A châng chuan i chau tih i inhria em? Nge, thisen chhuah tawp lo tur hliam te tak te i nei em? I taksaah hian blue spot i nei mai thei em? A châng chuan hengte hi kan taksa chhunga taksa peng te tak te spleen hi a thawk nasa lutuk vang a ni thei . Vawiin hian he dinhmun (Hypersplenism) hi han sawi ila, ṭhian nena inbiakna ang maiin.
Hei hi eng nge ni (Hypersplenism)?
A awlsam zawngin, hypersplenism chu i spleen-in hna a thawh nasat lutuk hi a ni. Spleen hnathawh ber pakhat chu kan thisen atanga cell hlui, chhia te paih chhuah hi a ni. Kan in chhunga bawlhhlawh paihtu ang maiin spleen hian hna a thawk a. But sometimes, when the spleen starts working too hard , a tih tur aia rang zawkin thisen cell hrisel te chu a paih chhuak tan thin. Chu chu kan taksa hian thisen cell tlakchhamna, a nih loh leh ``Cytopenia'' a tawk thin. Thil tha tak tak chu lakchhuah thuai lutuk ang mai a ni.
He dinhmun hian engtin nge i taksa a nghawng?
Hypersplenism hian i taksaa thisen cell chi hrang hrang emaw, chi hrang hrang emaw a tihhniam thei a ni. Hei hian hetiang dinhmun hi a thlen thei a ni:
- Anemia : Hei hi thisen zam (red blood cells) tlahniam a ni . Red cells hi kan taksa pum puia oxygen phurtu a ni. Chuvângin, an hniam chuan i chau reng thei a, i vawt thei a, a châng chuan i lu a buai thei a, thawk pawh i harsat phah thei bawk . I taksain fuel a tlakchham ang mai a ni.
- Leukopenia: Hei hi thisen var tlahniam a ni. White cell hi kan taksaa natna dotu ‘sipai’ ang mai a ni. Chuvangin white cells a tlem chuan natna vei theihna a sang hle. Khawsik leh khawsik ang chi thil hi a thleng fo thei.
- Thrombocytopenia: Hei hi platelet tlahniam a ni. Platelets hian thisen zam a pui thin. Thisen chhuah tihtawp nan an pawimawh hle a, hliam tenau atanga lo chhuak pawh nise. Chuvangin an hniam chuan thisen chhuah tihtawp a harsa thei a, taksaah hliam a lo lang thei a, hmui pawh thisen a chhuak thei bawk .
Hetiang dinhmun (hypersplenism) hi mi thenkhat tan chuan a na lo thei hle a, thenkhat tan chuan a na hle thei bawk. Thisen cell tlahniam dan pawh mi hrang hrangah a inang lo. Mi thenkhat chuan nghawng lian tham an nei lo thei a, enkawlna an mamawh lo thei bawk. Mahse, a bik takin he natna hi natna khirh tak dang nena inzawm a nih chuan i hriselna zawng zawng tichhe thei thil pawimawh tak a ni thei.
Engtin nge hypersplenism hi a lo awm?
Hypersplenism hi i ril a lian lo (`(Splenomegaly)`) vang a ni fo thin. Ngaihtuah teh, i spleen a lian chhoh zel chuan thisen a vawn theih zat a pung zel a ni. Tichuan, spleen hian vawi khatah thisen cell tam zawk a keng tel ta a ni. Hetianga a vawn tlat hian thisen a filter chhuah zat pawh a tipung a, a tawpah chuan a tih tur aia tam cell hrisel tak tak pawh a paih chhuak tan ta a ni.
Hengte hi spleen lian (hypersplenism) thlentu ber thenkhat chu hetiang hi a ni:
- Liver natna : I liver tichhe thei dinhmun, chronic hepatitis emaw cirrhosis emaw te hian liver leh spleen kaltlanga thisen kalna thisen kalna kawngah pressure a tisang thei a ni Hei hi portal hypertension an ti a. Hei hian thisen volume a tipung a, chu chuan spleen a ti hring emaw, a ti lian emaw a ni.
- Infection: Viral infection thenkhat, mononucleosis (kissing disease tia hriat bawk) leh HIV, bacteria infection (tuberculosis, endocarditis, thinlung chhunga infection pakhat), leh parasitic infection (malaria, toxoplasmosis ang chi) te hian spleen-a immune system-ah harsatna nasa tak a siam thei a ni. Hei hian spleen hian a mamawh aia tam antibodies leh immune cells a siam chhuak thin. Hetianga cell siam tam lutuk (hyperplasia) hian spleen pum pui a tipung thei a ni.
- Autoimmune diseases: Hun rei tak chhunga inflammatory condition lupus, sarcoidosis, leh rheumatoid arthritis te hian immune system a tichak lutuk a, hyperplasia (spleen cells overproduction) a thlen thei a ni. Hei hi kan taksa hriselna (immune system) ngeiin kan cell-te a beih hian a ni.
- Cancer: Thisen kaihhnawih cancer, leukemia emaw myeloproliferative neoplasms (MPNs) leh lymphomas-ah te chuan cancer cell te chu spleen-ah an lut a, chutah chuan an pung tan thin. Hei hian spleen a ti lian bawk.
- Thisen lama harsatna: Thisen sen (red blood cells) tihchhiat thuai theihna tur dinhmun, hemolytic anemia (thisen sen a tihchhiat thuai thin) leh neutropenia te hian phurrit lian tak a siam a, chu chuan chu chu a paih chhuak thei a ni. Kan thawhrim lutuk chuan kan chau thin ang bawkin.
- Metabolic disorder rochun atanga lo chhuak:Thisenah thil chi hrang hrang a lo awm khawm a, taksa peng hrang hrangah a awm khawm a, Niemann-Pick natna, Gaucher natna, leh sickle cell natna te pawh hian spleen hi a nghawng thei a, a ti lian thei bawk.
(Hypersplenism) natna lan chhuah dan chu engte nge ni?
A châng chuan hypersplenism nei chung pawhin symptom i nei lo thei bawk. Chu chu he thila buaina chu a ni. Mahse, symptoms a lo lang a nih chuan:
- Spleen lian zawk chhinchhiahna: 1.1.
- I pum veilam chunglam ah natna emaw nuam lo emaw i nei thei . Mi ṭhenkhat tân chuan hei hi thil rit ang maiin a lang mai thei.
- A châng chuan i kut hmanga i khawih hian spleen chu i hre thei ṭhin. A tlangpuiin chutiang chuan spleen hi kan hre lo.
- Spleen lian zawk chuan a hnuaia pum chu a press avangin, ei tur tlemte i ei hnuah pawh i khat thei . Hei hian chaw ei chak lohna a thlen thei bawk.
- Anemia chhinchhiahna: Kan sawi tawh ang khan thisen sen (red blood cells) hi kan taksa tissue-a oxygen phurtu a ni. Chuvangin an tlem chuan tissue te chu oxygen an tlachham ta a ni. Chumi avang chuan:
- I luak chhuak thei a, i chak lo a, i chau bawk (hnathawh tlem i thawh hnuah pawh i chau hle).
- I khawsik mai mai thei a , lu na pawh i nei fo mai thei .
- I vun chu a sen hmel hle mai thei . Mi dangte chuan i hmai an en a, "Engvangin nge i sen?"
Heng symptoms pakhat emaw a aia tam emaw i neih chuan doctor pan a, thurawn lak a pawimawh hle.
Engtin nge hypersplenism i vei tih i hriat theih ang?
Doctor chuan i spleen a lian em (`(Splenomegaly)`) a enfiah hmasa ang a, i thisena cell awm zat pawh a teh bawk ang.
- A châng chuan, i doctor chuan taksa enfiahnaah i rilru a lian tawh tih a hre thei . Doctor chuan i pum veilam chu a hre mai ang.
- Chu chu finfiah nan ultrasound tih theih a ni. Hei hian spleen lian leh te dik takin a teh thei a ni.
- Full blood count (CBC) test hian i thisenah eng cell chi hrang hrang (red cells, white cells, platelets) a hniam tih leh eng chen nge a hniam tih chiang takin a hriat theih. Hei hi fiahna pawimawh ber a ni.
Hypersplenism hi engtin nge enkawl a nih?
Hypersplenism hi a side effect a ni fo va, a hnuaia natna dang, na zawk, a hnuaia awmte chhinchhiahna a ni bawk. Chuvangin, a hnuaia natna awm hi i la hriat chhuah loh emaw, a enkawl tan loh emaw a nih chuan, i doctor chuan chu chu a ngaihtuah hmasa ang. I doctor pawhin a chhan dik tak hriat nan test tam zawk a tih a ngai dawn bawk. A chhan bulpui ber enkawl a nih chuan spleen hnathawh chu a pangngaiin a awm leh fo thin.
Hypersplenism enkawl dan chu a nasat danah a innghat. A huam thei ang:
- Thisen pek: I thisen cell hniam zat chu thisen pek hmangin a lo awm leh thin. Hei hi i thisen sen a tlem chuan red cell pek a ni a, i platelet a hniam chuan platelet i pe thei bawk.
- Low-dose radiation therapy emaw radiofrequency ablation: Heng method pahnih hi doctor-te chuan taksa chhunga tissue, cancer tumor ang chite target leh tihchhiat nan an hmang a ni. Heng hmanrua te hi hypersplenism enkawl nan leh i spleen lian tawh chu a normal size-ah tihtlem nan hman theih a ni. I doctor chuan i hypersplenism a nasat a, a hnuaia natna awm chu spleen tihtlem nan enkawl theih a nih loh chuan hei hi a rawt thei ang.
- Splenectomy: A nasat deuh deuhah chuan, enkawlna dangin a hlawhtlin loh chuan, i doctor chuan i spleen thenkhat emaw, a zawng zawng emaw lak chhuah a rawt thei ang. Spleen tel lovin i nung thei a, mahse i immune system a tichak lo. I damdawi lam dinhmun hnuaia awmte ngaihtuah chuan hei hian a ṭhatna aiin a tichhe zawk thei a ni. Chuvangin, splenectomy hi a tawp ber atan tih a ni tlangpui. He surgery hi i neih chuan i doctor chuan natna tlanglawn laka invenna tur vaccine bik engemaw zat laksak turin a rawt mai thei che a ni. A then phei chuan i spleen lakchhuah hnua nitin ei tur prophylactic antibiotics pawh an pe thei bawk.
Hetiang dinhmun hi eng nge ka beisei theih ang?
Hypersplenism hi enkawl theih a ni. Mahse, i prognosis chu i dinhmun hnuaia awm (underlying condition)-ah a innghat a ni. Thil awm dan thenkhat chu hun rei lote chhung atan (e.g., hri kai thenkhat), thenkhat chu rei tak (e.g., cirrhosis, autoimmune natna thenkhat), thenkhat chu a zual zel (e.g., cancer thenkhat) a ni. Hypersplenism hian thisen cell count a tihhniam (e.g., cytopenia) a nih chuan thisen pek hian i thisen cell count a siam tha thei a ni. A pawimawh ber chu doctor nen hnaih taka thawk ho a, i enkawl dan tur uluk taka zawm hi a ni.
(Hypersplenism) leh (Splenomegaly) hi eng nge an danglamna?
Heng pahnih chungchang sawi dawn hian buaina tlem a awm thei a, chuvangin chu pawh chu i tichiang ang u.
- Splenomegaly tih awmzia chu i spleen chu a tlangpuiin a lian tihna a ni .
- Hypersplenism chu spleen lian zawk chu a thawk nasa lutuk a, thisen cell tam lutuk a paih chhuak a ni.
A awlsam zawngin Hypersplenism hi Splenomegaly side effect a ni. Thil chi hrang hrang hian spleen a ti lian thei a, a overactive thei bawk. Engpawhnise,Hypersplenism hi a awm ngai lo a, a chhan chu spleen a lian vang a ni. Chu chu, spleen overactive zawng zawng hi a lian vek lo a, mahse spleen lian zawng zawng hi overactive an ni vek lo tihna a ni. I hmu em? Car lian nei zawng zawng hian an khalh chak vek lo ang mai a ni a, mahse tlan chak zawk chuan lirthei lian zawk, chak zawk a thlang duh zawk tlangpui.
Hypersplenism hi a bul berah chuan damdawi lam thil dang chhinchhiahna a ni. I rilru chhung ngeiah natna a awm thei a, i taksa hmun dangah pawh a intan thei bawk. I spleen hian thisen dahkhawm leh filter-naah a inrawlh avangin, a nghawng natnate hi i thisen emaw, thisen kalna kawng emaw nen a inzawm fo thin.
Hypersplenism enkawlnaah hian a bulpui ber enkawlna a tel tlangpui. A tam zawkah chuan spleen ngei pawh hi a hnathawh dan pangngaiah a awm leh thei a ni. Mahse, i dinhmun a la awm reng chuan i thisen cell zat siam ṭhat leh nan thisen pek i ngai mai thei a, a nih loh leh i doctor chuan i ril chu direct-a enkawl a rel thei bawk.
Chuti a nih chuan, heng zawng zawng atang hian eng thil nge kan hriat reng tur? (In lama hruai tur thuchah)
Okay, hypersplenism chungchang hi kan sawi nasa hle. Thil awlsam tlemte hriat reng tur chu hetiang hi a ni:
- Hypersplenism chu i spleen-in hna a thawh tam lutuk a, a tul aia tam thisen cell (red cells, white cells, platelets) a paih chhuah hian a ni.
- Hei hi a chhan ber chu spleen lian (`(Splenomegaly)`) a ni . Spleen lian lutuk hi natna chi hrang hrang, liver disease, infection, leh cancer te avanga lo awm thei a ni.
- I rilru hah fo thin te, awlsam taka damlohna te, hliam tenau tak atang pawhin thisen chhuak rei tak a reh thin te, i pum veilam chunglam a na te, chaw tlemte i ei hnu pawha i khat thin te ang chi symptoms i neih chuan doctor thurawn lak a pawimawh hle.
- Hypersplenism hi a bulpui enkawlna hmanga enkawl a ni. A châng chuan thisen cell pek te, rilṭâm lian lo tûra enkawlna te, a hnuhnûng ber atân rilṭâm lak chhuah te a ngai thei a ni.
- Hei hi enkawl theih a ni. Chuvangin hlauthawng lo tur leh doctor thupek uluk taka zawm a pawimawh.
Heng symptoms te hi i neih chuan hlau lova doctor nena inbiak a tha ber tih hre reng ang che. Chumi hnuah chuan test tul tak tak an run thei a, eng nge dik lo tih chiang takin an zawng chhuak thei a, a tul angin enkawlna an pe thei bawk. I natna hmuhchhuah hma chuan enkawl a awlsam ang a, a rah pawh a tha zawk ang.











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