Nausen piang thar kan en hian a chang chuan nu leh pate chuan naute hian a number pangngai aia kut emaw ke ruh emaw pakhat emaw a aia tam emaw a nei tih an hmuh chuan an mangang deuh a, an hlau deuh bawk. Hei hi i hmuh hian tlem a lungngaihna leh lungngaihna i neih hi thil pangngai tak a ni. Mahse , hlau suh, a dik em? Hei hi a tam zawkah chuan harsatna lian tak, pawi tak a ni lo. Vawiin hian hetianga kut zungtang tam zawk neih theihna dinhmun kan sawi dawn a, chu chu damdawi lam chuan polydactyly an ti a ni. Mi thenkhat chuan hei hi hyperdactyly an ti bawk.
Polydactyly chu eng nge ni? A awlsam zawngin...
A awlsam zawngin, polydactyly chu naute chu a tlangpuiin kut emaw ke emaw-ah kut zungtang emaw ke ruh pakhat emaw a aia tam emaw neia piang a ni a, a tlangpuiin panga a piang lo. Khawvela piansualna (or pian tirh laia awm dinhmun) awm tam ber zinga mi anga ngaih a ni . Doctor-te chuan a bik takin kut zungtang dang awm hi pianpui kut inthlauhna category zau takah a tel niin an sawi. Chumi awmzia chu naute chu kutah danglamna neiin a piang tihna a ni.
Tunah chuan, "Aw, hei hi ka naute chungah chauh a thleng em?" Chutiang chuan ngai suh. Hei hi i ngaihtuah angin thil mak a ni lo.
Doctor-te hian engtin nge hei hi an hriat?
Vawi tam tak chu doctor-te chuan naute i beisei laiin ultrasound scan laiin heng kut zungtang dang hi an hmu thei a ni. Tun hmaa i hriat loh pawhin naute pian veleh doctor-te chuan an hre nghal thei a, a chhan chu extra finger chu chiang taka hmuh theih a nih vang a ni.
Doctor-te chuan hetiang kut zungtang dang an hmuh hian naute chu uluk takin an enfiah a, hetiang chiah hi a ni em tih emaw, a kaihhnawih genetic disorder dang a nei em tih emaw an enfiah thin. A chhan chu a chang chuan he natna polydactyly an tih hi a mah chauhin a awm thei a, a nih loh leh genetic disease dang symptom angin a lo awm thei bawk.
I naute hian polydactyly a vei tih i hriat chuan hlauhna leh lungkham deuh deuh i neih hi thil pangngai a ni. Mahse hre reng ang che, he extra toe hian naute tan natna leh hrehawmna a thlen lo tlangpui.
Doctor te chuan awlsam takin he extra toe hi surgery tlemte hmangin an la chhuak thei a ni. Mahse, naute hian a kaihhnawih genetic condition dang a nei tih hmuhchhuah a nih chuan enkawl leh enkawl hran a ngai mai thei.
Polydactyly chi hrang hrangte chu engte nge ni?
Tunah chuan he natna chi hrang hrang, polydactyly hi han en ila. He classification hi eng finger-ah nge extra finger a inbun tih a zirin a ni. A chi thum a awm a, chungte chu:
1. Preaxial polydactyly: Hei hian ke ruh lian lam (kut a nih chuan) emaw ke ruh lian lam emaw a kawk a ni .(Kea chungah a nih chuan) Extra toe a awm. Doctor-te chuan kut ke ruh lian lam a extra toe chu ``radial polydactyly`` an ti a, ke ruh lian lam a extra toe chu ``tibial polydactyly`` an ti bawk.
2. Central polydactyly: Hei hi kut zungtang emaw ke ruh emaw laiah extra digit a lo awm hian a ni . Chumi awmzia chu extra digit chu index, middle, leh ring finger inkarah emaw, ke ruh lian leh ke ruh te tih loh chu ke ruh hmun dangah emaw a awm thei tihna a ni. Hei hi chi dang pahnih aiin a tam lo hle.
3. Postaxial polydactyly: Hei hi kut zungtang te tak te sir (kut emaw ke emaw ah) digit extra awm hi a ni. Doctor-te chuan kut zungtang te tak te sir lama digit extra awm chu ``ulnar polydactyly`` an ti a, kut zungtang te tak te sir lama digit awm chu ``fibular polydactyly`` an ti bawk. Hei hi polydactyly chi khat zingah chuan a tam ber a ni.
Hrethiam e? Okay, chuvangin he thil chhinchhiahna hi i en leh ang.
Polydactyly natna lan chhuah dan chu engte nge ni?
Dik tak chuan polydactyly chhinchhiahna awm chhun chu naute kut emaw ke emaw-ah kut zungtang emaw ke ruh panga aia tam a awm hi a ni. Heng extra fingers te hi pian tirh atangin chiang takin a lang.
Naute hian polydactyly chi hrang hrang a neih dan azirin heng extra fingers te hi a lo thanglian vek thei a, finger dang ang maiin a lang thei bawk. Mahse a tam zawkah chuan heng extra fingers te hi finger pangngai angin an lo thanglian tha lo. Ṭhenkhat chu vun aṭanga chhuak tê tê chauh an ni thei a, vun emaw, nerve emaw-ah an inzawm thei bawk. Ruh te tak te pawh a awm thei bawk.
Engvangin nge heng extra fingers te hi a lo lang? A chhante chu engte nge ni?
Tunah chuan zawhna i nei ta, "Engvangin nge kan naute chungah hetiang hian a lo awm?" Polydactyly a awm chhan ber chu nausen pum chhunga a lo thanglian lai hian a genes-ah inthlak danglamna a awm vang a ni. Kan taksa thanlen dan tur leh cell tinte hnathawh dan tur thupek zawng zawng awmna blueprint lian tak angin han ngaihtuah teh. Heng genes te hi nu leh pa atanga fate rochun a ni.
Chuvangin, nausen pum chhunga a awm laiin heng genes lo pian chhuahna kawngah hian tihbuai emaw, inthlak danglamna emaw a awm chuan naute taksaah inthlak danglamna chi hrang hrang a thlen thei a ni. Inthlâk danglamna ṭhenkhat chu hriat chhuah a ni ngai lo mai thei. Mahse a chang chuan heng genetic changes te hian congenital conditions polydactyly ang chi a thlen thei thin.
Naute kut leh ke thanna thununtu gene-te chu thil engemaw tibuaitu a nih chuan polydactyly neia piang a nih a rinawm zawk. Heng genes te hi genetic disorders in a nghawng thei a ni. Environment factor thenkhat (naupai laia nu emaw, boruak tichhe thei thil) pawhin hetiang hi a thlen thei niin an sawi bawk a, mahse genetic influences hi a bulpui ber a ni.
Polydactyly hmanga hmuh theih genetic condition thenkhat chu:
- Carpenter natna a ni
- Down syndrome tih hi a ni
- Fanconi thisen tlakchhamna (anemia) a awm
Heng bakah hian polydactyly hi genetic condition dang engemaw zat nen pawh hmuh theih a ni.
Tute nge polydactyly vei theihna chance sang zawk?
Nausen eng pawhah polydactyly hi awm thei mahse, naute thenkhat chuan he natna hi an nei tam zawk. A nghawng thei risk factor engemaw zat a awm a:
- Gender: Polydactyly hi hmeichhia aiin mipaah a tam zawk.
- Hnam: Hetiang dinhmun hi khawvel hmun hrang hranga hnam thenkhatah a tam zawk. Entîr nân, zirchianna ṭhenkhatah chuan hnam dang mipa naupangte aiin African hnam chhuak mipa naupangteah a let sâwm vêl zetin a tam zâwk tih a târ lang a ni . African hnam hmeichhe naupangte zingah hnam dang hmeichhe naupangte aiin a let sawmhnih velin a tam zawk tih an sawi bawk. Hei hi genetic influences nen a inzawm thei a ni.
- Chhungkaw chanchin: I chhungkuaa mi tu emaw, a bik takin i chhungte hnai tak (nu, pa, unau) chu polydactyly neia piang a nih chuan, emaw, chhungkaw history-a genetic diseases nei a nih chuan i naute pawhin polydactyly a vei a rinawm zawk.
Engtin nge doctor-te hian hei hi an nemnghet tak tak?
Kan sawi tawh ang khan i doctor hian naupai laiin ultrasound neih laiin hei hi a hmu thei mai thei. A nih loh chuan i naute pian hnua i enfiah hunah i doctor chuan a hre ngei ang. I naute kut emaw ke emaw a kut zungtang emaw ke ruh emaw extra chu a hre thei ang a, eng polydactyly nge a nih tih a hrilh thei ang che.
A châng chuan, i doctor chuan enkawlna hmain kut X-ray emaw, ke X-ray emaw neih a rawt thei a, a bîk takin ke ruh dang ruhte chu engtin nge a awm tih leh ke ruh dangte nêna an inzawm dân hriat nân.
Genetic testing chungchang pawh kan zir dawn em ni?
I chhungkuaa mi tu emaw chuan polydactyly a vei tawh a nih chuan, emaw, i vei nia i rinhlelh chuan genetic counselor nen inbiakna neih a tha hle . Genetic testing neih tur leh neih loh tur chungchangah an pui thei che a ni. Heng test hmang hian genetic change hrang hrang, gene variant te pawh a awm a, chu chuan polydactyly a thlen thei a ni.
Gene variant engemaw carrier i nih pawhin i fain chu genetic disease chu a nei dawn tihna a ni hauh lo tih hre reng ang che.
Genetic counselor chuan i hlauhawmna te, i hriselna humhim dan tur te, leh i fate hnena genetic harsatna i thlen theihna tur tihtlem nan i tih theih turte a hrilhfiah thei a ni.
Polydactyly hi engtin nge enkawl a nih?
Polydactyly enkawl dan hi a natna awm dan azirin a danglam deuh thei. Mahse enkawlna hman tlanglawn ber chu naute kut emaw ke emaw atanga extra digit lakchhuah hi a ni. He extra digit hi paih chhuah dan kawng hrang hrang a awm. Eng nge an nih hi han thlir ila:
1. Surgical ligature: Hetah hian doctor chuan extra finger bul vel chu hrui (ligature) khauh takin a khin a. Knot te tak te khih ang mai a ni. Hetianga nghet taka an khih chuan kut zungtang dang thisen kalna chu a tawp a, ni engemaw zat (kar khat emaw kar hnih emaw vel) hnuah a vawt a, a mah chauhin a tla thla thin. Hei hi kut zungtang te tak te, a lo thanglian tha lo, vunah a innghat mai mai te tan tih a ni fo thin.
2. In-office excision: Hetiang tih danah hian doctor chuan naute ke ruh (extra toe) awmna hmun chu a numb theih nan injection te tak te a pe ang. Tichuan, hmanraw bik (a then chuan cautery device an tih) hmangin a ke ruh (extra toe) chu an tan a, an la chhuak leh thin. Hei hi doctor office-a tih theih a ni bawk.
3. Surgical removal (Polydactyly surgery): A chang chuan extra toe chu a lo thang tha a, ke ruh dang nen ruh neiin a inzawm tha a nih chuan, a nih loh leh ke ruh extra te tan chuan a hmaa kan sawi tawh ang khan hmanraw awlsam tak tak te hian hna a thawk lo. Chutiang a nih chuan ke ruh extra chu lakchhuah nan operation tenau tak neih a ngai a ni. Hei hi naute a upat deuh hnuah, anesthesia hnuaiah tih a ni tlangpui.
Eng method pawh hmang ila, doctor chuan naute tana hmanraw tha ber leh him ber a thlang ang.
Enkawl zawhah engtikah nge Doctor ka hmuh leh ang?
Extra toe i lakchhuah hnuah a dam hma loh chuan a hmun chu uluk taka enkawl a ngai a ni. I naute ke ruh lakchhuahna hmunah hian danglamna emaw, nuam lo emaw i hmuh chuan i doctor nen inbia ngei tur a ni. Doctor pan nghal la, a bik takin a hnuaia symptoms te hi i neih chuan:
- Thisen chhuak a awm chuan
- Hliam atanga tui emaw, hnim emaw lo chhuak a awm chuan
- Chu hmuna vun rawng chu a danglam tawh ang tih a hriat chuan (a sen emaw, a sen emaw a inthlak ang chi) .
- Swelling a awm chuan
- Chu lai hmunah chuan naute chu a na ang tih a hriat chuan
Hetiang thil hi i hmu a nih chuan Doctor hnenah i hrilh nghal mai tur a ni lo maw?
Ka naute hian polydactyly a vei a nih chuan eng nge ka beisei ang?
I naute hian polydactyly a nei tih i hriat chuan hlau suh. I naute chu extra toe lakchhuah hnuah a dam kim theih i beisei thei ang. He extra toe hi lakchhuah hian a hmalam hun atana a thanlenna leh a hmasawnna a nghawng dawn lo.
Mahse, i fa hian nau piangsualna dang emaw, polydactyly nena inzawm genetic condition dang emaw a neih chuan enkawlna hrang hrang emaw, enkawlna bik emaw a mamawh thei a ni. I doctor chuan hei hi a hrilhfiah ang che.
I naute a pian hunah kut zungtang emaw ke ruh emaw extra hmuh chu mak tak leh hlauhawm tak a ni thei. Mahse, lungngai suh. Polydactyly hi enkawl theih a ni a, hun rei tak chhung chu i naute than leh thanlennaah nghawng a nei lo. Kut zungtang emaw ke ruh dang lak chhuah dan zawng zawng hian a dam thuai ang a, nakin lawkah i naute kut emaw ke emaw hman theihna a nghawng dawn lo. Hemi chungchangah emaw, genetic condition dang emaw chungchanga zawhna i neih chuan doctor nen inbiakna neih hreh suh.
A tawp berah chuan thil hriat reng tur (Take-Home Message) .
Okay, chuvangin, kan sawi tawh atanga ngaihtuah tur pawimawh ber berte chu hetiang hi a ni:
- Polydactyly chu naute chu kut zungtang emaw ke ruh pakhat emaw a aia tam emaw a neih belh a nih chuan a ni. I ngaihtuah angin a pawi lo hle a, a awm fo bawk.
- He extra toe hian naute chu a ti na lo tlangpui.
- Doctor te chuan he extra toe hi enkawlna awlsam tak hmangin an la chhuak thei a ni.
- Extra toe lakchhuah a nih hnuah naute chu a dam nghal vat a, a ke leh ke hman harsa a ti lo.
- A châng chuan polydactyly hi genetic condition dang nen a inzawm thei bawk. Hemi chungchang hi i doctor chuan a hriattir ang che.
- Ringhlelna, hlauhna, harsatna i neih chuan i doctor nen zalen takin inbiakna nei ngei ang che. I tanpui turin an awm reng a ni.
Chuvangin, he thu hi i tan a tangkai ngei ka beisei. I naupang tê chu hriselna ṭha neih ka duhsak a che!
` Polydactyly, extra fingers, piansualna, genetics, naute hriselna, surgery, naupang enkawlna











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