Kua whakaaro koe he aha te uaua toto nui rawa atu, nui rawa atu hoki o roto i tō tātou tinana? Ko te aorta, te aorta rānei . He rite ki te ara matua o roto i tō tātou tinana. E rere ana mai i te ngākau ki te puku. Koinei te mea e kawe ana i te toto ma, whai hāora e pupuhihia ana e te ngākau ki te tinana katoa. Nō reira, ki te he tetahi mea ki tēnei aorta, ka pā ki te tinana katoa. Koinei te rōpū mate e pā ana ki te aorta, e kiia nei e tātou ko te Aortopathy .

He aha te Aortopathy? Kia mārama tātou.

Ki te kī māmā noa, ko te aortopathy he kohinga o ngā āhuatanga e ngoikore ai, e kino ai rānei ngā pakitara o tō aorta. Whakaarohia, ka pupuhi tika tō ngākau i te toto ki roto i tēnei aorta i ia wā e pā ana. Nō reira, me tino kaha ēnei pakitara uaua kia tu atu ai i taua pēhanga. Engari, he aha te mea ka tupu mēnā ka ngoikore ēnei pakitara? Ka taea e rātou te pakaru, te wehe rānei. He tino morearea tēnei. Ka rerekē te pānga o te momo aortopathy kei a koe ki te aorta.

He aha ngā momo matua o te aortopathy?

He rerekē ngā momo aortopathy. Me kōrero tātou mō ētahi o ngā mea matua.

Te Aneurysm Aorta Puku (AAA)

Koinei te wā ka ngoikore te pakitara o tō aorta, e rere ana i roto i tō puku, ka pupuhi mai pērā i te poihau. Ka kiia hoki tēnei he aneurysm . Ko te nuinga o te wā ka pā tēnei āhuatanga ki te hunga neke atu i te 65 tau te pakeke, ki te hunga kaipaipa, ki te hunga rānei he take mōrearea mō te mate ngakau. He mea morearea tēnei "(AAA)" nā te mea ka pakaru ohorere, ka puta he toto e morearea ai te ora.

Te Aneurysm Aorta o te Uma (TAA)

He ngoikore, he whānui rānei tēnei o te wāhanga o te aorta e rere ana i roto i te uma. Kāore te mate `(TAA)` i te tino noa pērā i te `(AAA)`. Heoi, he nui ake te tūponotanga ka pā mai i roto i ngā whānau, arā, ka taea te tuku iho i roto i ngā whakatipuranga. Pērā i te `(AAA)`, ko te mōrearea matua o te `(TAA)` ko tōna pakaru pea.

Ko te āhua morearea e kiia nei ko te Aortic Dissection

He ahua uaua tēnei. Ko te mea e tupu ana i konei ko te pakaru o te paparanga o roto o te pakitara o te aorta. Ka puta tēnei i te wāhi e ngoikore ana te pakitara o te aorta. I ētahi wā, e ai ki te kōrero i mua ake nei, ka taea te tupu i te wāhi he aneurysm. Heoi, ka taea hoki te tupu me te kore he aneurysm. E rua ngā momo matua o tēnei. Ko te momo A he pakaru i te wāhanga o te aorta e tata ana ki te ngākau (arā, i mua i te āwhata aorta). Ko te momo B he pakaru i muri i te āwhata aorta, i roto i te uma, i te puku rānei. Ko tēnei "(Aortic Dissection)" he mate morearea e hiahia ana kia kitea wawetia me te rongoatia .

Me ako tātou mō te Aortopathy Familial?

Ko te Familial Aortopathy he mate ira e pā ana ki ngā whānau.Ko te aortopathy whānau he mate o ngā uaua nui e pā ana ki te hītori whānau o te mate aorta. He rerekētanga ira tō ēnei tāngata e nui ake ai te tūponotanga ka pāngia rātou e te mate aorta. I te nuinga o te wā, ka pā tēnei aortopathy tuku iho ki ngā uaua nui i roto i te uma, inā koa te pakiaka aorta, te aorta piki rānei.

E rua ngā wāhanga matua o tēnei hoki:

He aha te Aortopathy Syndromic?

Ka karangatia hoki tēnei e mātou ko te `(Syndromic hereditary thoracic aortic disease)`. He māmā noa iho, he mate ira tōu e pā ana ki tō aorta, ā, ka puta ai ētahi atu huringa i roto i tō tinana. Ko ētahi o ngā mate e arahi ana ki te mate aorta ko:

• Te mate Loeys-Dietz
• Te mate Marfan
• 'Te mate Turner'
• ``Te mate Ehlers-Danlos toto toto`'

Kia tūpato hoki tātou ki te Aortopathy Kore-syndromic

Ka kiia tēnei ko te "mate aortic thoracic tuku iho kāore i te mate pūkahukahu." I konei, kāore he mate ira motuhake kei a koe, engari he momo ira kei a koe e whakanui ana i tō tupono ki te whakawhanake i te mate aortic. Neke atu i te 50 ngā whakarerekētanga ira kua honoa e ngā kaipūtaiao ki tēnei aortopathy. Ko ētahi o ngā ira kua tino honoa ko:

• `ACTA2` (Koinei te mea e kitea whānuitia ana)
• `FOXE3`
• `LOX`
• `MYH11`
• `MYLK`

Kia maumahara, mēnā kua pāngia tētahi o tō whānau e te aneurysm, e te wetewete rānei o te aorta, kōrero ki tō tākuta mō ngā whakamātautau ira . Mēnā kua tāpaetia koe he mate aortic, me whai whakamātautau ira pea koe kia kitea ai mēnā kei te mōrearea hoki ētahi atu mema o tō whānau.

He aha te Aortopathy Bicuspid?

Ka kiia hoki tēnei ko te `(Bicuspid valve-associated aortopathy)`. Ko te tikanga, i tua atu i te aortic stenosis, he mate manawa whānau anō tōu e kiia nei ko te Bicuspid Aortic Valve (BAV) . He mate manawa whānau noa tēnei `(BAV)`, e pā ana ki te tata ki te kotahi i roto i te 50 pēpi.

Nā, ko tō takirere aorta tētahi o ngā "kūaha" e whā e whakahaere ana i te rere o te toto i roto i tō ngākau. Mā tēnei e whakahaere te rere o te toto mai i te ventricle maui, te ruma papu matua o te ngākau, ki roto i te aorta. E toru ngā rau o te takirere aorta hauora e tuwhera ana, e kati ana hoki hei whakahaere i te rere o te toto. Heoi, e rua noa ngā rau o te takirere aorta bicuspid. Kāore pea tēnei e puta he raruraru nui mō tētahi wā, engari ka taea e ia te puta he raruraru i roto i te wā.

Mena he bicuspid aortopathy tōu, e rua ngā rau o tō takirere aortic, ā, he whānui ake tō aorta i te mea noa (kua whānui). Mō te hunga he bicuspid aorta, ka puta te whānui i te nuinga o te wā i roto i te pakiaka aortic, i te ascending aorta rānei. Koinei ngā wāhanga o te aorta e tata ana ki te ngākau.

Ngā raruraru o te Bicuspid Aortopathy

Kāore pea he raruraru nui te aorta kua paku nui haere. Heoi, ki te nui rawa, ka puta he aneurysm. Ka pēhia e tēnei aneurysm ngā pakitara o te aorta, ka pakaru, ka motuhia rānei. Ko te hunga whai bicuspid aortopathy e iwa ngā wā ka nui ake te tūponotanga ka pāngia rātou e te aortic dissection i te hunga kāore i te mate.

He pēhea te noa o tēnei aortopathy?

Ka rerekē i runga i te momo mate. Ko te aneurysm aortic (AAA) te momo aortopathy tino noa, ā, koinei hoki te momo aneurysm tino noa. I te United States anake, tata ki te 200,000 ngā tāngata e kitea ana he AAA i ia tau. I te ao katoa, tata ki te 47,000 ngā tāngata e mate ana i ia tau mai i ngā momo aortopathy katoa.

He aha ngā tohu o te Aortopathy? Kaua e warewarehia ēnei!

Kāore he tohu o te mate pukupuku o te ngākau. Koinei te mea tino morearea. Koia te mea nui kia tirotirohia e te rata mēnā he āhuatanga mōrearea tōu.

Tērā ētahi tohu ka puta mai ina tata te pakaru o te aneurysm. Ko ngā tohu whakatūpato ka puta mai i mua i te pakaru ko:

• Kei te mākona tonu ahakoa i muri i te kai iti.
• Te mamae tonu i te tuara, i te papa, i te hope, i te waewae, i te puku rānei.
• Te rongo i te pao o te ngakau i te rohe o te puku.
• Te uaua ki te manawa.

He āhuatanga ohorere e morearea ana te pakaru o te aneurysm me te tapahi o te aorta! Mena kei a koe ēnei tohu e whai ake nei , waea atu ki te 1990 tonu mō te waka tūroro, haere rānei ki te rūma ohorere o te hōhipera tata:

• Te putanga ohorere mai o te mamae nui o te puku.
• He mamae ohorere, koi, nui hoki i te uma, i te tuara rānei o runga. Ka rite ki te mea e haehaetia ana i roto, ki te mea e werohia ana e te maripi, ki te mea rānei e werohia ana.
• Kiri piri, werawera nui rānei.
• Pōhēhētanga.
• Pōuriuri, ngoikore rānei.
• Ka piki ake te tere o te manawa.
• Whakapairuaki me te ruaki.
• Te uaua ki te manawa.
• Te uaua ki te kōrero.
• Te ngaronga o te tirohanga.
• Te ngoikore, te ngoikore rānei i tetahi taha o te tinana.

He aha ngā take o te Aortopathy?

He maha ngā take o te aortopathy. Ko ētahi ka kitea i te whānautanga, ko ētahi ka puta i muri mai i te ao.

• Ira: E ai ki te kōrero i mua ake nei, ka taea e ngā mate ira me ngā rerekētanga ira te whakaputa i te mate aorta. He maha ngā wā ka tukuna iho te aortopathy whānau i runga i te tikanga autosomal dominant. Ko te tikanga tēnei, ki te mea kei tētahi o ngā mātua te ira, e 50% te tūponotanga ka tukuna iho e tā rātou tamaiti.
• Mate ngākau whānau: E pā ana ēnei ki te aortopathy. Ehara i te mea ko te aortopathy te take o te mate ngākau whānau, engari he maha ngā wā ka kitea ngātahitia ēnei e rua. Tauira: 'Bicuspid aortic valve', 'Coarctation of the aorta', 'Pulmonary atresia with ventricular septal defect (VSD)', 'Tetralogy of Fallot', 'd-Transposition of the great arteries', 'Truncus arteriosus'. Ka taea hoki te puta te aortopathy i muri i ngā pokanga mō ētahi mate ngākau whānau. Tauira: 'Arterial switch operation (ASO)', 'Atrial baffle (Mustard/Senning) operation', 'The staged Norwood, Glenn and Fontan surgeries'.
• Atherosclerosis: Koinei te puranga o ngā putunga ngako (pēka) i roto i ngā uaua, ka āta whakawhāiti haere i a rātou. Ko te Atherosclerosis o te aorta te tino take o te aortopathy i muri mai.

Ko wai kei te nui ake te mōrearea ki te whakawhanake i te aortopathy?

He maha ngā āhuatanga mōrearea ka whai wāhi ki te whanaketanga o te aortopathy:

• Te momi hikareti me te whakamahi tupeka: He take nui tēnei mō te mōrearea . Ko te nuinga o ngā aneurysms ka puta i roto i te hunga momi hikareti, i te hunga rānei kua momi hikareti i mua.
• Te toto toto tiketike (hypertension): Ka taea e tēnei āhuatanga te ngoikore i ngā pakitara o ngā uaua toto i roto i te wā.
• Te koroheketanga: Ka piki ake te mōrearea o te whakawhanake i te aneurysm i muri i te 65 tau.
• Hītori whānau: Mena kua pāngia tētahi mema o te whānau e te aneurysm, e te tapahi rānei, kua nui ake tō tūponotanga.
• Te cholesterol teitei, te triglycerides teitei rānei: Mā te pikinga o ngā taumata ngako (lipids) i roto i te toto ka nui ake te mōrearea o ngā putunga ngako i roto i ngā uaua.
• Ngā mate pūnaha ārai mate: Ka taea e ngā mate pūnaha ārai mate pēnei i te 'Giant cell arteritis' me te 'Takayasu arteritis' te whakamumura i ngā pakitara o ngā uaua nui, ka ngoikore ai.
• Mate urutā: He onge noa iho, ka taea e ngā mate urutā pēnei i te syphilis, ngā mate huakita rānei o te pakitara o ngā uaua nui, te ngoikore.

Me pēhea te tautuhi i te aortopathy?

He maha ngā wā kāore he tohu, he tohu whakatūpato rānei o ngā aneurysm me ngā tapahi, nō reira kāore pea e kitea kia puta rā anō ngā raruraru nui. Heoi, ki te mea he āhuatanga mōrearea tōu, ka tirohia e tō tākuta tō aorta mō ngā tohu o te mate.

Ko ngā tikanga e whakamahia ana hei tautuhi i te aortopathy ko:

• Whakamātautau tinana: Ka tirohia e tō tākuta ngā āhuatanga katoa o tō hauora. Ka arotakehia hoki e ia ō tūponotanga mō te mate manawa. Ka uru atu ki tēnei te pātai mō tō hītori hauora, ngā āhuatanga o te noho (pēnei i te momi hikareti), me te hītori whānau.
• Whakamātautau ira: Ka tūtohu pea tō tākuta kia whakamātauria he whakamātautau ira. Mā tēnei ka kitea mēnā he whakarerekētanga ira kei a koe e pā ana ki te mate uaua o te ngakau.
• Ngā whakamātautau whakaahua: Ka tonoa pea e tō tākuta ēnei whakamātautau hei tirotiro i te rahi me te hauora o tō aorta. Ka inehia e ēnei whakamātautau te whānui o tō aorta, me te kite mēnā he whānui ake i te mea noa.

He aha ngā whakamātautau e whakamahia ana hei tautuhi i te Aortopathy?

• ``Matawai Tomography Rorohiko (CT)`'
• ``Whakaahua aukume aukume (MRI)''
• He matawai i te ngākau mā te whakamahi i te echocardiogram transthoracic (TTE)
• Ko te echocardiogram transesophageal (TEE) (he matawai ngākau mā roto i te esophagus)
• Te tirotiro i te puku mā te whakamahi i te ultrasound (he tirotiro i te puku mā te whakamahi i te ultrasound)

He painga me he ngoikoretanga o ia whakamātautau. Mā tō tākuta e whakamārama ko tēhea whakamātautau e hiahiatia ana e koe, me te take hoki. Tērā pea ka whakamahia e tō tākuta tētahi, neke atu rānei o ēnei whakamātautau hei aroturuki i tō aorta i roto i te wā. Me tango pea ēnei whakaahua i ngā wā auau (hei tauira, kotahi i te tau). Ko te auau o te wā e hiahiatia ana ēnei whakamātautau ka whakawhirinaki ki ō āhuatanga mōrearea me te hauora o tō aorta i tēnei wā.

He aha ngā maimoatanga mō te Aortopathy?

Ko te maimoatanga e whakawhirinaki ana ki tō āhua me tō mōrearea o ngā raruraru. Ka whakaritea e tō tākuta tō maimoatanga kia rite ki tō āhua me ō hiahia. Kei roto i ngā kōwhiringa maimoatanga ko ngā huringa āhua noho, ngā rongoā, ngā tikanga hauora, me te pokanga.

Me tīmata tātou ki ngā huringa o te āhua noho!

Mā ngā whakarerekētanga o te āhua noho ka āwhina i te whakaroa i te whanaketanga o ētahi momo mate aortic, me te whakaiti i te tūponotanga o te pahūtanga o te aneurysm. Mena he mate aortic tōu, he mea nui kia mahia ēnei e whai ake nei:

• Āta karohia te waipiro.
• Āta karohia te momi hikareti me ngā hua tupeka katoa.
• Kai i ngā kai hauora mō te ngākau.
• Whakakorikori tinana i ngā wā katoa (kia rite ki ngā tohutohu a tō tākuta).
• Kia mau tonu tō taumaha hauora.
• Whakahaerehia ngā āhuatanga mōrearea o te mate ngakau pērā i te toto toto tiketike me te cholesterol tiketike.

Mena e tika ana, kei reira anō ngā rongoā pēnei.

Tērā pea ka tohua e tō tākuta he rongoā hei āwhina i te whakaheke i tō toto toto. Ka whakaitihia e ngā rongoā toto toto te pēhanga o te toto ki ngā pakitara o ō uaua. Ka taea e tēnei te whakaiti i te mōrearea o te pakaru, te tapahi rānei o te aneurysm o te uaua nui. Ko ngā momo rongoā ka taea e koe te tango ko:

• ``Ngā aukati whākōkī tahuri angiotensin (ACE)''
• ``Ngā aukati i ngā kaiwhakawhiwhi angiotensin (ARB)''
• Ngā 'Pēta-aukati'
• 'Ngā aukati hongere konupūmā'
• Ngā rongoā diuretic (ngā rongoā e nui ai te mimi)

Ngā pokanga me ētahi atu tikanga hauora

Me hiahia ētahi tāngata ki te rongoā, ki te pokanga rānei mō te aortopathy. Kei roto i ēnei ko:

• Pokanga Aneurysm (pokanga tuwhera tuku iho)
• Te pokanga whakakapinga pakiaka aorta
• Te whakatikatika i te aneurysm endovascular (EVAR) - He maimoatanga tēnei e whakauru ana i tētahi ngongo mā roto i tētahi tapahi iti.
• Te whakatikatika i te aneurysm endovascular o te uma (TEVAR) - He maimoatanga ōrite anō hoki tēnei mō te uaua o te uma.

Me aha tātou hei whakaiti i te mōrearea o te aortopathy?

Ka taea e koe te whakaiti i tō tupono ki te pāngia e te aortopathy mā te whai i tētahi momo oranga hauora mō te ngākau. Anei ētahi tohutohu:

• Āraia ngā raau taero: Kāore te tupeka, ngā raau taero, me te waipiro e pai mō tō ngākau. Inaa, ka taea e rātou te kino i tō ngākau me ō uaua toto. Kati rawa te kai hikareti me ngā raau taero. Mō te waipiro, kia mōhio koe he aha te 'inu' me te whakawhāiti i te nui. E kī ana ngā tākuta kia kaua e neke atu i te kotahi 'inu' i te rā, ā, kia kaua e neke atu i te rua 'inu' i te rā mō ngā tāne.
• Kai i tētahi kai hauora mō te ngākau: Kei roto i tēnei ko te kai i ngā kai he iti te ngako kukū, te ngako whakawhiti, te konutai (tote), me te huka. Whakaitihia ngā warowaihā kua whakatikatikaina (pēnei i te taro mā) me te kai i ngā witi katoa (pēnei i te taro witi katoa, te raihi parauri). Kia mōhio hoki ki te pānga o te kai totika ki ō taumata cholesterol.
• Korikori Tinana: Kāore he tikanga korikori tinana kotahi e pai ana mō te katoa. Me mahi i tāu e pai ai. Me whai hoki i ngā tohutohu a tō tākuta mō te korikori tinana e haumaru ana mōu. Ko te tikanga, e taunaki ana ngā tākuta kia 150 meneti te roa o te korikori tinana kaha-waenga ia wiki. Ka uru atu pea ki tēnei ko te hikoi tere, te eke pahikara, te kaukau rānei.
• Whakahaerehia te ahotea: Ehara i te mea ngāwari pērā i te whakaaro. Engari he mea nui kia ngana ki te ako i ngā huarahi hou hei āwhina i a koe ki te whakatau i te ahotea i roto i tō oranga o ia rā. Me kōrero hoki ki tō whānau me ō hoa mō ngā tikanga e whai hua ana mō rātou.

He aha te tirohanga mō te tangata whai Aortopathy? (Tirohanga)

Ko tō tākuta te tangata pai hei pātai atu mō tō heke mai. Ka whakaarohia e ia ngā āhuatanga maha, hei tauira:

• Tō āhua hauora motuhake.
• Te tere o te haere whakamua o tō mate.
• Tō tau me tō ira tangata.
• Ngā āhuatanga mōrearea o te mate ngakau.
• Te hītori hauora o tō whānau.
• Tō hītori hauora katoa.

Kōrero ki tō tākuta mō ngā mea ka tumanakohia mō ngā rā kei te heke mai.

Mena he Aortopathy tōku, me pēhea taku tiaki i a au anō?

Mā tō tākuta koe e hoatu he aratohu mō te tiaki i a koe anō. Me whai i aua aratohu kia tika, ā, pātai atu ki tō tākuta mēnā he pātai āu. Me mahi e koe ēnei e whai ake nei:

• Āta karohia ngā mahi whakakori tinana taumaha, ngā hākinakina pā rānei.
• Whakaitihia, kati rawatia rānei te inu waipiro.
• Hurihia tō kai.
• Kati te momi hikareti, te whakamahi rānei i ngā hua tupeka.
• Tangohia tāu rongoā kia rite ki te mea i whakaritea.

Te Hapūtanga me te Aortopathy

Ka taea e te hāputanga te mōrearea mēnā he mate uaua ngakau tōu. Kōrero ki tō tākuta i mua i tō whakamahere kia hāpu ai, kia mōhio ai koe he haumaru mōu. Tērā pea me tiaki motuhake koe i te wā e hāpu ana (pēnei i ngā whakamātautau whakaahua auau) hei whakaiti i te tūponotanga o ngā raruraru. Āta karohia ngā rongoā kāore e haumaru i te wā e hāpu ana. Tērā pea me whakarerekē e tō tākuta ō rongoā.

Kia pēhea te wā me toro atu ahau ki te tākuta?

Tirohia tō tākuta mō ngā tirotiro ā-tau, me haere hoki ki ngā wā tirotiro katoa. Mā tō tākuta koe e kī atu ki a koe te auau o tō haerenga mai mō ngā tirotiro.

Mena i kitea he mate manawa whānau tōu i a koe e tamariki ana, tera pea he tākuta ngakau tamariki tōu i tiaki i tō āhua. Engari, i muri i tō ekenga ki te 18 tau, kāore pea koe i kitea he tohunga hou. E whakaatu ana ngā rangahau he maha ngā tāngata ka pōhēhē ina neke atu rātou i te tiaki tamariki ki te tiaki pakeke. Mena i rongoatia koe mō te mate manawa whānau i a koe e tamariki ana, he mea nui kia haere tonu te mahi tahi me te tākuta ngakau i a koe e pakeke ana. He pono tēnei ahakoa kāore koe e kite i tētahi raruraru. Ma tō tākuta ngakau koe e tohutohu mō tō mōrearea ki te aortopathy me ētahi atu āhuatanga i a koe e pakeke haere ana.

Hei whakamutunga, ko ngā mea tino nui hei maumahara (Karere hei tango ki te kāinga)

He mate kino te Aortopathy, ā, ka mate pea koe mēnā kāore koe e kite, e rongoā rānei. Mēnā kua pāngia tētahi o tō whānau e te aneurysm, e te wetewete rānei o te aorta, kōrero ki tō tākuta mō tō mōrearea. He nui ake te mōrearea o ētahi tāngata nā ngā āhuatanga ira, ngā mate ngakau whānau, ngā āhuatanga noho rānei pērā i te momi hikareti. Mā te noho i tētahi momo noho hauora mō te ngakau ka taea te whakaiti i tō mōrearea ki te aortopathy, ā, ka whakapakari i tō tinana katoa.Kia tiakina tō ngākau, nā te mea koia te pū o te manawa o tōu ao!

` Aoropathy, Aorta, Mate Manawa, Aneurysm, Wehenga Aorta, Ngā Mate Ira, Mamae Uma, Toto Toto Teitei, Momi hikareti, Hauora Manawa