A châng chuan i taksa pum puiah bump te te, itchy tak tak i nei nghal mai thei a ni lawm ni? A châng chuan hengte hi tuiin a khat blister lian takah a chang thei bawk. Mi tam tak chuan hei hi allergy pangngai emaw, rulhut seh ang chi emaw anga an ngaih laiin, fimkhur deuh deuh a ngai a, vun natna Bullous Pemphigoid tih a nih theih avangin. A hming hi a mak deuh mai thei, mahse hlau suh. Vawiin hian he thu hi i hriatthiam theih tur awlsam takin kan sawi dawn a ni.
Bullous Pemphigoid hi eng nge ni tak tak?
A awlsam zawngin, Bullous Pemphigoid hi vun natna hmuh tur awm lo tak a ni a, vun natna nasa tak leh tuiin a khat blisters khauh tak tak a lo awm thin
Heng blisters te hi a te a ni thei a, taksa hmun khatah chauh a awm thei a, taksa pum puiah a darh thei bawk. Vun inzawmkhawmna hmunah an awm tam ber. Entir nan:
- A hnuai lam (axilla) .
- Groin area ah chuan
- Pum chhung
- Kut leh ke fold-ah te
Ngaihtuah teh, i armpit chu a sen nghal a, ni engemaw zat chhung chu nasa takin a itche bawk. Ni hnih emaw ni thum emaw hnuah chuan chu hmunah chuan tuiin a khat blisters a lo awm tan thin. Chutiang chuan a intan tlangpui. Mi thenkhat tan chuan heng blisters te hi mucous membrane-ah te pawh a lo awm thei a, chu chu ka chhungah te, leiah te, kawr chhungah te, mit chhungah te pawh a awm thei a ni.
Hei hi immune system disorder a ni em? (Autoimmune Natna) 1.1.
Ni e, a dik e. Bullous Pemphigoid hi autoimmune natna a ni a . Tunah chuan chu chu eng nge ni tih i ngaihtuah tawh mai thei.
Kan taksa invenna (immune system) hi ram venghimtu sipai ang a ni. He system hna chu hnam dang natna hrik (bacteria, virus) do a, natna laka kan taksa venhim hi a ni. Mahse, autoimmune disease-ah chuan he sipaite hian kan cell hrisel tak takte chu a rawn bei sual tan ta a ni.
Bullous Pemphigoid ah hian immune system hian kan vun chunglam layer (the epidermis) leh a hnuaia layer (the dermis) inzawmkhawmtu tissue nalh tak chu a bei thin. He attack hian layer pahnih inkarah hian tui a awm khawm a, chu chuan chutiang blister lian tak tak, khauh tak chu a siam ta a ni.
He natna hi tuin nge vei tam ber?
He natna hi kum eng pawhah a vei thei a, mahse kum 60 chunglam ah a tam ber a, mahse, a chang chuan naupang zawkah a awm thei. Hmeichhia leh mipa pawh a nghawng vek a ni.
Tin, zirchianna atanga a lan dan chuan neurological disorder thenkhat nei te chu Bullous Pemphigoid vei theihna chance a sang deuh hlek a ni.
- Dementia natna (dementia) a awm
- Parkinson natna a ni
- Thai
- Epilepsy natna a ni
- Multiple sclerosis natna a ni
Hei hi thihna thlen thei a ni em?
A tlangpuiin, uluk taka enkawl a nih chuan he natna hi tha taka thunun theih a ni. Mahse, a chang chuan heng blisters te hi a puak a, a kai chuan natna chu a na thei hle. Hetiang natna hi a hlauhawm thei hle a, a bik takin kum upa tawh emaw, damdawi lam harsatna dang (zunthlum emaw, thinlung natna emaw) nei tan chuan a hlauhawm thei hle. Chuvangin, natna lan chhuah veleh Doctor pan vat a, enkawl tan a tha ber.
He natna lan chhuah dan berte chu engte nge ni?
He natna lan chhuah dan hi a hnuaia table atang hian chiang takin i hrethiam ang u.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Itching leh rashes nasa tak a awm | Natna hi tuar theih loh khawpa natna atanga intan a ni fo. A châng chuan crab ei hnu ang maiin a sen a, a blister thei bawk. |
| Tui khata khat blisters (Bullae) . | Hei hi a symptom ber a ni. Heng blisters te hi a tlangpuiin a lian a, a khauh a, a puak awlsam lo. A chhunga tui chu a chiang emaw, thisen hring deuh emaw a ni thei. |
| Blisters a puak hnuah | Blisters a puak chuan hliam te tak te (sore or ulcer) a siam thei. Heng hliamte hi tlem a na thei hle. |
| Blister chhehvel vun chu | Blister chhehvel vun chu a pangngai thei a, a sen a, a rawng a danglam deuh thei bawk. |
| Scarring a awm | A tha ber chu heng blisters te hian an dam hnuah hliam lian tham an hnutchhiah lo tlangpui. |
Eng thilin nge Bullous Pemphigoid hi a thlen?
Kan sawi tawh ang khan hei hi autoimmune condition a ni. Mahse doctor-te chuan kan immune system hian hetiang hian kan vun ngei pawh a rawn bei nghal mai chhan chiang tak an la hmu lo.
Amaherawhchu, thil \henkhat chu natna lo awm theihna tura ‘trigger’ ni thei tura ngaih a ni.
- Damdawi thenkhat: Damdawi thenkhat, a bik takin zunthlum natna atana hman thin, alogliptin ang chi te.
- Ultraviolet light (UV light): Ni ênga awm tam lutuk.
- Radiation therapy (Ionizing radiation): Cancer ang chi natna hrang hrang tan radiation therapy pek thin a ni.
Ei leh in hian hei hi a nghawng em?
Hei hi mi tam takin harsatna an neih a ni. Dik tak chuan diet leh Bullous Pemphigoid hi direct link a awm tih scientific evidence a awm lo. Mahse, damlo thenkhat chuan ei tur thenkhat (e.g., dairy, gluten) an ei loh hnuah an natna lan chhuah dan a reh tih an sawi.
Chutiang bawka i hriat chuan hemi chungchang hi i doctor nen sawipui a tha ber. Ani chuan ei leh in journal ziak turin a ti thei che a, ei tur ṭhenkhatin i natna lan chhuahna a thlen em tih en turin a ti thei che a ni.
A pawimawh ber chu Bullous Pemphigoid hi natna hrik kai theih a ni lo. Mi pakhat atanga mi dangah inbiakpawhna hmangin a darh lo. Chuvangin damlo hi inhlat leh hlauh chhan tur a awm lo.
Engtin nge doctor hian hei hi a hriat theih?
Heng symptoms nei doctor i pan chuan i vun hi uluk takin a enfiah hmasa ang. Tichuan zawhna tlemte an zawt ang che.
- Engtik atang khan nge heng symptoms te hi a lo intan?
- Blisters ah hian pus emaw thisen emaw a awm em?
- Khawsik i nei em?
- Damdawi thar i ei tan tawh a awm em?
Chumi hnuah chuan test eng emaw zat tih a tha a, a natna hmuhchhuah a nih leh nih loh finfiah a tha .
| Fiahna | Engnge i tih? |
|---|---|
| Thisen test a ni | I thisen sample lak a ni a, vun laka antibodies bik a awm leh awm loh test a ni. |
| Vun biopsy tih a ni | Hei hi test chiang ber a ni. A vun chu a blister awmna hmun atang chuan a numb deuh a, vun te tak te tak te chu la in microscope hmangin an enfiah thin. Chumi hnuah chuan vun layer hrang hrang inthen dan leh immune cells deposit dan enin natna hi finfiah theih a ni. |
Hei hi eng enkawlna nge ni?
Natna nasat dan azirin enkawl dan a inang lo. I doctor chuan i tana tha ber tur enkawlna a ruat ang.
Natna na lo nei te tan
Natna a na lutuk lo va, taksa pum puiah hian blister te te a awm a nih chuan steroid cream emaw ointment emaw hmangin blisters ah hian hnawih thin a ni .
Natna hniam lam emaw, na tak emaw nei tan
Natna hi taksa pumpuiah a darh tawh a, blister tam tak a awm chuan cream bakah damdawi ei tur pek a ngai mai thei.
- Oral Corticosteroids: Steroid pills te hi Prednisone ang chi te hi a ni. Hengte hian immune system hnathawh a control a, rang takin blisters siam chu a titawp thin.
- Steroid-sparing agents: Hun rei tak chhunga steroid hman avanga side effects tihziaawm nan damdawi dang dapsone, mycophenolate mofetil, leh azathioprine te pawh pek theih a ni.
Enkawlna dang
Mi thenkhat tan chuan steroid damdawi hi a tha lo a nih chuan doctor chuan antibiotic pill tetracycline emaw doxycycline emaw a pe thei bawk.
Engtin nge in lamah symptoms i control theih ang?
Damdawi ei lai hian in lama tih theih engemaw zat a awm a, hei hian he natna leh hahdam lohna hi a tihziaawm thei a ni.
| Thurawn | Engvangin nge a pawimawh? (Engvangin nge a pawimawh?) |
|---|---|
| Cotton ang chi natural fiber atanga siam thawmhnaw loose-fitting ha rawh. | Tight, rough thawmhnaw hian vun a tifai thei a, itching leh blisters a ti na zual thei. |
| Ni êng tam lutuk hi pumpelh rawh. Sunscreen hmang rawh. | Ni eng hian a chang chuan symptoms a ti na zual thei. |
| Hliam fai taka dah thin ang che. | Blisters te chu antiseptic soap leh tui hmangin silfai la, i doctor-in a rawt antibiotic ointment hmangin hnawih la, non-adhesive bandage hmangin khuh rawh. Hei hian hri kai venna kawngah a pui thei a ni. |
| I vun chu a hnim reng ang. | Moisturizing lotion tha tak, coconut oil emaw shea butter emaw hman hian vun vawt leh itching tihziaawmna kawngah a pui thei a ni. |
I hmuiah blisters i neih chuan hengte hi ngaihtuah ve bawk ang che
I hmuiah blisters i neih chuan ei leh in a harsa hle thei. Heng tips te hian chutih hunah chuan a pui ang che.
- Chaw nêm tak tak, soup, mashed potato, pudding, leh yogurt te ei rawh.
- Chaw lum a lum vek hnuah ei thin ang che.
- Chaw khauh leh rimtui tak tak chips, crackers, chhangphut chi hrang hrang, leh thlai leh thei raw te ei loh tur.
- Acid leh spicy ei tur lime, tomato, chili, leh salsa te ei loh tur.
- Zu hi pumpelh vek rawh.
He natna hi eng chen nge a awm ang? Eng nge thleng leh ang?
Bullous Pemphigoid hi mahni inrintawkna nei thei natna a ni a, a tlangpuiin kum engemaw zat (a tam zawkah chuan kum 5 vel) a awm thin. Enkawlna pawh a chhang tha hle bawk.
Mahse, he hun chhung hian natna hi a lo chhuak thei a ni. A chang chuan, symptoms te chu a bo vek (remission). Chutiang hun lai chuan i doctor chuan i damdawi ei zat tihtlem emaw, rei lo te chhung tihtawp emaw a tum mai thei. Symptoms a lo lang leh a (flare-up) chuan enkawlna i tan leh a ngai dawn a ni.
Engtikah nge Doctor ka hmuh ang?
I taksaah chhan hriat loha tui hring (water blisters) i lo awm a, chu chu i hrual (itching) nen a inzawm chuan doctor pan nghal tur a ni. Self -treat emaw, ignore emaw suh. I natna i hriatchhuah thuai a, i enkawl tan chuan harsatna i neih theihna a hniam zawk.
Take-Home Thuchah a ni
- Bullous pemphigoid hi vun natna a ni a, immune system hnathawh dan a inthlak danglam vang a ni. Natna hrik kai theih a ni lo.
- A lan chhuah dan ber chu vunah natna nasa tak leh vunah lian tak tak, khauh tak, tuiin a khat a ni.
- Hei hi kum upa lam zingah a tam ber a, mahse kum eng pawhah a lo awm thei.
- Heng symptoms te hi i neih chuan a chhan hriat chian lohvin doctor thurawn la nghal rawh.
- Enkawlna hian natna a thunun thei hle. Amaherawhchu, faina lamah fimkhur hle a pawimawh a, a hliam hi natna hrik a luh chuan a hlauhawm thei a ni.











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