Nu emaw, pa emaw kan nih angin kan naute a damloh huna kan hlauhthawnna leh lungkhamna kan neihte hi thuin sawi chhuah a har khawp mai, a ni lawm ni? Khawsik emaw, khawsik emaw pawh hian min ti lungngai thei hle. Chuvangin, kan fain natna lan chhuah dan danglam tak tak a lantir hian kan thinlung a thlawk chhuak thin hi thil mak a ni lo. Vawiin hian natna pakhat, i hriat ngai loh, mahse hriat a pawimawh em em chungchang kan sawi dawn a ni. Chu chu Kawasaki natna , a nih loh leh ``Kawasaki Disease`` a ni. Lungngai suh, hei hi hriat hmasak a, uluk taka enkawl a nih chuan tihdam theih vek a ni.
Kawasaki Natna hi eng nge ni? A awlsam zawngin...
A awlsam zawngin, Kawasaki natna hi kan taksa chhunga thisen kalna kawng (thisen kalna kawng) bangte a lo hring emaw, a lo hring emaw a ni Naupang tê, kum nga hnuai lam a nghawng ber a, naute thla 6 leh kum 2 inkarah a lang tam zawk. Mahse, a tlem hle nachungin, naupang kum upa zawk leh puitling tleirawlte pawh a nghawng thei a ni.
He natna hi Japanese doctor, Dr. Tomisaku Kawasaki-a’n a hmuhchhuah leh a sawifiah hmasak ber a ni. Chuvang chuan Kawasaki natna an ti a ni.
A pawimawh ber chu hei hi natna hrik kai theih a ni lo . Chumi awmzia chu i fa a\angin mi dangah a darh thei lo tihna a ni. Chuvangin ngaihtuah buai suh.
He natna hian thinlunga thisen phurtu thisen kalna kawngte a nghawng ber a ni. Coronary arteries kan ti a . Chu thisen kalna kawngte chu a lo hring a nih chuan thinlungah nghawng engemaw zat a nei thei a ni. Chuvang chuan he natna hi kan ngaihtuah em em a ni.
He natna hi engtin nge an hriat chhuah? Eng nge a lan chhuah dan?
Kawasaki natna lan chhuah dan hi a danglam deuh hlek. Vawi khatah an rawn lang tlangpui lo va, zawi zawiin an lang zawk. Doctor-te chuan heng symptoms te hi hriat reng nan trick tlem an hmang a, chu chu "CRASH and Burn" an ti a ni. Eng nge an nih i han thlir teh ang.
- "Burn" (fever): Hei hi a lan chhuah dan ber leh hmasa ber a ni. Ni nga emaw a aia rei emaw chhung chu khawsik sang tak a awm thin . He khawsik hi a chang chuan 39-40 degree Celsius (102-104 Fahrenheit) a thleng thei. Khawsik tihziaawmna damdawi hman tlanglawn tak tak hmang pawhin he khawsik hi a reh ngai lo.
Tunah chuan "CRASH" tih awmzia hi han en ila:
- C - Conjunctivitis (mit sen): Naupang mit pahnih var chu a sen vek . Mit natna ang mai a ni. Mahse thil danglam bik chu, mittui a chhuak lo. A sen mai mai a ni.
- R - Rash: Taksa zawng zawngah sen, itchy patches a lang a, a bik takin rilru, pum, hnungzang, a chang chuan kut leh keah te a lang. Heng patch te hi chi hrang hrang a awm thei. Naupang thenkhat chuan heng patches te hi diaper area (thighs leh buttocks) ah an hmu tam zawk mai thei.
- A - Adenopathy: Kawr chhunga lymph node (node) pakhat, a tlangpuiin a sir khatah a lo hring chhuak thin.Hei hi kut a vawn theih khawpa lian a ni thei a, centimetre 1.5 aia lian pawh a ni thei.
- S - Strawberry lei leh hmui danglamna dangte:
- Naupang hmui chu a vawt thei a, a chhe thei a, a châng chuan thisen chhuak thei khawpa sen a ni thei bawk .
- A lei chu a tir lamah chuan coating dum hmanga khuh a ni a, a hnuah a bo a , lei chu a sen a, a hring te te a lo lang a, strawberry ang mai a ni Chuvangin "strawberry tongue" an ti a ni.
- Kawng chhung leh kawr chhung lam pawh a sen thei bawk.
- H - Kut leh ke inthlak danglamna:
- A tir lamah chuan ke kutphah leh kephah chu a sen a, a hring chhuak thin . A ke ruhte chu a hring chhuak ang maiin a lang thei.
- Kar khat leh a chanve atanga kar hnih vel hnuah chuan vun chu kut zungtang leh a châng chuan kephah leh kephah aṭangin a lo chhuak ṭan ang Hei hi flake lian takah a chhuak thei.
Heng symptom lian ber berte bakah hian naupang thenkhat chuan harsatna dang an tawk thei bawk. Entir nan:
- Thinrim tak, tap chhuak .
- Luak chhuak, pum na, luak chhuak.
- Joint na leh a hring.
- A châng chuan jaundice ang chi symptoms pawh a lang thei bawk.
Ngaihtuah teh, i fate chu ni 4-5 chhung zet a khawsik a tlahniam lo a, a chunga kan sawi tak symptom thenkhat pawh an lantir a nih chuan doctor i pan ngei ngei tur a ni.
Engvangin nge hetiang hi a lo awm? Eng thilin nge Kawasaki natna hi a thlen?
Dik tak chuan Kawasaki natna thlen chhan dik tak hi hriat a la ni lo . Hemi chungchang hi Doctor leh Scientist ten an la zirchiang mek a ni. Mahse, a chhan nia ngaih thil engemaw zat a awm a:
- Infection: Taksa immune system hi bacteria emaw virus emaw ang chi thil vangin a overactive a, mahni thisen kalna kawng a bei thei niin an ngai. Mahse eng natna hrik nge a nih tih erawh hriat a la ni lo.
- Genetic predisposition: Chhungkaw thenkhatah chuan naupangte hian hetiang hi an nei tlem zawk tih hmuhchhuah a ni. Hei hian genetic connection engemaw zat a awm thei tihna a ni. Mahse, hei hi nu leh pa atanga fate hnena direct-a rochun natna a ni lo.
- Environment factors: Environment factor thenkhat pawhin hei hi a nghawng em tih pawh kan chhui mek bawk.
A pawimawh ber chu hei hi i tihsual avanga lo awm natna a ni lo tih hi a ni. Ngaihtuah buai suh.
Engtin nge doctor-te hian hei hi an hriat chian? (Diagnosis) tih a ni.
Kawasaki natna hriat theihna tur test chiang tak pakhat mah a awm lo . Chu chu thisen tlemte la a, "Aw, hetah hian Kawasaki a awm" tih theihna test a awm lo tihna a ni.
Doctor chuan naupangin he natna hi a neih leh neih loh chu a natna lan chhuah dan a\angin a zir chiang ang. A chunga kan sawi tak "CRASH and Burn" symptoms engemaw zat hi hun engemaw chen a awm tawh chuan doctor chuan rinhlelhna a nei thei a ni.
Chu bâkah, doctor chuan hetiang hi a ti thei bawk:
- Naupang chu uluk takin enfiah rawh: Khawsik, mit, hmui, vun, kawr leh ke leh ke te enfiah rawh.
- Thisen test dan: 1.1.
- ‘(CRP - C-Reactive Protein)` leh `(ESR - Erythrocyte Sedimentation Rate)` tih ang chi test te hi taksaah inflammation a awm leh awm loh enfiah thin a ni. Kawasaki i neih chuan hengte hi a sang hle thei.
- Thisen var leh platelet awm zat an enfiah thin.
- Liver function test pawh tih theih a ni.
- Zun test: Hri kai theihna dang awm lo turin tanpui rawh.
- Heart test `(Echocardiogram - Echo)`: Hei hi test pawimawh tak a ni . Hei hian thinlung hnathawh dan te, thinlung valve te, a bik takin coronary arteries te dinhmun a enfiah thei a ni. He test hian Kawasaki natnaah heng arteries te hi a hring leh a lian (aneurysm) em tih a hriat theih a ni. He `(Echo)` test hi a tlangpuiin natna hriatchhuah hnuah, kar engemaw zat hnuah tih thin a ni.
Doctor chuan heng zawng zawng hi a thlunzawm ang a, Kawasaki natna a nih leh nih loh a rel ang.
Enkawl a nih loh chuan eng nge thleng ang? Hei hi a hlauhawm em?
Kawasaki natna hi enkawl vat loh leh uluk taka enkawl loh chuan harsatna a thlen thei a ni . Chuvang chuan hriat hmasak a, enkawl tan a pawimawh.
Complication pawimawh leh hlauhawm ber chu coronary arteries (Coronary Artery Aneurysms) zau zel hi a ni. Chumi awmzia chu thinlunga thisen petu thisen kalna kawngte chu balloon ang maiin a hring chhuak tihna a ni. Chutiang ``(Aneurysm)`` a lo awm chuan a kal tlanga thisen kal chu a tikhawlo thei a, thisen zam a lo awm thei a, a chang chuan thisen kalna kawng a puak thei bawk (hei hi a thleng tlem hle). Hei hian nakin lawkah heart attack neih theihna a tipung a ni.
Harsatna dangte chu:
- Myocarditis natna (Myocarditis) a ni
- Thinlung chhehvel membrane a inflammation (pericarditis) .
- Heart valve lama harsatna nei
- Thinlung thawk mumal lo (Arrhythmias) .
Mahse, heng thute hi hre hlau suh. Kawasaki natna hi hriat hmasak a nih a, a lan chhuah atanga ni 10 chhunga enkawl tan a nih chuan heng harsatnate hi nasa takin a tlahniam thei a ni. Chuvang chuan a rang thei ang bera doctor hmu kan ti thin.
Hei hi engtin nge enkawl a nih?
Doctor chuan naupang chu Kawasaki natna a vei tih a nemnghet chuan naupang chu damdawi inah dahin enkawl a ni ang . Hei hi in lama enkawl theih a ni lo.
Enkawl dan tlangpui pahnih a awm a, chungte chu:
1. Intravenous Immunoglobulin (IVIG): Hei hi a enkawlna ber a ni. IVIG hi mi hrisel atanga lak chhuah antibodies awmna solution a ni. Naupang hnenah hian vein hmangin pek a ni a, saline ang mai a ni. Taksa chhunga overactive immune system a ti reh a, thisen kalna kawng a hring (swelling) a tihziaawm bawk. Vawikhat pek a ni tlangpui a, a zawh nan darkar 8-12 vel a ngai.
2. Aspirin hman tur: 1.1.
- A tirah chuan khawsik a reh a, taksaa inflammation a reh hma loh chuan aspirin dose sang tak pek thin a ni .
- Chumi hnuah chuan coronary arteries-a thisen zam a awm loh nan aspirin hniam tak chu kar 6-8 vel emaw, a aia rei emaw pek tur a ni . Doctor chuan naupang echocardiogram a zirin a hun chhung tur a rel ang.
Naupangte hnena aspirin pek hi kan rawt tlangpui lo a, a chhan chu natna hlauhawm tak Reye’s Syndrome tih a thlen thei a ni. Mahse, Kawasaki natnaah chuan aspirin hian a hlawkna a phak lo hle. Chuvangin Doctor thurawn anga pek a ni.
Enkawl lai hian doctor leh nurse-te chuan naupang chu uluk takin an enfiah a, thinlung hnathawh dan, khawsik leh a lan chhuah dan dangte an enfiah reng a ni.
Enkawl hnuah eng nge thleng? Naupang chu a pangngaiin a kir leh dawn em ni?
A tam zawkah chuan IVIG enkawl tan atanga ni khat emaw ni hnih emaw chhungin naupang khawsik chu a reh ang a, natna lanchhuahna dangte pawh a reh zauh zauh ang. Naupang chu a rilru a hahdam tan ang.
Heng thilte hi enkawl hnuah a pawimawh:
- Follow-up appointment: Damdawi in chhuahsan hnuah i fa chu doctor appointment-ah i hruai tur a ni.
- `(Echocardiogram)` test nawn leh: `(Echo)` test hi kar tlemte atanga thla engemaw zat danah coronary arteries dinhmun enfiah thin a ni ang. Hei hi engzat nge tih a nih tih chu naupang thinlung dinhmun a zirin a innghat ang.
- Aspirin tlem pek chhunzawm zel rawh: Doctor-in a tih hma loh chuan aspirin tlem pek kha titawp suh.
- Khawsik emaw, flu emaw i vei loh nan fimkhur rawh: Aspirin i ei laiin i fain chickenpox emaw influenza emaw a vei a nih chuan Reye’s Syndrome vei theihna a awm a, chuvangin chutiang natna vei te lakah i fa chu hla takah dah la. Tin, doctor thurawn angin kum tin i fa chu influenza laka vaccine lak tir thin a tha bawk.
- Vaccine thenkhat sawn: I doctor chuan IVIG enkawlna avang hian virus nung vaccine thenkhat (e.g. measles, mumps, rubella - MMR, chickenpox vaccine) thla engemaw zat sawn turin a fuih thei che a ni. Hemi chungchang pawh hi i doctor nen sawiho rawh.
Thu lawmawm tak chu Kawasaki natna hi enkawl vat a nih chuan naupang tam zawk chu an dam kim vek a, an thinlungah hun rei tak nghawng nei lovin nun pangngai an hmang thei a ni.
Doctor hmuh ka ngai em? Engtikah nge ka kal ang?
Ni e, a dik tak zet. I fain heng symptoms te hi a neih chuan doctor i pan nghal tur a ni .
A bik takin heng thilte hi fimkhur hle ang che:
- Ni 4-5 aia rei khawsik sang , a bik takin khawsik damdawi pangngai hmanga a reh loh chuan.
- Khawsik hi mit sen, hmui hrual, lei inthlak danglam, taksaah hliam, kut leh ke hring, leh kawrfual hring te ang chi chhinchhiahna pakhat emaw a aia tam emaw a awm chuan
Kawasaki natna hi a tlem hle. Mahse, a chang chuan virus natna tlanglawn dangte nen thliar hran a harsa thei hle. Chuvang chuan rinhlelhna i neih chuan, "hei hi natna tlanglawn tak angin a lang lo" tih i ngaihtuah a nih chuan, doctor pan a, thurawn dil a tha ber. A hmaa hriat chhuah a nih chuan enkawl tan thuai theih a ni a, harsatna a thlen theihna a tlahniam bawk.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Nu leh pa i nih angin Kawasaki Disease hi i ngaihtuah mai thei. Chu chu thil pangngai a ni. Mahse, hengte hi hre reng ang che:
- Kawasaki natna hi naupang tê tête thisen kalna kawng a ti na a .
- A lan chhuah dan ber chu ni engemaw zat chhung khawsik sang tak, mit sen, hmui leh hmui inthlak danglam, vun rawng, kut leh ke a hring a, chutah vun a hring chhuak, leh kawr chhunga lymph node a hring
- Hei hi natna hrik kai theih a ni lo .
- A chhan dik tak hriat ni lo mah se, a hun taka enkawl a nih chuan a dam vek thei .
- Enkawl loh chuan thinlunga thisen kalna kawngte a nghawng thei a ni . Chuvangin enkawl vat a pawimawh.
- Enkawlna chu damdawi ina dah leh damdawi `(IVIG)` leh `(Aspirin).` tih hmanga enkawl a ni
- I fain heng symptoms te hi a neih chuan doctor pan nghal rawh. Hlauthawng lo, hmalak vat a pawimawh.
I fa chu dam thuai turin duhsakna hlanin! He thu hi in tan a tangkai ngei ka beisei.
` Kawasaki natna, Kawasaki natna, naupang khawsik, mit sen, strawberry lei, thinlung natna, IVIG, aspirin therapy











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