I thinlung chu a na nghal vek em ni? Hei hi CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia) a ni thei!

A châng chuan, i chau lutuk emaw, i thinlunga thil lian tak tak, hlimna nasa tak, lungngaihna emaw, hlauhna emaw i hriat lai hian, i thinlung chu a thawk rang zawk a, i rilru a nghet hle tih i hria em? I mit a sen a, i lu a buai mai thei em? Mak ti suh, heng thilte hi naupang tê tê chungah pawh a thleng thei a ni. Vawiin hian heart rhythm-a thil thleng bik kan sawi dawn a, chu chu tlem a tlem hle mahse hriat a pawimawh hle.

CPVT (Catecolaminergic Polymorphic Ventricular Tachycardia) tih hi eng nge ni?

A awlsam zawngin sawi ila, CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia) hi thinlung rhythm-a awm thin a ni. Chutah chuan, i thinlung hnuai lam, chu chu thinlung hnuai lam, a nih loh leh doctor-te’n an tih angin, ventricles -te chu exercise i tih hian, i inkhelh a, a nih loh leh lungkhamna nasa tak i neih chuan, hlimna nasa tak, hlauhna, a nih loh leh phurna nasa tak i neih chuan rang takin leh a pangngai lo takin an thawk ṭan nghal a ni.

Hetiang hian han ngaihtuah teh: kan thinlung hi tui pump ang a ni. Taksa pum puia thisen pump chhuaktu a ni. Chuvangin, he thinlung hi a na lutuk a, chu chu rhythm pangngai lo takah a thawk a, thisen chu uluk taka pump chhuah a, taksa peng zawng zawnga thawn chhuah a harsat phah a ni. Hei hi a bul berah chuan CPVT-a thil thleng a ni.

He natna hi CPVT an tih hi engtiang chiahin nge a awm?

Dik tak chuan he CPVT an tih hi a tlem deuh a ni . Damdawi lam mithiamte sawi dan chuan mi sang sawm (10,000) zinga pakhat vel chauhvin he natna hi an vei nia chhut a ni. Chuvangin, mi zawng zawngin an hre vek lo mai thei.

Engvangin nge he CPVT hi a lo awm? A chhan chu eng nge ni?

Mi tam takin zawhna an nei a, "Engvangin nge hetiang hi a lo awm?" CPVT kan neih chhan ber chu kan genes inthlak danglamna, mutation . I hria em, kan taksa chhunga thil awm zawng zawng hi heng genes te hian a thunun vek a ni.

• A tam zawkah chuan he genetic variation hi i nu emaw i pa emaw atang emaw, an pahnih atang emaw hian i rochun thei a ni .
• Mahse, a tlem hle, chu chu a tlem hle a ni, he genetic variation hi mi thar taksaah randomly , nu leh pa atanga genetic influence engmah awm lovin a thleng thei a ni.

Chuvangin, he genetic change hian heart cells chhunga calcium ion control danah harsatna a siam a ni. Chu chu thinlung a stress lai emaw, exercise lak lai emawa thinlung a thawk chak zawk chhan ber a ni.

CPVT natna lan chhuah dante chu engte nge ni? Engtin nge kan hriat chian?

CPVT chhinchhiahna hi naupan lai atanga tan a ni tlangpui a, a tlangpuiin kum 7 leh 12 inkar a ni .

CPVT symptom ni thei thil thenkhat chu hetiang hi a ni:

• Mi pangngai aia tamI muhil fo thei a, a nih loh leh i lu a buai emaw, i lu a hah lo emaw pawh a ni thei. A châng chuan chhan hriat lohvin i hriatna i hloh thut mai thei a, i tlu mai thei bawk.
• Heart palpitations hi rang tak, rang tak, pounding sensation a ni a, i rilru chhungah mi pakhat a tlan lut ang maiin a lang .
• Mi thenkhat chuan seizures ang chi condition pawh an nei thei bawk . Hei hi a chhan chu thinlungin thisen a pump tha tawk loh chuan thluaka thisen a thlen zat a tlahniam vang a ni.

Pawimawh: I fa chu a inkhelh laiin, a tlan laiin, a zuang laiin a lu a buai thut a, a nih loh leh thawk harsatna a phunnawi a nih chuan ngaihthah mai mai suh. Damdawi lam thurawn lak nghal a pawimawh.

Engtin nge doctor hian CPVT hi dik taka a hriat theih ang?

Nangmah emaw i fa emaw hian heng symptoms te hi i neih chuan doctor chuan CPVT i vei em tih finfiah nan test eng emaw zat a ti ang.

• Echocardiogram - echo test: Hei hi thinlung ultrasound scan ang a ni. Sound wave hmangin i thinlung pianzia te, thinlung bangte hnathawh that dan te, valve te hnathawh tha em tih te, thisen kal dan te chiang takin a hmu thei a ni.
• ECG (Electrocardiogram): He test hian i thinlung electrical signal, a nih loh leh heart rhythm graph a la a. CPVT vei chuan a dinhmun pangngaia a awm laiin ECG-ah danglamna lian tham a lantir lo thei.
• Exercise Stress Test: Hei hi CPVT hriat theihna atana test pawimawh tak a ni. Treadmill-a i tlan lai emaw, bike i khalh lai emaw hian i heart rate leh ECG chu enfiah chhunzawm zel a ni. CPVT vei te hian he exercise an neih chhung hian heartbeat chak lo tak an nei tam zawk.
• Imaging test dang: A châng chuan, i doctor chuan i thinlung chu ngun zâwka en tûrin a rawt thei a, chu chu MRI (Magnetic Resonance Imaging ), cardiac catheterization , a nih loh leh coronary angiography te hi a ni.
• Genetic Tests: Heng test te hian thisen sample-a CPVT thlentu genetic changes (mutations) bikte an zawng thin. Hei hian natna hi a nemnghet thei a, chhungkaw member dangte pawh an hlauhawm em tih a hriat theih bawk.

A châng chuan i doctor chuan ni engemaw zât emaw, kar engemaw zât emaw i bun theih tûr machine tê tak tê a pe thei che a ni. Hei hi ambulatory monitor emaw Holter monitor emaw an ti a.Nitin hna i thawh lai leh inchhung hna pangngai i thawh laiin nitin (kum 24, 48, a aia rei pawh) i thinlung electrical activity chu a record a ni. Hei hian i doctor hnenah i thinlung a thawk dan tur a hriat chian tir a, symptom i neih loh lai pawhin.

CPVT enkawl dan tur chu engte nge ni?

Thinlung chu a thawk rang lutuk nghal a nih chuan, chu chu ventricular tachycardia (Ventricular Tachycardia) state-ah a kal a nih chuan nunna atana hlauhawm tak a ni thei. Chutiang hunah chuan thinlung rhythm pangngaia awm leh turin electric shock (Cardioversion emaw Defibrillation) a ngai mai thei. Hei hi emergency treatment angin an ti fo thin.

Mahse hun rei tak chhung atan chuan CPVT enkawlna tum ber chu heart rhythm chu a pangngai lo taka a chak loh nan leh rhythm pangngaia awm reng a ni. I enkawlna ruahmannaah hian a hnuaia mi pakhat emaw, a aia tam emaw a tel thei ang:

• Damdawi: 1.1.
• Beta-blockers: (e.g. Lopressor®, Corgard®) Heng damdawi te hian adrenaline ang hormone te thinlung chunga nghawng a tihziaawmna hmangin hna an thawk a ni. Hei hian exercise neih lai emaw, i stress lai emawa heart rate sang tak chu a control thei a ni. Hei hi CPVT damdawi chi khat pek ber a ni.
• Calcium Channel Blockers: (e.g. Cardizem®, Procardia®) A chang chuan he damdawi hi beta-blockers nen hian pek theih a ni.
• Heart rhythm control damdawi dang: Mi thenkhat chu damdawi dang, flecainide te pek an ni thei bawk.
• Implantable Cardioverter Defibrillator (ICD): Hei hi thil te tak te, battery hmanga siam a ni a, surgery hmanga rilru vun hnuaiah dah a ni. Thinlung rhythm a enkawl chhunzawm zel a ni. Thinlung rhythm chu hlauhawm takin a inthlak danglam nghal a nih chuan, chu device chuan electrical shock a pe chhuak nghal a, chu chu a siam ṭha leh ta a ni. Doctor-te chuan ICD hi risk sang tak nei leh damdawi hmang chauha an heart rhythm control harsa tak takte tan an rawt fo thin.
• Left Cardiac Sympathetic Denervation (LCSD): Hei hi surgical procedure a ni a, heart-a kal nerve thenkhat chu a paih chhuak thin. Hei hian thinlung tihchakna a ti tlem thei a, rhythm hlauhawm tak tak awm theihna a ti tlem thei bawk. He surgery hi ICD nei, mi mangang fo emaw, damdawi ei tha lo emaw tan ngaihtuah theih a ni.

Chu bâkah, i nun dânah inthlâk danglamna pawimawh tak tak i siam a ngai bawk ang .

• Exercise hahthlak tak tak , tlan chak emaw, rit phurh emaw ang chi hi tihtlem tur a ni.
• CPVT vei naupang tê tê tan chuan inelna infiamna aṭanga inthiarfihlim a ṭha ber , inelnaa hnehna chang tûra phurna leh nawrna chuan thinlung a ti na zual thei a ni.
• Stress tihziaawmna tur kawng hrang hrang practice a pawimawh hle bawk.

He CPVT hi a lo awm loh nan kan veng thei ang em?

CPVT hi genetic mutation avanga lo awm a nih avangin, a lo awm lohna tura ven theihna tur kawng a awm tak tak lo . A chhan chu kan thunun theih thil a nih loh vang a ni.

Mahse, CPVT hi hriat chhuah a nih veleh, uluk taka enkawl a nih chuan, chu chu doctor-in damdawi a pek chu hman dik a nih chuan, a sawi angin nunphung tihdanglam a ni a, doctor pan fo a nih chuan, CPVT vei pawh hian a tam zawkah chuan nun pangngai, quality sang takin a nung thei a ni.

I chhungkuaa mi pakhatin CPVT a vei tih hmuhchhuah a nih chuan chhungkaw member dangte, a bik takin naupangte tan genetic test leh genetic counselling ngaihtuah a pawimawh hle. Genetic counselor chuan he natna hi a hriatthiam theih nan a pui thei che a, i fate’n an rochun theihna chance chungchang a sawipui thei che a, chutiang chungchanga i tih theih tur ang chi thil pawimawh tak takte pawh sawipui thei che a ni.

CPVT avanga harsatna awm thei lo turin eng nge tih theih ang?

CPVT hi uluk taka control a nih loh chuan harsatna hlauhawm tak tak a awm thei a ni. I risk tihtlem nan heng thilte hi i ti thei ang:

• I doctor nen inbia la, i tana tha tur exercise plan him tak siam rawh. Exercise i chawlhsan vek a ngai lo, mahse eng exercise nge tha leh tha lo tih i hriat a ngai.
• Caffeine- containing drinks coffee, tea, chocolate thenkhat, leh soft drinks thenkhat te chu a theih ang angin tihtlem la, caffeine hian stimulant a nih avangin i heart rate a ti sang thei a ni.
• I symptoms te hi ngaihven fo ang che . I luak chhuak a, i rilru a na a, thawk harsa i tih chuan heng symptoms zinga pakhat mah hi ngaihthah suh. I doctor ko nghal rawh.
• I doctor-in damdawi a pek ni khat pawh ei loh ngai suh, a hun takah leh a dose dik takah ei rawh .
• A hun taka Doctor hmuh a, a tul anga test neih a pawimawh hle. Hei hi i dam chhung zawnga i tih tur a ni.

CPVT vei hian eng ang hmalam hun nge a beisei theih ang?

CPVT hi enkawl loh chuan hriselna lama harsatna leh harsatna a thlen thei a ni. Harsatna ṭhenkhat, sudden cardiac arrest , ang chite chu nunna atana hlauhawm tak a ni thei.

Mahse, thu lawmawm tak chu enkawlna dik leh nunphung hrisel tak an neih chuan CPVT vei tam zawk chuan thinlung rhythm pangngai an nei thei a, heng harsatnate hi nasa takin an tihziaawm thei a, nun hlim tak leh hlim takin an nung thei a ni.

CPVT i neih chuan i thinlung rhythm a normal tih chian nan dam chhung zawnga enkawl zui zel i mamawh ang.A tul a ni. Chu chu doctor pan fo a ngai tihna a ni a, a tul anga test neih a ngai tihna a ni. CPVT symptoms a lo lang leh a, exercise i tih zawh hnua luak chhuak ang chi te chu tihkhawtlai lohvin doctor rawn nghal rawh.

I doctor zawh tur thil

Nangmah emaw i fa emaw hian heng symptoms te hi i nei a nih chuan, emaw, CPVT i vei tih hmuhchhuah tawh i nih chuan, a hnuaia thilte hi i doctor hnenah chiang taka zawh chuan a \angkai hle ang:

• Heng symptoms awm chhan ber chu eng nge ni? Hei hi CPVT a ni em?
• CPVT ka neih leh neih loh chiang taka finfiah nan kei emaw ka fa emaw hian eng test dang nge kan neih ang?
• CPVT enkawlna tha ber berte chu engte nge ni? Kei/ka fa tan eng enkawlna nge tha ber?
• Heng enkawlnate hian eng hlawkna leh nghawng tha lo nge a neih?
• Doctor tlawh inkara, in lama symptoms enkawl nan emaw, emergency-ah emaw eng nge i tih tur?
• Ka nunphung (ei leh in, exercise) ah eng inthlak danglamna nge ka neih?
• Chhungkaw member dangte chu hlauhawmah an awm em? Anni pawh hi test an ni tur em ni?

A tawp berah chuan hriat reng tur (Take-Home Message) .

Chuvangin, rei tak kan sawi tawh, CPVT (Catecholaminergic Polymorphic Ventricular Tachycardia) dinhmun hi hlauhawm deuh angin lang mahse, a pawimawh ber chu hriat hmasak a, uluk taka enkawl hi a ni.

Diagnose dik tak, doctor-in a tih angin enkawl a nih chuan, leh nunphung tihdanglam awlsam tak tak a awm chuan, CPVT vei pawh hian a tam zawkah chuan nun pangngai, thawkrim leh hlim takin a nung thei a ni. Symptoms i neih chuan ngaihthah lova doctor pan vat a pawimawh tih hre reng ang che. He zinkawngah hian nangmah chauh i ni lo va, i tanpui thei tur leh enkawl thei tur doctor thiam tak tak leh healthcare professional an awm bawk. Chuvangin hlau suh, huaisen takin he thil hi hmachhawn rawh.

` CPVT, heart rhythm, heartbeat, ventricular tachycardia, genetic mutations, stroke, sudden cardiac arrest, naupang hriselna