Lu na tak, mit hmuhna fiah lo, leh hriatna hloh nghal i neih chuan han ngaihtuah teh? Chûngte chu buaina inzawm lo pathum niin i ngai mai thei. Mahse vawiinah hian heng symptom pathumte hi a inzawm khawm vek a, mahse khawtlang nunah sawi hlawh lo tak, thil awm lo tak tak kan sawi a ni. Hei hi "Susac Syndrome" an ti a. He hming hi i tan chuan thil thar a ni mai thei. Mahse hei hi hriat chian a pawimawh hle.
A awlsam zawngin, Susac Syndrome hi eng nge ni?
Susac Syndrome hi keimahni taksa invenna system, immune system-in kan taksa ngeiin a rawn bei sual palh a. Hei hi autoimmune condition kan ti a. Sipai pakhatin ram pakhat a humhim tih han mitthla teh, a mite ngei pawh a bei sual a ni.
He natnaah hian kan taksa chakna (immune system) hian kan taksa hmun pawimawh tak tak pathum-a thisen kalna kawng te tak te te chu a target a. Chu hmun pathum chu:
1. Thluak
2. Retina (Retina) a awm
3. Beng chhung lam (Cochlea) .
Chutiang a lo thlen chuan heng thisen kalna kawng chhung lam chu a lo hring chhuak thin. Tui pipe a inkhar ang bawkin heng thisen kalna kawng kal tlanga tui luang chu a tlahniam a, a chang chuan a inkhar vek bawk. Chu chuan thluak, mit leh bengte mamawh oxygen leh nutrients a hloh phah a ni. Chutah chuan he natna lanchhuahna hi a lo lang tan ta a ni.
He natna lan chhuah dan berte chu engte nge ni?
Susac Syndrome-ah hian heng hmunpui pathum nena inzawm symptoms hi a inzawm emaw, a hranin emaw a lang thei. Mahse a tlangpuiin a hmun pathumte hi a nghawng vek a ni. Heng symptoms te hi eng nge ni tih i lo en ang u.
| A nghawng part | Symptoms awm thei te |
|---|---|
| 1. Thluak |
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| 2. Mit |
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| 3. Beng chhung lam |
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A pawimawh ber chu mi zawng zawng hian heng symptoms zawng zawng hi a rualin kan tawng vek lo. Mi thenkhat chuan heng symptoms hi vawi khat an nei a, chutah chuan an lo kir leh tawh ngai lo mai thei. Mi dangte chuan kum engemaw zat chu symptoms an nei thei bawk.
Engvangin nge hetiang hi a thlen a, tute nge hlauhawm ber?
Kan sawi tawh ang khan hei hi a chhan dik tak chu hmuhchhuah a la ni lo . Thil hriat awm chhun chu autoimmune condition a ni tih hi a ni. Hriselna atanga lo piang natna a ni lo . Chumi awmzia chu naupangte hian an nu leh pate hian an neih chuan an nei ang tih finfiahna a awm lo tihna a ni.
Mahse, thil engemaw tak chuan he natna vei hlauhawm tak takte hi a hriat theih a:
- Gender: Hmeichhia hi mipa aiin a let thum velin he natna hi an vei tam zawk.
- Kum: Heng natna lan chhuah dan hi kum 20 leh 40 inkar mite zingah a lang tan fo thin .
Doctor-te hian engtin nge hei hi an hmuh?
Susac Syndrome hi natna dang tam tak nena a lan chhuah dan a inang avangin hriat a harsa thei hle. Entirnan, natna lan chhuah dan chu Multiple Sclerosis (MS), stroke, leh thluak natna (encephalitis) te nen a inang hle. Chuvang chuan Doctor chuan natna danglam tak niin a ngai sual mai thei.
Chuvangin, diagnosis dik tak siam turin special test engemawzat an nei thin.
- Taksa enfiahna
- Neurological exam a ni
- Mit lam enfiahna (Ophthalmological exam) a ni
Tin, heng special test te hi natna finfiah nan a pawimawh hle a ni.
| Fiahna | Hemi kawngah hian eng nge i zawn? |
|---|---|
| MRI scan (Magnetic Resonance Imaging) hmanga tihchhuah a ni. | Hei hian thluak thlalak chipchiar tak a la thin. Susac Syndrome vei tan chuan thluak dinglam leh veilam hemisphere inzawmkhawmtu thluak peng pakhat, corpus callosum-ah hian "snowballs" ang maia hliam dum hmuh tur a awm. Hei hi natna chhinchhiahna ziarang a ni. |
| Fluorescein angiography hmanga enfiah a ni | Hei hi mit retina-a thisen kalna kawngte enfiahna a ni. Hetiang tih danah hian kut chhunga thisen kalna (vein) pakhatah special dye inject a ni a, mit chhunga thisen kalna kawngte thlalak lak a ni. Hei hian thisen kalna kawng a inkhar em tih chiang takin a hmu thei a ni. |
| Audiogram hmanga siam a ni | Hei hi hriatna tehna test a ni. Susac Syndrome vei te hian hriat harsa an nei thei a, a bik takin aw hniam tak tak te chu an hrethiam lo thei a, tawng pawh an hrethiam lo thei bawk. He test hian hei hi a hre thei a ni. |
Eng nge a enkawl dan?
He natna enkawlna tum ber chu kan taksa hriselna (immune system) control hi a ni a, chu chu a thawk tha lo hle a ni. Chu chu a hnathawh tihtawp nan a ni. Hemi atana damdawi pek te hi immunosuppressants kan ti thin .
Heng enkawlnate hi hun rei tak chhung ei a ngai mai thei. Damdawi hman tlanglawn tak tak thenkhat chu:
- Corticosteroids - e.g. prednisone a ni
- Immunoglobulin (IVIG) hmanga thisen kal tlanga hman thin.
- Mycophenolate a ni
- Azathioprine a ni
- Cyclophosphamide hmanga siam a ni
- Rituximab a ni
Heng damdawi te hi pek dan hrang hrang a awm a. Ṭhenkhat chu pill angin an pe a, ṭhenkhat chu injection angin an pe a, damdawi ṭhenkhat chu thisenah (IV) saline solution angin an pe bawk.
Pawimawh tak: He damdawi hi doctor-in a tih ang chiah, course chhung zawnga ei a pawimawh hle. Enkawlna i skip emaw, nangmah chauha i chawlhsan emaw chuan i natna lan chhuah dan a lo lang leh theihna chance a sang hle.
Damdawi zawng zawng ang bawkin he damdawi hian side effect a nei thei a ni. Chuvangin enkawlna i tan hmain i doctor nen zalen takin sawiho rawh. Side effect a awm chuan hriattir nghal tur a ni.
Engtin nge nakin hun atan beiseina kan neih theih ang?
Susac Syndrome tih hming hi hlauhawm tak angin lang mahse, he natna hi enkawlna tha tak tak a awm . A bik takin natna hi hriatchhuah leh enkawl hmasak a nih chuan a rah chhuah a tha hle. Enkawl hmasak hian thluak, mit leh beng chhiatna nghet tak a veng thei a ni.
Mahse, enkawlna a tlai chuan a chang chuan mit leh hriatna chu a bo vek thei a ni. Mahse, hei hi a tlem hle.
He natna hi nunna atana hlauhawm a ni tlem hle. Chu chu dam rei zawng a ti tawi lo tihna a ni. Mahse, nitin nunphung a nghawng thei a ni. Tun hmaa thil tha tak tak, mit leh hriatna ang chi thilte a inthlak a, chubakah i ngaihtuahna leh hriatrengna a inthlak danglam chuan rilru lamah nghawng nasa tak a nei thei a ni. Chuvangin, hetiang natna hmuhchhuah hnua mental health counselor nena inbiakna hian mi tam tak tan hahdamna a thlen bawk.
Engtikah nge Doctor ka hmuh ang?
Nangmah emaw, i hriat mi tu emaw chuan a ruala a hnuaia inthlâk danglamna pakhat emaw, a aia tam emaw i tawn chuan, doctor pan hmasa phawt ang che .
- Mit hmuh dan inthlak danglam nghal (black spots, curtain-in a khuh ang maia inhriatna).
- Hriatna hloh nghal , luak chhuak, emaw beng ri bengchheng.
- Ngaihtuahna emaw hriatreng harsa (thluak hnathawh dan inthlak danglamna).
- Thiltih dan emaw mize emaw sawifiah theih loha inthlak danglamna .
- Heng symptoms te hian i nitin nun a tibuai a nih chuan .
I doctor chuan heng natna lan chhuah chhan dik tak hi a hre thei a, a tul anga enkawlna a pe thei che a, chu chuan hun rei tak chhunga harsatna awm thei tur venna kawngah a pui thei a ni.
Take-Home Thuchah a ni
- Susac Syndrome hi natna hmuh tur awm lo tak a ni a, keimahni taksa chakna (immune system) hian thluak, mit leh beng chhunga thisen kalna kawng te tak te te chu a bei thin a ni.
- He natna lan chhuah dan ber chu a lan chhuah dan pathum a ni a, chungte chu thluak hnathawhna lama harsatna (lu na, buai), mit lama harsatna, leh hriatna lama harsatna (lu na, hriatna hloh) te an ni.
- Hei hi thlahtu natna a ni lo va, hmeichhiaah a tam zawk.
- Symptoms a lan veleh doctor pan a, a rang lama diagnosis neih hian chhiatna awm reng tur a veng thei a ni.
- Enkawlnaah hian immune system control thei damdawi (immunosuppressants) te a tel a, doctor thupek zawm a pawimawh hle.
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