He mamae noa iho ō wheua me ō hononga i ētahi wā? Kei te ahua rānei kei te nui haere tō mahunga, ā, kei te poto haere ō waewae i a koe e pakeke haere ana? Tērā pea ka whakaaro koe he wāhanga noa ēnei o te koroheketanga. Engari i muri i ēnei mea, tera pea he āhuatanga huna, kāore i te kōrerotia e kiia nei ko te 'Paget's Disease of the Bone'. He ingoa hou pea tēnei ki a koe. Engari he āhuatanga tēnei ka pā puku ki te hauora o ō tātou wheua. I tēnei rā, ka kōrerohia e tātou he mea ngāwari, i roto i te huarahi e mārama ai koe.
He aha te mate a Paget o te wheua?
Hei mārama ki tēnei, me titiro tuatahi tātou ki te mahi a ō tātou wheua. Ehara i te mea he mea kore ora noa iho ō tātou wheua. He kiko ora e whakahou tonu ana i a rātou anō, e tango ana i ngā pūtau tawhito, e hanga ana i ngā mea hou. Ka kiia tēnei tukanga he whakahoutanga wheua. He rite ki te wawahi i tētahi whare tawhito, ā, ka hanga he whare hou, he kaha ake i tōna wāhi. He mea tino nui tēnei hei pupuri i te kaha o ō tātou wheua.
Heoi, mō te tangata e pāngia ana e te mate wheua o Paget, ka hē rawa tēnei tukanga. Anei ngā mea ka tupu:
1. Te tere o te pakaru o te wheua tawhito: Ka tere ake te pakaru o ngā pūtau wheua tawhito i te tikanga.
2. Te hanganga koretake o te wheua hou: Ka tere te hanga e te tinana he wheua hou hei whakakī i te āputa. Heoi, he ngoikore, he koretake, he nui, he pakarukaru hoki te wheua hou e hangaia ana. He rerekē anō hoki tōna āhua.
He rite tonu ki te mea ka tupu ina ngana te kaitākaro pēhi mohio ki te mahi i tetahi mea i roto i te tere, ā, ka mahi tere te tangata kāore i te mōhio ki taua mea. Ahakoa ka hanga e koe he pakitara, ka totoro, ka ngoikore, ka pakaru wawe. Koinei te mea ka tupu ki ō tātou wheua i roto i tēnei mate. Nā tēnei , ka whati ngāwari ngā wheua (ngā whati) ā, he tino teitei te tūponotanga ka pāngia e te mate rumatiki (arthritis) . Ko tētahi atu ingoa mō tēnei mate ko `(Osteitis Deformans)`.
He mate pukupuku tēnei? Kaua e whakapoauautia ki tētahi atu 'mate a Paget'!
He raruraru tēnei e pā ana ki te tini tāngata. Ko ētahi e mataku ana nā te rite o te ingoa.
Kia mahara mārama: Ehara te mate a Paget o te wheua i te mate pukupuku.
Heoi anō, he mea iti tēnei me mōhio koe ki konei. He tino onge , arā, he iti rawa te tūponotanga ka puta te mate pukupuku wheua (`osteosarcoma`) i roto i te wheua e pāngia ana e te mate a Paget. Engari he mea nui kia mahara he tino onge tēnei.
He maha atu anō ngā mate e kiia nei ko ngā 'Paget', engari kāore he pānga ki tēnei mate wheua.
- Te mate a Paget o te ū: He momo mate pukupuku ū onge tēnei e puta ana i te rohe o te uma.
- Te mate a Paget o te vulva:He momo mate pukupuku kiri onge tēnei e puta ana i te taha o te waha o te tenetene i roto i ngā wāhine.
Nō reira, kia mārama koe, ahakoa he rite ngā ingoa o ēnei mate e toru, he rerekē rawa ēnei āhuatanga hauora e toru, kāore he pānga ki a rātou anō.
Ko wai kei te nui ake te mōrearea ki te whakawhanake i tēnei mate?
Kāore anō kia kitea e ngā kaipūtaiao te tino pūtake o tēnei mate, engari e whakaponohia ana nā te huinga o ngā āhuatanga ira , arā, ngā awe tuku iho, me ngā āhuatanga taiao i puta ai.
Kei te ripanga i raro nei ētahi o ngā tino take mōrearea e whai wāhi ana ki te whanaketanga o tēnei mate.
| Tauwehenga mōrearea | Whakaahuatanga |
|---|---|
| Tau | He nui ake te mōrearea o te hunga neke atu i te 50 tau te pakeke ki te pāngia e tēnei mate. Ka piki ake tēnei mōrearea i a rātou e pakeke haere ana. |
| Hītori Whānau | Mena kei tētahi o ō whanaunga tata (whaea, pāpā, tuākana/teina) tēnei mate, he nui ake te tūponotanga ka pāngia koe e taua mate anō hoki. |
| Takenga Whenua | He mea noa tēnei mate i waenga i te iwi o ngā whenua Pākehā, inā koa ngā whenua pēnei i a Ingarangi, Itari, me Pāniora. |
| Ira tangata | He nui ake te tūponotanga o ngā tāne ki te pāngia e tēnei mate i ngā wāhine. |
He aha ngā tohu o tēnei mate? Me pēhea te mōhio ki tēnei?
Ko te mea whakamiharo mō tēnei mate, he tokomaha te hunga kāore he tohu . He iti noa iho rānei ō rātou tohu, kāore he aha. Nā tēnei, he maha ngā wā ka kitea tūponotia tēnei mate ina mahia he whakamātautau hihi-X, he whakamātautau toto rānei mō tētahi atu take.
Heoi, ki te puta ngā tohu, ka rerekē pea i runga i te wheua e pāngia ana. Ko ngā tohu tino kitea ko:
- Mamae wheua, mamae hononga rānei: Koinei te tohu matua, te tohu tino kitea. Ka taea te rongo hei mamae hohonu, pumau i roto i te wheua e pāngia ana, i te hononga tata rānei.
- Te āhua o te wheua: I roto i te wā, ka rerekē pea te āhua o ngā wheua. Hei tauira, ki te pāngia te angaanga, ka nui haere pea te upoko, ki te pāngia rānei ngā waewae, ka piko pea ngā waewae.
- Ngā whati: Nā te ngoikore o ngā wheua hou, ka whati ngāwari ahakoa he hinganga iti, he aituā rānei.
- Te ānini me te ngaronga o te rongo: Mena ka pā te mate ki ngā wheua o te angaanga, ka taea e te matotoru o aua wheua te whakapōrearea i ngā io, te ānini, me te ngaronga o te rongo.
- Mamae tuara: Mena ka pāngia te tuaiwi, ka puta pea ngā tohu pēnei i te mamae tuara me te ngoikore o ngā waewae.
Me pēhea te tautuhi a te tākuta i tēnei mate?
E ai ki te kōrero i runga ake nei, he maha ngā wā ka kitea noa iho tēnei. Tērā pea ka tukuna koe e tō tākuta mō ēnei whakamātautau mēnā he tohu kei a koe, mēnā rānei he take kē atu e whakapaetia ai koe.
- Whakamātautau toto Alkaline Phosphatase (ALP): Koinei te whakamātautau tuatahi e whakaatu ana i tētahi tohu. Ka puta tēnei whākōkī e kiia nei ko te `ALP` i te wā e hangaia ana ngā pūtau wheua. I roto i te mate a Paget, nā te nui rawa o te tukanga hanganga wheua, he tino tiketike te taumata `ALP` i roto i te toto.
- Ngā hihi-X: Ko te huarahi pai ki te whakaū i te mate ko te whakamahi i te "hihi-X". Ka taea e ngā whakaahua "hihi-X" te wehewehe mārama i ngā wheua kua pāngia mai i ētahi atu wheua hauora. Ka taea e koe te kite i te pikinga o te matotoru me te rerekētanga o te āhua.
- Matawai Wheua: Ka mahia tēnei hei tirotiro ko ēhea ngā wheua o te tinana e pāngia ana e te mate, me tōna kaha. Ka werohia he iti o te tae irahiko ki roto i te uaua, ā, ka kitea ngā wāhi mate hei 'ira kanapa' ina matawaihia.
He aha ngā rongoā mō tēnei? Ka taea te whakaora katoa?
Tuatahi, ko te rongo pai. Kāore anō kia kitea he rongoā mō tēnei mate i tēnei wā . Kaua e manukanuka. He tino whai hua ngā maimoatanga hei whakaroa i te haere whakamua o te mate, hei whakahaere i ngā tohu, hei ārai hoki i ngā raruraru.
Ko te hunga anake e hiahiatia ana he maimoatanga e hiahiatia ana he tohumate, he hunga rānei kua pāngia e te mate ngā wāhi nui o te tinana pērā i te angaanga me te tuaiwi.
Rongoā
Ko te momo rongoā matua e whakamahia ana mō tēnei kaupapa ko ngā bisphosphonates . Ka whakahaere ēnei rongoā i te tukanga pakaru tere o te wheua.
- Koinei te rongoā tino whai hua me te whānui e whakamahia ana i roto i tēnei kāwai i tēnei wā.Zoledronate . He werohanga iti tēnei ('infusion') ka tukuna ki roto i te uaua. Mā te werohanga kotahi o tēnei rongoā, ka taea te whakahaere i te mate mō ngā tau.
- Engari kia maumahara, ka aukati noa ēnei rongoā i te horapa haere o te mate, engari kāore e taea te whakatika i ngā āhua rerekē o te wheua kua puta kē.
Pokanga
Me pokanga mō ngā raruraru i puta mai i te mate. Hei tauira:
- Mena he whati, whakatūria.
- Mena ka pakaru katoa tetahi hononga i te mate, me mahi he pokanga whakakapinga mo te hononga turi, te hononga hope rānei.
- Te whakatikatika anō i ngā wheua kua hē te tūnga.
- Ki te mea he ahotea kei roto i te io, whakaitihia taua pehanga.
Ko te wawe o te kitenga me te rongoā i tēnei mate, ko te wawe hoki o te ārai i ngā raruraru pēnei i te whati wheua me te rumatiki. Nō reira, he mea tino nui kia mōhio ki ngā tohu.
Karere Tangohia ki te Kāinga
- Ehara te Mate a Paget o te Wheua i te mate pukupuku, engari he mate mau tonu e ngoikore ai ngā wheua.
- He tokomaha te hunga kāore he tohu. Ko ngā tohu matua ko te mamae o te wheua, te āhua rerekē, me te whati ngāwari o te wheua.
- Ka taea te tautuhi ngāwari i te mate mā te whakamahi i ngā taumata teitei o te phosphatase kawakore i roto i te toto me ngā whakamātautau hihi-X .
- Ahakoa kāore e taea te whakaora katoa i te mate, ka taea te whakamahi i ngā rongoā pēnei i te bisphosphonates hei whakahaere tika i te mate me te ārai i ngā raruraru.
- Mena kua neke atu i te 50 tau te pakeke, he hītori whānau tōu kua pā ki tēnei mate, he mamae wheua rānei e pāngia ana e te mamae tonu, rerekē, kaua e warewaretia, engari me toro atu ki tō tākuta mō ētahi tohutohu.











💬 Comments (0)
Kaore ano kia tukuna he korero. Tāpirihia to korero ki konei mo te wa tuatahi.
Tāpirihia to korero