Whakaarohia kei te ngaro noa iho tō whakaaro, ā, i roto i te hēkona kotahi, ka pā mai te mamae upoko kino rawa atu i roto i tō ao... me te mea he uira e pā ana ki tō upoko. I roto i te rongoā, ka kiia tēnei he "Mate Ulo o te Whatiwhati". Koinei te tohu tino noa me te tino kino o te mate e kōrerohia ana e tātou i tēnei rā, arā, ko te RCVS. He āhuatanga ohorere hauora te mamae upoko pēnei me te hiahia kia tere te rongoā.
He aha te RCVS i te nuinga o te wā?
Ki te whakarapopototanga, ko te Reversible Cerebral Vasoconstriction Syndrome (RCVS) he āhuatanga e whakawhāiti ohorere ana, e aukati ana hoki i ngā oko toto o tō roro. He rite ki te paipa wai e pēhia ohoreretia ana. Ina aukatia ngā oko toto pēnei, kāore te roro e whiwhi i te nui o te toto e hiahiatia ana. Koinei te take e pāngia ai koe e te mamae o te upoko, pērā i te uira, i kōrerotia e au i mua ake nei.
Ko te kupu "whakahoki" i roto i te ingoa o tēnei mate, ko te tikanga ka taea te whakakore mā te maimoatanga tika . Heoi, ki te kore e rongoatia, ka arahi pea ki ngā mate kino pēnei i te whiu, te toto roro rānei. I ētahi wā, he tino rite ngā tohu ki ērā o te migraine, te whiu rānei, ā, he uaua ki te wehewehe i waenga i ngā mea e rua.
He mea tino nui: Ki te pāngia koe, tētahi atu rānei e mōhio ana koe e te ānini nui ohorere, ā, e rite ana ki te ānini kino rawa atu o tō rātou oranga, he āhuatanga ohorere hauora tēnā. Haere tonu ki te rūma ohorere o te hōhipera (ETU) tata rawa atu. Kaua e moumou taima.
He aha ngā tohu o tēnei mate?
Ko ngā tohu katoa o te RCVS i puta mai i te raruraru o te rere o te toto ki te roro. Me titiro tātou ki ēnei tohu.
| Tohu | He whakamārama māmā |
|---|---|
| Ngā mamae o te upoko | Ko te mamae upoko kino rawa atu tēnei i roto i tōku ao, ka tīmata ohorere mai. |
| Te aro ki te mārama me te tangi | Te āhua o te kore e taea te titiro ki te mārama, te rongo rānei i ngā oro (Photophobia me te Phonophobia) |
| Whakapairuaki me te ruaki | Te mamae o te upoko me te ruaki. |
| Ngā huringa tirohanga | Te tirohanga pōuri, te tirohanga takirua, te tirohanga ngoikore rānei. |
| ngoikore o te uaua | Te ahua o te ngoikore i tetahi taha o te tinana. |
| Pōhēhētanga | Te warewaretanga ki te wāhi me te wā, te ngaronga o te māramatanga. |
| Ngā mate hopuhopu | He āhua tau. |
| Ngā uauatanga kōrero (Aphasia) | Te uaua ki te kōrero, te uaua rānei ki te mārama ki ngā kōrero a ētahi atu. |
| Ngā tohu tāpiri ka puta mai i te toto ki roto i te roro (Subarachnoid Hemorrhage - SAH) | |
| Te pakari o te kaki | Te pakari o ngā uaua me te mamae o te kaki me ngā pakihiwi. |
| Ngā huringa whanonga | Te riri ohorere, te pukuriri. |
| Te ngoikore o te tinana | Te rongo i te ngau kino i tētahi wāhanga o te tinana. |
He aha ngā take o te RCVS?
Kei roto i ō tātou uaua toto he paparanga uaua maeneene. Mā ēnei uaua e whakahaere te rere o te toto mā te whakawhāiti me te whakangā. Engari i ētahi wā ka ohorere te pupuhi o ēnei uaua, ka tino piri rawa. Ka kiia tēnei ko te "vasospasm". Koinei te tino take o te RCVS.
He maha ngā take ka puta ai tēnei āhuatanga (vasospasm).
Te haputanga me te wā i muri i te whānautanga
Ko te tino take o te RCVS ko te hāputanga. Ko te mōrearea o tēnei mate ka tino teitei i roto i ngā wiki tuatahi e ono i muri i te whānautanga. E whakaponohia ana nā ngā huringa ohorere o ngā taumata homoni tēnei. Ka puta pea tēnei mōrearea ahakoa kāore koe e pāngia e ngā mate pēnei i te preeclampsia i te wā e hāpu ana.
Ko ētahi rongoā me te whakamahinga o ngā raau taero
Ka pā pea te RCVS i ētahi rongoā me ngā rongoā e pā ana ki tō pūnaha tohanga toto.
- Ko ētahi rongoā mō te pouri, inā koa ko ērā kei roto i te rōpū SSRI.
- Ngā rongoā mō te migraine (ngā triptan me ngā rongoā momo-ergot).
- Ngā rongoā pehi ārai mate.
- Ko ētahi rongoā mō te mate a Parkinson.
- Ngā rongoā whakaohooho (amphetamines, cocaine, pseudoephedrine).
- Te tarukino.
- Te nui rawa o te kawheine me ngā inu pūngao.
- Ngā pāreti nikotīni.
- Ngā raau taero pēnei i te `LSD` me te `MDMA` (ecstasy).
Ētahi atu āhuatanga hauora
Ka taea hoki e ētahi āhuatanga hauora e pā ana ki te roro, ki te tohanga toto rānei te whakanui ake i te mōrearea o te RCVS.
- Ngā maikurīni: Ko te hunga whai maikurīni ka nui ake te tūponotanga ka pāngia e te RCVS.
- Te nui o te konupūmā i roto i te toto (Hypercalcemia): Ka taea e te nui o te konupūmā te whakararuraru i te mahi a ngā uaua i roto i ngā oko toto.
- Ngā take homoni: E whakapaetia ana ko te homoni estrogen te take, koia te take e nui ake ai te kitea o tēnei mate i roto i ngā wāhine.
- Ka piki ake pea te mōrearea e ētahi āhuatanga tuku iho, pērā i te "Pheochromocytoma" (he pukupuku e whakaputa ana i te homoni adrenaline nui rawa) me te "Porphyria".
He aha ngā raruraru pea ka pā mai i te RCVS?
I mua, i whakaaro ngā tākuta ehara te RCVS i te mate kino. Engari e whakaatu ana ngā rangahau hou ka pā mai he raruraru i ētahi wā. Tata ki te 30% o te hunga whai RCVS ka mahue pea me ētahi hauātanga iti tuturu (pērā i te ngoikore o te uaua). Tata ki te 8% ka pāngia e ngā raruraru kino mō te wā roa.
Hei tāpiritanga, ka puta pea ngā raruraru nui pēnei i ēnei i roto i ngā rā torutoru i muri i te putanga mai o ngā tohu tuatahi:
- Te whiu ischemic: Te aukati i te oko toto e tuku toto ana ki te roro.
- Te toto i roto i te roro (te toto SAH, tētahi atu momo toto roro rānei): Te toto i waenganui i te roro me te angaanga.
- Ngā hopukanga.
Me pēhea te kitenga a ngā tākuta i tēnei?
He maha ngā tikanga e whakamahia ana e te tākuta hei tātaritanga i tēnei mate.
- He whakamātautau tinana me te whakamātautau io: Ka tirohia ō urupare, kaha, me ō kare ā-roto.
- Ngā whakamātautau toto: Tirohia mēnā he raruraru toto totoka, he mate pāwera, me te kore taurite o ngā taumata tote.
- Ngā matawai whakaahua: Koinei te huarahi tino nui hei tautuhi i te RCVS.
Ngā matawai whakaahua
Ka taea e ēnei momo matawai te "kite" i te roto o te upoko me te roro. Ka taea e rātou te tirotiro mēnā he oko toto kua āraia, he iti rānei te rere o te toto.
- Ngā matawai Tomography Computed (CT): Ina koa, ka taea e ngā angiogram CT te āwhina ki te aromatawai pai ake i te āhua o ngā uaua toto.
- Ngā matawai Whakaahua Āhuatanga Aukume (MRI): Ka taea hoki e tētahi matawai MRI motuhake e kiia nei ko te Angiogram Āhuatanga Aukume (MRA) te kite i te vasospasm i roto i ngā oko toto.
- Te ine i te tere o te rere o te toto i roto i te roro mā te whakamahi i te Doppler ultrasound Transcranial: Ka taea e tēnei te ine i te tere o te rere o te toto i roto i te roro.
I te nuinga o te wā, ka mahia tuatahitia he matawai CT. Nā te mea he tere. Ka taea te whakatau wawe mēnā he āhuatanga ohorere pēnei i te whiu, te toto rānei. I roto i te whiu, he mea nui ia hēkona, nō reira he mea tino nui taua tere. Kātahi, ki te tika, ka mahia he matawai MRI hei whakaū anō i te aukati i roto i ngā oko toto.
He aha ngā maimoatanga mō te RCVS?
E ai ki te ingoa, he mate tino ngāwari te rongoā i te RCVS. E rua ngā whāinga matua o te maimoatanga.
1. Mena ka kitea he take (hei tauira, he rongoā), tangohia taua take.
2. Hei whakaora i te vasospasm (te whakawhāiti) o ngā oko toto, me te whakahoki anō i a rātou ki te āhua noa.
Ko te momo rongoā e whakamahia whānuitia ana hei rongoā i tēnei mate (vasospasm) ko ngā aukati hongere konupūmā (CCB) . Mā ēnei rongoā ka aukati i te konupūmā kia kaua e uru ki ngā pūtau uaua i roto i ngā oko toto. Kātahi ka whakangāwari ngā uaua, ka whānui anō ngā oko toto, ā, ka hoki te rere o te toto ki te āhua noa.
He tino onge, i ētahi wā, ka taea te whakamahi i tētahi tikanga e kiia nei ko te "endovascular". Ko te whakauru i tētahi ngongo tino angiangi (catheter) mā roto i tētahi oko toto i te ringa, i te waewae rānei ki te oko toto kua āraia i te roro, kātahi ka werohia he rongoā, ka whakamahia rānei tētahi mea pēnei i te poihau hei whakawhanui i te oko toto (angioplasty).
Me pēhea tātou e tumanako ai mō tēnei āhuatanga?
Ko te nuinga o te hunga whai RCVS (tata ki te 80% - 85%) ka ora katoa, kāore he raruraru mō te wā roa. Nō reira, he pai te tumanako mō tēnei. Engari ko te mea nui ko te tautuhi wawe i te mate me te tīmata i te maimoatanga tika.
Kia maumahara, ko te tātaritanga me te maimoatanga wawe te huarahi pai ki te whakatutuki i ngā hua pai rawa atu. Ka taea e ngā whakaroa te arahi ki ngā raruraru kino.
Ngā mea ka taea e koe te mahi hei ārai i te hokinga mai o te RCVS
Nā te mea kāore i te tino mārama te take e whanake ai te RCVS, kāore e taea te ārai i ngā wā katoa. Heoi anō, tera ētahi mea ka taea e koe te mahi hei whakaiti i tō mōrearea. Ka hoatu e tō tākuta ētahi atu tohutohu mō tēnei.
- Mena kei te whakaarohia he rongoā i puta ai te RCVS, katihia, ā, karohia hoki ā muri ake nei.
- Te tango i ngā rongoā i tohua e te tākuta kia rite ki te whakahau me te tika.
- Kaua e whakamahi i tētahi rongoā, i tētahi tarukino rānei (ina koa ko ngā mea whakaohooho me te tarukino) me te kore he tohutohu hauora.
- Whakaitihia, kati rawatia rānei te inu kawheine me ngā inu pūngao.
Āhea koe me toro atu ki te tākuta, me te haere ki te ETU?
Mena kei a koe te RCVS, ka kī atu tō tākuta kia haere tonu koe ki te whare hauora. He mea nui kia haere tonu koe ki ēnei wā tirotiro. Mā tēnei, ka taea te aroturuki i tō āhua, ā, ka taea te whakarerekē i tō maimoatanga ina hiahiatia.
Āhea me haere tonu ki te Wāhanga Maimoatanga Ohotata (ETU):
Ki te pāngia koe e te ānini nui, e ngā tohumate pērā i te whiu (hei tauira, te ngoikore o te taha kotahi o te tinana, te uaua ki te kōrero, te panoni o te tirohanga), he āhuatanga ohorere hauora tonu tēnā. Kaua e tatari kia roa rawa. Haere ki te hōhipera i te wā e taea ai.
Karere Tangohia ki te Kāinga
- He āhuatanga ohorere hauora te ānini nui ohorere ("Ānini Pakū"). Haere tonu ki te Tari Ohorere o te hōhipera tata (ETU).
- He mate te RCVS i puta mai i te aukati ohorere o ngā oko toto i roto i te roro. Engari e ai ki te ingoa, he mate tino whakaora tēnei me te maimoatanga tika.
- He nui ake te mōrearea o tēnei mate i te wā e hapu ana, inā koa i ngā wiki tuatahi e ono i muri i te whānautanga.
- Ka ora katoa te nuinga o te tangata, kāore he raruraru mō te wā roa, engari he mea nui te tautuhi me te maimoatanga wawe.
- Whāia ngā tohutohu a tō tākuta. Tangohia ngā rongoā kua tohua, ā, karohia ngā raau taero me te waipiro mōrearea.











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