I naute lung a lo thang tha lo em ni? (Pulmonary Hypoplasia) A chanchin hi i zir chiang ang u!

Nausen piang thar i en hian i hlimna chu sawifiah theih loh a ni lawm ni? Mahse, a chang chuan chu hlimna rual chuan hlauhna tlem tal i rilruah a lo lang thin a, a bik takin naute thaw harsa a tih i hmuh chuan. Chutiang hunah chuan nu leh pate rilrua zawhna lo chhuak pakhat chu, "Ka naute hi thil dik lo a awm em?".. tih hi a ni. Vawiin hian hetiang dinhmun pawi tak, mahse hriat tur pawimawh tak chungchang kan sawi dawn a ni. Chu chu naute lung a lo thang tha lo tihna a ni a, chu chu damdawi lam chuan `(Pulmonary Hypoplasia)` kan tih hi a ni.

`(Pulmonary Hypoplasia)` tih hi eng nge ni? A awlsam zawngin i hrethiam ang u.

A awlsam zawngin sawi ila, Pulmonary Hypoplasia chu i naute chu a pum chhunga a awm laiin a lungphu chu beisei angin a lo thanglian loh vang a ni. This is a congenital condition , an pian tirh lamah an awm tihna a ni. A tam zawkah chuan hriselna dinhmun dang hnuaia awm vang a ni. Chu chu, lungte hian pum chhunga thanna tur hmun a nei tawk lo tihna a ni. A châng chuan, doctor-te chuan naute pian hmain, naupai laiin, ultrasound scan hmangin he natna hi an hmuchhuak ṭhin. A châng chuan naute pian hnu lawkah emaw, a pian hnu ni engemaw zat hnuah emaw a ni.

Tunah chuan en teh, kan lung chhungah hian boruak bawm te tak te alveoli an tih a awm a. Hengte hi thisenah oxygen kan lak luh belhkhawmtu an ni. Chumi hnuah thisen chuan he oxygen hi taksa pum puia tissue-ah a phur lut ta a ni. Chuvangin, lungte hi a lo thang tha lo a nih chuan heng air sacs te pawh hi an tlem zawk a ni. Chuti a nih chuan eng nge thleng? Taksa peng dang leh tissue te hian oxygen an hmu tlem hle. Hei hian thinlungin hna a thawk nasa zawk a, lung chhunga thisen sang pawh a tisang thei (pulmonary hypertension). Thing te tak te hian tui, hmun leh ei leh in a tlakchham chuan a thang tha thei lo ang bawkin han ngaihtuah teh.

Naute hian eng symptoms nge a lantir?

Nausen piang tharin Pulmonary Hypoplasia a vei chuan a natna lan chhuahna te chu:

• Vun, hmui, emaw kut zungtang (`(cyanosis)`) . Hei hi taksa peng hrang hrangin oxygen an dawn tlem vang a ni. A bik takin he blue color hi thisenah oxygen a tlem chuan a lo awm thin.
• Hnar kawngkhar alh chhuak . Chumi awmzia chu naute hian thawk a harsat avangin thaw lak tumin a bei nasa zawk tihna a ni. Kan tlan a, kan tlu a, kan hnar kan puak chhuak a, kan thawk kan chhuah ang bawkin.
• Thâwk harsa. Naute chuan thawk a chhuah laiin thawk hah emaw, thawk hah emaw a ti thei.
• Thâwk lak chakna (tachypnea) . Naute chu a pangngai aia a thaw chak zawk a nih chuan chu pawh chu chhinchhiahna a ni.

I naute hian heng symptoms pakhat emaw a aia tam emaw a neih chuan doctor pan nghal a tha ber. Hengte hi thawkna lam natna dang chhinchhiahna a ni thei bawk a, chuvangin diagnosis dik tak neih thuai a pawimawh.

Engvangin nge hetiang hi a lo awm? `(Pulmonary Hypoplasia)` awm chhan berte chu engte nge ni?

Pulmonary Hypoplasia hi hriselna lama harsatna dang vang a ni fo thin a, chu chuan nausen chhunga lung a lo thang tha thei lo. Heng dinhmunte hian lungte chu a thanlenna tur hmun mamawh nei lovin a awmtir thin. A hnuaia dinhmunte hi a tam ber a ni:

• Low amniotic fluid (oligohydramnios) : Naute chhehvela amniotic fluid a tlem chuan lung a pressure a siam thei a, a thang tha lo thei bawk. He tui hian naute tan cushion angin hna a thawk a, lung chu a lo thanglian thei a ni.
• Congenital Diaphragmatic Hernia (CDH) : Diaphragm hi rilru leh pum inthenna ruh a ni. A chhungah khur a awm a, pum chhung peng thenkhat (intestines leh liver ang chi) chu rilru chhungah a rawn chhuak a nih chuan lung tan hmun a tlem zawk. Tichuan lung chu a inflate thei lo va, a thang tha thei lo bawk.
• Omphalocele : Hetiang dinhmunah hian naute taksa peng thenkhat chu umbilical cord kaltlangin a chhuak a, chu chu membrane-in a khuh a ni. Hei hian naute pum chhunga pressure a thlak danglam thei a, lung hmasawnna a nghawng thei bawk.
• Prolonged Premature Rupture of Membranes (PROM) : Naute pian hmaa amniotic sac a rupture chuan, PROM tia hriat a ni a, a tui level a tlahniam thei a, lung hmasawnna a nghawng thei bawk.
• Cystic lung disease : Heng hi cancer ni lo tumor an ni a, lung chhungah hmun an luah a, lung tissue pangngai lo thang chakna tibuaitu an ni.
• Lung lama harsatna avanga thinlung lian zel : Entirnan, pianpui thinlung natna ``tricuspid atresia`` emaw ``Ebstein's anomaly`` emaw avanga thinlung a lo lian chuan lungah pressure a siam thei a ni.
• Abnormal or non-functioning diaphragm : Diaphragm hi lungphu a thawk tha tur chuan a pawimawh hle. A hnathawh danah harsatna a awm chuan lung hmasawnna pawh a nghawng thei bawk.

Mahse, a châng chuan doctor-te chuan ``Pulmonary Hypoplasia.`` awm chhan chiang tak an hmu thei lo.`` Primary pulmonary hypoplasia kan ti a ni. Hei hi 10% atanga 15% vel ah a thleng thin.

Hetiang dinhmun hi tute nge hlauhawm ber?

Naupai lai hian nausen chu pulmonary hypoplasia vei theihna a tipung thei a, chu chu oligohydramnios leh prematurity te hi a ni. Chung zingah chuan:

• Infection : Sexually transmitted infection (STIs) emaw bacterial infection bacterial vaginosis ang chi te hian i tui chu a hun hmain a ti chhe thei a ni.
• Cervical sei zawng tawi . Hei hi nau piang hma leh `(PROM)` thlentu a ni thei bawk.
• Multiple beisei, twins emaw triplets emaw ang chi . Hei hian nausen pum chhunga hmun tlem leh tui tlak hniam ang chi harsatna a thlen thei a ni.
• Amniocentesis : Hei hi naupai laiin test a ni. Mahse, a tlem hle a, tui bag chu a chhe thei a, fluid a leak thei bawk.
• Naupai laiin thisen sang emaw preeclampsia emaw a awm thin. Chungte chuan nausen (placenta) hnathawh a tichhe thei a, naute ei leh in leh oxygen a tihtlem bakah tui a hloh thei bawk.
• Zunthlum : Nuin zunthlum a neih chuan harsatna engemaw zat a thlen thei bawk.
• Dehydration : Nuin tui a in tlem chuan amniotic fluid level a tlahniam thei.

Hei vang hian doctor thupek dik taka zawm a pawimawh em em a, naupai laiin a hun taka clinic kal hi a pawimawh em em a ni. I hriselna enkawl hian i naute hriselna a nghawng nghal vek a ni.

Hei hian eng harsatna dang nge a thlen theih?

Lung a lo thang tha lo a nih chuan naute taksa peng dangah harsatna a thlen thei a ni. Hengte hi `(Pulmonary Hypoplasia):` avanga harsatna awm thei te an ni

• Thisen a oxygen level hniam (hypoxemia) : Hei hi harsatna lian ber a ni. Thluak leh taksa peng dangte a tichhe thei a ni.
• Naute lung chhunga thisen sang (pulmonary hypertension) : Chuap chhunga thisen kalna kawngte chu a zim a, chu chuan thinlungah pressure sang zawk a siam a ni.
• Trachea chak lo emaw, a lo thanlen dan dik lo emaw (tracheomalacia) : Hei hian thawk laiin thawkna kawng a tikhawlo thei a ni.
• Pneumothorax : Chuap atanga boruak a luang chhuak a, lung vel a khawlkhawm a, lung chu a tlakbuak ta a ni.
• Thâwk lama harsatna : Entirnan, bronchopulmonary dysplasia. Hengte hi a hnuah a thleng thei a, a bik takin nausen piang hmaah, ventilator nena an inzawm chuan a thleng thei a ni.
• Pulmonary hypoplasia thlentu underlying condition avanga harsatna dang awm thei te. Entîr nân, chaw ei harsatna, hriatna lama harsatna, leh ṭhanlenna tlai .

"Hetiang zawng zawng i hriat hian hlauhna i nei mai thei. Mahse, hre reng ang che, hriattirna pek hi hetiang dinhmun hmachhawn tur hian a tha ber a ni. I doctor-te nen inbia la, zawhna i neih zawng zawng zawt rawh."

Engtin nge doctor-te hian he natna hi an hriat theih?

A tam zawkah chuan doctor chuan naupai laiin ultrasound scan pangngai (routine ultrasound scan) hmangin Pulmonary Hypoplasia a nei tih a hmuchhuak thin. Scan hian naute lung lian leh te leh a rilru vel a teh a ni. MRI (magnetic resonance imaging) scan hmangin a natna hmuhchhuah chu a dik tih finfiah theih a ni bawk. MRI hian lung volume chiang zawkin a hmu thei a ni.

A châng chuan, doctor-in he natna hi pian tirh emaw, pian hnu ni engemaw zat hnuah emaw a hmuchhuak ang. I naute hian thawk harsatna a neih chuan doctor chuan chest X-ray hmangin pulmonary hypoplasia emaw lung natna dang emaw a enfiah ang. X-ray hian lung lian leh te, a dinhmun a tarlang thei a ni.

Hei hi eng enkawlna nge ni?

Pulmonary Hypoplasia enkawl dan chu a chhan, a natna nasat dan leh naupai lai emaw, nau piang hnua hmuhchhuah a nih leh nih lohah a innghat a ni. Enkawlna tum ber chu naute dam khawchhuahna atana an mamawh oxygen pek leh an lungte a theih ang anga thanlenna tura puih hi a ni. I naute hi Pulmonary Hypoplasia neia piang a nih chuan an lung chu anmahni chauhva thawk thei tura an lo thanglian hma emaw, doctor-te’n enkawlna dang an pek theih hma emaw chuan thawk turin i puih a ngai dawn a ni.

Obtetrician-gynecologist emaw neonatologist emaw-in a hman dan thenkhat chu hetiang hi a ni:

• Amnioinfusion : Naupai laiin amniotic fluid a tlem chuan he procedure hian artificial in a infuse thin. Hei hian lung chunga pressure tihziaawmna leh thanlenna a pui thei bawk.
• Fetal surgery emaw nau piang hnua surgery emaw : Entirnan, CDH an tih natna a awm chuan siamthat nan surgery tih theih a ni. A chang chuan he surgery hi naute pum chhunga a la awm laiin tih a ni.
• Oxygen therapy : Naute hi nasal cannula emaw, hmai chunga mask dah emaw hmangin oxygen pek a ni.
• Mechanical ventilation : Hei hian ventilator chu machine nena thlunzawm a, artificial taka thawk chhuahna tura puih a ni. Hei hi thlipui chhungah tube dahin tih a ni.
• Extracorporeal Membrane Oxygenation (ECMO) : Hei hi a bik takin, a buaithlak hle. Machine hian thisenah oxygen a dah belh a, carbon dioxide a paih chhuak a, chutih rualin naute lung leh thinlung chu chawlh hahdamna a pe bawk. Enkawlna dang zawng zawng a hlawhchham chuan natna khirh tak takah hman a ni.

I naute chu Pulmonary Hypoplasia neia piang a nih chuan eng nge thleng ang?

I naute hi lung a lo piang lo a nih chuan neonatologist (nau piang thar chungchanga specialist doctor) leh specialist dangte team-in an enfiah ang. A natna nasat dan leh taksa peng dangte a nghawng dan azirin medical team-ah hian:

• Kidney lama mithiam (Nephrologist) te .
• Pulmonologist (thluak lam thiam) te chuan .
• Cardiothoracic surgeon (Cardiothoracic surgeon) te chuan an rilru a buai em em a.
• Gastroenterologist (digestive system lama mithiam) te chuan .

Naute ``(Pulmonary Hypoplasia)`` vei te hi enkawl an ni fo thinNeonatal intensive care unit (NICU)-ah chuan naute chu specialized care leh enkawl reng reng an ni. Hun rei tak chhung lung lama harsatna leh hriselna lama harsatna dang an nei fo thin. Hei hian thawkna lama natna hrik kai fo te, asthma ang chi natna te, leh hmasawnna tlai te a huam a ni. Mahse, Pulmonary Hypoplasia vei naute thenkhat chuan an kum upat angin natna khirh tak an nei lo thei a, an lung pawh a lo thang chhunzawm zel thei a, an natna lan chhuah dan pawh a tha thei hle.

Engtin nge he dinhmun hi kan nunpui theih ang?

Naute lung tha lo tak tak te hi an dam thei tih chu a dik a ni. Mahse mi zawng zawng dinhmun a inang lo. `(Pulmonary Hypoplasia)` hmanga dam khawchhuah theihna hi heng thilteah hian a innghat a ni:

• A natna a nasat dan. Eng chen nge lung hi a lo thanglian tawh.
• A chhan bulpui ber chu. `(Pulmonary Hypoplasia)` thlentu natna bulpui ber chu eng nge ni a, engtiang chiahin nge a nasat tih.
• Naupai lai emaw, nau piang hnu emawa hmuhchhuah a nih pawhin. A hmaa hmuhchhuah a nih chuan a chang chuan a hmaa inrawlh theih a ni.
• Complication dang a awm em?

A pum puiin Pulmonary Hypoplasia vanga thihna hi 55% aia tam niin an sawi. A tlangpuiin Pulmonary Hypoplasia natna khirh ber berte nen nun a harsa hle. Hetiang sawi hi a lungchhiatthlak hle a, mahse thudik hriat a pawimawh. Mahse, damdawi lam thiamna a lo thang chho zel a, chutiang naute tanpui dan tur chu tunlai hian nasa takin a lo tha chho ta a ni.

Hei hi veng turin eng emaw kan ti thei ang em?

Pulmonary Hypoplasia hi natna dang avanga lo awm a nih fo avangin ven theih dan pakhat chauh a awm lo. Mahse, naute pian huna hriselna lama harsatna awm thei tihziaawmna tur kawng tha ber chu naupai hrisel tak neih theihna tura i obstetrician thurawn zawm hi a ni. I in enkawl thei ang:

• I dinhmun rei tak, zunthlum leh thisen sang te chu enkawl rawh .
• I naupai chhung hian nitin doctor pan thin ang che. Chutiang chuan harsatna a awm a nih chuan a hmain i hrechhuak thei ang.
• Meizial zu leh zu in loh vek tur a ni. Chungte chuan naute thanlennaah direct negative impact a nei a ni.
• Tui tam tak in thin ang che. Ni khatah tui litre 2-3 tal in a pawimawh hle.
• Sexly transmitted infection (STI) leh natna hrik kai theih dang lakah inveng rawh.

I obstetrician leh gynecologist hnena check-up neih fo hian harsatna awm thei te chu a hmain a hriat theih nan a pui thei a ni. A châng chuan doctor-te chuan naupai laiin Pulmonary Hypoplasia awm chhan bulpui chu an enkawl thei bawk. Hei hian i naute chu lung lian lo neia piang lo turin a pui thei a ni.

A tawp berah chuan i sawi tur chu...

I naute hi Pulmonary Hypoplasia nei a piang a nih chuan doctor team pakhatin i kalna apiangah an awmpui ang che. Anni chuan i natna nasatzia te, i enkawl dân tûr te, leh nakin hun tûr chu an hrilhfiah ang. I naute enkawlna chungchangah – emaw, nangmah hriselna chungchangah emaw thutlukna dik tak i siam theih nan zawhna i neih apiang zawt hreh suh.

"A theih chuan i rintlak leh i hmangaih tak takte personal support group siam rawh. Chu chu i pasal, i nu, i pa, i unau leh i ṭhian ṭha ber berte ang mi tihna a ni. An thlawpna hi i hmaa harsatna lo thleng apiang hmachhawn turin chakna ropui tak a ni ang. Chak taka awm hi a pawimawh hle. Beiseina hi bansan suh.

He thu hi i tan a \angkai ngei kan beisei. Damdawi lam thurawn dil turin doctor thiam tak i zawt fo tih hre reng ang che. He thuziak hi a tlangpui chauh a ni.

` Pulmonary Hypoplasia, lung tha lo, nau piang thar, thawk lama harsatna, pianpui natna, NICU, nausen hriselna, naupai harsatna te