A châng chuan i ruh leh ruhteah natna chauh i nei em? Nge i lu chu a lian deuh deuh a, i ke pawh a tawi deuh deuh niin i hria em? Chûngte chu tar pêng pângngai tak niin i ngai mai thei. Mahse heng thil hnung lamah hian ‘Paget’s Disease of the Bone’ an tih, sawi theih loh dinhmun thup a ni thei. He hming hi i tan chuan thil thar a ni mai thei. Mahse hei hi ngawi renga kan ruh hriselna tichhe thei dinhmun a ni. Vawiin hian awlsam takin, i hriatthiam theih tur angin kan sawi dawn a ni.
A awlsam zawngin, Paget-a Disease of the Bone tih hi eng nge ni?
Hei hi hrethiam tur chuan kan ruhte hnathawh dan hi han thlir hmasa ila. Kan ruhte hi thil nung lo mai a ni lo. Tissue nung, mahni insiam thar zel, cell hlui paih chhuakin, cell thar siam chhuak zel an ni. Hei hi bone remodeling kan ti a. In hlui tihchhiat a, a aiah in thar, chak zawk sak ang mai a ni. Hei hi kan ruh nghet taka vawn nan a pawimawh hle.
Mahse, Paget-a ruh natna vei mi pakhatah chuan he thil hi a kal sual vek a ni. Hetah hian thil thleng chu a awm:
1. Ruh hlui a chhe rang: Ruh cell hlui te chu a pangngai aia rang zawkin a chhe vek.
2. Ruh thar siam dan mumal lo: Taksain ruh thar a siam thuai a, a ruh chu a luah khat thin. Mahse, ruh thar lo piang chu a chak lo va, a mumal lo va, a lian a, a chhe thei bawk. A pianzia pawh a danglam hle.
A awlsam zawngin sawi ila, bass player tawnhriat ngah tak chuan hmanhmawh taka thil tih a tum a, chu chu engmah hre lo miin hmanhmawh taka a tih chuan thil thleng ang mai a ni. Kulh siam pawh nise, a zar a, a chak lo ang a, a chhe thuai ang. Chu chu he natnaah hian kan ruhte chungah a thleng thin. Because of this , ruh te hi a chhe awlsam (fractures) a, arthritis (arthritis) vei theihna chance a sang hle. He natna hming dang chu `(Osteitis Deformans)` tih a ni.
He natna hi cancer a ni em? ‘Paget natna’ dang nen chuan inthlau suh ang che!
Hei hi mi tam takin harsatna an neih a ni. Mi thenkhat chuan a hming a inang em avangin an hlauthawng thin.
Fiah takin hre reng ang che: Paget-a ruh natna hi cancer a ni lo.
Mahse, hetah hian thil tenawm tak hriat tur a awm. Very rarely , chu chu, a awm theihna a hniam hle a, Paget natnain a nghawng ruhah ruh cancer (`osteosarcoma`) a lo awm theihna chance tlemte a awm a ni. Mahse hei hi a tlem hle tih hriat reng a pawimawh.
Natna dang engemaw zat ‘Paget’s’ tia koh a awm a, mahse he ruh natna nen hian inzawmna an nei lo.
- Paget’s disease of the breast: Hei hi hnute cancer chi khat hmuh tur awm lo tak a ni a, nipple area-ah a awm thin.
- Paget-a natna vulva: 1.1.Hei hi hmeichhiaah chuan vun cancer chi khat, vagina hmui vel a awm thin a ni.
Chuvangin, heng natna pathumte hian hming inang nei mah se, hengte hi damdawi lam dinhmun inang lo tak tak pathum, inzawmna nei lo an ni tih hrethiam rawh.
Tute nge he natna vei theihna sang zawk?
Scientist-te chuan he natna thlen chhan dik tak hi an la hmuchhuak lo a, mahse, genetic factors pahnih , chu chu hereditary influences, leh environmental factors -te inzawmkhawm vang niin an ngai.
A hnuaia table-ah hian he natna lo awm chhan lian ber berte tarlan a ni.
| Risk factor a ni | Hrilhfiahna |
|---|---|
| Kum | Kum 50 chunglamte chu he natna hi an vei theihna a sang zawk a ni. He risk hi kum upa lam a zirin a sang chho zel a ni. |
| Chhungkaw chanchin | I chhungte hnai tak (nu, pa, unau) zinga pakhatin he natna hi a neih chuan nang pawhin i vei a rinawm zawk. |
| Hnam Hmun atanga lo piang | He natna hi Europe ram, a bik takin England, Italy leh Spain ang ramte zingah hian hmuh tur a awm fo. |
| Sex hman dan | Hmeichhia aiin mipain he natna hi an vei tam deuh deuh a ni. |
He natna lan chhuah dan engte nge ni? Engtin nge i hriat chian?
He natna mak tak chu mi tam tak chuan symptoms an nei lo tak zet a ni . A nih loh leh symptom tenau tak tak, ngaihthah theih loh tak tak an nei bawk. Chumi avang chuan he natna hi chhan dang vanga X-ray emaw thisen test emaw tih a nih chuan accident-a hmuhchhuah a ni fo thin.
Mahse, symptoms a awm tak tak chuan ruh natna a zirin a danglam thei. A lan chhuah dan tlangpui chu:
- Ruh emaw ruh natna: Hei hi a lan chhuah dan ber leh langsar ber a ni. Ruh natna emaw, a kianga ruh emawa natna thuk tak, natna awm reng angin hriat theih a ni.
- Bone deformity: Hun kal zelah ruh pianzia a danglam thei. Entirnan, lu ruh a khawih chuan a lu chu a lian deuh thei a, a ke a khawih chuan ke chu a kun thei bawk.
- Fractures: Ruh lo piang tharte chu a chak lo a, a tlakbuak emaw, accident tenau emaw a awm pawhin awlsam takin a chhe thei a ni.
- Lu na leh hriatna hloh: Natna hian luruh ruh a nghawng chuan chu ruh a thim chuan nerve compression, lu na leh hriatna hloh a thlen thei a ni.
- Back pain: Ruhro a nghawng a nih chuan hnungzang na leh ke ruh natna ang chi symptoms a awm thei.
He natna hi engtin nge doctor hian a hriat theih ang?
A chunga kan sawi tawh ang khan hei hi thil thleng mai maiin hmuhchhuah a ni fo thin. I doctor chuan heng test-na atan hian symptom i neih chuan emaw, chhan dang avanga test i neih chuan rinhlelhna a siam emaw chuan a refer thei che a ni.
- Alkaline Phosphatase (ALP) thisen test: Hei hi test hmasa ber a ni a, clue a pe thei a ni. He enzyme `ALP` an tih hi ruh cell a lo pian lai hian a lo piang chhuak thin a ni. Paget natnaah chuan ruh siam dan a tam lutuk avangin thisenah `ALP` level a sang hle.
- X-ray: Natna finfiah dan tha ber chu ``X-ray`` hmanga tih a ni. ``X-ray`` thlalak hian ruh natna vei te chu ruh hrisel dang aiin chiang takin a thliar hrang thei a ni. An thickness a lo pung dan leh an pianzia a inthlak dan te chu i hmu thei.
- Bone Scan: Hei hi taksaa ruh engte nge natnain a nghawng tih chiang taka hriat theih nan leh a nasat zia hriat nan tih a ni. Radioactive dye tlemte chu vein pakhatah inject a ni a, a natna hmunte chu scan a nih chuan ‘bright spots’ anga hmuh a ni.
Hei hi eng enkawlna nge ni? A dam kim thei ang em?
Pakhatnaah chuan, chanchin ṭha chu. Tunah hian he natna hi damdawi a la awm lo . Mahse, lungngai suh. Natna zual zel tur tihkhawtlai nan te, symptoms control nan te, harsatna awm thei tur venna atan te enkawlna tha tak tak a awm a.
Enkawlna hi symptomatic nei tan chauh a ngai a, a nih loh leh an natnain hmun pawimawh tak tak, luruh leh ruhro a nghawng tawh tan chauh a ngai a ni.
Damdawi ei tur
Hemi atana damdawi hman ber chu bisphosphonates a ni . Heng damdawi te hian ruh chhe chak tak chu a control a ni.
- Tunah hian he category-a damdawi tha ber leh hman lar ber a ni.Zoledronate a ni . Hei hi vein pakhata injection te tak te (`infusion`) pek a ni. He damdawi hi vawi khat injection hmang hian kum tam tak chhung chu natna hi a thunun theih a ni.
- Mahse hre reng ang che, heng damdawi te hian natna darh zel tur chu a titawp mai a, mahse ruh chhiatna lo awm tawh chu a siam tha thei lo.
Inzai
Natna avanga harsatna awmte chu zai a ngai a ni. Entir nan:
- Fracture a awm chuan set rawh.
- Natnain ruh a tihchhiat vek chuan khup emaw hip ruh thlak emaw surgery tih tur a ni.
- Ruh dik lo (misaligned bonnes) te chu realignment (realignment) a ni.
- Nervous tension a awm chuan chu pressure chu tihziaawm rawh.
He natna hi hriat chian leh enkawl a nih hma chuan ruh tliak leh ruh natna ang chi harsatna te chu a rang thei ang bera ven theih a ni. Chuvang chuan a natna lan chhuah dan fimkhur a pawimawh hle.
Take-Home Thuchah a ni
- Paget’s Disease of the Bone hi cancer a ni lo va, ruh tichak lo thei khawpa natna rei tak a ni.
- Mi tam tak chuan symptoms an nei lo. A lan chhuah dan ber chu ruh na, deformity, leh ruh tliak awlsam te a ni thei.
- Thisenah alkaline phosphatase level sang leh X-ray test hmangin awlsam takin natna hi hriat theih a ni.
- Natna hi tihdam kim theih ni lo mah se, damdawi bisphosphonates ang chi hmangin natna hi tha taka control theih a ni a, harsatna awm thei tur venna atan pawh hman theih a ni.
- Kum 50 aia upa i nih chuan, chhungkaw history-ah he natna hi i vei a nih chuan, emaw, ruh natna danglam tak, awm reng i neih chuan ngaihthah suh la, i doctor hnenah thurawn dil ngei ang che.











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