I vunah hian hmun mak tak a awm em? DFSP (Dermatofibrosarcoma Protuberans) a ni thei!

I vunah hian bump te tak te emaw, a rawng danglam emaw i hmu ngai em? A chang chuan kan ngaihven vak lo a ni lawm ni? Mahse, a châng chuan hetiang thil tenau tak pawh hi ngaihtuahawm tak a ni thei. Vawiin hian vun cancer chi khat hmuh tur awm lo mahse pawimawh tak kan sawi dawn a ni. Dermatofibrosarcoma Protuberans , a tawi zawngin DFSP tih a ni.

DFSP (Dermatofibrosarcoma Protuberans) hi eng nge ni?

A awlsam zawngin DFSP hi vun cancer chi khat, a lo thang chak lo hle a, mahse a tlem deuh hlek a ni. Kan vun layer lai tak, dermis -ah a intan a ni. Doctor in DFSP a tih pawh i hre mai thei.

Hei hi zawi zawia lo thang chak a nih avangin taksa peng dangah a darh tam lo hle. Mahse, ngaihthah erawh a tha lo. Enkawlna mumal tak neih a, he tumor hi paih chhuah a pawimawh hle. Chumi hnuah chauh chuan cancer lo kir leh (recurrence) emaw, taksa peng danga darh (metastatic cancer) emaw chu ven theih a ni. Enkawlna dik tak a awm chuan DFSP vei chuan dam theihna chance a nei tha hle.

He DFSP hi tumor mai mai a ni em? Nge cancer a ni em?

Ni lo, DFSP hi benign tumor chauh a ni lo. Malignant condition a ni. A dik tak chuan soft tissue cancer chi khat a ni a, soft tissue sarcoma chi khat a ni. Sarcomas hi cancer, taksa ruh, thau leh vun ang chi hmuna lo awm thin a ni. A châng chuan, ruhte pawh a nghawng thei bawk.

DFSP hi taksa peng dangah a darh (metastasize) thei em?

DFSP hi a tlangpuiin cancer chi khat, taksa pum puia darh chak lutuk a ni lo. Mahse, a tlem hle a, DFSP vei mi 20 zinga pakhat velin cancer hi a bul tanna hmun aia zauah a darh thei a ni. Hei hi metastatic cancer an ti a .

Hei hi enkawl loh a nih chuan, emaw, cancer hi vun thuk takah, thau tissue leh muscle-ah a darh tawh a nih chuan a darh tam ber.

Thil dang pakhat chu, a chhan dik tak hriat ni lo mah se, naupai laiin DFSP a lo awm chuan a na zual thei a ni.

Tin, DFSP vei mi tlemte chuan fibrosarcomatous dermatofibrosarcoma protuberans (DFSP-FS) tih hming pu, a darh chak zawk, a darh chak zawk chi an nei thei bawk. Heng DFSP-FS tumor te hi surgery hmanga lakchhuah ni mahse, a lo let leh duh zawk a, hmun dangah pawh a darh thei bawk.

Hetiang dinhmun hi engtiang chiahin nge DFSP tia koh a nih?

DFSP hi cancer chi khat hmuh tur awm lo tak a ni. Khawvel pumah kum khatah mi maktaduai khatah mi pali vel chauh a nghawng a ni. DFSP hi soft tissue sarcoma zawng zawng zinga 1% leh 6% inkar a ni.

He cancer hi puitling kum 20 leh 50 inkar ah a tam ber a, mahse naupang te te pawhin he vun cancer hi an vei thei bawk. Naute thenkhat chuan an pian tirh atangin DFSP an nei thei. Research atanga a lan dan chuan hnam dang mite aiin mipa dumte hian an vei tam zawk a ni.

DFSP chi hrang hrangte chu engte nge ni?

Pathologist, microscope hmanga taksa tissue enfiah thin doctor te chuan cell te enfiahin eng chi DFSP nge i neih tih chiang takin an hrilh thei che a ni. A chi hrang hrang a awm a, chungte chu:

• Bednar tumors (pigmented DFSP tia hriat bawk): Heng cell chi hrang hrangah hian vun rawng pe theitu pigment melanin , a tam hle. Hei vang hian heng tumor te hi rawng chi hrang hrang, sen, brown, blue, leh purple te pawh a awm thei. Hetiang chi hi DFSP diagnose 5% vel a ni.
• Giant cell fibroblastoma: Hetiang chi hi chu giant cell awmna atanga hriat theih a ni. Hetiang chi hi naupang leh puitling naupangte zingah a awm tam ber avangin juvenile DFSP an ti bawk.
• Fibrosarcomatous dermatofibrosarcoma protuberans (DFSP-FS): A hmaa kan sawi tawh ang khan hei hi soft tissue sarcoma chi khat, a nasat em em, a darh chak em em a ni.
• Myxoid DFSPs: Hengte hi connective tissue chi khat, myxoid stroma an tih atanga siam a ni. Hetiang DFSP chi hi a tlem hle.

Eng thilin nge DFSP hi a thlen?

Mak tak maiin DFSP vei mi 10 zinga 9 chuan genetic mutation an nei a, chu chuan he natna hi a thlen a ni . He gene mutation hi kan pian hnuah kan cell-ah a thleng thin. Chumi awmzia chu DFSP hi kan nu leh pate hnen atanga kan rochun genetic defect avanga lo awm a ni lo tihna a ni.

DFSP siam chhuahna atana risk factors awmte chu engte nge ni?

Hnam bakah hian vun hliam emaw, hliam emaw chi hrang hrang neih hian DFSP vei theihna a tipung thei a ni. Vun hi a hliam theih dan kawng hrang hrang a awm a:

• Kangmei chhuak
• Radiation therapy hmanga enkawl mek a ni
• Surgery hmanga incision te pawh a awm
• Tattoo a awm bawk

Ngaihtuah teh, kang na tak leh hliam lian tak i nei tawh a ni. A nih loh leh, natna dang avanga radiation treatment i nei tawh bawk. Hetiang thilin vun a tihchhiat hian nakin lawkah DFSP ang natna hi a lo awm theihna chance tlemte a awm a, a tlem hle nachungin. Chuvang chuan vun inthlak danglamna hi kan fimkhur reng tur a ni.

DFSP natna lan chhuah dante chu engte nge ni?

DFSP natna lan chhuah hmasak dan hi a fiah lo em em a, kan hre lo emaw, kan hmu lo emaw pawh a ni thei. Heng tumor te hi rilru, hnungzang, kekawrte, pum emaw, hnute emaw-ah a lo awm tam ber. Kut, ke, lu vun leh ka chhungah te pawh an lo thang lian thei bawk.

A tirah chuan vunah hian hliam ang chi hmun te tak te i hmu mai thei.A flat a, a na lo bawk. A khawih chuan a rough deuhin a lang thei a, a rawng pawh a danglam deuh thei bawk.

Nausen leh naupang tê têah chuan DFSP hi pianpui chhinchhiahna angin a lang thei . Heng hmunte hi inch chanve atanga inches hnih (centimetre 1 atanga 5) vel a zau an ni tlangpui.

DFSP symptoms hi cancer a lo lian chhoh zel chuan a lang chiang hle. Tumor a lo lian zel chuan vun chunglam (epidermis) ah a nawr lut thin. Hei hian vun chung lamah lump khauh tak (nodules) a siam thin . "Protuberance" tih thumal hi "protruding" tihna a ni.

Heng bumps-ah hian heng symptoms te hi i hmu mai thei:

• A crack thei a, thisen a chhuak thei bawk.
• Vunah nghet takin a innghat (a sawn kual theih loh).
• I upat deuh deuh chuan i vun chu a inzawm khawm thin.
• A khawih pawh a harsa hle a, rubber ang maiin a awm bawk.
• A rawng chu sen-brown, purple, blue, emaw red emaw a ni thei.
• A khawih chuan a hmin deuh mai thei.

DFSP ang chi symptoms thlentu condition dang a awm em?

Ni e, cancer ni lo vun natna, cellular dermatofibroma tih a awm a. Hei hi DFSP nen hian a inang hle thei a, a bik takin a tir lamah chuan. Cellular dermatofibromas hi soft tissue tumor tha lo tak a ni. Ke-ah an awm tam ber. A chang chuan an itch thei a, an na thei bawk. Dermatofibromas tam zawk hi chu enkawl a ngai lo. Amaherawhchu, a pahnih hi inthlunzawm loh hi a finthlak a, chuvangin i vunah thil thar i hmuh chuan doctor pan a finthlak hle.

Engtin nge DFSP (Dermatofibrosarcoma Protuberans) hi an hriat theih?

DFSP hi dermatologist , doctor-te’n an hmuchhuak a, vun cancer leh vun natna chungchangah training bik nei an ni. I doctor chuan vun lump emaw spot emaw sample tlemte a la hmasa ang a, lab-ah test turin a thawn ang (a skin biopsy) . Lump zawng zawng chu lakchhuah a ni a, lab-ah thawn theih a ni. Chumi hnuah chuan pathologist-te chuan microscope hmangin tissue chu an en ang a, cancer cell a awm leh awm loh an en ang.

Skin biopsy-in DFSP i nei tih a finfiah chuan MRI scan tir turin an ti thei che a ni . Hei hian tumor lian tham tak leh vunah eng chen nge a darh tih hriat theih nan a pui ang. He information hi enkawlna ruahmanna atan a pawimawh hle.

DFSP (Dermatofibrosarcoma Protuberans) hi eng enkawlna nge ni?

DFSP enkawlna ber leh tha ber chu surgery hmanga tumor lakchhuah hi a ni. Dermatologist te hian DFSP tumor te paih chhuah nan hian Mohs surgery tih hming pu special procedure an hmang tlangpui. He surgery neih chhunga thil thlengte chu hetiang hi a ni:

• A hmasa berin enkawlna hmunah local anesthetic an inject a, chuvang chuan natna i nei lo ang.
• Tichuan, doctor chuan a cut chhuak a, cancer tumor chu a la chhuak ta a ni. Mahse tumor chauh ni lovin a chhehvel vun hrisel tak tak awmna hmun tlemte pawh a awm bawk. Hei hi margin an ti a .
• A dawtah chuan tissue lakchhuahna kil (border) te chu microscope hmangin an enfiah a, cancer cell a la awm em tih an enfiah thin.
• A sir lamah cancer cell a la awm a nih chuan doctor chuan operation an tihna hmun atang chuan tissue engemaw zat a la chhuak leh ang.
• Chutiang chuan tissue lakchhuahna chu a margin-a cancer cell hmuh tur a awm loh thlengin a chhunzawm zel a ni.
• Cancer chu lak chhuah vek a nih hnuah a tul chuan reconstructive surgery tih a ni.

Surgery tel lova DFSP enkawlna dang a awm em?

DFSP tumor te hi surgery hmanga lakchhuah ni mahse a chang chuan a lo let leh thei. Typical wide excision hnuah kum thum chhunga an lo kir leh theihna chance 20% atanga 30% vel a awm. Mohs surgery hnuah hian he risk hi 4% atanga 5% ah a tlahniam thin. Mahse, fimkhur reng a pawimawh a, kum 10 emaw a aia rei emaw hnuah pawh tumor hi a lo lang leh thei a ni.

A châng chuan, cancer hi taksa hmun dangah a darh tawh a nih chuan (metastatic DFSP), emaw, tumor chu a lian lutuk emaw, a awmna hmuna awm lutuk emaw, operation hmanga lak chhuah theih loh a nih chuan doctor-te chuan Imatinib tih damdawi an hmang ṭhin. He damdawi hian tumor chu a ti tlem thei bawk a, surgery hmanga lakchhuah a awlsam phah hle.

Tin, operation hmanga cancer chu a bo vek thei lo a nih chuan, emaw, operation tih theih a nih loh chuan radiation therapy hman theih a ni bawk.

DFSP vei tan chuan eng nge a hmalam hun?

Hei hi thu thlamuanthlak tak a ni tak zet a ni. DFSP hi cancer zawi zawia lo thang chak, indolent, enkawl dan dik a nih avangin mi 99% aia tam chu kum 10 emaw a aia rei emaw an dam thei ang. Chuvangin, a pawimawh ber chu hlauthawng lo leh doctor thurawn zawm hi a ni.

Ka thlîr dân siam ṭha tûrin eng nge ka tih theih ang?

I thlirna tihchangtlun nan thil engemaw zat i tih theih a awm a:

• Skin self-exam neih fo thin ang che. I vunah danglamna thar, hmul, leh lumps awm apiang zawng rawh. Eng emaw i hriat chuan doctor hnenah hrilh nghal rawh.
• Enkawl zawhah kum thum hmasa berah thla thum atanga thla ruk danah tal vun checkup turin doctor pan thin ang che. Tichuan kum khatah vawi khat checkup la, a nih loh leh doctor-in a tih angin.
• Ni chhuahna tur tlem ber. Ni atanga UV rays hian vun cancer dang a thlen theihna a tipung a ni. Chuvangin, ni chhuahna hmuna i chhuah hunah sunscreen hmang la, invenna thawmhnaw ha la , ni lum ber laiin pawn lama i hun hman kha tihtlem rawh.

Engtikah nge Doctor ka hmuh ang?

I vunah danglamna thar i hmuh chuan, a bik takin a hnuaia mi hi i neih chuan doctor pan ngei ngei tur a ni:

• Bumps thar, persistent bumps emaw spots emaw, vun thar lo thang lian emaw.
• Warts, birthmarks, scars hlui, emaw tattoos inthlak danglamna.
• Vun chunga bumps te hi thisen chhuah awlsam a nih chuan.

Vun inthlak danglamna hi a hlauhawm lo fo thei tih hre reng ang che. Mahse, inthlak danglamna thenkhat chu vun cancer chhinchhiahna a ni thei. Chuvangin, rinhlelhna i neih chuan doctor pan a, a chinfel dan tur ngaihtuah a tha ber.

Ka doctor hnenah eng nge ka zawh ang?

DFSP i vei nia hriat i nih chuan i doctor hnenah zawhna i zawt mai thei a, chungte chu:

• Engvangin nge he vun cancer hi ka neih?
• Vun cancer chi dang ka vei theihna hlauhawm ka ni em?
• Ka tan enge inenkawlna tha ber?
• He cancer hi taksa peng dangah a darh theihna tur a awm em?
• Cancer screening atan engzat nge ka lo kal ang?

Hêng zawhnate chhânna hriatna hian natna chungchâng hriatthiamna ṭha zâwk i neih theih nân a ṭanpui ang che a, i enkawl dân leh i hmalam hun tûr ruahmannate pawh chiang zâwk tûrin a ṭanpui thei bawk ang che.

A tawp berah chuan thil hriat reng tur

DFSP hi vun cancer hmuh tur awm lo mah se, taksa peng dangah a darh a rinawm loh hle. Mahse, a thanna tihtawp nan surgery hmanga enkawl a pawimawh hle. Hriat hmasak leh enkawl dan dik chuan i thlirna chu nasa takin a tichangtlung thei a ni. Chuvangin, i vun hi fimkhur la, thil danglam tak i hmuh chuan doctor rawn rawh. Nangmah chauh i ni lo va, he zinkawng zawh tura pui theitu doctor an awm bawk.

` DFSP, vun cancer, vun cancer, vun lum, Mohs surgery, cancer symptom, vun natna