Nu ni tur i nih angin i naute chu hrisel taka khawvela lo kal chu i nghakhlel hle mai thei. Mahse, a châng chuan beisei loh hrisêlna lama harsatna a awm thei a ni. Vawiin hian piansualna na tak, mi tam takin an la hriat ngai loh chungchang kan sawi dawn a ni. Hei hi Anencephaly an ti a. Hei hi hriat chian a pawimawh hle.
Anencephaly hi eng nge ni tak tak?
A awlsam zawngin sawi ila, anencephaly chu thluak leh luruh hmun thenkhatte a lo thanglian dan tur dik tak nei lovin naute piang a ni. Hei hi a tlem hle a, a na hle bawk.
Hei hi tlem tal i hrethiam zawk ang u. I naupai lai hian kar hmasa lamah chuan i naute thluak leh ruhro chu cell flat disc angin a lo piang tan a. Leaf flat tak chu tube-a rolling ang maiin ngaihtuah la, he cell disc hi zawi zawiin a inzawm khawm a, tube ang maia siam a ni. Hei hi neural tube kan ti a . He neural tube hi naupai atanga ni 28-32 chhungin khar vek tur a ni.
Mahse, eng emaw chhan vanga he neural tube hi a khar kim lo a nih chuan kawngkhar te tak te a awm reng a ni. Hei hi neural tube defect kan tih chu a ni . Anencephaly hi chutiang neural tube defect pakhat a ni. Chutiang a nih chuan neural tube chu luruh bul lamah a inhawng reng a ni. Chuvang chuan thluak hmalam leh chunglam leh a kaihhnawih luruh te chu a lo thang lian lo.
Eng thilin nge anencephaly thlen thei?
Hei hi a chhan pakhat chauh hriat chian a harsa hle. Thil hrang hrang inzawmkhawm chuan hei hi a thlen thei a ni. Genetic factors, nutritional deficiency, leh nuin naupai laia thil engemaw a tawn thin te hi a pawimawh ber zinga mi a ni.
A hnuaia table-ah hian heng risk factors te hi i sawifiah belh leh ang u.
| Risk factor a ni | Hrilhfiahna |
|---|---|
| Folic Acid tlakchhamna a awm | A chhan ber chu naupai hma leh naupai laiin folic acid ei tlem vang a ni. He vitamin hi naute neural tube thanna atan a pawimawh hle. |
| Damdawi thenkhat | Damdawi thenkhat, rilru natna, bipolar disorder, leh migraine enkawlna atana hman thin, Phenytoin, Carbamazepine, leh Valproic acid , te hian a hlauhawmna a tipung thei a ni. |
| Zunthlum thunun theih loh | Nuin zunthlum a vei a, naupai laiin a thisen sugar level mumal taka control a nih loh chuan naute thanlenna kawngah nghawng tha lo tak a nei thei a ni. |
| Taksa lumna sang | Naupai kar tir lamah (neural tube a lo insiam lai hian) khawsik sang tak neih emaw, tui lum tak tak, hot tub emaw sauna emaw-a awm chu a hlauhawm thei hle. |
| Thau lutuk | Nu naupai tam lutuk hi naupai tirh lamah naute thanna tichhe theitu a ni. |
| Genetic dinhmun (genetic) a awm | Anencephaly hi genetic condition thenkhat vang pawh a ni thei a, chu chu Trisomy 18. Mahse, hengte hi rochun atanga lo chhuak a ni lo va, random genetic changes a ni zawk. |
| Opioid ruihhlo hman dan | Zirna thenkhatah chuan nu naupai thla hnih hmasa berah opioid painkillers Codeine, Tramadol, leh Morphine te hmangtute fate chu neural tube defects an nei tam zawk tih hmuhchhuah a ni. |
Naupai lai hian he natna hi hriat theih a ni em?
Ni e, a dik tak zet. I nau neih hmaa i enkawlna kawngah hian i doctor chuan heng neural tube chhiatna chi hrang hrangte enfiah nan test eng emaw zat a nei ang.
- Ultrasound Scan hmanga tihchhuah a ni:Hei hi a hmanraw ber a ni. Scan hmang hian doctor chuan naute lu ruh, thluak leh ruhro insiam dan a hmu thei a ni. Anencephaly hi scan hmangin chiang takin a hriat theih tlangpui.
- Quad Marker Screen Blood Test: Hei hi nu thisen test a ni. Nu thisenah Alpha-fetoprotein (AFP) an tih chemical level a teh a ni. AFP hi naute thin (liver) atanga siam a ni. Nu thisena AFP level chu a danglam bik hle a nih chuan naute hian neural tube defect (anencephaly ang chi) a nei thei tih a tilang thei a ni.
- Fetal MRI scan: Ultrasound scan atanga thil chiang lo a awm chuan MRI scan hmangin naute thluak leh ruhro thlalak chiang zawk, chipchiar zawk hmuh theih a ni
- Amniocentesis: He test-ah hian doctor chuan naute chhehvel amniotic fluid sample tlemte lak nan needle nalh tak tak a hmang a. He fluid hi enzyme pakhat AFP leh acetylcholinesterase level sang tak a awm leh awm loh test a ni. Hengte hi a sang lutuk hi neural tube defect a nihna chhinchhiahna a ni bawk.
Hei hi enkawl dan tur a awm em?
Hei hi he thupui lungchhiatthlak ber a ni.
Vanduaithlak takin anencephaly hi enkawlna leh damdawi a awm lo.
Hei hi tuar harsa tak a ni. Neural tube defect nei naupai tam tak chu nau paiah a tawp thin. Anencephaly vei naute thenkhat chu thi anga piang an ni. Naute chu engtin emaw takin nung chungin a piang a nih pawhin a dam chhung chu darkar engemaw zat emaw, ni engemaw zat emaw chauh a ni.
Hetiang dinhmun hi hriatchhuah a nih chuan i doctor leh damdawi ina thawktute chuan nang leh i chhungte chu emotional support tul tak an pe ang che. Naute a pian veleh chuan chu hun rei lote chhunga naute nena hun tam thei ang ber hman theihna tur thil tul an siamsak ang.
A hlauhawmna tihziaawmna turin eng nge kan tih theih ang?
Anencephaly hi 100% vela ven theih a nih loh laiin, a hlauhawmna nasa taka tihtlem nan thil engemaw zat kan tih theih a awm. Hei hi chhungkaw din tum hmeichhiate tan a pawimawh hle.
- Folic Acid: Hei hi a pawimawh ber a ni. Naute neih i tum a nih chuan , naupai hma thla 3 tal nitin folic acid microgram 400 (400 mcg) ei tan rawh.Naupai hnu thla 3 hmasa berah hetiang hian i ei chhunzawm tur a ni. I doctor chuan i mamawh zat dik tak chu a rawn rawt ang che.
- Damdawi chungchangah fimkhur rawh: Naute neih i tum a nih chuan tuna i damdawi ei mek zawng zawng (a bik takin epilepsy emaw rilru lam natna ang chi natna atan) i doctor nen sawiho rawh. A tul chuan a dang him zawk a rawt thei bawk.
- Opioid painkillers ei loh tur: Naupai emaw, naupai emaw i tih chuan i doctor thurawn tel lova opioid painkiller ei loh tur a ni.
- I taksa lumna control: Naupai lai hian hot tub leh sauna-a kal loh tur. Khawsik i neih chuan him taka khawsik tihziaawm dan tur doctor rawn la.
- Taksa rihna hrisel vawng reng rawh: Naute i neih hma pawhin taksa rihna hrisel neih tum ang che.
- Diabetes enkawl dan: Zunthlum i neih chuan i naupai hma leh i naupai chhung zawnga enkawl dan tha ber tur i doctor nen sawiho rawh.
Take-Home Thuchah a ni
- Anencephaly hi nausen thluak leh luruh a lo thanglian tha tawk lo, nausen piansualna pawi tak, thihna thlen thei a ni.
- Hetiang dinhmun hi enkawlna a awm lo.
- Nau neih i tum a nih chuan naupai hma thla engemaw zat folic acid ei a pawimawh hle. Hei hian neural tube defects awm theihna chu nasa takin a tihziaawm thei a ni.
- Nau i pai hmain i doctor nen i damdawi ei tur eng pawh leh zunthlum ang chi damdawi lam dinhmun te sawipui hmasa phawt ang che.
- Naupai laiin scan hmangin heng natna te hi a hmain a hriat theih a ni. Chuvangin clinic hi skip ngai suh.











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