndria ya na di pawa plant dɛn we de gi ilɛktrishɔn to da siti de. we wi yuz di it we wi de it εn di כksijεn we wi de blo, dεn sכm sכm maytochכndria dεm ya de prodyuz 90% pan di enεji we wi bכdi nid fכ rכn, jomp, tink, wok,
εn fכ sכt, liv. Ɛspɛshali na di ɔgan dɛn we de wok ɔltɛm ɛn we nid mɔ ɛnaji, lɛk wi
at, bren, ɛn mɔsul dɛn, bɔku bɔku pan dɛn maytochondria ya de. Bikɔs dɛn ɔgan dɛn de nid mɔ ‘kɔrɛnt’ pas ɔda wan dɛn.
So wetin na dɛn mitochondrial sik ya?
Imajin, wetin go apin if dɛn pawa plant dɛn we a bin tɔk bɔt bin stɔp fɔ wok fayn wantɛm wantɛm ɛn stɔp fɔ mek inof ɛnaji? Di wan ol siti go dak, ɛn wi bɔdi nɔ go wok fayn bak. Na da tɛm de kɔndishɔn dɛn we dɛn kɔl
‘Mitochondrial Diseases’ kin kam. Dɛn tin ya kin de
fɔ lɔng tɛm , we min se dɛn kin las fɔ ɔl dɛn layf. Bɔku tɛm, dɛn kin gɛt dɛn jɛnɛtiks, we min se
dɛn kin gɛt frɔm mama ɛn papa to pikin dɛn. Sɔmtɛm dɛn sik ya kin de we dɛn bɔn am, ɛn ɔda tɛm dɛn kin apin leta.
Wetin na di tin dɛn we kin mek pɔsin gɛt dɛn sik ya?
Bɔku tɛm, di men rizin fɔ dis na bikɔs ɔf di jɛnɛtiks. Dat min se sɔm tin dɛn we nɔ fayn na di jin dɛn we wi gɛt frɔm wi mama ɛn papa. Dis kin apin pan sɔm men we dɛn.
| Tayp fɔ Inhɛritɛshɔn | Fɔ tɔk am simpul wan... |
|---|
| Ɔtosɔmal Risɛsiv Inhɛritɛns | insay dis kes, di pikin kin gεt wan difεktiv jin (mutated gene) frכm di mama εn papa. Dɔn, ɛni pikin na di famili gɛt 25% chans fɔ gɛt di sik. |
| Ɔtosɔmal Dɔminant Inhɛritɛns | Wetin kin apin ya na dat di pikin kin gɛt wan jin we nɔ fayn frɔm wan mama ɔ papa nɔmɔ, we na di mama ɔ di papa. Dɔn, ɛni pikin na di famili gɛt 50% chans fɔ gɛt di sik. |
| Mitochondrial Inhɛritɛshɔn we pɔsin kin gɛt | Dis wan spɛshal smɔl. di maytochכndria dεm gεt dεn yon DNA. insay dis inhεrit, mama we gεt difεktiv maytochכndria gεt 100% chans fכ כl in pikin dεm fכ inhεrit dis sik. |
| Random Muteshɔn dɛn we dɛn kin mek | Na smɔl tɛm nɔmɔ, di chenj kin apin we di pikin in jin dɛn jɔs kam, ɛn di mama ɛn papa nɔ gɛt ɛni fɔlt. |
Apat frɔm dat, di maytochondrial dysfunction kin gɛt fɔ du wit sɔm kayn mɛrɛsin, lɛk Alzaima, muscular dystrophy, dayabitis, ɛn sɔm kayn kansa.
Wetin na di sayn dɛm fɔ dɛn sik ya?
Dis na di say we bɔku pipul dɛn kin kɔnfyus. De sayn dɛm fɔ dɛn sik ya kin difrɛn frɔm wan pɔrsin to ɔda pɔrsin. Di rizin na dat di sayn dɛm kin difrɛn difrɛn wan fɔ di ɔgan na di bɔdi wae gɛt dis sik. Pan ɔl we sɔm pipul dɛn kin gɛt sayn dɛn we
nɔ kin rili at fɔ si, ɔda wan dɛn kin gɛt bad bad wan.
Dɛn sayn ya kin sho pan ɛni ej. Dɔn bak, bikɔs dɛn sayn ya tan lɛk ɔda kɔmɔn sik dɛn, sɔntɛnde i kin at fɔ no di sik.
Di tebul dɔŋ ya de sho sɔm pan de sayn dɛm wae kin apun.
| Sistem/ɔgan we dɛn afɛkt | Sɔm sayn dɛn we kin apin |
|---|
| Grɔw ɛn mɔsul dɛn | I nɔ kin gro fayn, di mɔsul dɛn kin wik, ɛn i kin taya we i de du ɛksɛsayz. |
| Bren ɛn di nerv dɛn | Lanin disabiliti, divɛlɔpmɛnt delay, ɔtizm spɛktrum disɔda, maygren, siiz, strok, ɛn dimɛnshɔn. |
| Ɔgan dɛn we de mek pɔsin fil fayn | I nɔ kin ebul fɔ si ɛn yɛri fayn. |
| Ɔgan dɛn we de insay di bɔdi | At, kidni ɔ liva sik, dayabitis, tayroyd prɔblɛm. |
| Dijestiv sistɛm | I nɔ izi fɔ swɛla, bɛlɛ de at, dayarɛa ɔ kɔnstipɛshɔn, vɔmit. |
Aw fɔ no di sik?
As a bin dɔn tɔk bifo tɛm, di sayn dɛm fɔ dɛn sik ya kin rili difrɛn, so i kin tranga smɔl fɔ no wetin na di sik.
Dɛn nɔ kin ebul fɔ no am wit wan tɛst. Na dat mek dɔktɔ kin chɛk pɔsin we sik ɛn sɛn dɛn fɔ du difrɛn tɛst dɛn.
Test dɛn we dɛn kin du bɔku tɛm
- Fɔ tek tɛm rivyu di famili in mɛrɛsin istri .
- Fɔ du wan kɔmplit ɛgzam fɔ di bɔdi ɛn di nyurolɔjik .
- fכ no di kεmikכl chenj dεm na di bכdi tru bכdi εn urine tεst (Mεtabolik εgzam).
- MRI skan (especially fכ bren prכblεm).
- Wan ECG (Electrocardiogram) ɔ Echocardiogram tɛst fɔ chɛk aw di at de wok.
- Speshal DNA tɛst fɔ no di tin dɛn we nɔ fayn na di jɛnɛtiks .
- Sɔntɛnde, i kin nid fɔ tek smɔl mɔsul ɔ skin fɔ tɛst (bayopsi) .
Wetin na di tritmɛnt dɛm fɔ dis?
Wan kwɛstyɔn we bɔku pipul dɛn kin aks na if kɔmplit mɛrɛsin de fɔ dis. Fɔ tɔk tru,
no patikyula mɛrɛsin nɔ de yet fɔ di sik dɛn we de na di maytochondrial. Bɔt, nɔ fred dat. Bɔrku tritmɛnt de fɔ kɔntrol de sik ɛn fɔ mek di sik nɔr de go bifo kwik kwik wan. Di tritmɛnt dipen pan di sikman in sik, di ɔgan dɛm we di sik afɛkt, ɛn aw di sik bad. Ilɛksɛf tu pipul dɛn we gɛt di sem sik gɛt di sem tritmɛnt, i nɔ kin wok di sem we.
Sɔm pan di men we dɛn fɔ trit am:
- Vitamin ɛn supamakit dɛn: Sɔm vaytamɛn dɛn kin ɛp fɔ mek di maytochondrial wok fayn.
- Ɛksesaiz: Ɛspɛshali ɛksesaiz we de mek yu mɔsul dɛn strɔng. Dɛn fɔ du dɛn tin ya ɔnda di gayd we yu dɔktɔ ɔ pɔsin we de mɛn yu bɔdi go gi yu.
- Fizik tritmɛnt , ɔkupeshɔn tɛrapi, ɛn tɔk tɛrapi : Dɛn tin ya kin ɛp di pɔsin fɔ du di tin dɛn we i kin du ɛvride izi wan.
Dɔn bak, dɛn kin advays di wan dɛn we sik fɔ de fa frɔm sɔm tin dɛn. Fɔ ɛgzampul, i rili impɔtant fɔ avɔyd tin dɛn lɛk fɔ de na say we kol ɔ wam pasmak, fɔ angri, fɔ nɔ slip fayn, fɔ strɛs,
fɔ smok, ɛn fɔ drink rɔm .
Mɛsej we dɛn kin kɛr go na os
- Maytochondria tan lεk sכm sכm pawa plant dεm we de gi enεji to di sεl dεm na wi bכdi.
- Di sik dɛm wae kin kam wae dɛn nɔr de woke fayn kin te fɔ lɔng tɛm ɛn bɔrku tɛm dɛn kin gɛt frɔm dɛn jɛnɛtiks.
- Di sayn dɛm kin rili difrɛn ɛn kin bi se yu mɔsul dɛn kin wik , yu nɔ kin ebul fɔ gro fayn, yu nɔ kin si ɛn yɛri fayn, ɛn at sik.
- Pan ɔl we no patikyula mɛrɛsin nɔ de fɔ dɛn sik ya, yu kin liv gud layf bay we yu kɔntrol di sayn dɛn ɛn ajɔst di we aw yu de liv yu layf.
- If yu ɔ sɔmbɔdi na yu famili gɛt dis sik, i rili impɔtant fɔ tɔk to yu dɔktɔ bɔt aw fɔ advays yu bɔt yu jɛnɛtiks bifo yu bɔn pikin. Di bɛst tin fɔ du na fɔ nɔ panik, bɔt fɔ gɛt di rayt advays frɔm dɔktɔ.
Maytochכndria, Maytochכndria, Maytochכndrial Sik, Jεnεtik Sik, Enεji, Sεl dεm, Simptom dεm, Tritmεnt
💬 Comments (0)
No kɔmɛnt nɔ de yet. Ad yu kɔmɛnt ya fɔ di fɔs tɛm.
Ad yu kɔmɛnt