I taksaah lump i nei em? Hei hi Epithelioid Sarcoma a ni thei ang em? I chhui chiang ang u!

I taksa hmun dangah lump emaw tumor te tak te i hmuh hian tlem a lungkham deuh hi thil pangngai a ni lawm ni? Chutiang hunah chuan thil tam tak i ngaihtuah thin. "Eng nge hei hi? A hlauhawm em?" Hetiang zawhna hi rilruah a lo lang thin. Vawiin hian cancer chi khat hmuh tur awm lo tak, chutiang lumps anga lo lang thei chungchang kan sawi dawn a ni . Chu chu Epithelioid Sarcoma an ti a. A hming hi a mak deuhin a lang thei a, mahse hriat a hlawh hle.

Epithelioid Sarcoma hi eng nge ni? A dik tak chuan...

A awlsam zawngin sawi ila, Epithelioid Sarcoma (ES) hi cancer chi khat hmuh tur awm lo tak a ni a, cancer pawl pakhat , soft tissue sarcomas tia koh zinga mi a ni. “Soft tissue” tih hian kan taksa chhunga thil awmte, taksa ruh, thau, thisen kalna kawng leh nerve te a kawk a ni. Chuvangin he cancer hi chutiang hmunah chuan a lo awm thin.

I kut hmawr, i kut, i kut zungtang, i ke hnuai lam, a nih loh leh i kephah hnuai lama hnim hring (lump) angin a intan fo thin . Mahse, i taksa khawi hmunah pawh a lo thang lian thei. A châng chuan, lump pakhat aia tam a lo awm thei bawk. Mi thenkhat chuan vunah lump awmna hmunah ulcer an nei bawk.

A tha ber chu, epithelioid sarcoma hi cancer a lo thang chak lo hle a ni . Ngaihtuah teh, mi thenkhat chuan thla tam tak chhung, kum tam tak chhung pawh he cancer chi hi an nei thei a, a lan chhuahna engmah an lantir lo. Chumi awmzia chu i taksa chhungah i hriat loh pawhin a thang lian thei tihna a ni.

Hei hi epithelial sarcoma an ti bawk. Hei hi chi hnih a awm a, chungte chu distal leh proximal te an ni. Chu pawh chu han en ila.

Hei hi chi hrang hrang a awm em? Eng nge an nih?

Ni e, kan sawi tawh ang khan epithelioid sarcoma hi chi hnih a awm a.

• Distal type: Hei hi a tam ber a ni . “Distal” tih awmzia chu taksa lairil atanga hla tak tihna a ni. Chumi awmzia chu he chi hi i kut, ke, i kut hmalam, leh i ke hnuai lam ang chi hmunah a awm tam ber tihna a ni .

• Proximal type: Hei hi a rarest type a ni . “Proximal” tih awmzia chu taksa lairil hnaih zawk tihna a ni. Chuvangin, he Proximal Epithelioid Sarcoma (PES) hi i rilru, i pum, i kekawrte, mipat hmeichhiatna (i.e. penis emaw vulva), emaw lu leh kawr ang chi hmunah te a lo awm thei a ni.

A tlangpuiin he proximal type hi chu distal type aiin a lian deuh deuh thin.Tawrawt. Chu chu a darh chak deuh thei a, a na zual thei tihna a ni. Chumi avang chuan enkawl chu a harsa deuh thei a ni.

Epithelioid sarcoma hi engtiang chiahin nge a awm? Tuin nge dawng thei ber?

Hei hi a takah chuan cancer hmuh tur awm lo tak a ni. Ngaihtuah teh, soft tissue sarcoma chi hrang hrang 50 chuang a awm. An vai hian puitling cancer zawng zawng zinga 1% vel an ni. Tin, chutah chuan, he epithelioid sarcoma hi, hetah pawh hian, a tlem hle a, chu soft tissue sarcoma zinga 1% vel a ni. Chumi awmzia chu, a tlem tak zet, a tlem tak zet tihna a ni.

Mithiamte sawi dan chuan America ang ramah pawh tunah hian he epithelioid sarcoma vei hi 1,000 aia tlem lo an awm a ni. Chuvangin hei hi a tlem zia chu i ngaihtuah thei ang.

Atlangpuiin,

• Distal type ES – a tam ber chi – hian tleirawl leh puitling naupangte a nghawng nasa ber.
• Proximal type ES – a awm lo, a na deuh deuh chi – hi puitling kum upa zawkah hmuh a ni ber .

Eng nge a lan chhuah dan? Engtin nge i hriat chian?

A tir lamah chuan epithelioid sarcoma hian symptom a nei lo thei. Hei hian a dik lohna i hmu lo mai thei tihna a ni. Mahse, tumor a lo lian zel chuan symptoms i hmu thei a, chungte chu:

• Lump emaw swelling thar emaw a lo lang thin. Hei hi a te emaw, a lian emaw pawh a ni thei.
• Lump awmna vun chung lamah ulceration a awm a , chu chu hliam te tak te emaw, hliam emaw ang chi a ni.
• Natna a awm. Mahse hei hi tumor chu a lian deuh a, a chhehvel taksa ruh emaw nerve emaw a press phawt chuan a thleng thin. Mi zawng zawng hian hrehawmna kan tawng vek lo.
• Hun rei tak atanga lo awm tawh lump chu a lian chho zel ang maiin a lang .

Pawimawh: I taksa khawi hmunah pawh hetiang lump thar emaw, swelling emaw i hmuh chuan, emaw, a awm tawh chu a lian chho zel ang tih i hriat chuan, doctor pan ngei ang Thil awlsam tak a ni thei a, mahse check out tir hi a tha ber.

Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?

Dik tak chuan doctor-te chuan epithelioid sarcoma thlentu dik tak chu an la sawi chiang thei lo. Mahse, zirchianna chuan SMARCB1 tih gene-a thil danglam tak nen a inzawm tih hmuhchhuah a ni. He gene hian kan taksain protein siam turin min hrilh a ni. He gene mutation hi dam chhungin a thleng tlangpui. Chu chu i pianpui thil a ni lo tihna a ni a, a tam zawkah chuan.

Soft tissue sarcoma tam zawk ang bawkin, epithelioid sarcomas hi a chhan chiang tak awm lovin a lo awm fo thin . Mahse, a hmaa cancer an neih hnua hriatchhuah an ni tlangpui.Hei hi radiation therapy hmang tawhte tan chuan a vei theihna chance a sang deuh hlek a ni.

Tin, mithiamte chuan chhungkaw cancer syndrome thenkhat nei te pawh hi epithelioid sarcoma vei theihna chance a sang deuh thei tih an hmuchhuak bawk. Chung dinhmun thenkhat chu:

• Gardner natna a ni
• Neurofibromatosis chi khat leh chi 2 a awm
• Retinoblastoma natna a ni
• Li-Fraumeni natna a ni
• Tuberous sclerosis natna hlauhawm tak a ni
• Werner natna a ni
• Gorlin natna (Gorlin syndrome) a ni

Hei hi a buaithlak deuh a, mahse hriat a tha. Hetiang dinhmun hi i neih chuan doctor nen thurawn dang dil rawh.

He natna hi taksa pum puiah a darh zel em?

A tam zawkah chuan epithelioid sarcoma hi hmun dangah a darh (metastasize) lo . Chu chu a bul tanna hmunah a awm reng tihna a ni. Mahse, a chang chuan a bik takin proximal type ang chi aggressive zawkte chuan a darh thei a ni. A awm chuan i lymph node, lung, leh ruh- ah a kal a rinawm ber .

Engtin nge hei hi i hriat chian? (Diagnosis) tih a ni.

Doctor chuan epithelioid sarcoma a hriat theih nan test eng emaw zat a nei ang. A bulpui berte chu:

• Taksa enfiah : Doctor chuan a enfiah ang che, lump awmna hmun leh a lian leh te ang chi thil te a enfiah ang.
• Biopsy: Hei hi test pawimawh ber a ni . A hnah te tak te tak te chu lak a ni a, microscope hmangin an enfiah thin. Chutah chauh chuan cancer a nih leh nih loh kan hre chiang thei ang a, a nih chuan eng chi nge a nih tih pawh kan hre thei ang.
• Thisen atanga cancer enfiah dan : Cancer chhinchhiahna thenkhat chu thisenah hmuh tur a awm thei.
• MRI scan (Magnetic Resonance Imaging – MRI): Hei hian tumor awmna hmun, a lian leh te, a chhehvel tissue-a a darh leh darh loh chiang takin a hmu thei a ni.
• CT scan (Computed Tomography – CT scans): Hei hian tumor chu a en thei bawk a, cancer chu hmun dang, lungah a darh tawh em tih a en thei bawk.
• PET scan (Positron Emission Tomography – PET scans): Hei hian taksa chhunga cancer cells active na hmun zawng turin a pui thin.

Heng test zawng zawng hi i tih a ngai lo mai thei. I doctor chuan i dinhmun a zirin eng test nge a tul tih a rel ang.

Eng nge a enkawl dan?

I doctor chuan thil engemaw zat a zirin enkawl dan tur a thlang ang a, chung zingah chuan tumor lian leh te, a awmna hmun te, cancer hi hmun dangah a darh tawh em tih te, i taksain a dam theih dan te, leh i duh dan te a ni.

Inzai

Epithelioid sarcoma enkawlna ber leh hman tlanglawn ber chu operation hmanga tumor lakchhuah hi a ni . Cancer hi a bul hnaia lymph node-ah a darh tawh a nih chuan surgeon pawhin a la chhuak thei bawk.

Radiation hmanga enkawlna a ni

Hei hi cancer enkawlna tlanglawn dang a ni. Energy sang tak nei X-ray hmangin cancer cell te a tichhia a ni. Doctor-te chuan operation hmaa tumor tihtlem nan he enkawlna hi an pe thei a ni. A nih loh leh, operation hnua cancer cell la awm zawng zawng tihhlum nan hman theih a ni bawk.

Chemotherapy hmanga enkawl a ni

Cancer chu i taksa hmun dangah a darh tawh a nih chuan, i doctor chuan chemotherapy a rawt thei ang . Hei hian cancer cell tihhlumna tur damdawi bik pek che a huam a ni. Heng damdawi te hi thisen kal tlanga pek a ni fo. Mahse, pill, tui, vunah cream hnawih emaw, injection emaw angin pek theih a ni bawk.

Targeted Drug Therapy hmanga enkawlna a ni

Hei hi enkawlna thar tak a ni. Cancer cell te lo thanglian leh inthen dan controltu gene leh protein chauh target thei damdawi pek a ni. Chumi awmzia chu cell hrisel tak takte chu an tichhe tlem zawk tihna a ni. Hemi atan hian damdawi chi hrang hrang hman a ni. I doctor chuan i dinhmun a zirin enkawlna tur ruahmanna bik a siam ang che. Tazemetostat hi damdawi chi khat a ni a, epithelioid sarcoma tan hman thin a ni. Surgery hmanga lak chhuah kim theih loh cancer cell enkawlnaah a pui a ni.

Hei hi a thlen loh nan a veng thei ang em?

Thil lungchhiatthlak tak chu, epithelioid sarcoma hi chhan hriat lohvin a lo awm tlangpui avangin, a lo awm loh nan kan veng thei lo . Chumi awmzia chu, "Hetiang hi i tih chuan a thleng lovang," tih hi a harsa tihna a ni.

Epithelioid sarcoma i neih chuan eng nge thleng? Dam theih a ni em?

He thu i hriat hian hlauthawng tih hi thil pangngai tak a ni. Mahse, epithelioid sarcoma hi enkawl theih natna a ni a , a bik takin a hmaa man a nih chuan . I doctor chuan test thenkhat a ti ang a, tumor hi engzat nge a lian tih leh hmun dangah a darh tawh em tih a enfiah ang. Tichuan, i tana tha tur treatment plan an siam ang.

Doctor team enkawltu an awm thei bawk. Chung zingah chuan:

• I primary care physician ( doctor rawn hmu tlangpui che).
• Oncologist: Chung zingah chuan orthopaedic oncologist te, oncology surgeon te, leh chemotherapy leh radiation therapy pe thin doctor te an tel a ni.
• Dermatologist: Vun lama harsatna nei tan.
• Pathologist: I thisen leh biopsy test report en a, chipchiar taka pe che thinte.
• Therapists: Hetiang natna avanga lo awm thin stress leh hlauhna te hmachhawn tura puitu che.

Epithelioid sarcoma tihdam vek theihna awmchhun chu operation hmanga tumor chu paih vek hi a ni . Mahse, tihbo vek theih a ni lo fo mai thei.

Surgeon-in tumor chu a la chhuak kim thei lo a nih chuan i doctor chuan i dinhmun control nan treatment hrang hrang a rawt fo ang. Epithelioid sarcoma hi cancer zawi zawia lo thang lian a nih avangin, he natna vei tam tak hian dam rei tak, hlim takin an la nung thei tho a ni .

He natna damchhuah zat chungchangah hian research report tam tak a awm a. Amaherawhchu, natna awm lo tak a nih avangin statistics a inang lo hle. Report thenkhatah chuan kum nga chhunga damchhuah zat hi 25% atanga 92% inkar a ni. Thil tam takah a innghat a, chu chu natna awm dan leh enkawlna dawn danah a innghat a ni.

Engtikah nge Doctor ka hmuh ang?

I taksa khawi hmunah pawh lump emaw swelling danglam tak i hmuh chuan ngaihthah suh. Doctor pan ngei ngei tur a ni. Epithelioid sarcoma vei te hian an kut hmawr, kut, kut zungtang, ke hnuai lam emaw, ke kephah emaw ah lump an nei tam ber. Mahse, heng tumor te hi taksa khawi hmunah pawh a lo awm thei tih hre reng ang che.

Doctor hnenah eng zawhna nge i zawh tur?

Nangmah emaw, i hmangaih tak emaw chu epithelioid sarcoma vei nia hriat i nih chuan, i doctor zawh theih tur zawhna ṭhenkhat chu hetiang hi a ni:

• Khawiah nge tumor chu a awm?
• Tumor pakhat chauh ka nei em? Nge midang an awm em?
• Cancer hian taksa peng dangah a darh tawh em?
• Eng enkawlna nge i rawt?
• Ka enkawlna hian eng chen nge a daih ang?
• Enkawl lai hian engtin nge ka awm ang? (Side effects ang chi thil)
• Hemi chungchang hi ka hriat belh theihna tur hmun a awm em? (website rintlak, lehkhabu ang chi)

Hetiang diagnosis i dawn hian hlauhna, thinrim leh lungawi lohna i neih hi thil pangngai a ni. Enkawl hma, enkawl lai leh enkawl zawh hnua i beisei tur chungchang i doctor nen sawiho rawh. Counselor emaw therapist emaw nena inbiakna neih pawh a \angkai thei bawk. Hetiang hun lai hian i tawrh mek emotion complex tak takte chu hmachhawn turin an pui thei che a ni. A theih chuan nangmah ang bawka thil tawk mekte nen support group-ah tel ve rawh. Hei hian mahni chauha awm lo turin a pui thei che a ni.

Take-Home Thuchah a ni

• Epithelioid sarcoma hi a awm lo hle a, soft tissue cancer na tak a ni .
• Vawi tam tak chu taksa peng hrang hrangah lumps a awm thinRash angin a lang thei a, a chang chuan vun natna a awm thei bawk.
• A tir lamah chuan symptoms a lang lo thei .
• SMARCB1 tih gene-a chhiatna nen a inzawm a, mahse a chhan dik tak erawh hriat a la ni lo.
• Surgery hi a enkawlna ber a ni . Radiation therapy, chemotherapy, leh targeted drugs te pawh hman a ni.
• It is difficult to prevent , mahse a hmaa hriatchhuah a nih chuan enkawl theih a ni .
• I taksaah lump thar i hmuh chuan doctor pan nghal rawh.
• Hlau suh la, hlau suh la, damdawi lam thurawn dik tak zawm bawk ang che . Nangmah chauh i ni lo, i tanpui tur doctor leh i hmangaih tak tak an awm.

He thuziak hi thu tlangpui chauh a ni tih hre reng ang che. Thil ngaihtuah tur i neih chuan Doctor rawn pan a tha ber.