He aha te Felty Syndrome? He mea nui tēnei mō te hunga e pāngia ana e te mate rumatiki!

Tērā pea ka pāngia koe e te mamae o ngā hononga, te pupuhi, me te paku pakari o ō waewae i te ata, tika? I te nuinga o te wā, ka puta pea ēnei i te mate rumatiki. Engari i mōhio koe he raruraru anō kei roto i tēnei mate rumatiki, engari kāore i te tino mōhiotia, engari he mea tino nui kia mōhiotia? Ko te Felty Syndrome tēnā. Me kōrero tātou mō tēnei i tēnei rā.

He aha rawa te mate Felty?

Ki te kī māmā noa, ko te Felty Syndrome he huinga o ngā āhuatanga e toru e puta tahi ana. Ko ēnei:

• Te mate rumatiki - He mumura hononga e mōhiotia ana e te tini o koutou.
• Neutropenia - He whakahekenga tēnei o te maha o ngā neutrophils, he momo toto mā i roto i te toto.
• Te whēkau nui – Ko te tikanga tēnei ka nui ake te whēkau nui, he okana o te tinana, i te mea noa.

He maha ngā wā ka tīmata i te rumatiki rheumatoid (RA). Ko ētahi atu āhuatanga e rua ka puta hei raruraru o te RA. Ka kiia ēnei e ngā tākuta he 'whakaaturanga extra-articular'. Arā, kāore te rumatiki e herea noa ki ngā hononga, engari ka pā ki ngā hononga i waho o aua hononga. Nā te tukanga mumura e puta ai te rumatiki tēnei. Ahakoa he mea noa te puta o ēnei momo pānga i waho o ngā hononga me te RA, he āhua onge te Felty Syndrome.

He aha te pānga o tēnei ki a koe?

Ka tīmata te mate a Felty me te Rheumatoid Arthritis. Kātahi ka pāngia koe e te mamae nui me te pupuhi i ō hononga. Kātahi, ina puta ngā āhuatanga pēnei i te Neutropenia me te Splenomegaly, ka pāngia tō pūnaha ārai mate . Ko te Neutropenia he whakahekenga i roto i tētahi momo toto ma e kiia nei ko te neutrophils. He momo pūtau tino nui ēnei neutrophils e tiaki ana i tō tātou tinana mai i ngā mate. Nō reira, ina heke iho, ka piki ake te tūponotanga o te whakawhanake i ngā mate. Ko te whēkau nui ake tētahi atu take mō tēnei whakahekenga o te neutrophils.

He pēhea te noa o tēnei āhuatanga?

E pā ana te mate a Felty ki te 2% o te hunga e pāngia ana e te mate rumatiki. Pērā i te RA, e toru ngā wā ka nui ake te kitea o te mate a Felty i roto i ngā wāhine i ngā tāne. He mea whakamīharo, tata ki te katoa o te hunga e pāngia ana e te mate a Felty he 'seropositive'. Ko te tikanga tēnei, e whakaū ana ngā whakamātautau kei roto i ō rātou toto tetahi mea e kiia nei ko ngā paturopi rheumatoid factor. Ko te hunga 'seronegative', arā, ko te hunga kāore i a rātou aua paturopi, he onge te pāngia e te mate a Felty.

He aha ngā tohu o tēnei?

He maha ngā wā, ko ngā tohu tuatahi ka puta ko ngā tohu o te rumatiki. Kei roto i ēnei:

• Mamae hononga
• Te pupuhi o ngā hononga
• Te pakari o ngā hononga, inā koa i te ata

Hei tauira, tera pea ka pāngia ētahi atu tāngata e ētahi atu tohu i tua atu i te RA i roto i ō rātou hononga.

• Ngā puku e puta mai ana i raro i te kiri e tata ana ki ngā hononga (e kiia ana ēnei he pona rheumatoid)
• Ngā kōpuku lymph pupuhi i ngā wāhi pēnei i te kaki me ngā kēkē
• Tērā pea ka pupuhi te ate, ā, ka mamae hoki ina pā atu.
• Ngā kanohi maroke me te waha (e kiia ana tēnei ko te mate Sjogren)
• He whero, he pupuhi ngā kanohi (e kiia ana tēnei ko te episcleritis)
• Ngā whara kiri, inā koa ki ngā waewae
• Ngā tohu o te toto i raro i te kiri
• Te uaua ki te manawa nā te pupuhi o ngā pukahukahu
• Te mamae o te uma nā te pupuhi huri noa i te ngākau
• Kirika
• Te ngenge me te mangere
• Te ngaronga o te hiahia kai, te ngaronga taumaha rānei e kore e whakamāramatia

Haunga ēnei, he tohu anō kei te Felty Syndrome. I ētahi wā ka puta mai ēnei tohu i mua i te tīmatanga o ngā tohu o te RA.

• Ngā mate pāwera auau, roa hoki. Hei tauira, ko te makariri, te mamae o te puku, me ngā mate kiri.
• Pupuhi te ate. Tērā pea ka pā ki te ringa, ā, ka mamae pea.
• Te rerekētanga o te kiri (pērā i ngā ira).

Engari ko te mea whakamiharo, i ētahi wā ka taea te tautuhi i a koe kei te mate koe i te Felty Syndrome, engari kāore he tohu. Mā ngā whakamātautau toto me ngā matawai ka taea te whakaatu kei a koe ngā mate e toru i mua i te rongonga i tētahi tohu.

I tehea tau ka tīmata tēnei?

Ko te Mate Felty ka puta i te hunga kaumātua, i waenga i te 50 me te 70 tau te pakeke. Mō te nuinga o te tangata, ka puta te Mate Felty i muri i te pāngia e ngā tohu o te rumatiki rheumatoid mō te 10 ki te 15 tau.

He aha i puta ai te mate Felty?

He 'mate pūnaha ārai mate' te mate rumatiki. Ko te tikanga o tēnei ka whakaekea e tō tātou ake pūnaha ārai mate ngā wāhanga o tō tātou ake tinana me te mea he hoariri. He tokomaha ngā kaipūtaiao e whakapono ana ko te Felty Syndrome he raruraru nui o te RA. I roto i ēnei mate pūnaha ārai mate, ka whakaputahia e ō tātou tinana he 'paturopi' hei ārai i ētahi pūmua. Ka haere ēnei paturopi ki te hopu i aua pūmua ka tohu kia whakangaromia. Koinei te pikinga o te mumura.

Kāore pea ēnei paturopi e kitea i ngā wā katoa i roto i te RA. Heoi, i roto i te hunga whai mate Felty Syndrome, e tino kitea ana ēnei paturopi. Ko te noho mai o ēnei paturopi te take e kaha ake ai te RA me te piki haere o ētahi atu pānga i waho o ngā hononga (ngā whakaaturanga i waho o te hononga). Ko te RA me ngā paturopi e kiia ana ko te 'seropositive RA'. E whakaatu ana ngā rangahau he hononga kei waenganui i te seropositive RA me te Felty Syndrome me ētahi 'āhuatanga ira'. Ko te tikanga ka taea te tuku iho i roto i ngā whakatipuranga ki tētahi taumata.

He aha te take e puta ai te neutropenia me te splenomegaly i te mate rumatiki (RA)?

Te Putanga o te Neutropenia

Ko te Neutropenia he whakahekenga o te maha o ngā toto toto mā e kiia nei ko ngā neutrophils. E rua ngā take matua mō tēnei. Ko tētahi, kāore tō hinu wheua e whakaputa ana i ngā neutrophils i te nui. Kei te whakangaromia rānei ngā neutrophils i roto i tō tinana. I roto i te Felty Syndrome, ka puta ēnei e rua. Ka taea e te tukanga ārai mate i whakahuatia i mua ake nei te whakararuraru i te whakaputanga o ngā neutrophils i roto i te hinu wheua, ā, ka taea hoki te whakangaro i ngā neutrophils kua hangaia kētia. Waihoki, ko te whēkau nui tētahi atu take mō te whakahekenga o ngā neutrophils.

Te Putanga o te Splenomegaly

Ko te mahi a tō whēkau he tātari i ngā pūtau toto tawhito, koretake hoki i roto i ō toto. Engari ina nui rawa tō whēkau (splenomegaly), ka nui rawa tana mahi, ā, ka tīmata te tango i te maha o ngā pūtau toto pai. I ētahi wā, ka nui ake te whēkau i te mate rumatiki. Kāore anō kia mārama te take tuturu. Ka nui ake hoki te whēkau me te kore he neutropenia. Waihoki, he tino onge, ka puta te Felty Syndrome me te kore he whēkau nui.

He aha ngā raruraru kino o te Felty Syndrome?

Nā te mea ka ngoikore tō pūnaha ārai mate e te Felty Syndrome, he nui ake tō tūponotanga ki te pāngia e ngā mate urutā maha, kino hoki . Ahakoa he mate iti noa iho tōu e ngāwari ana te rongoā, ka taea e tēnei mate te kino rawa atu, ā, ka roa pea, ka mōrearea hoki te ora i ētahi wā. Ka taea e ngā mate kitakita kāore e taea te whakahaere te arahi ki tētahi mate kino e kiia nei ko te sepsis. He nui ake hoki te tūponotanga o te hunga whai Felty Syndrome ki te pāngia e ētahi momo mate pukupuku, pērā i te lymphoma.

Kaua e wehi ina rongo koe i ēnei mea. Kei reira ēnei tūponotanga, engari ka taea te whakahaere mā te maimoatanga me te aro tika.

Me pēhea te mōhio ki tēnei?

Ka tātaritatia e ngā tākuta te Felty Syndrome ina kitea e rātou te mate rumatiki, te neutropenia, me te splenomegaly. (He onge te tātaritanga mēnā kāore he whēkau nui.)

Ko ngā whakamātautau e mahia ana i te nuinga o te wā ko:

• Ngā whakamātautau toto: He tatau toto katoa, hei tirotiro i te maha o ngā neutrophils.
• Ngā hihi-X o ngā hononga: Tirohia mēnā he mate rumatiki.
• Ngā matawai whatukuhu: Hei tauira, he matawai ultrasound, he matawai CT rānei.
• Te koiora wheua:Mā tēnei ka āwhina kia kore ai he atu āhuatanga hauora e pā mai.

He aha te rongoā mō tēnei?

E toru ngā whāinga matua mō te rongoā i te Felty Syndrome:

• Te whakahaere i te āhua taketake o te Rūmatoid Arthritis.
• Mena he kino rawa te neutropenia, me rongoā tika.
• Te ārai i ngā mate urutā me te rongoā i a rātou mēnā ka puta.

Tērā pea ka puta te Felty Syndrome i te mate rumatiki (RA) kāore i te rongoatia, kāore rānei i te tino whakahaeretia. Mō te tini o te tangata, ka pai ake te neutropenia i te pai ake o tā rātou RA. Nō reira, ka titiro tuatahi ngā tākuta ki te whiriwhiri i ngā rongoā whai hua hei ārai i te mate rumatiki (DMARD) mō te RA. Ka ngana hoki rātou ki te karo i ngā rongoā ārai mate i te mea ka taea.

He maha ngā momo DMARD ka taea te whakamahi mō te Felty Syndrome:

• Methotrexate me te waikawa folic (whakaiti i ngā pānga taha o te methotrexate)
• Abatacept
• Rituximab
• Leflunomide

Engari, ki te kore tō neutropenia e pai ake me ēnei DMARD, ki te tino kino rānei tō neutropenia, ki te mea rānei kua pāngia koe e te mate, ka whakamātau tō tākuta i ētahi atu maimoatanga hei whakanui ake i tō maha o ngā neutrophil. Kei roto pea i ēnei:

• He kano ārai mate e kiia nei ko te G-CSF (granulocyte colony-stimulating factor).
• Ngā rongoā corticosteroid wā poto.
• 'Te tango i te whēkau e kaha rawa ana te mahi' - Ko te tikanga tēnei mā te pokanga e tango.

Waihoki, ka mahi ngā tākuta i ngā mahi motuhake hei tiaki i a koe mai i ngā mate urutā, inā koa mēnā ka pā tō maimoatanga ki tō pūnaha ārai mate. Tērā pea ka tūtohu rātou i ngā mea pēnei i:

• Te tango i ngā paturopi whānui-whānui.
• Te whiwhi i ngā werohanga e tika ana.
• Kia aro nui ki te hauora o tō waha me ō niho.

Ki te pāngia tetahi tangata e te mate Felty Syndrome, ka tino aro nui ngā tākuta ki tēnei mate. Ki te pā tēnei ki a koe , me tere tonu te whiwhi maimoatanga . Ka tohua e tō tākuta he rongoā kaha.

He aha te roanga o te oranga mō te hunga e pāngia ana e te mate Felty Syndrome?

Kāore he tatauranga o nāianei mō te roanga o te oranga o te hunga e pāngia ana e te Mate Felty. Heoi, i te nuinga o te wā, kua tino pai ake ngā maimoatanga i ngā tau tata nei. Nō reira, he nui te tūponotanga ka angitu tetahi maimoatanga māu. Ko te mōrearea nui o te mate i roto i te Mate Felty kei te haere tonu mai i ngā mate kino . Nō reira, mā te mahi i ngā mahi hei tiaki i a koe mai i ngā mate ka nui te pānga ki tō hauora mō te wā roa.

He raruraru onge, ā, he maha ngā wā ka warewarehia te Felty Syndrome o te mate rumatiki (RA). Mēnā he roa tō mate RA kāore i te whakahaeretia, ki te kore rānei e mahi pai ō rongoā pērā i mua, ka pāngia pea koe e te Felty Syndrome. Ka pāngia ētahi tāngata e te mate kāore he tohu. He mea whakararuraru pea te mōhio ka pāngia hoki ō pūtau toto e te mate e pā ana ki ō hononga.

Mena kei te pāngia koe e te RA, me ētahi atu tohumate pea, ka uaua pea te kimi i tētahi tātaritanga hou. Engari kāore te Felty Syndrome e puta mai i ngā tohumate hou maha, ā, kāore pea e hiahiatia he maimoatanga tāpiri. Ko te mea nui kia mōhio koe ki ngā mōrearea. Mā te mahi tahi me tō tākuta ki te rongoā i tō RA me te ārai i ngā mate, ka taea e koe te whakahaere i te Felty Syndrome.

Hei whakamutunga, ngā mea hei maumahara

Ko te Felty Syndrome he āhuatanga ka pā ki ētahi tāngata e pangia ana e te mate rumatiki (RA). Ko tōna āhuatanga he hekenga o te maha o ngā toto mā e kiia nei ko ngā neutrophils i roto i ō toto (neutropenia) me te nui haere o te whēkau (splenomegaly).

• Ko te mōrearea matua ko te maha o ngā mate urutā, nō reira he mea tino nui kia tiakina koe i ngā mate urutā.
• Ahakoa he āhua whakamataku tēnei, ka taea te whakahaere pai i tēnei āhuatanga mā te maimoatanga hauora me ngā tohutohu tika .
• Mena kei a koe te RA, kia tūpato ki ēnei tohu tāpiri. Mena he āwangawanga āu , me kōrero ki tō tākuta. Ka taea e rātou te āwhina i a koe.

Te Mate Felty , te Rūmātiki, te Neutropenia, te Splenomegaly, te Rūmātiki, te Mumura o ngā Hononga, ngā Neutrophils, te Wāhanga, te Ārai Mate